ICD 10 || Tabular list of inclusions and four-character subcategories || CHAPTER I Certain infectious and parasitic diseases (A00–B99) - CHAPTER XI Diseases of the digestive system (K00–K93)

CHAPTER I

Certain infectious and parasitic diseases (A00–B99)

Incl.: diseases generally recognized as communicable or transmissible

Use additional code (U82–U84), if desired, to identify resistance to antimicrobial drugs.

Excl.: carrier or suspected carrier of infectious disease (Z22.-) certain localized infections – see body system-related chapters

infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium [except obstetrical tetanus] (O98.-)

infectious and parasitic diseases specific to the perinatal period [except tetanus neonatorum, congenital syphilis, perinatal gonococcal infection and perinatal human immunodeficiency virus [HIV] disease] (P35–P39) influenza and other acute respiratory infections (J00–J22)

This chapter contains the following blocks:

A00–A09 Intestinal infectious diseases A15–A19 Tuberculosis

A20–A28 Certain zoonotic bacterial diseases A30–A49 Other bacterial diseases

A50–A64 Infections with a predominantly sexual mode of transmission A65–A69 Other spirochaetal diseases

A70–A74 Other diseases caused by chlamydiae A75–A79 Rickettsioses

A80–A89 Viral infections of the central nervous system

A90–A99   Arthropod-borne viral fevers and viral haemorrhagic fevers B00–B09 Viral infections characterized by skin and mucous membrane lesions B15–B19 Viral hepatitis

B20–B24 Human immunodeficiency virus [HIV] disease B25–B34 Other viral diseases

B35–B49   Mycoses B50–B64 Protozoal diseases B65–B83 Helminthiases

B85–B89 Pediculosis, acariasis and other infestations B90–B94 Sequelae of infectious and parasitic diseases B95–B98 Bacterial, viral and other infectious agents B99–B99 Other infectious diseases

ntestinal infectious diseases (A00–A09)

  A00 Cholera

A00.0 Cholera due to Vibrio cholerae 01, biovar cholerae

Classical cholera

A00.1 Cholera due to Vibrio cholerae 01, biovar eltor

Cholera eltor

A00.9 Cholera, unspecified

  A01 Typhoid and paratyphoid fevers

A01.0 Typhoid fever

Infection due to Salmonella typhi

A01.1 Paratyphoid fever A A01.2 Paratyphoid fever B A01.3 Paratyphoid fever C

A01.4 Paratyphoid fever, unspecified

Infection due to Salmonella paratyphi NOS

  A02 Other Salmonella infections

Incl.: infection or foodborne intoxication due to any Salmonella species other than S. typhi and S. paratyphi

A02.0 Salmonella enteritis

Salmonellosis

A02.1 Salmonella sepsis

A02.2 Localized Salmonella infections

Salmonella:

• arthritis† (M01.3*)

• meningitis† (G01*)

• osteomyelitis† (M90.2*)

• pneumonia† (J17.0*)

• renal tubulo-interstitial disease† (N16.0*) A02.8 Other specified Salmonella infections A02.9 Salmonella infection, unspecified

  A03 Shigellosis

A03.0 Shigellosis due to Shigella dysenteriae

Group A shigellosis [Shiga–Kruse dysentery]

A03.1 Shigellosis due to Shigella flexneri

Group B shigellosis

A03.2 Shigellosis due to Shigella boydii

Group C shigellosis

A03.3 Shigellosis due to Shigella sonnei

Group D shigellosis

A03.8 Other shigellosis

A03.9 Shigellosis, unspecified

Bacillary dysentery NOS

  A04 Other bacterial intestinal infection

Excl.: foodborne intoxications elsewhere classified tuberculous enteritis (A18.3)

A04.0 Enteropathogenic Escherichia coli infection A04.1 Enterotoxigenic Escherichia coli infection A04.2 Enteroinvasive Escherichia coli infection A04.3 Enterohaemorrhagic Escherichia coli infection A04.4 Other intestinal Escherichia coli infections

Escherichia coli enteritis NOS

A04.5 Campylobacter enteritis

A04.6 Enteritis due to Yersinia enterocolitica

Excl.: extraintestinal yersiniosis (A28.2)

A04.7 Enterocolitis due to Clostridium difficile Foodborne intoxication by Clostridium difficile Pseudomembranous colitis

A04.8 Other specified bacterial intestinal infections A04.9 Bacterial intestinal infection, unspecified

Bacterial enteritis NOS

  A05 Other bacterial foodborne intoxications, not elsewhere classified

Excl.: Clostridium difficile foodborne intoxication and infection (A04.7)

Escherichia coli infection (A04.0–A04.4) listeriosis (A32.-)

Salmonella foodborne intoxication and infection (A02.-) toxic effect of noxious foodstuffs (T61–T62)

A05.0 Foodborne staphylococcal intoxication A05.1 Botulism

Classical foodborne intoxication due to Clostridium botulinum

A05.2 Foodborne Clostridium perfringens [Clostridium welchii] intoxication

Enteritis necroticans Pig-bel

A05.3 Foodborne Vibrio parahaemolyticus intoxication A05.4 Foodborne Bacillus cereus intoxication

A05.8 Other specified bacterial foodborne intoxications A05.9 Bacterial foodborne intoxication, unspecified

  A06 Amoebiasis

Incl.: infection due to Entamoeba histolytica

Excl.: other protozoal intestinal diseases (A07.-)

A06.0 Acute amoebic dysentery

Acute amoebiasis Intestinal amoebiasis NOS

A06.1 Chronic intestinal amoebiasis A06.2 Amoebic nondysenteric colitis

A06.3 Amoeboma of intestine

Amoeboma NOS

A06.4† Amoebic liver abscess (K77.0*)

Hepatic amoebiasis

A06.5† Amoebic lung abscess (J99.8*)

Amoebic abscess of lung (and liver)

A06.6† Amoebic brain abscess (G07*)

Amoebic abscess of brain (and liver)(and lung)

A06.7 Cutaneous amoebiasis

A06.8 Amoebic infection of other sites

Amoebic:

• appendicitis

• balanitis† (N51.2*)

A06.9 Amoebiasis, unspecified

  A07 Other protozoal intestinal diseases

A07.0 Balantidiasis

Balantidial dysentery A07.1 Giardiasis [lambliasis] A07.2 Cryptosporidiosis

A07.3 Isosporiasis

Infection due to Isospora belli and Isospora hominis

Intestinal coccidiosis Isosporosis

A07.8 Other specified protozoal intestinal diseases

Intestinal trichomoniasis Sarcocystosis Sarcosporidiosis

A07.9 Protozoal intestinal disease, unspecified

Flagellate diarrhoea Protozoal:

• colitis

• diarrhoea

• dysentery

  A08 Viral and other specified intestinal infections

Excl.: influenza with involvement of gastrointestinal tract (J09, J10.8, J11.8)

A08.0 Rotaviral enteritis

A08.1 Acute gastroenteropathy due to Norwalk agent

Small round structured virus enteritis

A08.2 Adenoviral enteritis A08.3 Other viral enteritis

A08.4 Viral intestinal infection, unspecified

Viral:

• enteritis NOS

• gastroenteritis NOS

• gastroenteropathy NOS

A08.5 Other specified intestinal infections

 A09 Other gastroenteritis and colitis of infectious and unspecified origin

Excl.: due to bacterial, protozoal, viral and other specified infectious agents (A00–A08)

noninfective (see noninfectious) diarrhoea (K52.9) noninfective (see noninfectious) diarrhoea:

• neonatal (P78.3)

A09.0 Other and unspecified gastroenteritis and colitis of infectious origin

Catarrh, enteric or intestinal Diarrhoea:

• acute bloody

• acute haemorrhagic

• acute watery

• dysenteric

• epidemic Infectious or septic:

Infectious diarrhoea NOS

A09.9 Gastroenteritis and colitis of unspecified origin

Incl.: Neonatal diarrhoea NOS

Tuberculosis (A15–A19)

Incl.: infections due to Mycobacterium tuberculosis and Mycobacterium bovis

Excl.: congenital tuberculosis (P37.0)

human immunodeficieny [HIV] disease resulting in tuberculosis (B20.0) pneumoconiosis associated with tuberculosis (J65)

sequelae of tuberculosis (B90.-) silicotuberculosis (J65)

  A15 Respiratory tuberculosis, bacteriologically and histologically confirmed

A15.0 Tuberculosis of lung, confirmed by sputum microscopy with or without culture

Tuberculous:

• bronchiectasis

• fibrosis of lung

• pneumonia

• pneumothorax

confirmed by sputum microscopy with or without culture

A15.1 Tuberculosis of lung, confirmed by culture only

Conditions listed in A15.0, confirmed by culture only

A15.2 Tuberculosis of lung, confirmed histologically

Conditions listed in A15.0, confirmed histologically

A15.3 Tuberculosis of lung, confirmed by unspecified means Conditions listed in A15.0, confirmed but unspecified whether bacteriologically or histologically

A15.4 Tuberculosis of intrathoracic lymph nodes, confirmed bacteriologically and histologically

Tuberculosis of lymph nodes:

• hilar

• mediastinal

• tracheobronchial

confirmed bacteriologically and histologically

Excl.: specified as primary (A15.7)

A15.5 Tuberculosis of larynx, trachea and bronchus, confirmed bacteriologically and histologically

Tuberculosis of:

• bronchus

• glottis

• larynx

• trachea

confirmed bacteriologically and histologically

 

A15.6 Tuberculous pleurisy, confirmed bacteriologically and histologically

Tuberculosis of pleura Tuberculous empyema confirmed bacteriologically and histologically

Excl.: in primary respiratory tuberculosis, confirmed bacteriologically and histologically (A15.7)

A15.7 Primary respiratory tuberculosis, confirmed bacteriologically and histologically

A15.8 Other respiratory tuberculosis, confirmed bacteriologically and histologically

Mediastinal tuberculosis Nasopharyngeal tuberculosis Tuberculosis of:

• nose

• sinus [any nasal]

confirmed bacteriologically and histologically

A15.9 Respiratory tuberculosis unspecified, confirmed bacteriologically and histologically

  A16 Respiratory tuberculosis, not confirmed bacteriologically or histologically

A16.0 Tuberculosis of lung, bacteriologically and histologically negative

Tuberculous:

• bronchiectasis

• fibrosis of lung

• pneumonia

• pneumothorax

bacteriologically and histologically

A16.1 Tuberculosis of lung, bacteriological and histological examination not done

Conditions listed in A16.0, bacteriological and histological examination not done

A16.2 Tuberculosis of lung, without mention of bacteriological or histological confirmation

Tuberculosis of lung Tuberculous:

• bronchiectasis

• fibrosis of lung

• pneumonia

• pneumothorax

NOS (without mention of bacteriological or histological confirmation)

 

A16.3 Tuberculosis of intrathoracic lymph nodes, without mention of bacteriological or histological confirmation

Tuberculosis of lymph nodes:

• hilar

• intrathoracic

• mediastinal

• tracheobronchial

NOS (without mention of bacteriological or histological confirmation)

Excl.: when specified as primary (A16.7)

A16.4 Tuberculosis of larynx, trachea and bronchus, without mention of bacteriological or histological confirmation

Tuberculosis of:

• bronchus

• glottis

• larynx

• trachea

NOS (without mention of bacteriological or histological confirmation)

A16.5 Tuberculous pleurisy, without mention of bacteriological or histological confirmation

Tuberculosis of pleura Tuberculous:

• empyema

• pleurisy NOS (without mention of bacteriological or histological confirmation)

Excl.: in primary respiratory tuberculosis (A16.7)

A16.7 Primary respiratory tuberculosis without mention of bacteriological or histological confirmation

Primary:

• respiratory tuberculosis NOS

• tuberculous complex

A16.8 Other respiratory tuberculosis, without mention of bacteriological or histological confirmation

Mediastinal tuberculosis Nasopharyngeal tuberculosis Tuberculosis of:

• nose

• sinus [any nasal]

NOS (without mention of bacteriological or histological confirmation)

A16.9 Respiratory tuberculosis unspecified, without mention of bacteriological or histological confirmation

Respiratory tuberculosis NOS Tuberculosis NOS

 

  A17† Tuberculosis of nervous system

A17.0† Tuberculous meningitis (G01*) Tuberculosis of meninges (cerebral)(spinal) Tuberculous leptomeningitis

A17.1† Meningeal tuberculoma (G07*)

Tuberculoma of meninges

A17.8† Other tuberculosis of nervous system

Tuberculoma Tuberculosis of brain (G07*) spinal cord (G07*)

Tuberculous:

• abscess of brain (G07*)

• meningoencephalitis (G05.0*)

• myelitis (G05.0*)

• polyneuropathy (G63.0*)

A17.9† Tuberculosis of nervous system, unspecified (G99.8*)

  A18 Tuberculosis of other organs

A18.0† Tuberculosis of bones and joints

Tuberculosis of:

• hip (M01.1*)

• knee (M01.1*)

• vertebral column (M49.0*) Tuberculous:

• arthritis (M01.1*)

• mastoiditis (H75.0*)

• necrosis of bone (M90.0*)

• osteitis (M90.0*)

• osteomyelitis (M90.0*)

• synovitis (M68.0*)

• tenosynovitis (M68.0*)

A18.1† Tuberculosis of genitourinary system

Tuberculosis of:

• bladder (N33.0*)

• cervix (N74.0*)

• kidney (N29.1*)

• male genital organs (N51.-*)

• ureter (N29.1*)

Tuberculous female pelvic inflammatory disease (N74.1*)

A18.2 Tuberculous peripheral lymphadenopathy

Tuberculous adenitis

Excl.: tuberculosis of lymph nodes:

• intrathoracic (A15.4, A16.3)

• mesenteric and retroperitoneal (A18.3)

tuberculous tracheobronchial adenopathy (A15.4, A16.3)

 

A18.3 Tuberculosis of intestines, peritoneum and mesenteric glands

Tuberculosis (of):

• anus and rectum† (K93.0*)

• intestine (large)(small)† (K93.0*)

• retroperitoneal (lymph nodes) Tuberculous:

• ascites

• enteritis† (K93.0*)

• peritonitis† (K67.3*)

A18.4 Tuberculosis of skin and subcutaneous tissue

Erythema induratum, tuberculous Lupus:

• exedens

• vulgaris:

– NOS

– of eyelid† (H03.1*) Scrofuloderma

Excl.: lupus erythematosus (L93.-) lupus erythematosus

• systemic (M32.-)

A18.5 Tuberculosis of eye

Tuberculous:

• chorioretinitis† (H32.0*)

• episcleritis† (H19.0*)

• interstitial keratitis† (H19.2*)

• iridocyclitis† (H22.0*)

• keratoconjunctivitis (interstitial)(phlyctenular)† (H19.2*)

Excl.: lupus vulgaris of eyelid (A18.4)

A18.6 Tuberculosis of ear

Tuberculous otitis media† (H67.0*)

Excl.: tuberculous mastoiditis (A18.0†)

A18.7† Tuberculosis of adrenal glands (E35.1*)

Addison disease, tuberculous

A18.8 Tuberculosis of other specified organs

Tuberculosis of:

• endocardium† (I39.8*)

• myocardium† (I41.0*)

• oesophagus† (K23.0*)

• pericardium† (I32.0*)

• thyroid gland† (E35.0*)

Tuberculous cerebral arteritis† (I68.1*)

 

  A19 Miliary tuberculosis

Incl.: tuberculosis:

• disseminated

• generalized tuberculous polyserositis

A19.0 Acute miliary tuberculosis of a single specified site A19.1 Acute miliary tuberculosis of multiple sites

A19.2 Acute miliary tuberculosis, unspecified A19.8 Other miliary tuberculosis

A19.9 Miliary tuberculosis, unspecified

Certain zoonotic bacterial diseases (A20–A28)

  A20 Plague

Incl.: infection due to Yersinia pestis

A20.0 Bubonic plague

A20.1 Cellulocutaneous plague A20.2 Pneumonic  plague A20.3 Plague meningitis

A20.7 Septicaemic plague

A20.8 Other forms of plague

Abortive plague Asymptomatic plague Pestis minor

A20.9 Plague, unspecified

  A21 Tularaemia

Incl.: deer-fly fever

infection due to Francisella tularensis

rabbit fever

A21.0 Ulceroglandular tularaemia A21.1 Oculoglandular tularaemia

Ophthalmic tularaemia

A21.2 Pulmonary tularaemia A21.3 Gastrointestinal tularaemia

Abdominal tularaemia

 

A21.7 Generalized tularaemia A21.8 Other forms of tularaemia A21.9 Tularaemia, unspecified

  A22 Anthrax

Incl.: infection due to Bacillus anthracis

A22.0 Cutaneous anthrax

Malignant:

• carbuncle

• pustule

A22.1 Pulmonary anthrax

Inhalation anthrax Ragpicker’s disease Woolsorter’s disease

A22.2 Gastrointestinal anthrax A22.7 Anthrax sepsis

A22.8 Other forms of anthrax

Anthrax meningitis† (G01*)

A22.9 Anthrax, unspecified

  A23 Brucellosis

Incl.: fever:

• Malta

• Mediterranean

• undulant

A23.0 Brucellosis due to Brucella melitensis A23.1 Brucellosis due to Brucella abortus A23.2 Brucellosis due to Brucella suis A23.3 Brucellosis due to Brucella canis A23.8 Other brucellosis

A23.9 Brucellosis, unspecified

  A24 Glanders and melioidosis

A24.0 Glanders

Infection due to Pseudomonas mallei Infection due to Burkholderia mallei Malleus

A24.1 Acute and fulminating melioidosis

Melioidosis:

• pneumonia

• sepsis

 

A24.2 Subacute and chronic melioidosis A24.3 Other melioidosis

A24.4 Melioidosis, unspecified

Infection due to Pseudomonas pseudomallei NOS Infection due to Burkholderia pseudomallei NOS Whitmore’s disease

  A25 Rat-bite fevers

A25.0 Spirillosis

Sodoku

A25.1 Streptobacillosis

Epidemic arthritic erythema Haverhill fever Streptobacillary rat-bite fever

A25.9 Rat-bite fever, unspecified

  A26 Erysipeloid

A26.0 Cutaneous erysipeloid

Erythema migrans

A26.7 Erysipelothrix sepsis A26.8 Other forms of erysipeloid A26.9 Erysipeloid, unspecified

  A27 Leptospirosis

A27.0 Leptospirosis icterohaemorrhagica

Leptospirosis due to Leptospira interrogans serovar icterohaemorrhagiae

A27.8 Other forms of leptospirosis A27.9 Leptospirosis, unspecified

  A28 Other zoonotic bacterial diseases, not elsewhere classified

A28.0 Pasteurellosis A28.1 Cat-scratch disease

Cat-scratch fever

A28.2 Extraintestinal yersiniosis

Excl.: enteritis due to Yersinia enterocolitica (A04.6) plague (A20.-)

A28.8 Other specified zoonotic bacterial diseases, not elsewhere classified

A28.9 Zoonotic bacterial disease, unspecified

 

Other bacterial diseases (A30–A49)

  A30 Leprosy [Hansen disease]

Incl.: infection due to Mycobacterium leprae

Excl.: sequelae of leprosy (B92)

A30.0 Indeterminate leprosy

I leprosy

A30.1 Tuberculoid leprosy

TT leprosy

A30.2 Borderline tuberculoid leprosy

BT leprosy

A30.3 Borderline leprosy

BB leprosy

A30.4 Borderline lepromatous leprosy

BL leprosy

A30.5 Lepromatous leprosy

LL leprosy

A30.8 Other forms of leprosy A30.9 Leprosy, unspecified

  A31 Infection due to other mycobacteria

Excl.: leprosy (A30.-)

tuberculosis (A15–A19)

A31.0 Pulmonary mycobacterial infection

Infection due to Mycobacterium:

• avium

• intracellulare [Battey bacillus]

• kansasii

A31.1 Cutaneous mycobacterial infection

Buruli ulcer

Infection due to Mycobacterium:

• marinum

• ulcerans

A31.8 Other mycobacterial infections A31.9 Mycobacterial infection, unspecified

Atypical Mycobacterium infection NOS

Mycobacteriosis NOS

 

  A32 Listeriosis

Incl.: listerial foodborne infection

Excl.: neonatal (disseminated) listeriosis (P37.2)

A32.0 Cutaneous listeriosis

A32.1† Listerial meningitis and meningoencephalitis

Listerial:

• meningitis (G01*)

• meningoencephalitis (G05.0*)

A32.7 Listerial sepsis

A32.8 Other forms of listeriosis

Listerial:

• cerebral arteritis† (I68.1*)

• endocarditis† (I39.8*) Oculoglandular listeriosis

A32.9 Listeriosis, unspecified

  A33 Tetanus neonatorum

  A34 Obstetrical tetanus

  A35 Other tetanus

Incl.: tetanus NOS

Excl.: tetanus:

• neonatorum (A33)

• obstetrical (A34)

  A36 Diphtheria

A36.0 Pharyngeal diphtheria

Diphtheritic membranous angina Tonsillar diphtheria

A36.1 Nasopharyngeal diphtheria A36.2 Laryngeal diphtheria

Diphtheritic laryngotracheitis

A36.3 Cutaneous diphtheria

Excl.: erythrasma (L08.1)

A36.8 Other diphtheria

Diphtheritic:

• conjunctivitis† (H13.1*)

• myocarditis† (I41.0*)

• polyneuritis† (G63.0*)

A36.9 Diphtheria, unspecified

 

  A37 Whooping cough

A37.0 Whooping cough due to Bordetella pertussis A37.1 Whooping cough due to Bordetella parapertussis A37.8 Whooping cough due to other Bordetella species A37.9 Whooping cough, unspecified

  A38 Scarlet fever

Incl.:  scarlatina

Excl.: streptococcal sore throat (J02.0)

  A39 Meningococcal infection

A39.0† Meningococcal meningitis (G01*)

A39.1† Waterhouse–Friderichsen syndrome (E35.1*) Meningococcal haemorrhagic adrenalitis Meningococcic adrenal syndrome

A39.2 Acute meningococcaemia A39.3 Chronic meningococcaemia

A39.4 Meningococcaemia, unspecified

Meningococcal bacteraemia NOS

A39.5† Meningococcal heart disease

Meningococcal:

• carditis NOS (I52.0*)

• endocarditis (I39.8*)

• myocarditis (I41.0*)

• pericarditis (I32.0*)

A39.8 Other meningococcal infections

Meningococcal:

• arthritis† (M01.0*)

• conjunctivitis† (H13.1*)

• encephalitis† (G05.0*)

• retrobulbar neuritis† (H48.1*) Postmeningococcal arthritis† (M03.0*)

A39.9 Meningococcal infection, unspecified

Meningococcal disease NOS

 

  A40 Streptococcal sepsis

Use additional code (R57.2) if desired, to identify septic shock.

Excl.: during labour (O75.3) following:

• abortion or ectopic or molar pregnancy (O03–O07, O08.0)

• immunization (T88.0)

• infusion, transfusion or therapeutic injection (T80.2) neonatal (P36.0–P36.1)

postprocedural (T81.4) puerperal (O85)

A40.0 Sepsis due to Streptococcus, group A A40.1 Sepsis due to Streptococcus, group B A40.2 Sepsis due to Streptococcus, group D A40.3 Sepsis due to Streptococcus pneumoniae

Pneumococcal sepsis

A40.8 Other streptococcal sepsis

A40.9 Streptococcal sepsis, unspecified

  A41 Other sepsis

Use additional code (R57.2) if desired, to identify septic shock.

Excl.: bacteraemia NOS (A49.9) during labour (O75.3) following:

• abortion or ectopic or molar pregnancy (O03–O07, O08.0)

• immunization (T88.0)

• infusion, transfusion or therapeutic injection (T80.2) sepsis (due to)(in):

• actinomycotic (A42.7)

• anthrax (A22.7)

• candidal (B37.7)

• Erysipelothrix (A26.7)

• extraintestinal yersiniosis (A28.2)

• gonococcal (A54.8)

• herpesviral (B00.7)

• listerial (A32.7)

• meningococcal (A39.2–A39.4)

• neonatal (P36.-)

• postprocedural (T81.4)

• puerperal (O85)

• streptococcal (A40.-)

• tularaemia (A21.7) septic:

• melioidosis (A24.1)

• plague (A20.7)

 

116

 

toxic shock syndrome (A48.3)

 

A41.0 Sepsis due to Staphylococcus aureus

A41.1 Sepsis due to other specified Staphylococcus

Sepsis due to coagulase-negative Staphylococcus A41.2 Sepsis due to unspecified Staphylococcus A41.3 Sepsis due to Haemophilus influenzae

A41.4 Sepsis due to anaerobes

Excl.: gas gangrene (A48.0)

A41.5 Sepsis due to other Gram-negative organisms

Gram-negative sepsis NOS

A41.8 Other specified sepsis A41.9 Sepsis, unspecified

Septicaemia

  A42 Actinomycosis

Excl.: actinomycetoma (B47.1) A42.0 Pulmonary actinomycosis A42.1 Abdominal actinomycosis A42.2 Cervicofacial actinomycosis A42.7 Actinomycotic sepsis

A42.8 Other forms of actinomycosis A42.9 Actinomycosis, unspecified

  A43 Nocardiosis

A43.0 Pulmonary nocardiosis A43.1 Cutaneous nocardiosis A43.8 Other forms of nocardiosis A43.9 Nocardiosis, unspecified

  A44 Bartonellosis

A44.0 Systemic bartonellosis

Oroya fever

A44.1 Cutaneous and mucocutaneous bartonellosis

Verruga peruana

A44.8 Other forms of bartonellosis A44.9 Bartonellosis, unspecified

 

  A46 Erysipelas

Excl.: postpartum or puerperal erysipelas (O86.8)

  A48 Other bacterial diseases, not elsewhere classified

Excl.: actinomycetoma (B47.1)

A48.0 Gas gangrene

Clostridial:

• cellulitis

• myonecrosis

A48.1 Legionnaires disease

A48.2 Nonpneumonic Legionnaires disease [Pontiac fever] A48.3 Toxic shock syndrome

Excl.: endotoxic shock NOS (R57.8) sepsis NOS (A41.9)

A48.4 Brazilian purpuric fever

Systemic Haemophilus aegyptius infection

A48.8 Other specified bacterial diseases

  A49 Bacterial infection of unspecified site

Excl.: bacterial agents as the cause of diseases classified to other chapters (B95–B96)

chlamydial infection NOS (A74.9) meningococcal infection NOS (A39.9) rickettsial infection NOS (A79.9) spirochaetal infection NOS (A69.9)

A49.0 Staphylococcal infection, unspecified site

A49.1 Streptococcal and enterococcal infection, unspecified site A49.2 Haemophilus influenzae infection, unspecified site

A49.3 Mycoplasma infection, unspecified site A49.8 Other bacterial infections of unspecified site

A49.9 Bacterial infection, unspecified

Bacteraemia NOS

Infections with a predominantly sexual mode of transmission

(A50–A64)

Excl.: human immunodeficiency virus [HIV] disease (B20–B24) nonspecific and nongonococcal urethritis (N34.1)

Reiter disease (M02.3)

  A50 Congenital syphilis

A50.0 Early congenital syphilis, symptomatic

Any congenital syphilitic condition specified as early or manifest less than two years after birth.

Early congenital syphilis:

• cutaneous

• mucocutaneous

• visceral

Early congenital syphilitic:

• laryngitis

• oculopathy

• osteochondropathy

• pharyngitis

• pneumonia

• rhinitis

A50.1 Early congenital syphilis, latent

Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth.

A50.2 Early congenital syphilis, unspecified

Congenital syphilis NOS less than two years after birth.

A50.3 Late congenital syphilitic oculopathy

Late congenital syphilitic interstitial keratitis† (H19.2*) Late congenital syphilitic oculopathy NEC† (H58.8*)

Excl.: Hutchinson triad (A50.5)

A50.4 Late congenital neurosyphilis [juvenile neurosyphilis]

Dementia paralytica juvenilis Juvenile:

• general paresis

• tabes dorsalis

• taboparetic neurosyphilis Late congenital syphilitic:

• encephalitis† (G05.0*)

• meningitis† (G01*)

• polyneuropathy† (G63.0*)

Use additional code, if desired, to identify any associated mental disorder.

Excl.: Hutchinson triad (A50.5)

A50.5 Other late congenital syphilis, symptomatic

Any congenital syphilitic condition specified as late or manifest two years or more after birth.

Clutton joints† (M03.1*) Hutchinson:

• teeth

• triad

Late congenital:

• cardiovascular syphilis† (I98.0*)

• syphilitic:

– arthropathy† (M03.1*)

– osteochondropathy† (M90.2*) Syphilitic saddle nose

A50.6 Late congenital syphilis, latent

Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth.

A50.7 Late congenital syphilis, unspecified

Congenital syphilis NOS two years or more after birth.

A50.9 Congenital syphilis, unspecified

  A51 Early syphilis

A51.0 Primary genital syphilis

Syphilitic chancre NOS

A51.1 Primary anal syphilis

A51.2 Primary syphilis of other sites

A51.3 Secondary syphilis of skin and mucous membranes

Condyloma latum Syphilitic:

• alopecia† (L99.8*)

• leukoderma† (L99.8*)

• mucous patch

A51.4 Other secondary syphilis

Secondary syphilitic:

• female pelvic inflammatory disease† (N74.2*)

• iridocyclitis† (H22.0*)

• lymphadenopathy

• meningitis† (G01*)

• myositis† (M63.0*)

• oculopathy NEC† (H58.8*)

• periostitis† (M90.1*)

A51.5 Early syphilis, latent

Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after infection.

A51.9 Early syphilis, unspecified

  A52 Late syphilis

A52.0† Cardiovascular syphilis

Cardiovascular syphilis NOS (I98.0*) Syphilitic:

• aneurysm of aorta (I79.0*)

• aortic incompetence (I39.1*)

• aortitis (I79.1*)

• arteritis, cerebral (I68.1*)

• endocarditis NOS (I39.8*)

• myocarditis (I41.0*)

• pericarditis (I32.0*)

• pulmonary regurgitation (I39.3*)

A52.1 Symptomatic neurosyphilis Charcot arthropathy† (M14.6*) Late syphilitic:

• acoustic neuritis† (H94.0*)

• encephalitis† (G05.0*)

• meningitis† (G01*)

• optic atrophy† (H48.0*)

• polyneuropathy† (G63.0*)

• retrobulbar neuritis† (H48.1*) Syphilitic parkinsonism† (G22*) Tabes dorsalis

A52.2 Asymptomatic neurosyphilis A52.3 Neurosyphilis, unspecified

A52.7 Other symptomatic late syphilis

Glomerular disease in syphilis† (N08.0*)

Gumma (syphilitic)

Late or tertiary syphilis any sites, except those classified to A52.0–A52.3

Late syphilitic:

• bursitis† (M73.1*)

• chorioretinitis† (H32.0*)

• episcleritis† (H19.0*)

• female pelvic inflammatory disease† (N74.2*)

• leukoderma† (L99.8*)

• oculopathy NEC† (H58.8*)

• peritonitis† (K67.2*) Syphilis [stage unspecified] of:

• bone† (M90.2*)

• liver† (K77.0*)

• lung† (J99.8*)

• muscle† (M63.0*)

• synovium† (M68.0*)

A52.8 Late syphilis, latent

Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after infection.

A52.9 Late syphilis, unspecified

  A53 Other and unspecified syphilis

A53.0 Latent syphilis, unspecified as early or late

Latent syphilis NOS

Positive serological reaction for syphilis

A53.9 Syphilis, unspecified

Infection due to Treponema pallidum NOS Syphilis (acquired) NOS

Excl.: syphilis NOS causing death under two years of age (A50.2)

  A54 Gonococcal infection

A54.0 Gonococcal infection of lower genitourinary tract without periurethral or accessory gland abscess

Gonococcal:

• cervicitis NOS

• cystitis NOS

• urethritis NOS

• vulvovaginitis NOS

Excl.: with:

• genitourinary gland abscess (A54.1)

• periurethral abscess (A54.1)

A54.1 Gonococcal infection of lower genitourinary tract with periurethral and accessory gland abscess

Gonococcal Bartholin gland abscess

A54.2 Gonococcal pelviperitonitis and other gonococcal genitourinary infections

Gonococcal:

• epididymitis† (N51.1*)

• female pelvic inflammatory disease† (N74.3*)

• orchitis† (N51.1*)

• prostatitis† (N51.0*)

Excl.: gonococcal peritonitis (A54.8)

A54.3 Gonococcal infection of eye

Gonococcal:

• conjunctivitis† (H13.1*)

• iridocyclitis† (H22.0*)

Ophthalmia neonatorum due to gonococcus

A54.4† Gonococcal infection of musculoskeletal system

Gonococcal:

• arthritis (M01.3*)

• bursitis (M73.0*)

• osteomyelitis (M90.2*)

• synovitis (M68.0*)

• tenosynovitis (M68.0*)

A54.5 Gonococcal pharyngitis

A54.6 Gonococcal infection of anus and rectum A54.8 Other gonococcal infections

Gonococcal:

• brain abscess† (G07*)

• endocarditis† (I39.8*)

• meningitis† (G01*)

• myocarditis† (I41.0*)

• pericarditis† (I32.0*)

• peritonitis† (K67.1*)

• pneumonia† (J17.0*)

• sepsis

• skin lesions

Excl.: gonococcal pelviperitonitis (A54.2)

A54.9 Gonococcal infection, unspecified

  A55 Chlamydial lymphogranuloma (venereum)

Incl.: climatic or tropical bubo Durand–Nicolas–Favre disease esthiomene

lymphogranuloma inguinale

  A56 Other sexually transmitted chlamydial diseases

Incl.: sexually transmitted diseases due to Chlamydia trachomatis

Excl.: chlamydial:

• lymphogranuloma (A55)

• neonatal:

– conjunctivitis (P39.1)

– pneumonia (P23.1) conditions classified to A74.-

A56.0 Chlamydial infection of lower genitourinary tract

Chlamydial:

• cervicitis

• cystitis

• urethritis

• vulvovaginitis

A56.1 Chlamydial infection of pelviperitoneum and other genitourinary organs

Chlamydial:

• epididymitis† (N51.1*)

• female pelvic inflammatory disease† (N74.4*)

• orchitis† (N51.1*)

A56.2 Chlamydial infection of genitourinary tract, unspecified A56.3 Chlamydial infection of anus and rectum

A56.4 Chlamydial infection of pharynx

A56.8 Sexually transmitted chlamydial infection of other sites

  A57 Chancroid

Incl.: ulcus molle

  A58 Granuloma inguinale

Incl.:  donovanosis

  A59 Trichomoniasis

Excl.: intestinal trichomoniasis (A07.8)

A59.0 Urogenital trichomoniasis

Leukorrhoea (vaginalis)

Prostatitis† (N51.0*) due to Trichomonas (vaginalis)

A59.8 Trichomoniasis of other sites A59.9 Trichomoniasis, unspecified

  A60 Anogenital herpesviral [herpes simplex] infection

A60.0 Herpesviral infection of genitalia and urogenital tract

Herpesviral infection of genital tract:

• female† (N77.0-N77.1*)

• male† (N51.-*)

A60.1 Herpesviral infection of perianal skin and rectum A60.9 Anogenital herpesviral infection, unspecified

  A63 Other predominantly sexually transmitted diseases, not elsewhere classified

Excl.: molluscum contagiosum (B08.1) papilloma of cervix (D26.0)

A63.0 Anogenital (venereal) warts

A63.8 Other specified predominantly sexually transmitted diseases

  A64 Unspecified sexually transmitted disease

Incl.: venereal disease NOS

Other spirochaetal diseases (A65–A69)

Excl.: leptospirosis (A27.-)

syphilis (A50–A53)

  A65 Nonvenereal syphilis

Incl.: bejel

endemic syphilis njovera

  A66 Yaws

Incl.: bouba

framboesia (tropica) pian

A66.0 Initial lesions of yaws

Chancre of yaws

Framboesia, initial or primary Initial framboesial ulcer Mother yaw

A66.1 Multiple papillomata and wet crab yaws

Framboesioma Pianoma

Plantar or palmar papilloma of yaws

A66.2 Other early skin lesions of yaws

Cutaneous yaws, less than five years after infection

Early yaws (cutaneous)(macular)(maculopapular)(micropapular)(papular) Framboeside of early yaws

A66.3 Hyperkeratosis of yaws

Ghoul hand

Hyperkeratosis, palmar or plantar (early)(late) due to yaws Worm-eaten soles

A66.4 Gummata and ulcers of yaws

Gummatous framboeside Nodular late yaws (ulcerated)

A66.5 Gangosa

Rhinopharyngitis mutilans

A66.6

A66.7 Other manifestations of yaws Juxta-articular nodules of yaws Mucosal yaws

A66.8 Latent yaws

Yaws without clinical manifestations, with positive serology

A66.9 Yaws, unspecified

  A67 Pinta [carate]

A67.0 Primary lesions of pinta A67.1 Intermediate lesions of pinta

Pintids

A67.2 Late lesions of pinta

Cardiovascular lesions† (I98.1*)

Skin lesions:

• achromic

• cicatricial

• dyschromic

of pinta [carate]

A67.3 Mixed lesions of pinta

Achromic with hyperchromic skin lesions of pinta [carate]

A67.9 Pinta, unspecified

  A68 Relapsing fevers

Incl.:   recurrent fever

Excl.: Lyme disease (A69.2)

A68.0 Louse-borne relapsing fever

Relapsing fever due to Borrelia recurrentis

A68.1 Tick-borne relapsing fever

Relapsing fever due to any Borrelia species other than Borrelia recurrentis

A68.9 Relapsing fever, unspecified

  A69 Other spirochaetal infections

A69.0 Necrotizing ulcerative stomatitis

Cancrum oris Fusospirochaetal gangrene Noma

Stomatitis gangrenosa

A69.1 Other Vincent infections

Fusospirochaetal pharyngitis Necrotizing ulcerative (acute):

• gingivitis

• gingivostomatitis Spirochaetal stomatitis Trench mouth Vincent:

• angina

• gingivitis

A69.2 Lyme disease

Erythema chronicum migrans due to Borrelia burgdorferi

A69.8 Other specified spirochaetal infections A69.9 Spirochaetal infection, unspecified

Other diseases caused by chlamydiae (A70–A74)

  A70 Chlamydia psittaci infection

Incl.: ornithosis

parrot fever psittacosis

  A71 Trachoma

Excl.: sequelae of trachoma (B94.0)

A71.0 Initial stage of trachoma

Trachoma dubium

A71.1 Active stage of trachoma

Granular conjunctivitis (trachomatous) Trachomatous:

• follicular conjunctivitis

• pannus

A71.9 Trachoma, unspecified

  A74 Other diseases caused by chlamydiae

Excl.: chlamydial pneumonia (J16.0) neonatal chlamydial:

• conjunctivitis (P39.1)

• pneumonia (P23.1)

sexually transmitted chlamydial diseases (A55–A56)

A74.0† Chlamydial conjunctivitis (H13.1*)

Paratrachoma

A74.8 Other chlamydial diseases

Chlamydial peritonitis† (K67.0*)

A74.9 Chlamydial infection, unspecified

Chlamydiosis NOS

Rickettsioses (A75–A79)

  A75 Typhus fever

Excl.: rickettsiosis due to Neorickettsia sennetsu [Ehrlichia sennetsu] (A79.8)

A75.0 Epidemic louse-borne typhus fever due to Rickettsia prowazekii

Classical typhus (fever) Epidemic (louse-borne) typhus

A75.1 Recrudescent typhus [Brill disease]

Brill-Zinsser disease

A75.2 Typhus fever due to Rickettsia typhi

Murine (flea-borne) typhus

A75.3 Typhus fever due to Rickettsia tsutsugamushi

Scrub (mite-borne) typhus Tsutsugamushi fever

A75.9 Typhus fever, unspecified

Typhus (fever) NOS

  A77 Spotted fever [tick-borne rickettsioses]

A77.0 Spotted fever due to Rickettsia rickettsii

Rocky Mountain spotted fever Sao Paulo fever

A77.1 Spotted fever due to Rickettsia conorii

African tick typhus Boutonneuse fever India tick typhus Kenya tick typhus Marseilles fever

Mediterranean tick fever

A77.2 Spotted fever due to Rickettsia sibirica

North Asian tick fever Siberian tick typhus

A77.3 Spotted fever due to Rickettsia australis

Queensland tick typhus

A77.8 Other spotted fevers A77.9 Spotted fever, unspecified

Tick-borne typhus NOS

  A78 Q fever

Incl.: infection due to Coxiella burnetii

Nine Mile fever quadrilateral fever

  A79 Other rickettsioses

A79.0 Trench fever Quintan fever Wolhynian fever

A79.1 Rickettsialpox due to Rickettsia akari

Kew Garden fever Vesicular rickettsiosis

A79.8 Other specified rickettsioses

Rickettsiosis due to Neorickettsia sennetsu [Ehrlichia sennetsu]

A79.9 Rickettsiosis, unspecified

Rickettsial infection NOS

 

Viral infections of the central nervous system (A80–A89)

Excl.: sequelae of:

• poliomyelitis (B91)

• viral encephalitis (B94.1)

  A80 Acute poliomyelitis

A80.0 Acute paralytic poliomyelitis, vaccine-associated A80.1 Acute paralytic poliomyelitis, wild virus, imported A80.2 Acute paralytic poliomyelitis, wild virus, indigenous A80.3 Acute paralytic poliomyelitis, other and unspecified A80.4 Acute nonparalytic poliomyelitis

A80.9 Acute poliomyelitis, unspecified

  A81 Atypical virus infections of central nervous system

Incl.: prion diseases of the central nervous system

A81.0 Creutzfeldt–Jakob disease

Subacute spongiform encephalopathy

A81.1 Subacute sclerosing panencephalitis

Dawson inclusion body encephalitis

Van Bogaert sclerosing leukoencephalopathy

A81.2 Progressive multifocal leukoencephalopathy

Multifocal leukoencephalopathy NOS

A81.8 Other atypical virus infections of central nervous system

Kuru

A81.9 Atypical virus infection of central nervous system, unspecified

Prion disease of central nervous system NOS

  A82 Rabies

A82.0 Sylvatic rabies

A82.1 Urban rabies

A82.9 Rabies, unspecified

  A83 Mosquito-borne viral encephalitis

Incl.: mosquito-borne viral meningoencephalitis

Excl.: Venezuelan equine encephalitis (A92.2)

A83.0 Japanese encephalitis

 

A83.1 Western equine encephalitis A83.2 Eastern equine encephalitis A83.3 St Louis encephalitis

A83.4 Australian encephalitis

Kunjin virus disease

A83.5 California encephalitis

California meningoencephalitis La Crosse encephalitis

A83.6 Rocio virus disease

A83.8 Other mosquito-borne viral encephalitis

A83.9 Mosquito-borne viral encephalitis, unspecified

  A84 Tick-borne viral encephalitis

Incl.: tick-borne viral meningoencephalitis

A84.0 Far Eastern tick-borne encephalitis [Russian spring–summer encephalitis]

A84.1 Central European tick-borne encephalitis A84.8 Other tick-borne viral encephalitis

Louping ill

Powassan virus disease

A84.9 Tick-borne viral encephalitis, unspecified

  A85 Other viral encephalitis, not elsewhere classified

Incl.: specified viral:

• encephalomyelitis NEC

• meningoencephalitis NEC

Excl.: benign myalgic encephalomyelitis (G93.3) encephalitis due to:

• herpesvirus [herpes simplex] (B00.4)

• measles virus (B05.0)

• mumps virus (B26.2)

• poliomyelitis virus (A80.-)

• zoster (B02.0)

lymphocytic choriomeningitis (A87.2)

A85.0† Enteroviral encephalitis (G05.1*)

Enteroviral encephalomyelitis

A85.1† Adenoviral encephalitis (G05.1*)

Adenoviral meningoencephalitis

A85.2 Arthropod-borne viral encephalitis, unspecified

 

A85.8 Other specified viral encephalitis

Encephalitis lethargica

Von Economo–Cruchet disease

  A86 Unspecified viral encephalitis

Incl.: viral:

• encephalomyelitis NOS

• meningoencephalitis NOS

  A87 Viral meningitis

Excl.: meningitis due to:

• herpesvirus [herpes simplex] (B00.3)

• measles virus (B05.1)

• mumps virus (B26.1)

• poliomyelitis virus (A80.-)

• zoster (B02.1)

A87.0† Enteroviral meningitis (G02.0*) Coxsackievirus meningitis Echovirus meningitis

A87.1† Adenoviral meningitis (G02.0*) A87.2 Lymphocytic choriomeningitis

Lymphocytic meningoencephalitis

A87.8 Other viral meningitis

A87.9 Viral meningitis, unspecified

  A88 Other viral infections of central nervous system, not elsewhere classified

Excl.: viral:

• encephalitis NOS (A86)

• meningitis NOS (A87.9)

A88.0 Enteroviral exanthematous fever [Boston exanthem] A88.1 Epidemic vertigo

A88.8 Other specified viral infections of central nervous system

  A89 Unspecified viral infection of central nervous system

Arthropod-borne viral fevers and viral haemorrhagic fevers

(A92–A99)

  A92 Other mosquito-borne viral fevers

Excl.: Ross River disease (B33.1)

A92.0 Chikungunya virus disease

Chikungunya (haemorrhagic) fever

A92.1 O’nyong-nyong fever A92.2 Venezuelan equine fever

Venezuelan equine:

• encephalitis

• encephalomyelitis virus disease

A92.3 West Nile virus infection

West Nile fever

A92.4 Rift Valley fever

A92.8 Other specified mosquito-borne viral fevers A92.9 Mosquito-borne viral fever, unspecified

  A93 Other arthropod-borne viral fevers, not elsewhere classified

A93.0 Oropouche virus disease

Oropouche fever

A93.1 Sandfly fever Pappataci fever Phlebotomus fever

A93.2 Colorado tick fever

A93.8 Other specified arthropod-borne viral fevers

Piry virus disease

Severe fever with thrombocytopenia syndrome [SFTS] Vesicular stomatitis virus disease [Indiana fever]

  A94 Unspecified arthropod-borne viral fever

Incl.: arboviral fever NOS arbovirus infection NOS

  A95 Yellow fever

A95.0 Sylvatic yellow fever

Jungle yellow fever

A95.1 Urban yellow fever

A95.9 Yellow fever, unspecified

  A96 Arenaviral haemorrhagic fever

A96.0 Junin haemorrhagic fever

Argentinian haemorrhagic fever

A96.1 Machupo haemorrhagic fever

Bolivian haemorrhagic fever

A96.2 Lassa fever

A96.8 Other arenaviral haemorrhagic fevers A96.9 Arenaviral haemorrhagic fever, unspecified

  A97 Dengue

Dengue is a viral disease transmitted by the bite of a mosquito infected by dengue viruses. It is one disease entity with different clinical presentations and often with unpredictable clinical evolution and outcome. Most patients recover following a self-limiting non-severe clinical course like nausea, vomiting, rash, aches and pains, but a small proportion progress to severe disease, mostly characterized by plasma leakage with or without haemorrhage, although severe haemorrhages or severe organ impairment can occur, with or without dengue shock.

A97.0 Dengue without warning signs

Incl.:   dengue haemorrhagic fever grades 1 and 2 dengue haemorrhagic fever without warning signs

A97.1 Dengue with warning signs

Clinical warning signs are: abdominal pain or tenderness, mucosal bleeding, lethargy and/or restlessness, rapid decrease in platelet count, increase in haematocrit. Other signs can include: persistent vomiting, visible fluid accumulation, liver enlargement more than 2 cm.

Incl.: dengue haemorrhagic fever with warning signs

A97.2 Severe dengue

Clinical signs include: 1. severe plasma leakage leading to shock (dengue shock syndrome – DSS) and/or fluid accumulation with respiratory distress; 2. severe bleeding as evaluated by clinician;

3. severe organ involvement: liver aspartate transaminase (AST) or alanine aminotransferase (ALT) 1000, CNS: impaired consciousness (encephalitis), involvement of other organs, as myocarditis or nephritis

Incl.: Severe dengue fever

Severe dengue haemorrhagic fever

A97.9 Dengue, unspecified

Incl.: Dengue fever [DF] NOS

  A98 Other viral haemorrhagic fevers, not elsewhere classified

Excl.: chikungunya haemorrhagic fever (A92.0) dengue haemorrhagic fever (A97.-)

A98.0 Crimean-Congo haemorrhagic fever

Central Asian haemorrhagic fever A98.1 Omsk haemorrhagic fever A98.2 Kyasanur Forest disease A98.3 Marburg virus disease A98.4 Ebola virus disease

A98.5 Haemorrhagic fever with renal syndrome

Haemorrhagic fever:

• epidemic

• Korean

• Russian Hantaanvirus disease

Hantaanvirus disease with renal manifestations Nephropathia epidemica

Excl.: hantavirus (cardio-)pulmonary syndrome (B33.4† , J17.1*)

A98.8 Other specified viral haemorrhagic fevers

  A99 Unspecified viral haemorrhagic fever

Viral infections characterized by skin and mucous membrane lesions

(B00–B09)

  B00 Herpesviral [herpes simplex] infections

Excl.: anogenital herpesviral infection (A60.-) congenital herpesviral infection (P35.2) gammaherpesviral mononucleosis (B27.0) herpangina (B08.5)

B00.0 Eczema herpeticum

Kaposi varicelliform eruption

B00.1 Herpesviral vesicular dermatitis

Herpes simplex:

• facialis

• labialis

Vesicular dermatitis of:

• ear

• lip due to human (alpha) herpes virus 2

B00.2 Herpesviral gingivostomatitis and pharyngotonsillitis

Herpesviral pharyngitis

B00.3† Herpesviral meningitis (G02.0*) B00.4† Herpesviral encephalitis (G05.1*)

Herpesviral meningoencephalitis Simian B disease

B00.5 Herpesviral ocular disease

Herpesviral:

• conjunctivitis† (H13.1*)

• dermatitis of eyelid† (H03.1*)

• iridocyclitis† (H22.0*)

• iritis† (H22.0*)

• keratitis† (H19.1*)

• keratoconjunctivitis† (H19.1*)

• uveitis, anterior† (H22.0*)

B00.7 Disseminated herpesviral disease

Herpesviral sepsis

B00.8 Other forms of herpesviral infection

Herpesviral:

• hepatitis† (K77.0*)

• whitlow† (L99.8*)

B00.9 Herpesviral infection, unspecified

Herpes simplex infection NOS

  B01 Varicella [chickenpox] B01.0† Varicella meningitis (G02.0*) B01.1† Varicella encephalitis (G05.1*)

Postchickenpox encephalitis

Varicella encephalomyelitis

B01.2† Varicella pneumonia (J17.1*) B01.8 Varicella with other complications B01.9 Varicella without complication

Varicella NOS

  B02 Zoster [herpes zoster]

Incl.: shingles

zona

B02.0† Zoster encephalitis (G05.1*)

Zoster meningoencephalitis

B02.1† Zoster meningitis (G02.0*)

B02.2† Zoster with other nervous system involvement

Postherpetic:

• geniculate ganglionitis (G53.0*)

• polyneuropathy (G63.0*)

• trigeminal neuralgia (G53.0*)

B02.3 Zoster ocular disease

Zoster:

• blepharitis† (H03.1*)

• conjunctivitis† (H13.1*)

• iridocyclitis† (H22.0*)

• iritis† (H22.0*)

• keratitis† (H19.2*)

• keratoconjunctivitis† (H19.2*)

• scleritis† (H19.0*)

B02.7 Disseminated zoster

B02.8 Zoster with other complications B02.9 Zoster without complication

Zoster NOS

  B03 Smallpox1

  B04 Monkeypox

1 In 1980, the 33rd World Health Assembly declared that smallpox had been eradicated. The classification is maintained for surveillance purposes.

  B05 Measles

Incl.: morbilli

Excl.: subacute sclerosing panencephalitis (A81.1)

B05.0† Measles complicated by encephalitis (G05.1*)

Postmeasles encephalitis

B05.1† Measles complicated by meningitis (G02.0*)

Postmeasles meningitis

B05.2† Measles complicated by pneumonia (J17.1*)

Postmeasles pneumonia

B05.3† Measles complicated by otitis media (H67.1*)

Postmeasles otitis media

B05.4 Measles with intestinal complications B05.8 Measles with other complications

Measles keratitis and keratoconjunctivitis† (H19.2*)

B05.9 Measles without complication

Measles NOS

  B06 Rubella [German measles]

Excl.: congenital rubella (P35.0)

B06.0† Rubella with neurological complications

Rubella:

• encephalitis (G05.1*)

• meningitis (G02.0*)

• meningoencephalitis (G05.1*)

B06.8 Rubella with other complications

Rubella:

• arthritis† (M01.4*)

• pneumonia† (J17.1*)

B06.9 Rubella without complication

Rubella NOS

 

  B07 Viral warts

Incl.: verruca:

• simplex

• vulgaris

Excl.: anogenital (venereal) warts (A63.0) papilloma of:

• bladder (D41.4)

• cervix (D26.0)

• larynx (D14.1)

  B08 Other viral infections characterized by skin and mucous membrane lesions, not elsewhere classified

Excl.: vesicular stomatitis virus disease (A93.8)

B08.0 Other orthopoxvirus infections

Cowpox

Orf virus disease Pseudocowpox [milker’s node] Vaccinia

Excl.: monkeypox (B04)

B08.1 Molluscum contagiosum

B08.2 Exanthema subitum [sixth disease] B08.3 Erythema infectiosum [fifth disease]

B08.4 Enteroviral vesicular stomatitis with exanthem

Hand, foot and mouth disease

B08.5 Enteroviral vesicular pharyngitis

Herpangina

B08.8 Other specified viral infections characterized by skin and mucous membrane lesions

Enteroviral lymphonodular pharyngitis Foot-and-mouth disease

Tanapox virus disease Yaba pox virus disease

  B09 Unspecified viral infection characterized by skin and mucous membrane lesions

Incl.: viral:

• enanthema NOS

• exanthema NOS

 

Viral hepatitis (B15–B19)

Use additional code (Chapter XX), if desired, to identify drug, if post-transfusion hepatitis.

Excl.: cytomegaloviral hepatitis (B25.1)

herpesviral [herpes simplex] hepatitis (B00.8) sequelae of viral hepatitis (B94.2)

  B15 Acute hepatitis A

B15.0 Hepatitis A with hepatic coma B15.9 Hepatitis A without hepatic coma

Hepatitis A (acute)(viral) NOS

  B16 Acute hepatitis B

B16.0 Acute hepatitis B with delta-agent (coinfection) with hepatic coma B16.1 Acute hepatitis B with delta-agent (coinfection) without

hepatic coma

B16.2 Acute hepatitis B without delta-agent with hepatic coma

B16.9 Acute hepatitis B without delta-agent and without hepatic coma

Acute hepatitis B (viral) NOS

  B17 Other acute viral hepatitis

B17.0 Acute delta-(super)infection of hepatitis B carrier B17.1 Acute hepatitis C

B17.2 Acute hepatitis E

B17.8 Other specified acute viral hepatitis

Hepatitis non-A non-B (acute)(viral) NEC

B17.9 Acute viral hepatitis, unspecified

Acute hepatitis NOS

Acute infectious hepatitis NOS

  B18 Chronic viral hepatitis

B18.0 Chronic viral hepatitis B with delta-agent B18.1 Chronic viral hepatitis B without delta-agent

Hepatitis B (viral) NOS

B18.2 Chronic viral hepatitis C B18.8 Other chronic viral hepatitis

B18.9 Chronic viral hepatitis, unspecified

 

  B19 Unspecified viral hepatitis

B19.0 Unspecified viral hepatitis with hepatic coma B19.9 Unspecified viral hepatitis without hepatic coma

Viral hepatitis NOS

Human immunodeficiency virus [HIV] disease (B20–B24)

Excl.: asymptomatic human immunodeficiency virus [HIV] infection status (Z21) complicating pregnancy, childbirth and the puerperium (O98.7)

  B20 Human immunodeficiency virus [HIV] disease resulting in infectious and parasitic diseases

Excl.: acute HIV infection syndrome (B23.0)

B20.0 HIV disease resulting in mycobacterial infection

HIV disease resulting in tuberculosis

B20.1 HIV disease resulting in other bacterial infections B20.2 HIV disease resulting in cytomegaloviral disease B20.3 HIV disease resulting in other viral infections B20.4 HIV disease resulting in candidiasis

B20.5 HIV disease resulting in other mycoses

B20.6 HIV disease resulting in Pneumocystis jirovecii pneumonia

HIV disease resulting in Pneumocystis carinii pneumonia

B20.7 HIV disease resulting in multiple infections

B20.8 HIV disease resulting in other infectious and parasitic diseases B20.9 HIV disease resulting in unspecified infectious or parasitic disease

HIV disease resulting in infection NOS

  B21 Human immunodeficiency virus [HIV] disease resulting in malignant neoplasms

B21.0 HIV disease resulting in Kaposi sarcoma B21.1 HIV disease resulting in Burkitt lymphoma

B21.2 HIV disease resulting in other types of non-Hodgkin lymphoma

B21.3 HIV disease resulting in other malignant neoplasms of lymphoid, haematopoietic and related tissue

B21.7 HIV disease resulting in multiple malignant neoplasms B21.8 HIV disease resulting in other malignant neoplasms B21.9 HIV disease resulting in unspecified malignant neoplasm

 

  B22 Human immunodeficiency virus [HIV] disease resulting in other specified diseases

B22.0 HIV disease resulting in encephalopathy

HIV dementia

B22.1 HIV disease resulting in lymphoid interstitial pneumonitis B22.2 HIV disease resulting in wasting syndrome

HIV disease resulting in failure to thrive

Slim disease

B22.7 HIV disease resulting in multiple diseases classified elsewhere

Note: For use of this category, reference should be made to the morbidity or mortality coding rules and guidelines in Volume 2.

  B23 Human immunodeficiency virus [HIV] disease resulting in other conditions

B23.0 Acute HIV infection syndrome

B23.1 HIV disease resulting in (persistent) generalized lymphadenopathy

B23.2 HIV disease resulting in haematological and immunological abnormalities, not elsewhere classified

B23.8 HIV disease resulting in other specified conditions

  B24 Unspecified human immunodeficiency virus [HIV] disease

Incl.: acquired immunodeficiency syndrome [AIDS] NOS AIDS-related complex [ARC] NOS

Other viral diseases (B25–B34)

  B25 Cytomegaloviral disease

Excl.: congenital cytomegalovirus infection (P35.1) cytomegaloviral mononucleosis (B27.1)

B25.0† Cytomegaloviral pneumonitis (J17.1*) B25.1† Cytomegaloviral hepatitis (K77.0*) B25.2† Cytomegaloviral pancreatitis (K87.1*) B25.8 Other cytomegaloviral diseases B25.9 Cytomegaloviral disease, unspecified

 

  B26 Mumps

Incl.: parotitis:

• epidemic

• infectious

B26.0† Mumps orchitis (N51.1*) B26.1† Mumps meningitis (G02.0*) B26.2† Mumps encephalitis (G05.1*) B26.3† Mumps pancreatitis (K87.1*)

B26.8 Mumps with other complications

Mumps:

• arthritis† (M01.5*)

• myocarditis† (I41.1*)

• nephritis† (N08.0*)

• polyneuropathy† (G63.0*)

B26.9 Mumps without complication

Mumps:

• NOS

• parotitis NOS

  B27 Infectious mononucleosis

Incl.:   glandular fever

monocytic angina Pfeiffer disease

B27.0 Gammaherpesviral mononucleosis

Mononucleosis due to Epstein–Barr virus B27.1 Cytomegaloviral mononucleosis B27.8 Other infectious mononucleosis

B27.9 Infectious mononucleosis, unspecified

  B30 Viral conjunctivitis

Excl.: ocular disease:

• herpesviral [herpes simplex] (B00.5)

• zoster (B02.3)

B30.0† Keratoconjunctivitis due to adenovirus (H19.2*)

Epidemic keratoconjunctivitis Shipyard eye

B30.1† Conjunctivitis due to adenovirus (H13.1*) Acute adenoviral follicular conjunctivitis Swimming-pool conjunctivitis

B30.2 Viral pharyngoconjunctivitis

 

B30.3† Acute epidemic haemorrhagic conjunctivitis (enteroviral) (H13.1*)

Conjunctivitis due to:

• coxsackievirus 24

• enterovirus 70

Haemorrhagic conjunctivitis (acute)(epidemic)

B30.8† Other viral conjunctivitis (H13.1*)

Newcastle conjunctivitis

B30.9 Viral conjunctivitis, unspecified

  B33 Other viral diseases, not elsewhere classified

B33.0 Epidemic myalgia

Bornholm disease

B33.1 Ross River disease

Epidemic polyarthritis and exanthema Ross River fever

B33.2 Viral carditis

B33.3 Retrovirus infections, not elsewhere classified

Retrovirus infection NOS

B33.4† Hantavirus (cardio-)pulmonary syndrome [HPS][HCPS] (J17.1*)

Hantaavirus disease with pulmonary manifestations Sin Nombre virus disease

Use additional code (N17.9), if desired, to identify any renal failure associated with HPS caused by the Andes, Bayou and Black Creek Canal hantaavirus etiologies.

Excl.: haemorrhagic fever with renal manifestations (A98.5)

B33.8 Other specified viral diseases

  B34 Viral infection of unspecified site

Excl.: cytomegaloviral disease NOS (B25.9)

herpesvirus [herpes simplex] infection NOS (B00.9) retrovirus infection NOS (B33.3) viral agents as the cause of diseases classified to other chapters (B97.-)

B34.0 Adenovirus infection, unspecified site B34.1 Enterovirus infection, unspecified site

Coxsackievirus infection NOS Echovirus infection NOS

B34.2 Coronavirus infection, unspecified site

Excl.: severe acute respiratory syndrome [SARS] (U04.9)

 

B34.3 Parvovirus infection, unspecified site B34.4 Papovavirus infection, unspecified site B34.8 Other viral infections of unspecified site B34.9 Viral infection, unspecified

Viraemia NOS

Mycoses (B35–B49)

Excl.: hypersensitivity pneumonitis due to organic dust (J67.-) mycosis fungoides (C84.0)

  B35 Dermatophytosis

Incl.: favus

infections due to species of Epidermophyton, Microsporum and

Trichophyton tinea, any type except those in B36.-

B35.0 Tinea barbae and tinea capitis

Beard ringworm Kerion

Scalp ringworm Sycosis, mycotic

B35.1 Tinea unguium

Dermatophytic onychia Dermatophytosis of nail Onychomycosis Ringworm of nails

B35.2 Tinea manuum Dermatophytosis of hand Hand ringworm

B35.3 Tinea pedis

Athlete’s foot Dermatophytosis of foot Foot ringworm

B35.4 Tinea corporis

Ringworm of the body

B35.5 Tinea imbricata

Tokelau

B35.6 Tinea inguinalis [Tinea cruris]

Dhobi itch Groin ringworm Jock itch

 

B35.8 Other dermatophytoses

Dermatophytosis:

• disseminated

• granulomatous

B35.9 Dermatophytosis, unspecified

Ringworm NOS

  B36 Other superficial mycoses

B36.0 Pityriasis versicolor

Tinea:

• flava

• versicolor

B36.1 Tinea nigra

Keratomycosis nigricans palmaris Microsporosis nigra

Pityriasis nigra

B36.2 White piedra

Tinea blanca

B36.3 Black piedra

B36.8 Other specified superficial mycoses B36.9 Superficial mycosis, unspecified

  B37 Candidiasis

Incl.:  candidosis

moniliasis

Excl.: neonatal candidiasis (P37.5)

B37.0 Candidal stomatitis

Oral thrush

B37.1 Pulmonary candidiasis B37.2 Candidiasis of skin and nail

Candidal:

• onychia

• paronychia

Excl.: diaper [napkin] dermatitis (L22)

B37.3† Candidiasis of vulva and vagina (N77.1*)

Candidal vulvovaginitis Monilial vulvovaginitis Vaginal thrush

 

B37.4 Candidiasis of other urogenital sites

Candidal:

• balanitis† (N51.2*)

• urethritis† (N37.0*)

B37.5† Candidal meningitis (G02.1*) B37.6† Candidal endocarditis (I39.8*) B37.7 Candidal sepsis

B37.8 Candidiasis of other sites

Candidal:

• cheilitis

• enteritis

B37.9 Candidiasis, unspecified

Thrush NOS

  B38 Coccidioidomycosis

B38.0 Acute pulmonary coccidioidomycosis B38.1 Chronic pulmonary coccidioidomycosis

B38.2 Pulmonary coccidioidomycosis, unspecified B38.3 Cutaneous coccidioidomycosis

B38.4† Coccidioidomycosis meningitis (G02.1*)

B38.7 Disseminated coccidioidomycosis

Generalized coccidioidomycosis

B38.8 Other forms of coccidioidomycosis B38.9 Coccidioidomycosis, unspecified

  B39 Histoplasmosis

B39.0 Acute pulmonary histoplasmosis capsulati B39.1 Chronic pulmonary histoplasmosis capsulati

B39.2 Pulmonary histoplasmosis capsulati, unspecified

B39.3 Disseminated histoplasmosis capsulati

Generalized histoplasmosis capsulati

B39.4 Histoplasmosis capsulati, unspecified

American histoplasmosis

B39.5 Histoplasmosis duboisii

African histoplasmosis

B39.9 Histoplasmosis, unspecified

 

  B40 Blastomycosis

Excl.: Brazilian blastomycosis (B41.-) keloidal blastomycosis (B48.0)

B40.0 Acute pulmonary blastomycosis B40.1 Chronic pulmonary blastomycosis

B40.2 Pulmonary blastomycosis, unspecified B40.3 Cutaneous blastomycosis

B40.7 Disseminated blastomycosis

Generalized blastomycosis

B40.8 Other forms of blastomycosis B40.9 Blastomycosis, unspecified

  B41 Paracoccidioidomycosis

Incl.: Brazilian blastomycosis Lutz disease

B41.0 Pulmonary paracoccidioidomycosis B41.7 Disseminated paracoccidioidomycosis

Generalized paracoccidioidomycosis

B41.8 Other forms of paracoccidioidomycosis B41.9 Paracoccidioidomycosis, unspecified

  B42 Sporotrichosis

B42.0† Pulmonary sporotrichosis (J99.8*) B42.1 Lymphocutaneous sporotrichosis B42.7 Disseminated sporotrichosis

Generalized sporotrichosis

B42.8 Other forms of sporotrichosis B42.9 Sporotrichosis, unspecified

  B43 Chromomycosis and phaeomycotic abscess

B43.0 Cutaneous chromomycosis

Dermatitis verrucosa

B43.1 Phaeomycotic brain abscess

Cerebral chromomycosis

B43.2 Subcutaneous phaeomycotic abscess and cyst B43.8 Other forms of chromomycosis

B43.9 Chromomycosis, unspecified

 

  B44 Aspergillosis

Incl.: aspergilloma

B44.0 Invasive pulmonary aspergillosis B44.1 Other pulmonary aspergillosis B44.2 Tonsillar aspergillosis

B44.7 Disseminated aspergillosis

Generalized aspergillosis

B44.8 Other forms of aspergillosis B44.9 Aspergillosis, unspecified

  B45 Cryptococcosis

B45.0 Pulmonary cryptococcosis B45.1 Cerebral cryptococcosis

Cryptococcal meningitis† (G02.1*)

Cryptococcosis meningocerebralis B45.2 Cutaneous cryptococcosis B45.3 Osseous cryptococcosis

B45.7 Disseminated cryptococcosis

Generalized cryptococcosis

B45.8 Other forms of cryptococcosis B45.9 Cryptococcosis, unspecified

  B46 Zygomycosis

B46.0 Pulmonary mucormycosis B46.1 Rhinocerebral mucormycosis B46.2 Gastrointestinal mucormycosis B46.3 Cutaneous mucormycosis

Subcutaneous mucormycosis

B46.4 Disseminated mucormycosis

Generalized mucormycosis

B46.5 Mucormycosis, unspecified B46.8 Other zygomycoses

Entomophthoromycosis

B46.9 Zygomycosis, unspecified

Phycomycosis NOS

 

  B47 Mycetoma

B47.0 Eumycetoma Madura foot, mycotic Maduromycosis

B47.1 Actinomycetoma

B47.9 Mycetoma, unspecified

Madura foot NOS

  B48 Other mycoses, not elsewhere classified

B48.0 Lobomycosis Keloidal blastomycosis Lobo disease

B48.1 Rhinosporidiosis B48.2 Allescheriasis

Infection due to Pseudallescheria boydii

Excl.: eumycetoma (B47.0)

B48.3 Geotrichosis

Geotrichum stomatitis

B48.4 Penicillosis

B48.7 Opportunistic mycoses

Mycoses caused by fungi of low virulence that can establish an infection only     as a consequence of factors such as the presence of debilitating disease or the administration of immunosuppressive and other therapeutic agents or radiation therapy. Most of the causal fungi are normally saprophytic in soil and decaying vegetation.

B48.8 Other specified mycoses

Adiaspiromycosis

  B49 Unspecified mycosis

Incl.: fungaemia NOS

Protozoal diseases (B50–B64)

Excl.: amoebiasis (A06.-)

other protozoal intestinal diseases (A07.-)

  B50 Plasmodium falciparum malaria

Incl.: mixed infections of Plasmodium falciparum with any other

Plasmodium species

 

B50.0 Plasmodium falciparum malaria with cerebral complications

Cerebral malaria NOS

B50.8 Other severe and complicated Plasmodium falciparum malaria

Severe or complicated Plasmodium falciparum malaria NOS

B50.9 Plasmodium falciparum malaria, unspecified

  B51 Plasmodium vivax malaria

Incl.: mixed infections of Plasmodium vivax with other Plasmodium

species, except Plasmodium falciparum

Excl.: when mixed with Plasmodium falciparum (B50.-) B51.0 Plasmodium vivax malaria with rupture of spleen B51.8 Plasmodium vivax malaria with other complications B51.9 Plasmodium vivax malaria without complication

Plasmodium vivax malaria NOS

  B52 Plasmodium malariae malaria

Incl.: mixed infections of Plasmodium malariae with other Plasmodium

species, except Plasmodium falciparum and Plasmodium vivax

Excl.: when mixed with Plasmodium:

• falciparum (B50.-)

• vivax (B51.-)

B52.0 Plasmodium malariae malaria with nephropathy

B52.8 Plasmodium malariae malaria with other complications B52.9 Plasmodium malariae malaria without complication

Plasmodium malariae malaria NOS

  B53 Other parasitologically confirmed malaria

B53.0 Plasmodium ovale malaria

Excl.: when mixed with Plasmodium:

• falciparum (B50.-)

• malariae (B52.-)

• vivax (B51.-)

B53.1 Malaria due to simian plasmodia

Excl.:  when mixed with Plasmodium:

• falciparum (B50.-)

• malariae (B52.-)

• ovale (B53.0)

• vivax (B51.-)

 

B53.8 Other parasitologically confirmed malaria, not elsewhere classified

Parasitologically confirmed malaria NOS

  B54 Unspecified malaria

Incl.: clinically diagnosed malaria without parasitological confirmation

  B55 Leishmaniasis

B55.0 Visceral leishmaniasis

Kala-azar

Post-kala-azar dermal leishmaniasis B55.1 Cutaneous leishmaniasis B55.2 Mucocutaneous leishmaniasis B55.9 Leishmaniasis, unspecified

  B56 African trypanosomiasis

B56.0 Gambiense trypanosomiasis

Infection due to Trypanosoma brucei gambiense

West African sleeping sickness

B56.1 Rhodesiense trypanosomiasis

East African sleeping sickness

Infection due to Trypanosoma brucei rhodesiense

B56.9 African trypanosomiasis, unspecified

Sleeping sickness NOS

Trypanosomiasis NOS, in places where African trypanosomiasis is prevalent

  B57 Chagas disease

Incl.:  American trypanosomiasis infection due to Trypanosoma cruzi

B57.0† Acute Chagas disease with heart involvement (I41.2*, I98.1*)

Acute Chagas disease with:

• cardiovascular involvement NEC (I98.1*)

• myocarditis (I41.2*)

B57.1 Acute Chagas disease without heart involvement

Acute Chagas disease NOS

B57.2 Chagas disease (chronic) with heart involvement

American trypanosomiasis NOS Chagas disease (chronic)(with):

• NOS

• cardiovascular involvement NEC† (I98.1*)

• myocarditis† (I41.2*)

Trypanosomiasis NOS, in places where Chagas disease is prevalent

 

B57.3 Chagas disease (chronic) with digestive system involvement B57.4 Chagas disease (chronic) with nervous system involvement B57.5 Chagas disease (chronic) with other organ involvement

  B58 Toxoplasmosis

Incl.: infection due to Toxoplasma gondii

Excl.: congenital toxoplasmosis (P37.1)

B58.0† Toxoplasma oculopathy

Toxoplasma chorioretinitis (H32.0*)

B58.1† Toxoplasma hepatitis (K77.0*)

B58.2† Toxoplasma meningoencephalitis (G05.2*) B58.3† Pulmonary toxoplasmosis (J17.3*)

B58.8 Toxoplasmosis with other organ involvement

Toxoplasma:

• myocarditis† (I41.2*)

• myositis† (M63.1*)

B58.9 Toxoplasmosis, unspecified

  B59† Pneumocystosis (J17.3*)

Incl.: pneumonia due to:

• Pneumocystis carinii

• Pneumocystis jirovecii

  B60 Other protozoal diseases, not elsewhere classified

Excl.:  cryptosporidiosis (A07.2) intestinal microsporidiosis (A07.8) isosporiasis (A07.3)

B60.0 Babesiosis

Piroplasmosis

B60.1 Acanthamoebiasis

Conjunctivitis due to Acanthamoeba† (H13.1*) Keratoconjunctivitis due to Acanthamoeba† (H19.2*)

B60.2 Naegleriasis

Primary amoebic meningoencephalitis† (G05.2*)

B60.8 Other specified protozoal diseases

Microsporidiosis

  B64 Unspecified protozoal disease

 

Helminthiases (B65–B83)

  B65 Schistosomiasis [bilharziasis]

Incl.: snail fever

B65.0 Schistosomiasis due to Schistosoma haematobium [urinary schistosomiasis]

B65.1 Schistosomiasis due to Schistosoma mansoni [intestinal schistosomiasis]

B65.2 Schistosomiasis due to Schistosoma japonicum

Asiatic schistosomiasis

B65.3 Cercarial dermatitis

Swimmer’s itch

B65.8 Other schistosomiases

Infection due to Schistosoma:

• intercalatum

• mattheei

• mekongi

B65.9 Schistosomiasis, unspecified

  B66 Other fluke infections

B66.0 Opisthorchiasis

Infection due to:

• cat liver fluke

• Opisthorchis (felineus)(viverrini)

B66.1 Clonorchiasis

Chinese liver fluke disease Infection due to Clonorchis sinensis Oriental liver fluke disease

B66.2 Dicrocoeliasis

Infection due to Dicrocoelium dendriticum

Lancet fluke infection

B66.3 Fascioliasis

Infection due to Fasciola:

• gigantica

• hepatica

• indica

Sheep liver fluke disease

 

B66.4 Paragonimiasis

Infection due to Paragonimus species Lung fluke disease

Pulmonary distomiasis

B66.5 Fasciolopsiasis

Infection due to Fasciolopsis buski

Intestinal distomiasis

B66.8 Other specified fluke infections

Echinostomiasis Heterophyiasis Metagonimiasis Nanophyetiasis Watsoniasis

B66.9 Fluke infection, unspecified

  B67 Echinococcosis

Incl.: hydatidosis

B67.0 Echinococcus granulosus infection of liver B67.1 Echinococcus granulosus infection of lung B67.2 Echinococcus granulosus infection of bone

B67.3 Echinococcus granulosus infection, other and multiple sites

B67.4 Echinococcus granulosus infection, unspecified

Dog tapeworm (infection)

B67.5 Echinococcus multilocularis infection of liver

B67.6 Echinococcus multilocularis infection, other and multiple sites B67.7 Echinococcus multilocularis infection, unspecified

B67.8 Echinococcosis, unspecified, of liver

B67.9 Echinococcosis, other and unspecified

Echinococcosis NOS

  B68 Taeniasis

Excl.:  cysticercosis (B69.-)

B68.0         Taenia solium taeniasis

Pork tapeworm (infection)

B68.1 Taenia saginata taeniasis

Beef tapeworm (infection)

Infection due to adult tapeworm Taenia saginata

B68.9 Taeniasis, unspecified

 

  B69 Cysticercosis

Incl.: cysticerciasis infection due to larval form of Taenia solium

B69.0 Cysticercosis of central nervous system B69.1 Cysticercosis of eye

B69.8 Cysticercosis of other sites B69.9 Cysticercosis, unspecified

  B70 Diphyllobothriasis and sparganosis

B70.0 Diphyllobothriasis

Diphyllobothrium (adult)(latum)(pacificum) infection Fish tapeworm (infection)

Excl.: larval diphyllobothriasis (B70.1)

B70.1 Sparganosis

Infection due to:

• Sparganum (mansoni)(proliferum)

• Spirometra larvae Larval diphyllobothriasis Spirometrosis

  B71 Other cestode infections

B71.0 Hymenolepiasis

Dwarf tapeworm (infection) Rat tapeworm (infection)

B71.1 Dipylidiasis

B71.8 Other specified cestode infections

Coenurosis

B71.9 Cestode infection, unspecified

Tapeworm (infection) NOS

  B72 Dracunculiasis

Incl.: Guinea worm infection

infection due to Dracunculus medinensis

  B73 Onchocerciasis

Incl.: Onchocerca volvulus infection onchocercosis

river blindness

  B74 Filariasis

Excl.: onchocerciasis (B73)

tropical (pulmonary) eosinophilia NOS (J82)

 

B74.0 Filariasis due to Wuchereria bancrofti

Bancroftian:

• elephantiasis

• filariasis

B74.1 Filariasis due to Brugia malayi B74.2 Filariasis due to Brugia timori B74.3 Loiasis

Calabar swelling

Eyeworm disease of Africa

Loa loa infection

B74.4 Mansonelliasis

Infection due to Mansonella:

• ozzardi

• perstans

• streptocerca

B74.8 Other filariases

Dirofilariasis

B74.9 Filariasis, unspecified

  B75 Trichinellosis

Incl.: infection due to Trichinella species trichiniasis

  B76 Hookworm diseases

Incl.: uncinariasis

B76.0 Ancylostomiasis

Infection due to Ancylostoma species

B76.1 Necatoriasis

Infection due to Necator americanus

B76.8 Other hookworm diseases B76.9 Hookworm disease, unspecified

Cutaneous larva migrans NOS

  B77 Ascariasis

Incl.: ascaridiasis

roundworm infection

B77.0 Ascariasis with intestinal complications B77.8 Ascariasis with other complications B77.9 Ascariasis, unspecified

 

  B78 Strongyloidiasis

Excl.: trichostrongyliasis (B81.2) B78.0 Intestinal strongyloidiasis B78.1 Cutaneous strongyloidiasis B78.7 Disseminated strongyloidiasis B78.9 Strongyloidiasis, unspecified

  B79 Trichuriasis

Incl.: trichocephaliasis

whipworm (disease)(infection)

  B80 Enterobiasis

Incl.: oxyuriasis

pinworm infection threadworm infection

  B81 Other intestinal helminthiases, not elsewhere classified

Excl.: angiostrongyliasis due to:

• Angiostrongylus costaricensis (B83.2)

• Parastrongylus costaricensis (B83.2)

B81.0 Anisakiasis

Infection due to Anisakis larvae

B81.1 Intestinal capillariasis

Capillariasis NOS

Infection due to Capillaria philippinensis

Excl.: hepatic capillariasis (B83.8)

B81.2 Trichostrongyliasis

B81.3 Intestinal angiostrongyliasis

Angiostrongyliasis due to

• Angiostrongylus costaricensis

• Parastrongylus costaricensis

B81.4 Mixed intestinal helminthiases

Infection due to intestinal helminths classifiable to more than one of the categories B65.0–B81.3 and B81.8

Mixed helminthiasis NOS

B81.8 Other specified intestinal helminthiases

Infection due to:

• Oesophagostomum species [oesophagostomiasis]

• Ternidens deminutus [ternidensiasis]

• Ternidens diminutus [ternidensiasis]

 

  B82 Unspecified intestinal parasitism B82.0 Intestinal helminthiasis, unspecified B82.9 Intestinal parasitism, unspecified

  B83 Other helminthiases

Excl.: capillariasis:

• NOS (B81.1)

• intestinal (B81.1)

B83.0 Visceral larva migrans

Toxocariasis

B83.1        Gnathostomiasis

Wandering swelling

B83.2 Angiostrongyliasis due to Parastrongylus cantonensis Angiostrongyliasis due to Angiostrongylus cantonensis Eosinophilic meningoencephalitis† (G05.2*)

Excl.: intestinal angiostrongyliasis (B81.3)

B83.3 Syngamiasis

Syngamosis

B83.4 Internal hirudiniasis

Excl.: external hirudiniasis (B88.3)

B83.8 Other specified helminthiases Acanthocephaliasis Gongylonemiasis

Hepatic capillariasis Metastrongyliasis Thelaziasis

B83.9 Helminthiasis, unspecified

Worms NOS

Excl.: intestinal helminthiasis NOS (B82.0)

Pediculosis, acariasis and other infestations (B85–B89)

  B85 Pediculosis and phthiriasis

B85.0 Pediculosis due to Pediculus humanus capitis

Head-louse infestation

B85.1 Pediculosis due to Pediculus humanus corporis

Body-louse infestation

 

B85.2 Pediculosis, unspecified B85.3 Phthiriasis

Infestation by:

• crab-louse

• Phthirus pubis

B85.4 Mixed pediculosis and phthiriasis

Infestation classifiable to more than one of the categories B85.0–B85.3

  B86 Scabies

Incl.: sarcoptic itch

  B87 Myiasis

Incl.: infestation by larvae of flies

B87.0 Cutaneous myiasis

Creeping myiasis

B87.1 Wound myiasis

Traumatic myiasis

B87.2 Ocular myiasis

B87.3 Nasopharyngeal myiasis

Laryngeal myiasis

B87.4 Aural myiasis

B87.8 Myiasis of other sites

Genitourinary myiasis Intestinal myiasis

B87.9 Myiasis, unspecified

  B88 Other infestations

B88.0 Other acariasis

Acarine dermatitis Dermatitis due to:

• Demodex species

• Dermanyssus gallinae

• Liponyssoides sanguineus

Trombiculosis

Excl.: scabies (B86)

B88.1 Tungiasis [sandflea infestation] B88.2 Other arthropod infestations

Scarabiasis

 

B88.3 External hirudiniasis

Leech infestation NOS

Excl.: internal hirudiniasis (B83.4)

B88.8 Other specified infestations Ichthyoparasitism due to Vandellia cirrhosa Linguatulosis

Porocephaliasis

B88.9 Infestation, unspecified

Infestation (skin) NOS Infestation by mites NOS Skin parasites NOS

  B89 Unspecified parasitic disease

Sequelae of infectious and parasitic diseases (B90–B94)

Note: Categories B90–B94 are to be used to indicate conditions in categories A00– B89 as the cause of sequelae, which are themselves classified elsewhere. The ‘sequelae’ include conditions specified as such; they also include late effects of diseases classifiable to the above categories if there is evidence that the disease itself is no longer present. For use of these categories, reference should be made to the morbidity or mortality coding rules and guidelines in Volume 2.

Not to be used for chronic infections. Code current infections to chronic or active infectious disease as appropriate.

  B90 Sequelae of tuberculosis

B90.0 Sequelae of central nervous system tuberculosis B90.1 Sequelae of genitourinary tuberculosis

B90.2 Sequelae of tuberculosis of bones and joints B90.8 Sequelae of tuberculosis of other organs

B90.9 Sequelae of respiratory and unspecified tuberculosis

Sequelae of tuberculosis NOS

  B91 Sequelae of poliomyelitis

Excl.: postpolio syndrome (G14)

  B92 Sequelae of leprosy

 

  B94 Sequelae of other and unspecified infectious and parasitic diseases

B94.0 Sequelae of trachoma

B94.1 Sequelae of viral encephalitis B94.2 Sequelae of viral hepatitis

B94.8 Sequelae of other specified infectious and parasitic diseases B94.9 Sequelae of unspecified infectious or parasitic disease

Bacterial, viral and other infectious agents (B95–B98)

Note:  These categories should never be used in primary coding. They are provided for use as supplementary or additional codes when it is desired to identify the infectious agent(s) in diseases classified elsewhere.

  B95 Streptococcus and Staphylococcus as the cause of diseases classified to other chapters

B95.0 Streptococcus, group A, as the cause of diseases classified to other chapters

B95.1 Streptococcus, group B, as the cause of diseases classified to other chapters

B95.2 Streptococcus, group D, and enterococcus as the cause of diseases classified to other chapters

B95.3 Streptococcus pneumoniae as the cause of diseases classified to other chapters

B95.4 Other Streptococcus as the cause of diseases classified to other chapters

B95.5 Unspecified Streptococcus as the cause of diseases classified to other chapters

B95.6 Staphylococcus aureus as the cause of diseases classified to other chapters

B95.7 Other Staphylococcus as the cause of diseases classified to other chapters

B95.8 Unspecified Staphylococcus as the cause of diseases classified to other chapters

 

  B96 Other specified bacterial agents as the cause of diseases classified to other chapters

B96.0 Mycoplasma pneumoniae [M. pneumoniae] as the cause of diseases classified to other chapters

Pleuro-pneumonia-like-organism [PPLO]

B96.1 Klebsiella pneumoniae [K. pneumoniae] as the cause of diseases classified to other chapters

B96.2 Escherichia coli [E. coli] as the cause of diseases classified to other chapters

B96.3 Haemophilus influenzae [H. influenzae] as the cause of diseases classified to other chapters

B96.4 Proteus (mirabilis)(morganii) as the cause of diseases classified to other chapters

B96.5 Pseudomonas (aeruginosa) as the cause of diseases classified to other chapters

B96.6 Bacillus fragilis [B. fragilis] as the cause of diseases classified to other chapters

B96.7 Clostridium perfringens [C. perfringens] as the cause of diseases classified to other chapters

B96.8 Other specified bacterial agents as the cause of diseases classified to other chapters

  B97 Viral agents as the cause of diseases classified to other chapters

B97.0 Adenovirus as the cause of diseases classified to other chapters

B97.1 Enterovirus as the cause of diseases classified to other chapters

Coxsackievirus Echovirus

B97.2 Coronavirus as the cause of diseases classified to other chapters

B97.3 Retrovirus as the cause of diseases classified to other chapters

Lentivirus Oncovirus

B97.4 Respiratory syncytial virus as the cause of diseases classified to other chapters

B97.5 Reovirus as the cause of diseases classified to other chapters

 

B97.6 Parvovirus as the cause of diseases classified to other chapters

B97.7 Papillomavirus as the cause of diseases classified to other chapters

B97.8 Other viral agents as the cause of diseases classified to other chapters

Human metapneumovirus

  B98 Other specified infectious agents as the cause of diseases classified to other chapters

B98.0 Helicobacter pylori [H.pylori] as the cause of diseases classified to other chapters

B98.1 Vibrio vulnificus as the cause of diseases classified to other chapters

Other infectious diseases (B99)

  B99 Other and unspecified infectious diseases

CHAPTER II

Neoplasms (C00–D48)

This chapter contains the following blocks:

C00–C97 Malignant neoplasms

C00–C75 Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic and related tissue

C00–C14 Malignant neoplasms of lip, oral cavity and pharynx C15–C26 Malignant neoplasms of digestive organs

C30–C39 Malignant neoplasms of respiratory and intrathoracic organs C40–C41 Malignant neoplasms of bone and articular cartilage C43–C44 Melanoma and other malignant neoplasms of skin C45–C49 Malignant neoplasms of mesothelial and soft tissue C50–C50 Malignant neoplasm of breast

C51–C58 Malignant neoplasms of female genital organs C60–C63 Malignant neoplasms of male genital organs C64–C68 Malignant neoplasms of urinary tract

C69–C72 Malignant neoplasms of eye, brain and other parts of central nervous system

C73–C75 Malignant neoplasms of thyroid and other endocrine glands C76–C80 Malignant neoplasms of ill-defined, secondary and unspecified sites C81–C96 Malignant neoplasms, stated or presumed to be primary, of

lymphoid, haematopoietic and related tissue

C97 Malignant neoplasms of independent (primary) multiple sites D00–D09 In situ neoplasms

D10–D36 Benign neoplasms

D37–D48 Neoplasms of uncertain or unknown behaviour

Notes

1. Primary, ill-defined, secondary and unspecified sites of malignant neoplasms

Categories C76−C80 include malignant neoplasms for which there is no clear indication of the original site of the cancer, or the cancer is stated to be ‘disseminated’, ‘scattered’ or ‘spread’ without mention of the primary site. In both cases the primary site is considered to be unknown.

2. Functional activity

All neoplasms are classified in this chapter, whether they are functionally active or   not. An additional code from Chapter IV may be used, if desired, to identify functional activity associated with any neoplasm. For example, catecholamine-producing malignant phaeochromocytoma of adrenal gland should be coded to C74 with additional code E27.5; basophil adenoma of pituitary gland with Cushing syndrome should be coded to D35.2 with additional code E24.0.

3. Morphology

There are a number of major morphological (histological) groups of malignant neoplasms: carcinomas including squamous (cell) and adenocarcinomas; sarcomas; other soft tissue tumours including mesotheliomas; lymphomas (Hodgkin and non- Hodgkin); leukaemia; other specified and site-specific types; and unspecified cancers. Cancer is a generic term and may be used for any of the above groups, although it      is rarely applied to the malignant neoplasms of lymphatic, haematopoietic and related tissue. ‘Carcinoma’ is sometimes used incorrectly as a synonym for ‘cancer’.

In Chapter II, neoplasms are classified predominantly by site within broad groupings for behaviour. In a few exceptional cases, morphology is indicated in the category and subcategory titles.

For those wishing to identify the histological type of neoplasm, the list of morphology codes of ICD-O is available for separate download online. The list formerly included in ICD-10 was outdated because it was derived from the second edition of the International classification of diseases for oncology (ICD-O). ICD-O is a dual-axis classification providing independent coding systems for topography and morphology. Morphology codes have six digits: the first four digits identify the histological type; the fifth digit  is the behaviour code (malignant primary, malignant secondary (metastatic), in situ, benign, uncertain whether malignant or benign); and the sixth digit is a grading code (differentiation) for solid tumours, and is also used as a special code for lymphomas and leukaemias.

The ICD-O lists can be downloaded from the classification website of WHO (www.who.int/classifications).

4. Use of subcategories in Chapter II

Attention is drawn to the special use of subcategory .8 in this chapter [see note 5]. Where it has been necessary to provide subcategories for ‘other’, these have generally been designated as subcategory .7.

5. Malignant neoplasms overlapping site boundaries and the use of subcategory .8 (overlapping lesion)

Categories C00−C75 classify primary malignant neoplasms according to their point   of origin. Many three-character categories are further divided into named parts or subcategories of the organ in question. A neoplasm that overlaps two or more contiguous sites within a three-character category, and whose point of origin cannot be determined, should be classified to the subcategory .8 (‘overlapping lesion’), unless the combination is specifically indexed elsewhere. For example, carcinoma of oesophagus and stomach is specifically indexed to C16.0 (cardia), while carcinoma of the tip and ventral surface of the tongue should be assigned to C02.8. On the other hand, carcinoma of the tip of the tongue extending to involve the ventral surface should be coded to C02.1, as the point of origin, the tip, is known. ‘Overlapping’ implies that the sites involved are contiguous (next to each other). Numerically consecutive subcategories are frequently anatomically contiguous, but this is not invariably so (e.g. bladder C67.-) and the coder may need to consult anatomical texts to determine the topographical relationships.

Sometimes a neoplasm overlaps the boundaries of three-character categories within certain systems. To take care of this, the following subcategories have been designated:

C02.8 Overlapping lesion of tongue

C08.8 Overlapping lesion of major salivary glands C14.8 Overlapping lesion of lip, oral cavity and pharynx C21.8 Overlapping lesion of rectum, anus and anal canal C24.8 Overlapping lesion of biliary tract

C26.8 Overlapping lesion of digestive system

C39.8 Overlapping lesion of respiratory and intrathoracic organs C41.8 Overlapping lesion of bone and articular cartilage

C49.8 Overlapping lesion of connective and soft tissue C57.8 Overlapping lesion of female genital organs C63.8 Overlapping lesion of male genital organs C68.8 Overlapping lesion of urinary organs

C72.8 Overlapping lesion of central nervous system

An example of this is a carcinoma of the stomach and small intestine, which should be coded to C26.8 (Overlapping lesion of digestive system).

6. Malignant neoplasms of ectopic tissue

Malignant neoplasms of ectopic tissue are to be coded to the site where they are found,

e.g. ectopic pancreatic malignant neoplasms of ovary are coded to ovary (C56).

7. Use of the Alphabetical index in coding neoplasms

In addition to site, morphology and behaviour must also be taken into consideration when coding neoplasms, and reference should always be made first to the Alphabetical index entry for the morphological description.

The introductory pages of Volume 3 include general instructions about the correct use of the Alphabetical index. The specific instructions and examples pertaining to neoplasms should be consulted to ensure correct use of the categories and subcategories in Chapter II.

8. Use of the International classification of diseases for oncology (ICD-O)

For certain morphological types, Chapter II provides a rather restricted topographical classification, or none at all. The topography codes of ICD-O use for all neoplasms essentially the same three- and four-character categories that Chapter II uses for malignant neoplasms (C00−C77, C80), thus providing increased specificity of site for other neoplasms (malignant secondary (metastatic), benign, in situ and uncertain or unknown).

It is therefore recommended that agencies interested in identifying both the site and morphology of tumours, e.g. cancer registries, cancer hospitals, pathology departments and other agencies specializing in cancer, use ICD-O.

Malignant neoplasms (C00–C97)

Use additional code (U85), if desired, to identify resistance, non-responsiveness and refractive properties of the neoplasm to antineoplastic drugs.

Malignant neoplasms, stated or presumed to be primary, of specified sites, except of lymphoid, haematopoietic and related tissue

(C00–C75)

Malignant neoplasms of lip, oral cavity and pharynx (C00–C14)

  C00 Malignant neoplasm of lip

Excl.: skin of lip (C43.0, C44.0)

C00.0 External upper lip

Upper lip:

• NOS

• lipstick area

• vermilion border

C00.1 External lower lip

Lower lip:

• NOS

• lipstick area

• vermilion border

C00.2 External lip, unspecified

Vermilion border NOS

C00.3 Upper lip, inner aspect

Upper lip:

• buccal aspect

• frenulum

• mucosa

• oral aspect

C00.4 Lower lip, inner aspect

Lower lip:

• buccal aspect

• frenulum

• mucosa

• oral aspect

C00.5 Lip, unspecified, inner aspect

Lip, not specified whether upper or lower:

• buccal aspect

• frenulum

• mucosa

• oral aspect

C00.6 Commissure of lip

C00.8 Overlapping lesion of lip

[See note 5 at the beginning of this chapter]

C00.9 Lip, unspecified

  C01 Malignant neoplasm of base of tongue

Incl.: dorsal surface of base of tongue fixed part of tongue NOS posterior third of tongue

  C02 Malignant neoplasm of other and unspecified parts of tongue

C02.0 Dorsal surface of tongue

Anterior two-thirds of tongue, dorsal surface

Excl.: dorsal surface of base of tongue (C01)

C02.1 Border of tongue

Tip of tongue

C02.2 Ventral surface of tongue

Anterior two-thirds of tongue, ventral surface Frenulum linguae

C02.3 Anterior two-thirds of tongue, part unspecified

Middle one third of tongue NOS Mobile part of tongue NOS

C02.4 Lingual tonsil

Excl.: tonsil NOS (C09.9)

C02.8 Overlapping lesion of tongue

[See note 5 at the beginning of this chapter]

Malignant neoplasm of tongue whose point of origin cannot be classified to any one of the categories C01–C02.4

C02.9 Tongue, unspecified

  C03 Malignant neoplasm of gum

Incl.: alveolar (ridge) mucosa gingiva

Excl.: malignant odontogenic neoplasms (C41.0–C41.1)

C03.0 Upper gum

C03.1 Lower gum

C03.9 Gum, unspecified

  C04 Malignant neoplasm of floor of mouth

C04.0 Anterior floor of mouth

Anterior to the premolar–canine junction

C04.1 Lateral floor of mouth

C04.8 Overlapping lesion of floor of mouth

[See note 5 at the beginning of this chapter]

C04.9 Floor of mouth, unspecified

  C05 Malignant neoplasm of palate

C05.0 Hard palate

C05.1 Soft palate

Excl.: nasopharyngeal surface of soft palate (C11.3)

C05.2 Uvula

C05.8 Overlapping lesion of palate

[See note 5 at the beginning of this chapter]

C05.9 Palate, unspecified

Roof of mouth

  C06 Malignant neoplasm of other and unspecified parts of mouth

C06.0 Cheek mucosa Buccal mucosa NOS Internal cheek

C06.1 Vestibule of mouth

Buccal sulcus (upper)(lower) Labial sulcus (upper)(lower)

C06.2 Retromolar area

C06.8 Overlapping lesion of other and unspecified parts of mouth

[See note 5 at the beginning of this chapter]

C06.9 Mouth, unspecified

Minor salivary gland, unspecified site Oral cavity NOS

  C07 Malignant neoplasm of parotid gland

  C08 Malignant neoplasm of other and unspecified major salivary glands

Excl.: malignant neoplasms of specified minor salivary glands which are classified according to their anatomical location

malignant neoplasms of minor salivary glands NOS (C06.9) parotid gland (C07)

C08.0 Submandibular gland

Submaxillary gland

C08.1 Sublingual gland

C08.8 Overlapping lesion of major salivary glands

[See note 5 at the beginning of this chapter]

Malignant neoplasm of major salivary glands whose point of origin cannot be classified to any one of the categories C07–C08.1

C08.9 Major salivary gland, unspecified

Salivary gland (major) NOS

  C09 Malignant neoplasm of tonsil

Excl.: lingual tonsil (C02.4) pharyngeal tonsil (C11.1)

C09.0 Tonsillar fossa

C09.1 Tonsillar pillar (anterior)(posterior)

C09.8 Overlapping lesion of tonsil

[See note 5 at the beginning of this chapter]

C09.9 Tonsil, unspecified

Tonsil:

• NOS

• faucial

• palatine

  C10 Malignant neoplasm of oropharynx

Excl.: tonsil (C09.-)

C10.0 Vallecula

C10.1 Anterior surface of epiglottis Epiglottis, free border [margin] Glossoepiglottic fold(s)

Excl.: epiglottis (suprahyoid portion) NOS (C32.1)

C10.2 Lateral wall of oropharynx C10.3 Posterior wall of oropharynx C10.4 Branchial cleft

Branchial cyst [site of neoplasm]

C10.8 Overlapping lesion of oropharynx [See note 5 at the beginning of this chapter] Junctional region of oropharynx

C10.9 Oropharynx, unspecified

  C11 Malignant neoplasm of nasopharynx

C11.0 Superior wall of nasopharynx

Roof of nasopharynx

C11.1 Posterior wall of nasopharynx

Adenoid Pharyngeal tonsil

C11.2 Lateral wall of nasopharynx

Fossa of Rosenmüller Opening of auditory tube Pharyngeal recess

C11.3 Anterior wall of nasopharynx

Floor of nasopharynx

Nasopharyngeal (anterior)(posterior) surface of soft palate Posterior margin of nasal:

• choana

• septum

C11.8 Overlapping lesion of nasopharynx

[See note 5 at the beginning of this chapter]

C11.9 Nasopharynx, unspecified

Nasopharyngeal wall NOS

  C12 Malignant neoplasm of piriform sinus

Incl.: piriform fossa

  C13 Malignant neoplasm of hypopharynx

Excl.: piriform sinus (C12)

C13.0 Postcricoid region

C13.1 Aryepiglottic fold, hypopharyngeal aspect

Aryepiglottic fold:

• NOS

• marginal zone

Excl.: aryepiglottic fold, laryngeal aspect (C32.1)

C13.2 Posterior wall of hypopharynx C13.8 Overlapping lesion of hypopharynx

[See note 5 at the beginning of this chapter]

C13.9 Hypopharynx, unspecified

Hypopharyngeal wall NOS

  C14 Malignant neoplasm of other and ill-defined sites in the lip, oral cavity and pharynx

Excl.: oral cavity NOS (C06.9) C14.0 Pharynx, unspecified C14.2 Waldeyer’s ring

C14.8 Overlapping lesion of lip, oral cavity and pharynx

[See note 5 at the beginning of this chapter]

Malignant neoplasm of lip, oral cavity and pharynx whose point of origin cannot be classified to any one of the categories C00–C14.2

Malignant neoplasms of digestive organs (C15–C26)

  C15 Malignant neoplasm of oesophagus

Note: Two alternative subclassifications are given:

.0–.2 by anatomical description

.3–.5 by thirds

This departure from the principle that categories should be mutually exclusive is deliberate, since both forms of terminology are in use but the resulting anatomical divisions are not analogous.

C15.0 Cervical part of oesophagus C15.1 Thoracic part of oesophagus C15.2 Abdominal part of oesophagus C15.3 Upper third of oesophagus C15.4 Middle third of oesophagus C15.5 Lower third of oesophagus

C15.8 Overlapping lesion of oesophagus

[See note 5 at the beginning of this chapter]

C15.9 Oesophagus, unspecified

  C16 Malignant neoplasm of stomach

C16.0 Cardia

Cardiac orifice

Cardio-oesophageal junction Gastro-oesophageal junction Oesophagus and stomach

C16.1 Fundus of stomach C16.2 Body of stomach C16.3 Pyloric antrum

Gastric antrum

C16.4 Pylorus Prepylorus Pyloric canal

C16.5 Lesser curvature of stomach, unspecified

Lesser curvature of stomach, not classifiable to C16.1–C16.4

C16.6 Greater curvature of stomach, unspecified

Greater curvature of stomach, not classifiable to C16.0–C16.4

C16.8 Overlapping lesion of stomach

[See note 5 at the beginning of this chapter]

C16.9 Stomach, unspecified

Gastric cancer NOS

  C17 Malignant neoplasm of small intestine

C17.0 Duodenum

C17.1 Jejunum

C17.2 Ileum

Excl.: ileocaecal valve (C18.0)

C17.3 Meckel’s diverticulum

C17.8 Overlapping lesion of small intestine

[See note 5 at the beginning of this chapter]

C17.9 Small intestine, unspecified

  C18 Malignant neoplasm of colon

C18.0 Caecum

Ileocaecal valve

C18.1 Appendix

C18.2 Ascending colon C18.3 Hepatic flexure C18.4 Transverse colon C18.5 Splenic flexure C18.6 Descending colon C18.7 Sigmoid colon

Sigmoid (flexure)

Excl.: rectosigmoid junction (C19)

C18.8 Overlapping lesion of colon

[See note 5 at the beginning of this chapter]

C18.9 Colon, unspecified

Large intestine NOS

  C19 Malignant neoplasm of rectosigmoid junction

Incl.: colon with rectum rectosigmoid (colon)

  C20 Malignant neoplasm of rectum

Incl.: rectal ampulla

  C21 Malignant neoplasm of anus and anal canal

C21.0 Anus, unspecified

Excl.: anal:

• margin (C43.5, C44.5)

• skin (C43.5, C44.5)

perianal skin (C43.5, C44.5)

C21.1 Anal canal

Anal sphincter

C21.2 Cloacogenic zone

C21.8 Overlapping lesion of rectum, anus and anal canal

[See note 5 at the beginning of this chapter] Anorectal junction

Anorectum

Malignant neoplasm of rectum, anus and anal canal whose point of origin cannot be classified to any one of the categories C20–C21.2

  C22 Malignant neoplasm of liver and intrahepatic bile ducts

Excl.: biliary tract NOS (C24.9)

secondary malignant neoplasm of liver (C78.7)

C22.0 Liver cell carcinoma

Hepatocellular carcinoma Hepatoma

C22.1 Intrahepatic bile duct carcinoma

Cholangiocarcinoma

C22.2 Hepatoblastoma C22.3 Angiosarcoma of liver

Kupffer cell sarcoma

C22.4 Other sarcomas of liver

C22.7 Other specified carcinomas of liver C22.9 Liver, unspecified

 

  C23 Malignant neoplasm of gallbladder

  C24 Malignant neoplasm of other and unspecified parts of biliary tract

Excl.: intrahepatic bile duct (C22.1)

C24.0 Extrahepatic bile duct

Biliary duct or passage NOS Common bile duct

Cystic duct Hepatic duct

C24.1 Ampulla of Vater

C24.8 Overlapping lesion of biliary tract

[See note 5 at the beginning of this chapter]

Malignant neoplasm involving both intrahepatic and extrahepatic bile ducts

Malignant neoplasm of biliary tract whose point of origin cannot be classified to any one of the categories C22.0–C24.1

C24.9 Biliary tract, unspecified

  C25 Malignant neoplasm of pancreas

C25.0 Head of pancreas C25.1 Body of pancreas C25.2 Tail of pancreas C25.3 Pancreatic duct C25.4 Endocrine pancreas

Islets of Langerhans

C25.7 Other parts of pancreas

Neck of pancreas

C25.8 Overlapping lesion of pancreas

[See note 5 at the beginning of this chapter]

C25.9 Pancreas, unspecified

  C26 Malignant neoplasm of other and ill-defined digestive organs

Excl.: peritoneum and retroperitoneum (C48.-)

C26.0 Intestinal tract, part unspecified

Intestine NOS

 

C26.1 Spleen

Excl.: follicular lymphoma (C82.-) Hodgkin lymphoma (C81.-)

mature T/NK-cell lymphomas (C84.-) non-follicular lymphoma (C83.-)

non-Hodgkin lymphoma, other and unspecified types (C85.-)

C26.8 Overlapping lesion of digestive system

[See note 5 at the beginning of this chapter]

Malignant neoplasm of digestive organs whose point of origin cannot be classified to any one of the categories C15–C26.1

Excl.: cardio-oesophageal junction (C16.0)

C26.9 Ill-defined sites within the digestive system

Alimentary canal or tract NOS Gastrointestinal tract NOS

Malignant neoplasms of respiratory and intrathoracic organs

(C30–C39)

Incl.: middle ear

Excl.: mesothelioma (C45.-)

  C30 Malignant neoplasm of nasal cavity and middle ear

C30.0 Nasal cavity Cartilage of nose Concha, nasal Internal nose Septum of nose Vestibule of nose

Excl.: nasal bone (C41.0) nose NOS (C76.0)

olfactory bulb (C72.2)

posterior margin of nasal septum and choana (C11.3) skin of nose (C43.3, C44.3)

C30.1 Middle ear Eustachian tube Inner ear Mastoid air cells

Excl.: auricular canal (external) (C43.2, C44.2) bone of ear (meatus) (C41.0)

cartilage of ear (C49.0)

skin of (external) ear (C43.2, C44.2)

 

  C31 Malignant neoplasm of accessory sinuses

C31.0 Maxillary sinus

Antrum (Highmore)(maxillary)

C31.1 Ethmoidal sinus C31.2 Frontal sinus C31.3 Sphenoidal sinus

C31.8 Overlapping lesion of accessory sinuses

[See note 5 at the beginning of this chapter]

C31.9 Accessory sinus, unspecified

  C32 Malignant neoplasm of larynx

C32.0 Glottis

Intrinsic larynx

Vocal cord (true) NOS

C32.1 Supraglottis

Aryepiglottic fold, laryngeal aspect Epiglottis (suprahyoid portion) NOS Extrinsic larynx

False vocal cord

Posterior (laryngeal) surface of epiglottis Ventricular bands

Excl.: anterior surface of epiglottis (C10.1) aryepiglottic fold:

• NOS (C13.1)

• hypopharyngeal aspect (C13.1)

• marginal zone (C13.1)

C32.2 Subglottis

C32.3 Laryngeal cartilage

C32.8 Overlapping lesion of larynx

[See note 5 at the beginning of this chapter]

C32.9 Larynx, unspecified

  C33 Malignant neoplasm of trachea

 

  C34 Malignant neoplasm of bronchus and lung

C34.0 Main bronchus

Carina

Hilus (of lung)

C34.1 Upper lobe, bronchus or lung C34.2 Middle lobe, bronchus or lung C34.3 Lower lobe, bronchus or lung

C34.8 Overlapping lesion of bronchus and lung

[See note 5 at the beginning of this chapter]

C34.9 Bronchus or lung, unspecified

  C37 Malignant neoplasm of thymus

  C38 Malignant neoplasm of heart, mediastinum and pleura

Excl.: mesothelioma (C45.-)

C38.0 Heart

Pericardium

Excl.: great vessels (C49.3) C38.1 Anterior mediastinum C38.2 Posterior mediastinum

C38.3 Mediastinum, part unspecified C38.4 Pleura

C38.8 Overlapping lesion of heart, mediastinum and pleura

[See note 5 at the beginning of this chapter]

  C39 Malignant neoplasm of other and ill-defined sites in the respiratory system and intrathoracic organs

Excl.: intrathoracic NOS (C76.1) thoracic NOS (C76.1)

C39.0 Upper respiratory tract, part unspecified

C39.8 Overlapping lesion of respiratory and intrathoracic organs

[See note 5 at the beginning of this chapter]

Malignant neoplasm of respiratory and intrathoracic organs whose point of origin cannot be classified to any one of the categories C30–C39.0

C39.9 Ill-defined sites within the respiratory system

Respiratory tract NOS

 

Malignant neoplasms of bone and articular cartilage (C40–C41)

Excl.: bone marrow NOS (C96.7) synovia (C49.-)

  C40 Malignant neoplasm of bone and articular cartilage of limbs

C40.0 Scapula and long bones of upper limb C40.1 Short bones of upper limb

C40.2 Long bones of lower limb C40.3 Short bones of lower limb

C40.8 Overlapping lesion of bone and articular cartilage of limbs

[See note 5 at the beginning of this chapter]

C40.9 Bone and articular cartilage of limb, unspecified

  C41 Malignant neoplasm of bone and articular cartilage of other and unspecified sites

Excl.: bones of limbs (C40.-) cartilage of:

• ear (C49.0)

• larynx (C32.3)

• limbs (C40.-)

• nose (C30.0)

C41.0 Bones of skull and face

Maxilla (superior) Orbital bone

Excl.: carcinoma, any type except intraosseous or odontogenic of:

• maxillary sinus (C31.0)

• upper jaw (C03.0)

jaw bone (lower) (C41.1)

C41.1 Mandible

Lower jaw bone

Excl.: carcinoma, any type except intraosseous or odontogenic of:

• jaw NOS (C03.9)

• jaw NOS

• lower (C03.1)

upper jaw bone (C41.0)

C41.2 Vertebral column

Excl.: sacrum and coccyx (C41.4)

 

C41.3 Ribs, sternum and clavicle

C41.4 Pelvic bones, sacrum and coccyx

C41.8 Overlapping lesion of bone and articular cartilage

[See note 5 at the beginning of this chapter]

Malignant neoplasm of bone and articular cartilage whose point of origin cannot be classified to any one of the categories C40–C41.4

C41.9 Bone and articular cartilage, unspecified

Melanoma and other malignant neoplasms of skin (C43–C44)

  C43 Malignant melanoma of skin

Excl.: malignant melanoma of skin of genital organs (C51–C52, C60.-, C63.-)

C43.0 Malignant melanoma of lip

Excl.: vermilion border of lip (C00.0–C00.2)

C43.1 Malignant melanoma of eyelid, including canthus

C43.2 Malignant melanoma of ear and external auricular canal C43.3 Malignant melanoma of other and unspecified parts of face C43.4 Malignant melanoma of scalp and neck

C43.5 Malignant melanoma of trunk

Anal:

• margin

• skin Perianal skin Skin of breast

Excl.: anus NOS (C21.0)

C43.6 Malignant melanoma of upper limb, including shoulder C43.7 Malignant melanoma of lower limb, including hip C43.8 Overlapping malignant melanoma of skin

[See note 5 at the beginning of this chapter]

C43.9 Malignant melanoma of skin, unspecified

Melanoma (malignant) NOS

 

  C44 Other malignant neoplasms of skin

Incl.: malignant neoplasm of:

• sebaceous glands

• sweat glands

Excl.: Kaposi sarcoma (C46.-)

malignant melanoma of skin (C43.-)

skin of genital organs (C51–C52, C60.-, C63.-)

C44.0 Skin of lip

Basal cell carcinoma of lip

Excl.: malignant neoplasm of lip (C00.-)

C44.1 Skin of eyelid, including canthus

Excl.: connective tissue of eyelid (C49.0)

C44.2 Skin of ear and external auricular canal

Excl.: connective tissue of ear (C49.0)

C44.3 Skin of other and unspecified parts of face C44.4 Skin of scalp and neck

C44.5 Skin of trunk

Anal:

• margin

• skin Perianal skin Skin of breast

Excl.: anus NOS (C21.0)

C44.6 Skin of upper limb, including shoulder C44.7 Skin of lower limb, including hip C44.8 Overlapping lesion of skin

[See note 5 at the beginning of this chapter]

C44.9 Malignant neoplasm of skin, unspecified

Malignant neoplasms of mesothelial and soft tissue (C45–C49)

  C45 Mesothelioma

C45.0 Mesothelioma of pleura

Excl.: other malignant neoplasms of pleura (C38.4)

 

C45.1 Mesothelioma of peritoneum

Mesentery Mesocolon Omentum

Peritoneum (parietal)(pelvic)

Excl.: other malignant neoplasms of peritoneum (C48.-)

C45.2 Mesothelioma of pericardium

Excl.: other malignant neoplasms of pericardium (C38.0)

C45.7 Mesothelioma of other sites C45.9 Mesothelioma, unspecified

  C46 Kaposi sarcoma

C46.0 Kaposi sarcoma of skin

C46.1 Kaposi sarcoma of soft tissue C46.2 Kaposi sarcoma of palate

C46.3 Kaposi sarcoma of lymph nodes C46.7 Kaposi sarcoma of other sites C46.8 Kaposi sarcoma of multiple organs C46.9 Kaposi sarcoma, unspecified

  C47 Malignant neoplasm of peripheral nerves and autonomic nervous system

Incl.: sympathetic and parasympathetic nerves and ganglia

C47.0 Peripheral nerves of head, face and neck

Excl.: peripheral nerves of orbit (C69.6)

C47.1 Peripheral nerves of upper limb, including shoulder C47.2 Peripheral nerves of lower limb, including hip C47.3 Peripheral nerves of thorax

C47.4 Peripheral nerves of abdomen C47.5 Peripheral nerves of pelvis

C47.6 Peripheral nerves of trunk, unspecified

C47.8 Overlapping lesion of peripheral nerves and autonomic nervous system

[See note 5 at the beginning of this chapter]

C47.9 Peripheral nerves and autonomic nervous system, unspecified

 

  C48 Malignant neoplasm of retroperitoneum and peritoneum

Excl.: Kaposi sarcoma (C46.1) mesothelioma (C45.-)

C48.0 Retroperitoneum

C48.1 Specified parts of peritoneum

Mesentery Mesocolon Omentum Peritoneum:

• parietal

• pelvic

C48.2 Peritoneum, unspecified

C48.8 Overlapping lesion of retroperitoneum and peritoneum

[See note 5 at the beginning of this chapter]

  C49 Malignant neoplasm of other connective and soft tissue

Incl.: blood vessel bursa cartilage fascia

fat

ligament, except uterine lymphatic vessel muscle

synovia

tendon (sheath)

Excl.: cartilage (of):

• articular (C40–C41)

• larynx (C32.3)

• nose (C30.0)

connective tissue of breast (C50.-) Kaposi sarcoma (C46.-) mesothelioma (C45.-)

peripheral nerves and autonomic nervous system (C47.-) peritoneum (C48.-)

retroperitoneum (C48.0)

C49.0 Connective and soft tissue of head, face and neck

Connective tissue of:

• ear

• eyelid

Excl.: connective tissue of orbit (C69.6)

C49.1 Connective and soft tissue of upper limb, including shoulder C49.2 Connective and soft tissue of lower limb, including hip

 

C49.3 Connective and soft tissue of thorax

Axilla Diaphragm Great vessels

Excl.: breast (C50.-)

heart (C38.0)

mediastinum (C38.1–C38.3) thymus (C37)

C49.4 Connective and soft tissue of abdomen

Abdominal wall Hypochondrium

C49.5 Connective and soft tissue of pelvis

Buttock Groin Perineum

C49.6 Connective and soft tissue of trunk, unspecified

Back NOS

C49.8 Overlapping lesion of connective and soft tissue

[See note 5 at the beginning of this chapter]

Malignant neoplasm of connective and soft tissue whose point of origin cannot be classified to any one of the categories C47–C49.6

C49.9 Connective and soft tissue, unspecified

Malignant neoplasm of breast (C50)

  C50 Malignant neoplasm of breast

Incl.: connective tissue of breast

Excl.: skin of breast (C43.5, C44.5)

C50.0 Nipple and areola

C50.1 Central portion of breast

C50.2 Upper-inner quadrant of breast C50.3 Lower-inner quadrant of breast C50.4 Upper-outer quadrant of breast C50.5 Lower-outer quadrant of breast C50.6 Axillary tail of breast

C50.8 Overlapping lesion of breast

[See note 5 at the beginning of this chapter]

C50.9 Breast, unspecified

 

Malignant neoplasms of female genital organs (C51–C58)

Incl.: skin of female genital organs

  C51 Malignant neoplasm of vulva

C51.0 Labium majus

Bartholin [greater vestibular] gland

C51.1 Labium minus

C51.2 Clitoris

C51.8 Overlapping lesion of vulva

[See note 5 at the beginning of this chapter]

C51.9 Vulva, unspecified

External female genitalia NOS Pudendum

  C52 Malignant neoplasm of vagina

  C53 Malignant neoplasm of cervix uteri

C53.0 Endocervix

C53.1 Exocervix

C53.8 Overlapping lesion of cervix uteri

[See note 5 at the beginning of this chapter]

C53.9 Cervix uteri, unspecified

  C54 Malignant neoplasm of corpus uteri

C54.0 Isthmus uteri

Lower uterine segment

C54.1 Endometrium

C54.2 Myometrium

C54.3 Fundus uteri

C54.8 Overlapping lesion of corpus uteri

[See note 5 at the beginning of this chapter]

C54.9 Corpus uteri, unspecified

  C55 Malignant neoplasm of uterus, part unspecified

  C56 Malignant neoplasm of ovary

 

  C57 Malignant neoplasm of other and unspecified female genital organs

C57.0 Fallopian tube

Oviduct Uterine tube

C57.1 Broad ligament C57.2 Round ligament C57.3 Parametrium

Uterine ligament NOS

C57.4 Uterine adnexa, unspecified

C57.7 Other specified female genital organs

Wolffian body or duct

C57.8 Overlapping lesion of female genital organs

[See note 5 at the beginning of this chapter]

Malignant neoplasm of female genital organs whose point of origin cannot be classified to any one of the categories C51–C57.7, C58 Tubo-ovarian

Utero-ovarian

C57.9 Female genital organ, unspecified

Female genitourinary tract NOS

  C58 Malignant neoplasm of placenta

Incl.: choriocarcinoma NOS chorionepithelioma NOS

Excl.: chorioadenoma (destruens) (D39.2) hydatidiform mole:

• NOS (O01.9)

• invasive (D39.2)

• malignant (D39.2)

Malignant neoplasms of male genital organs (C60–C63)

Incl.: skin of male genital organs

  C60 Malignant neoplasm of penis

C60.0 Prepuce

Foreskin

C60.1 Glans penis

C60.2 Body of penis

Corpus cavernosum

 

C60.8 Overlapping lesion of penis

[See note 5 at the beginning of this chapter]

C60.9 Penis, unspecified

Skin of penis NOS

  C61 Malignant neoplasm of prostate

  C62 Malignant neoplasm of testis

C62.0 Undescended testis

Ectopic testis [site of neoplasm] Retained testis [site of neoplasm]

C62.1 Descended testis

Scrotal testis

C62.9 Testis, unspecified

  C63 Malignant neoplasm of other and unspecified male genital organs

C63.0 Epididymis C63.1 Spermatic cord C63.2 Scrotum

Skin of scrotum

C63.7 Other specified male genital organs

Seminal vesicle Tunica vaginalis

C63.8 Overlapping lesion of male genital organs

[See note 5 at the beginning of this chapter]

Malignant neoplasm of male genital organs whose point of origin cannot be classified to any one of the categories C60–C63.7

C63.9 Male genital organ, unspecified

Male genitourinary tract NOS

Malignant neoplasms of urinary tract (C64–C68)

  C64 Malignant neoplasm of kidney, except renal pelvis

Excl.: renal:

• calyces (C65)

• pelvis (C65)

 

  C65 Malignant neoplasm of renal pelvis

Incl.: pelviureteric junction renal calyces

  C66 Malignant neoplasm of ureter

Excl.: ureteric orifice of bladder (C67.6)

  C67 Malignant neoplasm of bladder

C67.0 Trigone of bladder C67.1 Dome of bladder C67.2 Lateral wall of bladder

C67.3 Anterior wall of bladder

C67.4 Posterior wall of bladder C67.5 Bladder neck

Internal urethral orifice

C67.6 Ureteric orifice

C67.7 Urachus

C67.8 Overlapping lesion of bladder

[See note 5 at the beginning of this chapter]

C67.9 Bladder, unspecified

  C68 Malignant neoplasm of other and unspecified urinary organs

Excl.: genitourinary tract NOS:

• female (C57.9)

• male (C63.9)

C68.0 Urethra

Excl.: urethral orifice of bladder (C67.5)

C68.1 Paraurethral gland

C68.8 Overlapping lesion of urinary organs

[See note 5 at the beginning of this chapter]

Malignant neoplasm of urinary organs whose point of origin cannot be classified to any one of the categories C64–C68.1

C68.9 Urinary organ, unspecified

Urinary system NOS

 

Malignant neoplasms of eye, brain and other parts of central nervous system

(C69–C72)

  C69 Malignant neoplasm of eye and adnexa

Excl.: connective tissue of eyelid (C49.0) eyelid (skin) (C43.1, C44.1)

optic nerve (C72.3)

C69.0 Conjunctiva

C69.1 Cornea

C69.2 Retina

C69.3 Choroid

C69.4 Ciliary body

C69.5 Lacrimal gland and duct

Lacrimal sac Nasolacrimal duct

C69.6 Orbit

Connective tissue of orbit Extraocular muscle Peripheral nerves of orbit Retrobulbar tissue

Retro-ocular tissue

Excl.: orbital bone (C41.0)

C69.8 Overlapping lesion of eye and adnexa

[See note 5 at the beginning of this chapter]

C69.9 Eye, unspecified

Eyeball

  C70 Malignant neoplasm of meninges

C70.0 Cerebral meninges C70.1 Spinal meninges C70.9 Meninges, unspecified

  C71 Malignant neoplasm of brain

Excl.: cranial nerves (C72.2–C72.5) retrobulbar tissue (C69.6)

C71.0 Cerebrum, except lobes and ventricles

Supratentorial NOS

 

C71.1 Frontal lobe

C71.2 Temporal lobe

C71.3 Parietal lobe

C71.4 Occipital lobe C71.5 Cerebral ventricle

Excl.: fourth ventricle (C71.7)

C71.6 Cerebellum

C71.7 Brain stem Fourth ventricle Infratentorial NOS

C71.8 Overlapping lesion of brain

[See note 5 at the beginning of this chapter]

C71.9 Brain, unspecified

  C72 Malignant neoplasm of spinal cord, cranial nerves and other parts of central nervous system

Excl.: meninges (C70.-)

peripheral nerves and autonomic nervous system (C47.-)

C72.0 Spinal cord

C72.1 Cauda equina C72.2 Olfactory nerve

Olfactory bulb

C72.3 Optic nerve C72.4 Acoustic nerve

C72.5 Other and unspecified cranial nerves

Cranial nerve NOS

C72.8 Overlapping lesion of brain and other parts of central nervous system

[See note 5 at the beginning of this chapter]

Malignant neoplasm of brain and other parts of central nervous system whose point of origin cannot be classified to any one of the categories C70–C72.5

C72.9 Central nervous system, unspecified

Nervous system NOS

 

Malignant neoplasms of thyroid and other endocrine glands

(C73–C75)

  C73 Malignant neoplasm of thyroid gland

  C74 Malignant neoplasm of adrenal gland

C74.0 Cortex of adrenal gland C74.1 Medulla of adrenal gland C74.9 Adrenal gland, unspecified

  C75 Malignant neoplasm of other endocrine glands and related structures

Excl.: adrenal gland (C74.-) endocrine pancreas (C25.4) ovary (C56)

testis (C62.-) thymus (C37) thyroid gland (C73)

C75.0 Parathyroid gland C75.1 Pituitary gland

C75.2 Craniopharyngeal duct C75.3 Pineal gland

C75.4 Carotid body

C75.5 Aortic body and other paraganglia C75.8 Pluriglandular involvement, unspecified

Note: If the sites of multiple involvement are known, they should be

coded separately.

C75.9 Endocrine gland, unspecified

 

Malignant neoplasms of ill-defined, secondary and unspecified sites

(C76–C80)

  C76 Malignant neoplasm of other and ill-defined sites

Excl.: malignant neoplasm of:

• genitourinary tract NOS:

– female (C57.9)

– male (C63.9)

• lymphoid, haematopoietic and related tissue (C81–C96)

• unspecified site (C80.-)

C76.0 Head, face and neck

Cheek NOS Nose NOS

C76.1 Thorax

Axilla NOS Intrathoracic NOS Thoracic NOS

C76.2 Abdomen

C76.3 Pelvis

Groin NOS

Sites overlapping systems within the pelvis, such as:

• rectovaginal (septum)

• rectovesical (septum)

C76.4 Upper limb

C76.5 Lower limb

C76.7 Other ill-defined sites

C76.8 Overlapping lesion of other and ill-defined sites

[See note 5 at the beginning of this chapter]

  C77 Secondary and unspecified malignant neoplasm of lymph nodes

Excl.: malignant neoplasm of lymph nodes, specified as primary (C81–C86, C96.-)

C77.0 Lymph nodes of head, face and neck

Supraclavicular lymph nodes C77.1 Intrathoracic lymph nodes C77.2 Intra-abdominal lymph nodes

C77.3 Axillary and upper limb lymph nodes

Pectoral lymph nodes

 

C77.4 Inguinal and lower limb lymph nodes C77.5 Intrapelvic lymph nodes

C77.8 Lymph nodes of multiple regions C77.9 Lymph node, unspecified

  C78 Secondary malignant neoplasm of respiratory and digestive organs

C78.0 Secondary malignant neoplasm of lung

C78.1 Secondary malignant neoplasm of mediastinum C78.2 Secondary malignant neoplasm of pleura

Malignant pleural effusion NOS

C78.3 Secondary malignant neoplasm of other and unspecified respiratory organs

C78.4 Secondary malignant neoplasm of small intestine

C78.5 Secondary malignant neoplasm of large intestine and rectum C78.6 Secondary malignant neoplasm of retroperitoneum and

peritoneum

Malignant ascites NOS

C78.7 Secondary malignant neoplasm of liver and intrahepatic bile duct

C78.8 Secondary malignant neoplasm of other and unspecified digestive organs

  C79 Secondary malignant neoplasm of other and unspecified sites

C79.0 Secondary malignant neoplasm of kidney and renal pelvis C79.1 Secondary malignant neoplasm of bladder and other and

unspecified urinary organs

C79.2 Secondary malignant neoplasm of skin

C79.3 Secondary malignant neoplasm of brain and cerebral meninges

C79.4 Secondary malignant neoplasm of other and unspecified parts of nervous system

C79.5 Secondary malignant neoplasm of bone and bone marrow C79.6 Secondary malignant neoplasm of ovary

C79.7 Secondary malignant neoplasm of adrenal gland

 

C79.8 Secondary malignant neoplasm of other specified sites C79.9 Secondary malignant neoplasm, unspecified site

Carcinomatosis (secondary)

Disseminated (secondary):

• cancer NOS

• malignancy NOS Generalized (secondary):

• cancer NOS

• malignancy NOS

Multiple secondary cancer NOS Sarcomatosis (secondary) NOS

  C80 Malignant neoplasm, without specification of site

C80.0 Malignant neoplasm, primary site unknown, so stated

Primary site unknown

C80.9 Malignant neoplasm, primary site unspecified

Cancer NOS Carcinoma NOS Malignancy NOS

Malignant cachexia NOS Multiple cancer NOS

Excl.: multiple secondary cancer NOS (C79.9)

secondary malignant neoplasm, unspecified site (C79.9)

Malignant neoplasms, stated or presumed to be primary, of lymphoid, haematopoietic and related tissue

(C81–C96)

Excl.: secondary and unspecified neoplasm of lymph nodes (C77.-)

  C81 Hodgkin lymphoma

C81.0 Nodular lymphocyte predominant Hodgkin lymphoma C81.1 Nodular sclerosis (classical) Hodgkin lymphoma C81.2 Mixed cellularity (classical) Hodgkin lymphoma

C81.3 Lymphocyte depleted (classical) Hodgkin lymphoma

C81.4 Lymphocyte-rich (classical) Hodgkin lymphoma

Excl.: nodular lymphocyte predominant Hodgkin lymphoma (C81.0)

C81.7 Other (classical) Hodgkin lymphoma

Classic Hodgkin lymphoma, type not specified

C81.9 Hodgkin lymphoma, unspecified

 

  C82 Follicular lymphoma

Incl.: follicular lymphoma with or without diffuse areas

Excl.: mature T/NK-cell lymphoma (C84.-)

C82.0 Follicular lymphoma grade I C82.1 Follicular lymphoma grade II

C82.2 Follicular lymphoma grade III, unspecified C82.3 Follicular lymphoma grade IIIa

C82.4 Follicular lymphoma grade IIIb C82.5 Diffuse follicle centre lymphoma C82.6 Cutaneous follicle centre lymphoma C82.7 Other types of follicular lymphoma

C82.9 Follicular lymphoma, unspecified

Nodular lymphoma NOS

  C83 Non-follicular lymphoma

C83.0 Small cell B-cell lymphoma Lymphoplasmacytic lymphoma Nodal marginal zone lymphoma Non-leukaemic variant of B-CLL Splenic marginal zone lymphoma

Excl.: chronic lymphocytic leukaemia (C91.1) Waldenström macroglobulinaemia (C88.0) mature T/NK-cell lymphomas (C84.-)

C83.1 Mantle cell lymphoma

Centrocytic lymphoma

Malignant lymphomatous polyposis

C83.3 Diffuse large B-cell lymphoma

Anaplastic

CD30-positive Centroblastic Plasmablastic Immunoblastic Subtype not specified T-cell rich

diffuse large B-cell lymphoma

Excl.: mediastinal (thymic) large B-cell lymphoma (C85.2) mature T/NK-cell lymphomas (C84.-)

 

C83.5 Lymphoblastic (diffuse) lymphoma B-cell precursor lymphoma Lymphoblastic B-cell lymphoma Lymphoblastic lymphoma NOS Lymphoblastic T-cell lymphoma

T-cell precursor lymphoma

C83.7 Burkitt lymphoma

Atypical Burkitt lymphoma ‘Burkitt-like’ lymphoma

Excl.: mature B-cell leukaemia Burkitt-type (C91.8)

C83.8 Other non-follicular lymphoma Primary effusion B-cell lymphoma Intravascular large B-cell lymphoma Lymphoid granulomatosis

Excl.: mediastinal (thymic) large B-cell lymphoma (C85.2) T-cell rich B-cell lymphoma (C83.3)

C83.9 Non-follicular (diffuse) lymphoma, unspecified

  C84 Mature T/NK-cell lymphomas

C84.0 Mycosis fungoides C84.1 Sézary disease

C84.4 Peripheral T-cell lymphoma, not elsewhere classified

Lennert lymphoma Lymphoepithelioid lymphoma

C84.5 Other mature T/NK-cell lymphomas

Note: If T-cell  lineage or involvement is mentioned in conjunction with  a specific lymphoma, code to the more specific description.

Excl.: angioimmunoblastic T-cell lymphoma (C86.5) blastic NK-cell lymphoma (C86.4) enteropathy-type T-cell lymphoma (C86.2)

extranodal NK-cell lymphoma, nasal type (C86.0) hepatosplenic T-cell lymphoma (C86.1)

primary cutaneous CD30-positive T-cell proliferations (C86.6) subcutaneous panniculitis-like T-cell lymphoma (C86.3)

T-cell leukaemia (C91.-)

C84.6 Anaplastic large cell lymphoma, ALK-positive

Anaplastic large cell lymphoma, CD30-positive

C84.7 Anaplastic large cell lymphoma, ALK-negative

Excl.: primary cutaneous CD30-positive T-cell proliferations (C86.6)

C84.8 Cutaneous T-cell lymphoma, unspecified

 

C84.9 Mature T/NK-cell lymphoma, unspecified

NK/T cell lymphoma NOS

Excl.: mature T-cell lymphoma, not elsewhere classified (C84.4)

  C85 Other and unspecified types of non-Hodgkin lymphoma

C85.1 B-cell lymphoma, unspecified

Note: If B-cell lineage or involvement is mentioned in conjunction with a specific lymphoma, code to the more specific description.

C85.2 Mediastinal (thymic) large B-cell lymphoma C85.7 Other specified types of non-Hodgkin lymphoma C85.9 Non-Hodgkin lymphoma, unspecified

Lymphoma NOS Malignant lymphoma NOS

Non-Hodgkin lymphoma NOS

  C86 Other specified types of T/NK-cell lymphoma

Excl.: anaplastic large cell lymphoma, ALK negative (C84.7) anaplastic large cell lymphoma, ALK positive (C84.6)

C86.0 Extranodal NK/T-cell lymphoma, nasal type C86.1 Hepatosplenic T-cell lymphoma

Alpha-beta and gamma-delta types

C86.2 Enteropathy-type (intestinal) T-cell lymphoma

Enteropathy associated T-cell lymphoma

C86.3 Subcutaneous panniculitis-like T-cell lymphoma C86.4 Blastic NK-cell lymphoma

C86.5 Angioimmunoblastic T-cell lymphoma

Angioimmunoblastic lymphadenopathy with dysproteinaemia [AILD]

C86.6 Primary cutaneous CD30-positive T-cell proliferations

Lymphomatoid papulosis

Primary cutaneous anaplastic large-cell lymphoma Primary cutaneous CD30-positive large T-cell lymphoma

  C88 Malignant immunoproliferative diseases

C88.0 Waldenström macroglobulinaemia Lymphoplasmacytic lymphoma with IgM-production Macroglobulinaemia (primary)(idiopathic)

Excl.: small cell B-cell lymphoma (C83.0)

C88.2 Other heavy chain disease

Franklin disease

Gamma heavy chain disease Mu (µ) heavy chain disease

 

C88.3 Immunoproliferative small intestinal disease

Alpha heavy chain disease Mediterranean lymphoma

C88.4 Extranodal marginal zone B-cell lymphoma of mucosa- associated lymphoid tissue [MALT-lyphoma]

Note: Use additional code (C83.3) if desired, to specify transition to high malignant (diffuse large cell) lymphoma.

Lymphoma of skin-associated lymphoid tissue (SALT-lymphoma) Lymphoma of bronchial-associated lymphoid tissue (BALT-lymphoma)

C88.7 Other malignant immunoproliferative diseases C88.9 Malignant immunoproliferative disease, unspecified

Immunoproliferative disease NOS

  C90 Multiple myeloma and malignant plasma cell neoplasms

C90.0 Multiple myeloma

Kahler disease Medullary plasmacytoma Myelomatosis

Plasma cell myeloma

Excl.: solitary plasmacytoma (C90.3)

C90.1 Plasma cell leukaemia

Plasmacytic leukaemia

C90.2 Extramedullary plasmacytoma C90.3 Solitary plasmacytoma

Localized malignant plasma cell tumour NOS

Plasmacytoma NOS Solitary myeloma

  C91 Lymphoid leukaemia

C91.0 Acute lymphoblastic leukaemia [ALL]

Note: This code should only be used for T-cell and B-cell precursor leukaemia.

C91.1 Chronic lymphocytic leukaemia of B-cell type

Lymphoplasmacytic leukaemia Richter syndrome

Excl.: lymphoplasmacytic lymphoma (C83.0) C91.3 Prolymphocytic leukaemia of B-cell type C91.4 Hairy-cell leukaemia

Leukaemic reticuloendotheliosis

 

C91.5 ]

C91.6 Prolymphocytic leukaemia of T-cell type C91.7 Other lymphoid leukaemia

T-cell large granular lymphocytic leukaemia (associated with rheumatoid arthritis)

C91.8 Mature B-cell leukaemia Burkitt-type

Excl.: Burkitt lymphoma with little or no bone marrow infiltration (C83.7)

C91.9 Lymphoid leukaemia, unspecified

  C92 Myeloid leukaemia

Incl.: leukaemia:

• granulocytic

• myelogenous

C92.0 Acute myeloblastic leukaemia [AML]

Acute myeloblastic leukaemia, minimal differentiation Acute myeloblastic leukaemia (with maturation) AML1/ETO

AML M0 AML M1 AML M2

AML with t(8;21)

AML (without a FAB classification) NOS

Refractory anaemia with excess blasts in transformation

Excl.: acute exacerbation of chronic myeloid leukaemia (C92.1)

C92.1 Chronic myeloid leukaemia [CML], BCR/ABL-positive

Chronic myelogenous leukaemia:

• Philadelphia chromosome (Ph1) positive

• t(9:22)(q34;q11)

• with crisis of blast cells

Excl.: atypical chronic myeloid leukaemia, BCR/ABL-negative (C92.2) chronic myelomonocytic leukaemia (C93.1)

unclassified myeloproliferative disease (D47.1)

C92.2 Atypical chronic myeloid leukaemia, BCR/ABL-negative C92.3 Myeloid sarcoma

Note: A tumour of immature myeloid cells.

Chloroma Granulocytic sarcoma

 

C92.4 Acute promyelocytic leukaemia [PML]

AML M3

AML Me with t(15;17) and variants

C92.5 Acute myelomonocytic leukaemia

AML M4

AML M4 Eo with inv(16) or t(16;16)

C92.6 Acute myeloid leukaemia with 11q23-abnormality

Acute myeloid leukaemia with variation of MLL-gene

C92.7 Other myeloid leukaemia

Excl.: chronic eosinophilic leukaemia [hypereosinophilic syndrome] (D47.5)

C92.8 Acute myeloid leukaemia with multilineage dysplasia

Note: Acute myeloid leukaemia with dysplasia of remaining haematopoesis and/or myelodysplastic disease in its history

C92.9 Myeloid leukaemia, unspecified

  C93 Monocytic leukaemia

Incl.: monocytoid leukaemia

C93.0 Acute monoblastic/monocytic leukaemia

AML M5a AML M5b AML M5

C93.1 Chronic myelomonocytic leukaemia

Chronic monocytic leukaemia CMML-1

CMML-2

CMML with eosinophilia

C93.3 Juvenile myelomonocytic leukaemia C93.7 Other monocytic leukaemia

C93.9 Monocytic leukaemia, unspecified

  C94 Other leukaemias of specified cell type

Excl.: leukaemic reticuloendotheliosis (C91.4) plasma cell leukaemia (C90.1)

C94.0 Acute erythroid leukaemia Acute myeloid leukaemia M6 (a)(b) Erythroleukaemia

C94.2 Acute megakaryoblastic leukaemia

Acute myeloid leukaemia, M7 Acute megakaryocytic leukaemia

C94.3 Mast cell leukaemia

 

C94.4 Acute panmyelosis with myelofibrosis

Acute myelofibrosis

C94.6 Myelodysplastic and myeloproliferative disease, not elsewhere classified

C94.7 Other specified leukaemias Aggressive NK-cell leukaemia Acute basophilic leukaemia

  C95 Leukaemia of unspecified cell type

C95.0 Acute leukaemia of unspecified cell type

Acute bilineal leukaemia

Acute mixed lineage leukaemia Biphenotypic acute leukaemia

Stem cell leukaemia of unclear lineage

Excl.: acute exacerbation of unspecified chronic leukaemia (C95.1)

C95.1 Chronic leukaemia of unspecified cell type C95.7 Other leukaemia of unspecified cell type C95.9 Leukaemia, unspecified

  C96 Other and unspecified malignant neoplasms of lymphoid, haematopoietic and related tissue

C96.0 Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis [Letterer–Siwe disease]

Histiocytosis X, multisystemic

C96.2 Malignant mast cell tumour Aggressive systemic mastocytosis Mast cell sarcoma

Excl.: indolent mastocytosis (D47.0) mast cell leukaemia (C94.3)

mastocytosis (congenital) (cutaneous) (Q82.2)

C96.4 Sarcoma of dendritic cells (accessory cells)

Interdigiting dendritic cell sarcoma Langerhans-cell sarcoma

Sarcoma of follicular dendritic cells

C96.5 Multifocal and unisystemic Langerhans-cell histiocytosis

Hand–Schüller–Christian disease Histiocytosis X, multifocal

 

C96.6 Unifocal Langerhans-cell histiocytosis

Eosinophilic granuloma Histiocytosis X, unifocal Histiocytosis X NOS

Langerhans-cell histiocytosis NOS

C96.7 Other specified malignant neoplasms of lymphoid, haematopoietic and related tissue

C96.8 Histiocytic sarcoma

Malignant histiocytosis

C96.9 Malignant neoplasm of lymphoid, haematopoietic and related tissue, unspecified

Malignant neoplasms of independent (primary) multiple sites

(C97)

  C97 Malignant neoplasms of independent (primary) multiple sites

Note: For use of this category, reference should be made to the mortality coding rules and guidelines in Volume 2.

In situ neoplasms (D00–D09)

Note: Many in situ neoplasms are regarded as being located within a continuum of morphological change between dysplasia and invasive cancer. For example, for cervical intraepithelial neoplasia (CIN), three grades are recognized, the third of which (CIN III) includes both severe dysplasia and carcinoma in situ. This system of grading has been extended to other organs, such as vulva and vagina. Descriptions of grade III intraepithelial neoplasia, with or without mention of severe dysplasia, are assigned to this section; grades I and II are classified as dysplasia of the organ system involved and should be coded to the relevant body system chapter.

Incl.: Bowen disease erythroplasia  Queyrat erythroplasia

 

  D00 Carcinoma in situ of oral cavity, oesophagus and stomach

Excl.:  melanoma in situ (D03.-)

D00.0 Lip, oral cavity and pharynx

Aryepiglottic fold:

• NOS

• hypopharyngeal aspect

• marginal zone Vermilion border of lip

Excl.: aryepiglottic fold, laryngeal aspect (D02.0) epiglottis:

• NOS (D02.0)

• suprahyoid portion (D02.0) skin of lip (D03.0, D04.0)

D00.1 Oesophagus

D00.2 Stomach

  D01 Carcinoma in situ of other and unspecified digestive organs

Excl.: melanoma in situ (D03.-)

D01.0 Colon

Excl.: rectosigmoid junction (D01.1)

D01.1 Rectosigmoid junction D01.2 Rectum

D01.3 Anus and anal canal

Excl.: anal:

• margin (D03.5, D04.5)

• skin (D03.5, D04.5)

perianal skin (D03.5, D04.5)

D01.4 Other and unspecified parts of intestine

Excl.: ampulla of Vater (D01.5)

D01.5 Liver, gallbladder and bile ducts

Ampulla of Vater

D01.7 Other specified digestive organs

Pancreas

D01.9 Digestive organ, unspecified

 

  D02 Carcinoma in situ of middle ear and respiratory system

Excl.: melanoma in situ (D03.-)

D02.0 Larynx

Aryepiglottic fold, laryngeal aspect Epiglottis (suprahyoid portion)

Excl.: aryepiglottic fold:

• NOS (D00.0)

• hypopharyngeal aspect (D00.0)

• marginal zone (D00.0)

D02.1 Trachea

D02.2 Bronchus and lung

D02.3 Other parts of respiratory system

Accessory sinuses Middle ear

Nasal cavities

Excl.: ear (external)(skin) (D03.2, D04.2) nose:

• NOS (D09.7)

• skin (D03.3, D04.3)

D02.4 Respiratory system, unspecified

  D03 Melanoma in situ

D03.0 Melanoma in situ of lip

D03.1 Melanoma in situ of eyelid, including canthus

D03.2 Melanoma in situ of ear and external auricular canal D03.3 Melanoma in situ of other and unspecified parts of face D03.4 Melanoma in situ of scalp and neck

D03.5 Melanoma in situ of trunk

Anal:

• margin

• skin

Breast (skin)(soft tissue) Perianal skin

D03.6 Melanoma in situ of upper limb, including shoulder D03.7 Melanoma in situ of lower limb, including hip D03.8 Melanoma in situ of other sites

D03.9 Melanoma in situ, unspecified

 

  D04 Carcinoma in situ of skin

Excl.: erythroplasia of Queyrat (penis) NOS (D07.4) melanoma in situ (D03.-)

D04.0 Skin of lip

Excl.:  vermilion border of lip (D00.0)

D04.1 Skin of eyelid, including canthus

D04.2 Skin of ear and external auricular canal D04.3 Skin of other and unspecified parts of face D04.4 Skin of scalp and neck

D04.5 Skin of trunk

Anal:

• margin

• skin Perianal skin Skin of breast

Excl.: anus NOS (D01.3)

skin of genital organs (D07.-)

D04.6 Skin of upper limb, including shoulder D04.7 Skin of lower limb, including hip D04.8 Skin of other sites

D04.9 Skin, unspecified

  D05 Carcinoma in situ of breast

Excl.: carcinoma in situ of skin of breast (D04.5) melanoma in situ of breast (skin) (D03.5)

D05.0 Lobular carcinoma in situ D05.1 Intraductal carcinoma in situ

D05.7 Other carcinoma in situ of breast

D05.9 Carcinoma in situ of breast, unspecified

  D06 Carcinoma in situ of cervix uteri

Incl.: cervical intraepithelial neoplasia [CIN], grade III, with or without mention of severe dysplasia

Excl.: melanoma in situ of cervix (D03.5) severe dysplasia of cervix NOS (N87.2)

D06.0 Endocervix

D06.1 Exocervix

D06.7 Other parts of cervix D06.9 Cervix, unspecified

 

  D07 Carcinoma in situ of other and unspecified genital organs

Excl.: melanoma in situ (D03.5)

D07.0 Endometrium

D07.1 Vulva

Vulvar intraepithelial neoplasia [VIN], grade III, with or without mention of severe dysplasia

Excl.: severe dysplasia of vulva NOS (N90.2)

D07.2 Vagina

Vaginal intraepithelial neoplasia [VAIN], grade III, with or without mention of severe dysplasia

Excl.: severe dysplasia of vagina NOS (N89.2) D07.3 Other and unspecified female genital organs D07.4 Penis

Erythroplasia of Queyrat NOS

D07.5 Prostate

Excl.: low-grade dysplasia of prostate (N42.3)

D07.6 Other and unspecified male genital organs

  D09 Carcinoma in situ of other and unspecified sites

Excl.: melanoma in situ (D03.-)

D09.0 Bladder

D09.1 Other and unspecified urinary organs D09.2 Eye

Excl.: skin of eyelid (D04.1)

D09.3 Thyroid and other endocrine glands

Excl.: endocrine pancreas (D01.7) ovary (D07.3)

testis (D07.6)

D09.7 Carcinoma in situ of other specified sites D09.9 Carcinoma in situ, unspecified

 

Benign neoplasms (D10–D36)

  D10 Benign neoplasm of mouth and pharynx

D10.0 Lip

Lip (frenulum)(inner aspect)(mucosa)(vermilion border)

Excl.: skin of lip (D22.0, D23.0)

D10.1 Tongue

Lingual tonsil

D10.2 Floor of mouth

D10.3 Other and unspecified parts of mouth

Minor salivary gland NOS

Excl.: benign odontogenic neoplasms (D16.4–D16.5) mucosa of lip (D10.0)

nasopharyngeal surface of soft palate (D10.6)

D10.4 Tonsil

Tonsil (faucial)(palatine)

Excl.: lingual tonsil (D10.1) pharyngeal tonsil (D10.6) tonsillar:

• fossa (D10.5)

• pillars (D10.5)

D10.5 Other parts of oropharynx Epiglottis, anterior aspect Tonsillar:

• fossa

• pillars Vallecula

Excl.: epiglottis:

• NOS (D14.1)

• suprahyoid portion (D14.1)

D10.6 Nasopharynx

Pharyngeal tonsil

Posterior margin of septum and choanae

D10.7 Hypopharynx

D10.9 Pharynx, unspecified

 

  D11 Benign neoplasm of major salivary glands

Excl.: benign neoplasms of specified minor salivary glands which are classified according to their anatomical location

benign neoplasms of minor salivary glands NOS (D10.3)

D11.0 Parotid gland

D11.7 Other major salivary glands

Gland:

• sublingual

• submandibular

D11.9 Major salivary gland, unspecified

  D12 Benign neoplasm of colon, rectum, anus and anal canal

D12.0 Caecum

Ileocaecal valve

D12.1 Appendix

D12.2 Ascending colon D12.3 Transverse colon

Hepatic flexure Splenic flexure

D12.4 Descending colon D12.5 Sigmoid colon D12.6 Colon, unspecified

Adenomatosis of colon

Large intestine NOS

Polyposis (hereditary) of colon D12.7 Rectosigmoid junction D12.8 Rectum

D12.9 Anus and anal canal

Excl.: anal:

• margin (D22.5, D23.5)

• skin (D22.5, D23.5)

perianal skin (D22.5, D23.5)

  D13 Benign neoplasm of other and ill-defined parts of digestive system

D13.0 Oesophagus

D13.1 Stomach

D13.2 Duodenum

D13.3 Other and unspecified parts of small intestine

 

D13.4 Liver

Intrahepatic bile ducts

D13.5 Extrahepatic bile ducts D13.6 Pancreas

Excl.: endocrine pancreas (D13.7)

D13.7 Endocrine pancreas

Islet cell tumour Islets of Langerhans

D13.9 Ill-defined sites within the digestive system

Digestive system NOS Intestine NOS

Spleen

  D14 Benign neoplasm of middle ear and respiratory system

D14.0 Middle ear, nasal cavity and accessory sinuses

Cartilage of nose

Excl.: auricular canal (external) (D22.2, D23.2) bone of:

• ear (D16.4)

• nose (D16.4) cartilage of ear (D21.0)

ear (external)(skin) (D22.2, D23.2) nose:

• NOS (D36.7)

• skin (D22.3, D23.3)

olfactory bulb (D33.3) polyp (of):

• accessory sinus (J33.8)

• ear (middle) (H74.4)

• nasal (cavity) (J33.-)

posterior margin of septum and choanae (D10.6)

D14.1 Larynx

Epiglottis (suprahyoid portion)

Excl.: epiglottis, anterior aspect (D10.5) polyp of vocal cord and larynx (J38.1)

D14.2 Trachea

D14.3 Bronchus and lung

D14.4 Respiratory system, unspecified

 

  D15 Benign neoplasm of other and unspecified intrathoracic organs

Excl.: mesothelial tissue (D19.-)

D15.0 Thymus

D15.1 Heart

Excl.: great vessels (D21.3)

D15.2 Mediastinum

D15.7 Other specified intrathoracic organs D15.9 Intrathoracic organ, unspecified

  D16 Benign neoplasm of bone and articular cartilage

Excl.: connective tissue of:

• ear (D21.0)

• eyelid (D21.0)

• larynx (D14.1)

• nose (D14.0) synovia (D21.-)

D16.0 Scapula and long bones of upper limb D16.1 Short bones of upper limb

D16.2 Long bones of lower limb D16.3 Short bones of lower limb

D16.4 Bones of skull and face

Maxilla (superior) Orbital bone

Excl.: lower jaw bone (D16.5)

D16.5 Lower jaw bone D16.6 Vertebral column

Excl.: sacrum and coccyx (D16.8)

D16.7 Ribs, sternum and clavicle

D16.8 Pelvic bones, sacrum and coccyx

D16.9 Bone and articular cartilage, unspecified

  D17 Benign lipomatous neoplasm

D17.0 Benign lipomatous neoplasm of skin and subcutaneous tissue of head, face and neck

 

D17.1 Benign lipomatous neoplasm of skin and subcutaneous tissue of trunk

D17.2 Benign lipomatous neoplasm of skin and subcutaneous tissue of limbs

D17.3 Benign lipomatous neoplasm of skin and subcutaneous tissue of other and unspecified sites

D17.4 Benign lipomatous neoplasm of intrathoracic organs D17.5 Benign lipomatous neoplasm of intra-abdominal organs

Excl.: peritoneum and retroperitoneum (D17.7)

D17.6 Benign lipomatous neoplasm of spermatic cord D17.7 Benign lipomatous neoplasm of other sites

Peritoneum

Retroperitoneum

D17.9 Benign lipomatous neoplasm, unspecified

Lipoma NOS

  D18 Haemangioma and lymphangioma, any site

Excl.: blue or pigmented naevus (D22.-)

D18.0 Haemangioma, any site

Angioma NOS

D18.1 Lymphangioma, any site

  D19 Benign neoplasm of mesothelial tissue

D19.0 Mesothelial tissue of pleura D19.1 Mesothelial tissue of peritoneum D19.7 Mesothelial tissue of other sites D19.9 Mesothelial tissue, unspecified

Benign mesothelioma NOS

  D20 Benign neoplasm of soft tissue of retroperitoneum and peritoneum

Excl.: benign lipomatous neoplasm of peritoneum and retroperitoneum (D17.7)

mesothelial tissue (D19.-)

D20.0 Retroperitoneum D20.1 Peritoneum

 

  D21 Other benign neoplasms of connective and other soft tissue

Incl.: blood vessel bursa cartilage fascia

fat

ligament, except uterine lymphatic channel muscle

synovia

tendon (sheath)

Excl.: cartilage:

• articular (D16.-)

• larynx (D14.1)

• nose (D14.0)

connective tissue of breast (D24) haemangioma (D18.0) lipomatous neoplasm (D17.-) lymphangioma (D18.1)

peripheral nerves and autonomic nervous system (D36.1) peritoneum (D20.1)

retroperitoneum (D20.0) uterine:

• leiomyoma (D25.-)

• ligament, any (D28.2) vascular tissue (D18.-)

D21.0 Connective and other soft tissue of head, face and neck

Connective tissue of:

• ear

• eyelid

Excl.: connective tissue of orbit (D31.6)

D21.1 Connective and other soft tissue of upper limb, including shoulder

D21.2 Connective and other soft tissue of lower limb, including hip D21.3 Connective and other soft tissue of thorax

Axilla

Diaphragm Great vessels

Excl.: heart (D15.1)

mediastinum (D15.2) thymus (D15.0)

D21.4 Connective and other soft tissue of abdomen

 

D21.5 Connective and other soft tissue of pelvis

Excl.: uterine:

• leiomyoma (D25.-)

• ligament, any (D28.2)

D21.6 Connective and other soft tissue of trunk, unspecified

Back NOS

D21.9 Connective and other soft tissue, unspecified

  D22 Melanocytic naevi

naevus:

• NOS

• blue

• hairy

• pigmented

D22.0 Melanocytic naevi of lip

D22.1 Melanocytic naevi of eyelid, including canthus

D22.2 Melanocytic naevi of ear and external auricular canal D22.3 Melanocytic naevi of other and unspecified parts of face D22.4 Melanocytic naevi of scalp and neck

D22.5 Melanocytic naevi of trunk

Anal:

• margin

• skin Perianal skin Skin of breast

D22.6 Melanocytic naevi of upper limb, including shoulder D22.7 Melanocytic naevi of lower limb, including hip D22.9 Melanocytic naevi, unspecified

  D23 Other benign neoplasms of skin

Incl.: benign neoplasm of:

• hair follicles

• sebaceous glands

• sweat glands

Excl.: benign lipomatous neoplasms (D17.0–D17.3) melanocytic naevi (D22.-)

D23.0 Skin of lip

Excl.: vermilion border of lip (D10.0)

 

D23.1 Skin of eyelid, including canthus

D23.2 Skin of ear and external auricular canal D23.3 Skin of other and unspecified parts of face D23.4 Skin of scalp and neck

D23.5 Skin of trunk

Anal:

• margin

• skin Perianal skin Skin of breast

Excl.: anus NOS (D12.9)

skin of genital organs (D28–D29) D23.6 Skin of upper limb, including shoulder D23.7 Skin of lower limb, including hip D23.9 Skin, unspecified

  D24 Benign neoplasm of breast

Incl.: breast:

• connective tissue

• soft parts

Excl.: benign mammary dysplasia (N60.-) skin of breast (D22.5, D23.5)

  D25 Leiomyoma of uterus

fibromyoma of uterus

D25.0 Submucous leiomyoma of uterus D25.1 Intramural leiomyoma of uterus D25.2 Subserosal leiomyoma of uterus D25.9 Leiomyoma of uterus, unspecified

  D26 Other benign neoplasms of uterus

D26.0 Cervix uteri

D26.1 Corpus uteri

D26.7 Other parts of uterus D26.9 Uterus, unspecified

  D27 Benign neoplasm of ovary

 

  D28 Benign neoplasm of other and unspecified female genital organs

Incl.: adenomatous polyp

skin of female genital organs

D28.0 Vulva

D28.1 Vagina

D28.2 Uterine tubes and ligaments

Fallopian tube

Uterine ligament (broad)(round)

D28.7 Other specified female genital organs D28.9 Female genital organ, unspecified

  D29 Benign neoplasm of male genital organs

Incl.: skin of male genital organs

D29.0 Penis

D29.1 Prostate

Excl.: hyperplasia of prostate (adenomatous) (N40) prostatic:

• enlargement (N40)

• hypertrophy (N40)

D29.2 Testis

D29.3 Epididymis

D29.4 Scrotum

Skin of scrotum

D29.7 Other male genital organs

Seminal vesicle Spermatic cord Tunica vaginalis

D29.9 Male genital organ, unspecified

  D30 Benign neoplasm of urinary organs

D30.0 Kidney

Excl.: renal:

• calyces (D30.1)

• pelvis (D30.1)

D30.1 Renal pelvis

D30.2 Ureter

Excl.: ureteric orifice of bladder (D30.3)

 

D30.3 Bladder

Orifice of bladder:

• urethral

• ureteric

D30.4 Urethra

Excl.: urethral orifice of bladder (D30.3)

D30.7 Other urinary organs

Paraurethral glands

D30.9 Urinary organ, unspecified

Urinary system NOS

  D31 Benign neoplasm of eye and adnexa

Excl.: connective tissue of eyelid (D21.0) optic nerve (D33.3)

skin of eyelid (D22.1, D23.1)

D31.0 Conjunctiva

D31.1 Cornea

D31.2 Retina

D31.3 Choroid

D31.4 Ciliary body

D31.5 Lacrimal gland and duct

Lacrimal sac Nasolacrimal duct

D31.6 Orbit, unspecified

Connective tissue of orbit Extraocular muscle Peripheral nerves of orbit Retrobulbar tissue

Retro-ocular tissue

Excl.: orbital bone (D16.4)

D31.9 Eye, unspecified

Eyeball

  D32 Benign neoplasm of meninges

D32.0 Cerebral meninges D32.1 Spinal meninges D32.9 Meninges, unspecified

Meningioma NOS

 

  D33 Benign neoplasm of brain and other parts of central nervous system

Excl.: angioma (D18.0)

meninges (D32.-)

peripheral nerves and autonomic nervous system (D36.1) retro-ocular tissue (D31.6)

D33.0 Brain, supratentorial

Cerebral ventricle Cerebrum

Frontal

Occipital Parietal Temporal

lobe

Excl.: fourth ventricle (D33.1)

D33.1 Brain, infratentorial Brain stem Cerebellum

Fourth ventricle

D33.2 Brain, unspecified D33.3 Cranial nerves

Olfactory bulb

D33.4 Spinal cord

D33.7 Other specified parts of central nervous system D33.9 Central nervous system, unspecified

Nervous system (central) NOS

  D34 Benign neoplasm of thyroid gland

  D35 Benign neoplasm of other and unspecified endocrine glands

Excl.: endocrine pancreas (D13.7) ovary (D27)

testis (D29.2) thymus (D15.0)

D35.0 Adrenal gland D35.1 Parathyroid gland D35.2 Pituitary gland

D35.3 Craniopharyngeal duct D35.4 Pineal gland

D35.5 Carotid body

 

D35.6 Aortic body and other paraganglia D35.7 Other specified endocrine glands D35.8 Pluriglandular involvement

D35.9 Endocrine gland, unspecified

  D36 Benign neoplasm of other and unspecified sites

D36.0 Lymph nodes

D36.1 Peripheral nerves and autonomic nervous system

Excl.: peripheral nerves of orbit (D31.6)

D36.7 Other specified sites

Nose NOS

D36.9 Benign neoplasm of unspecified site

Neoplasms of uncertain or unknown behaviour (D37–D48)

Note: Categories D37–D48 classify by site neoplasms of uncertain or unknown behaviour, i.e. there is doubt whether the neoplasm is malignant or benign.

  D37 Neoplasm of uncertain or unknown behaviour of oral cavity and digestive organs

D37.0 Lip, oral cavity and pharynx

Aryepiglottic fold:

• NOS

• hypopharyngeal aspect

• marginal zone

Major and minor salivary glands Vermilion border of lip

Excl.: aryepiglottic fold, laryngeal aspect (D38.0) epiglottis:

• NOS (D38.0)

• suprahyoid portion (D38.0) skin of lip (D48.5)

D37.1 Stomach

D37.2 Small intestine

D37.3 Appendix

D37.4 Colon

D37.5 Rectum

Rectosigmoid junction

 

D37.6 Liver, gallbladder and bile ducts

Ampulla of Vater

D37.7 Other digestive organs

Anal:

• canal

• sphincter Anus NOS Intestine NOS Oesophagus Pancreas

Excl.: anal:

• margin (D48.5)

• skin (D48.5) perianal skin (D48.5)

D37.9 Digestive organ, unspecified

  D38 Neoplasm of uncertain or unknown behaviour of middle ear and respiratory and intrathoracic organs

Excl.: heart (D48.7)

D38.0 Larynx

Aryepiglottic fold, laryngeal aspect Epiglottis (suprahyoid portion)

Excl.: aryepiglottic fold:

• NOS (D37.0)

• hypopharyngeal aspect (D37.0)

• marginal zone (D37.0) D38.1 Trachea, bronchus and lung D38.2 Pleura

D38.3 Mediastinum

D38.4 Thymus

D38.5 Other respiratory organs

Accessory sinuses Cartilage of nose Middle ear

Nasal cavities

Excl.: ear (external)(skin) (D48.5) nose:

• NOS (D48.7)

• skin (D48.5)

D38.6 Respiratory organ, unspecified

 

  D39 Neoplasm of uncertain or unknown behaviour of female genital organs

D39.0 Uterus

D39.1 Ovary

D39.2 Placenta Chorioadenoma destruens Hydatidiform mole:

• invasive

• malignant

Excl.: hydatidiform mole NOS (O01.9)

D39.7 Other female genital organs

Skin of female genital organs

D39.9 Female genital organ, unspecified

  D40 Neoplasm of uncertain or unknown behaviour of male genital organs

D40.0 Prostate

D40.1 Testis

D40.7 Other male genital organs

Skin of male genital organs

D40.9 Male genital organ, unspecified

  D41 Neoplasm of uncertain or unknown behaviour of urinary organs

D41.0 Kidney

Excl.: renal pelvis (D41.1)

D41.1 Renal pelvis

D41.2 Ureter

D41.3 Urethra

D41.4 Bladder

D41.7 Other urinary organs D41.9 Urinary organ, unspecified

  D42 Neoplasm of uncertain or unknown behaviour of meninges

D42.0 Cerebral meninges D42.1 Spinal meninges D42.9 Meninges, unspecified

 

  D43 Neoplasm of uncertain or unknown behaviour of brain and central nervous system

Excl.: peripheral nerves and autonomic nervous system (D48.2)

D43.0 Brain, supratentorial

Cerebral ventricle Cerebrum

Frontal

Occipital Parietal Temporal

lobe

Excl.: fourth ventricle (D43.1)

D43.1 Brain, infratentorial Brain stem Cerebellum

Fourth ventricle D43.2 Brain, unspecified D43.3 Cranial nerves

D43.4 Spinal cord

D43.7 Other parts of central nervous system D43.9 Central nervous system, unspecified

Nervous system (central) NOS

  D44 Neoplasm of uncertain or unknown behaviour of endocrine glands

Excl.: endocrine pancreas (D37.7) ovary (D39.1)

testis (D40.1) thymus (D38.4)

D44.0 Thyroid gland

D44.1 Adrenal gland D44.2 Parathyroid gland D44.3 Pituitary gland

D44.4 Craniopharyngeal duct D44.5 Pineal gland

D44.6 Carotid body

D44.7 Aortic body and other paraganglia

 

D44.8 Pluriglandular involvement

Multiple endocrine adenomatosis

D44.9 Endocrine gland, unspecified

  D45 Polycythaemia vera

Note: Polycythaemia vera has been reclassified in ICD-O third edition with a malignant code. The code D45 will continue to be used, although it is located in the chapter for Neoplasms of uncertain or unknown behaviour. The modification of its classification is reserved for the revision of the ICD.

  D46 Myelodysplastic syndromes

Incl.: alykylating-agent-related myelodysplastic syndrome epipodophyllotoxin-related myelodysplastic syndrome therapy-related myelodysplastic syndrome NOS

Excl.: drug-induced aplastic anaemia (D61.1)

D46.0 Refractory anaemia without ringed sideroblasts, so stated

Note: without sideroblasts, without excess of blasts

D46.1 Refractory anaemia with ringed sideroblasts D46.2 Refractory anaemia with excess of blasts [RAEB]

Note: RAEB I

RAEB II

D46.4 Refractory anaemia, unspecified

D46.5 Refractory anaemia with multi-lineage dysplasia

D46.6 Myelodysplastic syndrome with isolated del(5q) chromosomal abnormality

5q-minus syndrome

D46.7 Other myelodysplastic syndromes

Excl.: chronic myelomonocytic leukaemia (C93.1)

D46.9 Myelodysplastic syndrome, unspecified

Myelodysplasia NOS Preleukaemia (syndrome) NOS

 

  D47 Other neoplasms of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue

D47.0 Histiocytic and mast cell tumours of uncertain and unknown behaviour

Indolent systematic mastocytosis Mast cell tumour NOS Mastocytoma NOS

Systemic mastocytosis, associated with clonal haematopoietic non-mast- cell disease (SM-AHNMD)

Excl.: mastocytosis (congenital) (cutaneous) (Q82.2)

D47.1 Chronic myeloproliferative disease Chronic neutrophilic leukaemia Myeloproliferative disease, unspecified

Excl.: atypical chronic myeloid leukaemia, BCR/ABL-negative (C92.2) chronic myeloid leukaemia [CML] BCR/ABL-positive (C92.1)

D47.2 Monoclonal gammopathy of undetermined significance (MGUS) D47.3 Essential (haemorrhagic) thrombocythaemia

Idiopathic haemorrhagic thrombocythaemia

D47.4 Osteomyelofibrosis

Chronic idiopathic myelofibrosis

Myelofibrosis (idiopathic) (with myeloid metaplasia) Myelosclerosis (megakaryocytic) with myeloid metaplasia Secondary myelofibrosis in myeloproliferative disease Excl.: acute myelofibrosis (C94.4)

D47.5 Chronic eosinophilic leukaemia [hypereosinophilic syndrome]

D47.7 Other specified neoplasms of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue

Histiocytic tumours of uncertain and unknown behaviour

D47.9 Neoplasm of uncertain or unknown behaviour of lymphoid, haematopoietic and related tissue, unspecified Lymphoproliferative disease NOS

  D48 Neoplasm of uncertain or unknown behaviour of other and unspecified sites

Excl.: neurofibromatosis (nonmalignant) (Q85.0)

 

D48.0 Bone and articular cartilage

Excl.: cartilage of:

• ear (D48.1)

• larynx (D38.0)

• nose (D38.5)

connective tissue of eyelid (D48.1) synovia (D48.1)

D48.1 Connective and other soft tissue

Connective tissue of:

• ear

• eyelid

Excl.: cartilage (of):

• articular (D48.0)

• larynx (D38.0)

• nose (D38.5)

connective tissue of breast (D48.6)

D48.2 Peripheral nerves and autonomic nervous system

Excl.: peripheral nerves of orbit (D48.7)

D48.3 Retroperitoneum D48.4 Peritoneum

D48.5 Skin

Anal:

• margin

• skin Perianal skin Skin of breast

Excl.: anus NOS (D37.7)

skin of genital organs (D39.7, D40.7) vermilion border of lip (D37.0)

D48.6 Breast

Connective tissue of breast Cystosarcoma phyllodes

Excl.: skin of breast (D48.5)

 

D48.7 Other specified sites

Eye Heart

Peripheral nerves of orbit

Excl.: connective tissue (D48.1) skin of eyelid (D48.5)

D48.9 Neoplasm of uncertain or unknown behaviour, unspecified

‘Growth’ NOS Neoplasm NOS New growth NOS Tumour NOS

CHAPTER III

Diseases of the blood and blood- forming organs and certain disorders involving the immune mechanism (D50–D89)

Excl.: autoimmune disease (systemic) NOS (M35.9)

certain conditions originating in the perinatal period (P00–P96) complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90) human immunodeficiency virus [HIV] disease (B20–B24)

injury, poisoning and certain other consequences of external causes (S00–T98)

neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

D50–D53 Nutritional anaemias D55–D59 Haemolytic anaemias D60–D64 Aplastic and other anaemias

D65–D69 Coagulation defects, purpura and other haemorrhagic conditions D70–D77 Other diseases of blood and blood-forming organs

D80–D89 Certain disorders involving the immune mechanism

Asterisk categories for this chapter are provided as follows:

D63* Anaemia in chronic diseases classified elsewhere

D77* Other disorders of blood and blood-forming organs in diseases classified elsewhere

 

Nutritional anaemias (D50–D53)

  D50 Iron deficiency anaemia

Incl.: anaemia:

• asiderotic

• hypochromic

D50.0 Iron deficiency anaemia secondary to blood loss (chronic)

Posthaemorrhagic anaemia (chronic)

Excl.: acute posthaemorrhagic anaemia (D62) congenital anaemia from fetal blood loss (P61.3)

D50.1 Sideropenic dysphagia

Kelly–Paterson syndrome Plummer–Vinson syndrome

D50.8 Other iron deficiency anaemias D50.9 Iron deficiency anaemia, unspecified

  D51 Vitamin B12 deficiency anaemia

Excl.: vitamin B12 deficiency (E53.8)

D51.0 Vitamin B12 deficiency anaemia due to intrinsic factor deficiency

Anaemia:

• Addison

• Biermer

• pernicious (congenital)

Congenital intrinsic factor deficiency

D51.1 Vitamin B12 deficiency anaemia due to selective vitamin B12 malabsorption with proteinuria

Imerslund(–Gräsbeck) syndrome Megaloblastic hereditary anaemia

D51.2 Transcobalamin II deficiency

D51.3 Other dietary vitamin B12 deficiency anaemia

Vegan anaemia

D51.8 Other vitamin B12 deficiency anaemias D51.9 Vitamin B12 deficiency anaemia, unspecified

 

  D52 Folate deficiency anaemia

D52.0 Dietary folate deficiency anaemia

Nutritional megaloblastic anaemia

D52.1 Drug-induced folate deficiency anaemia

Use additional external cause code (Chapter XX), if desired, to identify drug.

D52.8 Other folate deficiency anaemias D52.9 Folate deficiency anaemia, unspecified

Folic acid deficiency anaemia NOS

  D53 Other nutritional anaemias

Incl.: megaloblastic anaemia unresponsive to vitamin B12 or folate therapy

D53.0 Protein deficiency anaemia Amino-acid deficiency anaemia Orotaciduric anaemia

Excl.: Lesch–Nyhan syndrome (E79.1)

D53.1 Other megaloblastic anaemias, not elsewhere classified

Megaloblastic anaemia NOS

Excl.: Di Guglielmo disease (C94.0)

D53.2 Scorbutic anaemia

Excl.: scurvy (E54)

D53.8 Other specified nutritional anaemias

Anaemia associated with deficiency of:

• copper

• molybdenum

• zinc

Excl.: nutritional deficiencies without mention of anaemia, such as:

• copper deficiency (E61.0)

• molybdenum deficiency (E61.5)

• zinc deficiency (E60)

D53.9 Nutritional anaemia, unspecified

Simple chronic anaemia

Excl.: anaemia NOS (D64.9)

 

Haemolytic anaemias (D55–D59)

  D55 Anaemia due to enzyme disorders

Excl.: drug-induced enzyme deficiency anaemia (D59.2)

D55.0 Anaemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency

Favism

G6PD deficiency anaemia

D55.1 Anaemia due to other disorders of glutathione metabolism

Anaemia (due to):

• enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway

• haemolytic nonspherocytic (hereditary), type I

D55.2 Anaemia due to disorders of glycolytic enzymes

Anaemia:

• haemolytic nonspherocytic (hereditary), type II

• hexokinase deficiency

• pyruvate kinase [PK] deficiency

• triose-phosphate isomerase deficiency

D55.3 Anaemia due to disorders of nucleotide metabolism D55.8 Other anaemias due to enzyme disorders

D55.9 Anaemia due to enzyme disorder, unspecified

  D56 Thalassaemia

D56.0 Alpha thalassaemia

Excl.: hydrops fetalis due to haemolytic disease (P56.-)

D56.1 Beta thalassaemia

Cooley anaemia

Severe beta thalassaemia Thalassaemia:

• intermedia

• major

D56.2 Delta-beta thalassaemia D56.3 Thalassaemia trait

D56.4 Hereditary persistence of fetal haemoglobin [HPFH] D56.8 Other thalassaemias

D56.9 Thalassaemia, unspecified

Mediterranean anaemia (with other haemoglobinopathy) Thalassaemia (minor)(mixed)(with other haemoglobinopathy)

 

  D57 Sickle-cell disorders

Excl.: other haemoglobinopathies (D58.-)

D57.0 Sickle-cell anaemia with crisis

Hb-SS disease with crisis

D57.1 Sickle-cell anaemia without crisis

Sickle-cell:

anaemia

disease disorder

NOS

D57.2 Double heterozygous sickling disorders

Disease:

• Hb-SC

• Hb-SD

• Hb-SE

• sickle-cell thalassaemia

D57.3 Sickle-cell trait

Hb-S trait

Heterozygous haemoglobin S [HbAS]

D57.8 Other sickle-cell disorders

  D58 Other hereditary haemolytic anaemias

D58.0 Hereditary spherocytosis

Acholuric (familial) jaundice

Congenital (spherocytic) haemolytic icterus Minkowski–Chauffard syndrome

D58.1 Hereditary elliptocytosis

Elliptocytosis (congenital) Ovalocytosis (congenital)(hereditary)

D58.2 Other haemoglobinopathies Abnormal haemoglobin NOS Congenital Heinz body anaemia Disease:

• Hb-C

• Hb-D

• Hb-E Haemoglobinopathy NOS

Unstable haemoglobin haemolytic disease

Excl.: familial polycythaemia (D75.0) Hb-M disease (D74.0)

hereditary persistence of fetal haemoglobin [HPFH] (D56.4) high-altitude polycythaemia (D75.1)

methaemoglobinaemia (D74.-)

 

D58.8 Other specified hereditary haemolytic anaemias

Stomatocytosis

D58.9 Hereditary haemolytic anaemia, unspecified

  D59 Acquired haemolytic anaemia

D59.0 Drug-induced autoimmune haemolytic anaemia

Use additional external cause code (Chapter XX), if desired, to identify drug.

D59.1 Other autoimmune haemolytic anaemias Autoimmune haemolytic disease (cold type)(warm type) Chronic cold haemagglutinin disease

Cold agglutinin:

• disease

• haemoglobinuria Haemolytic anaemia:

• cold type (secondary)(symptomatic)

• warm type (secondary)(symptomatic)

Excl.: Evans syndrome (D69.3)

haemolytic disease of fetus and newborn (P55.-) paroxysmal cold haemoglobinuria (D59.6)

D59.2 Drug-induced nonautoimmune haemolytic anaemia

Drug-induced enzyme deficiency anaemia

Use additional external cause code (Chapter XX), if desired, to identify drug.

D59.3 Haemolytic-uraemic syndrome

D59.4 Other nonautoimmune haemolytic anaemias

Haemolytic anaemia:

• mechanical

• microangiopathic

• toxic

Use additional external cause code (Chapter XX), if desired, to identify cause.

D59.5 Paroxysmal nocturnal haemoglobinuria [Marchiafava–Micheli]

Excl.: haemoglobinuria NOS (R82.3)

D59.6 Haemoglobinuria due to haemolysis from other external causes

Haemoglobinuria:

• from exertion

• march

• paroxysmal cold

Use additional external cause code (Chapter XX), if desired, to identify cause.

Excl.: haemoglobinuria NOS (R82.3)

D59.8 Other acquired haemolytic anaemias D59.9 Acquired haemolytic anaemia, unspecified

Idiopathic haemolytic anaemia, chronic

 

Aplastic and other anaemias (D60–D64)

  D60 Acquired pure red cell aplasia [erythroblastopenia]

Incl.: red cell aplasia (acquired)(adult)(with thymoma)

D60.0 Chronic acquired pure red cell aplasia D60.1 Transient acquired pure red cell aplasia D60.8 Other acquired pure red cell aplasias D60.9 Acquired pure red cell aplasia, unspecified

  D61 Other aplastic anaemias

Excl.: agranulocytosis (D70)

D61.0 Constitutional aplastic anaemia

Aplasia, (pure) red cell (of):

• congenital

• infants

• primary Blackfan–Diamond syndrome Familial hypoplastic anaemia Fanconi anaemia

Pancytopenia with malformations

D61.1 Drug-induced aplastic anaemia

Use additional external cause code (Chapter XX), if desired, to identify drug.

D61.2 Aplastic anaemia due to other external agents

Use additional external cause code (Chapter XX), if desired, to identify cause.

D61.3 Idiopathic aplastic anaemia

D61.8 Other specified aplastic anaemias D61.9 Aplastic anaemia, unspecified

Hypoplastic anaemia NOS Medullary hypoplasia Panmyelophthisis

  D62 Acute posthaemorrhagic anaemia

Excl.: congenital anaemia from fetal blood loss (P61.3)

  D63* Anaemia in chronic diseases classified elsewhere

D63.0* Anaemia in neoplastic disease (C00–D48†)

D63.8* Anaemia in other chronic diseases classified elsewhere

Anaemia in chronic kidney disease ≥stage 3 (N18.3–N18.9†)

 

  D64 Other anaemias

Excl.: refractory anaemia:

• NOS (D46.4)

• with excess of blasts (D46.2)

• with excess of blasts

– with transformation (C92.0)

• with sideroblasts (D46.1)

• without sideroblasts (D46.0)

D64.0 Hereditary sideroblastic anaemia

Sex-linked hypochromic sideroblastic anaemia

D64.1 Secondary sideroblastic anaemia due to disease

Use additional code, if desired, to identify disease.

D64.2 Secondary sideroblastic anaemia due to drugs and toxins

Use additional external cause code (Chapter XX), if desired, to identify cause.

D64.3 Other sideroblastic anaemias

Sideroblastic anaemia:

• NOS

• pyridoxine-responsive NEC

D64.4 Congenital dyserythropoietic anaemia

Dyshaematopoietic anaemia (congenital)

Excl.: Blackfan–Diamond syndrome (D61.0) Di Guglielmo disease (C94.0)

D64.8 Other specified anaemias Infantile pseudoleukaemia Leukoerythroblastic anaemia

D64.9 Anaemia, unspecified

Coagulation defects, purpura and other haemorrhagic conditions

(D65–D69)

  D65 Disseminated intravascular coagulation [defibrination syndrome]

Incl.: afibrinogenaemia, acquired consumption coagulopathy

diffuse or disseminated intravascular coagulation [DIC] fibrinolytic haemorrhage, acquired

purpura:

• fibrinolytic

• fulminans

Excl.: that (complicating):

• abortion or ectopic or molar pregnancy (O00–O07, O08.1)

• pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

in newborn (P60)

  D66 Hereditary factor VIII deficiency

Incl.: deficiency factor VIII (with functional defect) haemophilia:

• NOS

• A

• classical

Excl.: factor VIII deficiency with vascular defect (D68.0)

  D67 Hereditary factor IX deficiency

Incl.: Christmas disease deficiency:

• factor IX (with functional defect)

• plasma thromboplastin component [PTC] haemophilia B

  D68 Other coagulation defects

Excl.: those complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.1)

• pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

D68.0 Von Willebrand disease

Angiohaemophilia

Factor VIII deficiency with vascular defect Vascular haemophilia

Excl.: capillary fragility (hereditary) (D69.8) factor VIII deficiency:

• NOS (D66)

• with functional defect (D66)

D68.1 Hereditary factor XI deficiency

Haemophilia C

Plasma thromboplastin antecedent [PTA] deficiency

D68.2 Hereditary deficiency of other clotting factors

Congenital afibrinogenaemia Deficiency:

• AC globulin

• proaccelerin Deficiency of factor:

• I [fibrinogen]

• II [prothrombin]

• V [labile]

• VII [stable]

• X [Stuart–Prower]

• XII [Hageman]

• XIII [fibrin-stabilizing] Dysfibrinogenaemia (congenital) Hypoproconvertinaemia

Owren disease

D68.3 Haemorrhagic disorder due to circulating anticoagulants Haemorrhage during long-term use of anticoagulants Hyperheparinaemia

Increase in:

• antithrombin

• anti-VIIIa

• anti-IXa

• anti-Xa

• anti-XIa

Use additional external cause code (Chapter XX), if desired, to identify any administered anticoagulant.

Excl.: long-term use of anticoagulants without haemorrhage (Z92.1)

D68.4 Acquired coagulation factor deficiency

Deficiency of coagulation factor due to:

• liver disease

• vitamin K deficiency

Excl.: vitamin K deficiency of newborn (P53)

D68.5 Primary thrombophilia

Activated protein C resistance [factor V Leiden mutation] Deficiency:

• antithrombin

• protein C

• protein S

Prothrombin gene mutation

D68.6 Other thrombophilia

Anticardiolipin syndrome Antiphospholipid syndrome Presence of the lupus anticoagulant

Excl.: disseminated intravascular coagulation (D65) hyperhomocysteinemia (E72.1)

D68.8 Other specified coagulation defects D68.9 Coagulation defect, unspecified

  D69 Purpura and other haemorrhagic conditions

Excl.: benign hypergammaglobulinaemic purpura (D89.0) cryoglobulinaemic purpura (D89.1)

essential (haemorrhagic) thrombocythaemia (D47.3) purpura fulminans (D65)

thrombotic thrombocytopenic purpura (M31.1)

D69.0 Allergic purpura

Purpura:

• anaphylactoid

• Henoch(–Schönlein)

• nonthrombocytopenic:

– haemorrhagic

– idiopathic

• vascular Vasculitis, allergic

D69.1 Qualitative platelet defects Bernard–Soulier [giant platelet] syndrome Glanzmann’s disease

Grey platelet syndrome

Thromboasthenia (haemorrhagic)(hereditary) Thrombocytopathy

Excl.: von Willebrand disease (D68.0)

D69.2 Other nonthrombocytopenic purpura

Purpura:

• NOS

• senile

• simplex

D69.3 Idiopathic thrombocytopenic purpura

Evans syndrome

D69.4 Other primary thrombocytopenia

Excl.: thrombocytopenia with absent radius (Q87.2) transient neonatal thrombocytopenia (P61.0) Wiskott–Aldrich syndrome (D82.0)

D69.5 Secondary thrombocytopenia

Use additional external cause code (Chapter XX), if desired, to identify cause.

D69.6 Thrombocytopenia, unspecified

D69.8 Other specified haemorrhagic conditions

Capillary fragility (hereditary) Vascular pseudohaemophilia

D69.9 Haemorrhagic condition, unspecified

Other diseases of blood and blood-forming organs (D70–D77)

  D70 Agranulocytosis

Incl.: agranulocytic angina

infantile genetic agranulocytosis Kostmann disease

Neutropenia:

• NOS

• congenital

• cyclic

• drug-induced

• periodic

• splenic (primary)

• toxic

neutropenic splenomegaly Werner–Schultz disease

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: transient neonatal neutropenia (P61.5)

  D71 Functional disorders of polymorphonuclear neutrophils

Incl.: cell membrane receptor complex [CR3] defect chronic (childhood) granulomatous disease congenital dysphagocytosis

Progressive septic granulomatosis

  D72 Other disorders of white blood cells

Excl.:  basophilia (D75.8)

immunity disorders (D80-D89) neutropenia (D70)

abnormal white blood cells (count) (R72) preleukaemia (syndrome) (D46.9)

D72.0 Genetic anomalies of leukocytes

Anomaly (granulation)(granulocyte) or syndrome:

• Alder

• May–Hegglin

• Pelger–Huët Hereditary:

• leukocytic:

– hypersegmentation

– hyposegmentation

• leukomelanopathy

Excl.: Chediak(–Steinbrinck)–Higashi syndrome (E70.3)

D72.1 Eosinophilia

Eosinophilia:

• allergic

• hereditary

D72.8 Other specified disorders of white blood cells

Leukaemoid reaction:

• lymphocytic

• monocytic

• myelocytic Leukocytosis

Lymphocytosis (symptomatic) Lymphopenia

Monocytosis (symptomatic) Plasmacytosis

D72.9 Disorder of white blood cells, unspecified

  D73 Diseases of spleen

D73.0 Hyposplenism Asplenia, postsurgical Atrophy of spleen

Excl.: asplenia (congenital) (Q89.0)

D73.1 Hypersplenism

Excl.: splenomegaly:

• NOS (R16.1)

• congenital (Q89.0)

D73.2 Chronic congestive splenomegaly

D73.3 Abscess of spleen D73.4 Cyst of spleen D73.5 Infarction of spleen

Splenic rupture, nontraumatic Torsion of spleen

Excl.: traumatic rupture of spleen (S36.0)

D73.8 Other diseases of spleen

Fibrosis of spleen NOS Perisplenitis

Splenitis NOS

D73.9 Disease of spleen, unspecified

  D74 Methaemoglobinaemia

D74.0 Congenital methaemoglobinaemia

Congenital NADH-methaemoglobin reductase deficiency Haemoglobin-M [Hb-M] disease

Methaemoglobinaemia, hereditary

D74.8 Other methaemoglobinaemias

Acquired methaemoglobinaemia (with sulfhaemoglobinaemia) Toxic methaemoglobinaemia

Use additional external cause code (Chapter XX), if desired, to identify cause.

D74.9 Methaemoglobinaemia, unspecified

  D75 Other diseases of blood and blood-forming organs

Excl.: enlarged lymph nodes (R59.-) hypergammaglobulinaemia NOS (D89.2) lymphadenitis:

• NOS (I88.9)

• acute (L04.-)

• chronic (I88.1)

• mesenteric (acute)(chronic) (I88.0)

D75.0 Familial erythrocytosis

Polycythaemia:

• benign

• familial

Excl.: hereditary ovalocytosis (D58.1)

D75.1 Secondary polycythaemia Erythrocytosis NOS Polycythaemia:

• NOS

• acquired

• due to:

– erythropoietin

– fall in plasma volume

– high altitude

– stress

• emotional

• hypoxaemic

• nephrogenous

• relative

Excl.: polycythaemia:

• neonatorum (P61.1)

• vera (D45)

D75.8 Other specified diseases of blood and blood-forming organs

Basophilia

D75.9 Disease of blood and blood-forming organs, unspecified

  D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue Excl.: (Abt–)Letterer–Siwe disease (C96.0)

eosinophilic granuloma (C96.6) Hand–Schüller–Christian disease (C96.5) histiocytic sarcoma (C96.8)

histiocytosis X, multifocal (C96.5) histiocytosis X, unifocal (C96.6)

Langerhans-cell histiocytosis, multifocal (C96.5) Langerhans-cell histiocytosis, unifocal (C96.6) malignant histiocytosis (C96.8) reticuloendotheliosis:

• leukaemic (C91.4)

• nonlipid (C96.0) reticulosis:

• histiocytic medullary (C96.8) • lipomelanotic (I89.8)

• malignant NOS (C86.0)

D76.1 Haemophagocytic lymphohistiocytosis Familial haemophagocytic reticulosis Histiocytoses of mononuclear phagocytes

D76.2 Haemophagocytic syndrome, infection-associated

Use additional code, if desired, to identify infectious agent or disease.

D76.3 Other histiocytosis syndromes

Reticulohistiocytoma (giant-cell)

Sinus histiocytosis with massive lymphadenopathy Xanthogranuloma

  D77* Other disorders of blood and blood-forming organs in diseases classified elsewhere

Incl.: fibrosis of spleen in schistosomiasis [bilharziasis] (B65.-†)

Certain disorders involving the immune mechanism (D80–D89)

Incl.: defects in the complement system

immunodeficiency disorders, except human immunodeficiency virus [HIV] disease

sarcoidosis

Excl.: autoimmune disease (systemic) NOS (M35.9)

functional disorders of polymorphonuclear neutrophils (D71) human immunodeficiency virus [HIV] disease (B20–B24)

human immunodeficiency virus [HIV] disease complicating pregnancy childbirth and the puerperium (O98.7)

  D80 Immunodeficiency with predominantly antibody defects

D80.0 Hereditary hypogammaglobulinaemia

Autosomal recessive agammaglobulinaemia (Swiss type)

X-linked agammaglobulinaemia [Bruton] (with growth hormone deficiency)

D80.1 Nonfamilial hypogammaglobulinaemia

Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes Common variable agammaglobulinaemia [CVAgamma] Hypogammaglobulinaemia NOS

D80.2 Selective deficiency of immunoglobulin A [IgA]

D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses D80.4 Selective deficiency of immunoglobulin M [IgM]

D80.5 Immunodeficiency with increased immunoglobulin M [IgM]

D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia

D80.7 Transient hypogammaglobulinaemia of infancy

D80.8 Other immunodeficiencies with predominantly antibody defects

Kappa light chain deficiency

D80.9 Immunodeficiency with predominantly antibody defects, unspecified

  D81 Combined immunodeficiencies

Excl.: autosomal recessive agammaglobulinaemia (Swiss type) (D80.0)

D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis

D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers

D81.2 Severe combined immunodeficiency [SCID] with low or normal B-cell numbers

D81.3 Adenosine deaminase [ADA] deficiency D81.4 Nezelof syndrome

D81.5 Purine nucleoside phosphorylase [PNP] deficiency

D81.6 Major histocompatibility complex class I deficiency

Bare lymphocyte syndrome

D81.7 Major histocompatibility complex class II deficiency D81.8 Other combined immunodeficiencies

Biotin-dependent carboxylase deficiency

D81.9 Combined immunodeficiency, unspecified

Severe combined immunodeficiency disorder [SCID] NOS

  D82 Immunodeficiency associated with other major defects

Excl.: ataxia telangiectasia [Louis–Bar] (G11.3)

D82.0 Wiskott–Aldrich syndrome

Immunodeficiency with thrombocytopenia and eczema

D82.1 DiGeorge syndrome

Pharyngeal pouch syndrome Thymic:

• alymphoplasia

• aplasia or hypoplasia with immunodeficiency

D82.2 Immunodeficiency with short-limbed stature

D82.3 Immunodeficiency following hereditary defective response to Epstein–Barr virus

X-linked lymphoproliferative disease

D82.4 Hyperimmunoglobulin E [IgE] syndrome

D82.8 Immunodeficiency associated with other specified major defects

D82.9 Immunodeficiency associated with major defect, unspecified

 

  D83 Common variable immunodeficiency

D83.0 Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function

D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders

D83.2 Common variable immunodeficiency with autoantibodies to B- or T-cells

D83.8 Other common variable immunodeficiencies D83.9 Common variable immunodeficiency, unspecified

  D84 Other immunodeficiencies

D84.0 Lymphocyte function antigen-1 [LFA-1] defect D84.1 Defects in the complement system

C1 esterase inhibitor [C1-INH] deficiency

D84.8 Other specified immunodeficiencies D84.9 Immunodeficiency, unspecified

  D86 Sarcoidosis

D86.0 Sarcoidosis of lung

D86.1 Sarcoidosis of lymph nodes

D86.2 Sarcoidosis of lung with sarcoidosis of lymph nodes D86.3 Sarcoidosis of skin

D86.8 Sarcoidosis of other and combined sites

Iridocyclitis in sarcoidosis† (H22.1*)

Multiple cranial nerve palsies in sarcoidosis† (G53.2*) Sarcoid:

• arthropathy† (M14.8*)

• myocarditis† (I41.8*)

• myositis† (M63.3*) Uveoparotid fever [Heerfordt’s]

D86.9 Sarcoidosis, unspecified

  D89 Other disorders involving the immune mechanism, not elsewhere classified

Excl.: hyperglobulinaemia NOS (R77.1)

monoclonal gammopathy of undertermined significance [MGUS] (D47.2)

transplant failure and rejection (T86.-)

D89.0 Polyclonal hypergammaglobulinaemia Benign hypergammaglobulinaemic purpura Polyclonal gammopathy NOS

D89.1 Cryoglobulinaemia

Cryoglobulinaemia:

• essential

• idiopathic

• mixed

• primary

• secondary Cryoglobulinaemic:

• purpura

• vasculitis

D89.2 Hypergammaglobulinaemia, unspecified D89.3 Immune reconstitution syndrome

Immune reconstitution inflammatory syndrome [IRIS]

Use additional external cause code (Chapter XX), if desired, to identify drug.

D89.8 Other specified disorders involving the immune mechanism, not elsewhere classified

D89.9 Disorder involving the immune mechanism, unspecified

Immune disease NOS 

CHAPTER IV

Endocrine, nutritional and metabolic diseases

(E00–E90)

Note: All neoplasms, whether functionally active or not, are classified in Chapter

II. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16–E31, E34.-) may be used, if desired, as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other  conditions classified elsewhere.

Excl.: complications of pregnancy, childbirth and the puerperium (O00–O99) symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

transitory endocrine and metabolic disorders specific to fetus and newborn (P70–P74)

This chapter contains the following blocks:

E00–E07 Disorders of thyroid gland E10–E14 Diabetes mellitus

E15–E16 Other disorders of glucose regulation and pancreatic internal secretion E20–E35 Disorders of other endocrine glands

E40–E46 Malnutrition

E50–E64 Other nutritional deficiencies E65–E68 Obesity and other hyperalimentation E70–E90 Metabolic disorders

Asterisk categories for this chapter are provided as follows:

E35* Disorders of endocrine glands in diseases classified elsewhere E90* Nutritional and metabolic disorders in diseases classified elsewhere

Disorders of thyroid gland (E00–E07)

  E00 Congenital iodine-deficiency syndrome

Incl.:  endemic conditions associated with environmental iodine deficiency either directly or as a consequence of maternal iodine deficiency. Some of the conditions have no current hypothyroidism but are the consequence of inadequate thyroid hormone secretion in the developing fetus. Environmental goitrogens may be associated.

Use additional code (F70–F79), if desired, to identify associated mental retardation.

Excl.: subclinical iodine-deficiency hypothyroidism (E02)

E00.0 Congenital iodine-deficiency syndrome, neurological type

Endemic cretinism, neurological type

E00.1 Congenital iodine-deficiency syndrome, myxoedematous type

Endemic cretinism:

• hypothyroid

• myxoedematous type

E00.2 Congenital iodine-deficiency syndrome, mixed type

Endemic cretinism, mixed type

E00.9 Congenital iodine-deficiency syndrome, unspecified

Congenital iodine-deficiency hypothyroidism NOS Endemic cretinism NOS

  E01 Iodine-deficiency-related thyroid disorders and allied conditions

Excl.: congenital iodine-deficiency syndrome (E00.-) subclinical iodine-deficiency hypothyroidism (E02)

E01.0 Iodine-deficiency-related diffuse (endemic) goitre E01.1 Iodine-deficiency-related multinodular (endemic) goitre

Iodine-deficiency-related nodular goitre

E01.2 Iodine-deficiency-related (endemic) goitre, unspecified

Endemic goitre NOS

E01.8 Other iodine-deficiency-related thyroid disorders and allied conditions

Acquired iodine-deficiency hypothyroidism NOS

  E02 Subclinical iodine-deficiency hypothyroidism

  E03 Other hypothyroidism

Excl.: iodine-deficiency-related hypothyroidism (E00–E02) postprocedural hypothyroidism (E89.0)

E03.0 Congenital hypothyroidism with diffuse goitre

Goitre (nontoxic) congenital:

• NOS

• parenchymatous

Excl.: transitory congenital goitre with normal function (P72.0)

E03.1 Congenital hypothyroidism without goitre Aplasia of thyroid (with myxoedema) Congenital:

• atrophy of thyroid

• hypothyroidism NOS

E03.2 Hypothyroidism due to medicaments and other exogenous substances

Use additional external cause code (Chapter XX), if desired, to identify cause.

E03.3 Postinfectious hypothyroidism E03.4 Atrophy of thyroid (acquired)

Excl.: congenital atrophy of thyroid (E03.1)

E03.5 Myxoedema coma

E03.8 Other specified hypothyroidism E03.9 Hypothyroidism, unspecified

Myxoedema NOS

  E04 Other nontoxic goitre

Excl.: congenital goitre:

• NOS (E03.3)

• diffuse (E03.3)

• parenchymatous (E03.3)

iodine-deficiency-related goitre (E00–E02)

E04.0 Nontoxic diffuse goitre

Goitre, nontoxic:

• diffuse (colloid)

• simple

E04.1 Nontoxic single thyroid nodule Colloid nodule (cystic)(thyroid) Nontoxic uninodular goitre

Thyroid (cystic) nodule NOS

E04.2 Nontoxic multinodular goitre

Cystic goitre NOS

Multinodular (cystic) goitre NOS

E04.8 Other specified nontoxic goitre E04.9 Nontoxic goitre, unspecified

Goitre NOS

Nodular goitre (nontoxic) NOS

  E05 Thyrotoxicosis [hyperthyroidism]

Excl.: chronic thyroiditis with transient thyrotoxicosis (E06.2) neonatal thyrotoxicosis (P72.1)

E05.0 Thyrotoxicosis with diffuse goitre Exophthalmic or toxic goitre NOS Graves disease

Toxic diffuse goitre

E05.1 Thyrotoxicosis with toxic single thyroid nodule

Thyrotoxicosis with toxic uninodular goitre

E05.2 Thyrotoxicosis with toxic multinodular goitre

Toxic nodular goitre NOS

E05.3 Thyrotoxicosis from ectopic thyroid tissue E05.4 Thyrotoxicosis factitia

E05.5 Thyroid crisis or storm

E05.8 Other thyrotoxicosis

Overproduction of thyroid-stimulating hormone

Use additional external cause code (Chapter XX), if desired, to identify cause.

E05.9 Thyrotoxicosis, unspecified

Hyperthyroidism NOS

Thyrotoxic heart disease† (I43.8*)

  E06 Thyroiditis

Excl.: postpartum thyroiditis (O90.5)

E06.0 Acute thyroiditis

Abscess of thyroid Thyroiditis:

• pyogenic

• suppurative

Use additional code (B95–B98), if desired, to identify infectious agent.

E06.1 Subacute thyroiditis

Thyroiditis:

• de Quervain

• giant-cell

• granulomatous

• nonsuppurative

Excl.: autoimmune thyroiditis (E06.3)

E06.2 Chronic thyroiditis with transient thyrotoxicosis

Excl.: autoimmune thyroiditis (E06.3)

E06.3 Autoimmune thyroiditis

Hashimoto thyroiditis Hashitoxicosis (transient) Lymphadenoid goitre Lymphocytic thyroiditis Struma lymphomatosa

E06.4 Drug-induced thyroiditis

Use additional external cause code (Chapter XX), if desired, to identify drug.

E06.5 Other chronic thyroiditis

Thyroiditis:

• chronic:

– NOS

– fibrous

• ligneous

• Riedel

E06.9 Thyroiditis, unspecified

  E07 Other disorders of thyroid

E07.0 Hypersecretion of calcitonin C-cell hyperplasia of thyroid Hypersecretion of thyrocalcitonin

E07.1 Dyshormogenetic goitre

Familial dyshormogenetic goitre Pendred syndrome

Excl.: transitory congenital goitre with normal function (P72.0)

E07.8 Other specified disorders of thyroid

Abnormality of thyroid-binding globulin

Haemorrhage

Infarction of thyroid

Sick-euthyroid syndrome

E07.9 Disorder of thyroid, unspecified

Diabetes mellitus (E10–E14)

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

The following fourth-character subdivisions are for use with categories E10–E14:

.0 With coma

Diabetic:

• coma with or without ketoacidosis

• hyperosmolar coma

• hypoglycaemic coma Hyperglycaemic coma NOS

.1 With ketoacidosis

Diabetic:

• acidosis

• ketoacidosis

without mention of coma

.2† With renal complications

Diabetic nephropathy (N08.3*) Intracapillary glomerulonephrosis (N08.3*) Kimmelstiel–Wilson syndrome (N08.3*)

.3† With ophthalmic complications

Diabetic:

• cataract (H28.0*)

• retinopathy (H36.0*)

.4† With neurological complications

Diabetic:

• amyotrophy (G73.0*)

• autonomic neuropathy (G99.0*)

• mononeuropathy (G59.0*)

• polyneuropathy (G63.2*)

– autonomic (G99.0*)

.5 With peripheral circulatory complications

Diabetic:

• gangrene

• peripheral angiopathy† (I79.2*)

• ulcer

.6 With other specified complications

Diabetic arthropathy† (M14.2*) Neuropathic diabetic arthropathy† (M14.6*)

.7 With multiple complications

.8 With unspecified complications

.9 Without complications

  E10 Type 1 diabetes mellitus

[See before E10 for subdivisions]

Incl.: diabetes (mellitus):

• brittle

• juvenile-onset

• ketosis-prone

Excl.: diabetes mellitus (in):

• malnutrition-related (E12.-)

• neonatal (P70.2)

• pregnancy, childbirth and the puerperium (O24.-) glycosuria:

• NOS (R81)

• renal (E74.8)

impaired glucose tolerance (R73.0) postsurgical hypoinsulinaemia (E89.1)

  E11 Type 2 diabetes mellitus

[See before E10 for subdivisions]

Incl.: diabetes (mellitus)(nonobese)(obese):

• adult-onset

• maturity-onset

• nonketotic

• stable

non-insulin-dependent diabetes of the young

Excl.: diabetes mellitus (in):

• malnutrition-related (E12.-)

• neonatal (P70.2)

• pregnancy, childbirth and the puerperium (O24.-) glycosuria:

• NOS (R81)

• renal (E74.8)

impaired glucose tolerance (R73.0) postsurgical hypoinsulinaemia (E89.1)

 

  E12 Malnutrition-related diabetes mellitus

[See before E10 for subdivisions]

Incl.: malnutrition-related diabetes mellitus:

• type 1

• type 2

Excl.: diabetes mellitus in pregnancy, childbirth and the puerperium (O24.-) glycosuria:

• NOS (R81)

• renal (E74.8)

impaired glucose tolerance (R73.0) neonatal diabetes mellitus (P70.2) postsurgical hypoinsulinaemia (E89.1)

  E13 Other specified diabetes mellitus

[See before E10 for subdivisions]

Excl.: diabetes mellitus (in):

• malnutrition-related (E12.-)

• neonatal (P70.2)

• pregnancy, childbirth and the puerperium (O24.-)

• t ype 1 (E10.-)

• type 2 (E11.-) glycosuria:

• NOS (R81)

• renal (E74.8)

impaired glucose tolerance (R73.0) postsurgical hypoinsulinaemia (E89.1)

  E14 Unspecified diabetes mellitus

[See before E10 for subdivisions]

Incl.: diabetes NOS

Excl.: diabetes mellitus (in):

• malnutrition-related (E12.-)

• neonatal (P70.2)

• pregnancy, childbirth and the puerperium (O24.-)

• type 1 (E10.-)

• type 2 (E11.-) glycosuria:

• NOS (R81)

• renal (E74.8)

impaired glucose tolerance (R73.0) postsurgical hypoinsulinaemia (E89.1)

 

Other disorders of glucose regulation and pancreatic internal secretion

(E15–E16)

  E15 Nondiabetic hypoglycaemic coma

Incl.: drug-induced insulin coma in nondiabetic hyperinsulinism with hypoglycaemic coma hypoglycaemic coma NOS

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

  E16 Other disorders of pancreatic internal secretion

E16.0 Drug-induced hypoglycaemia without coma

Use additional external cause code (Chapter XX), if desired, to identify drug.

E16.1 Other hypoglycaemia

Functional nonhyperinsulinaemic hypoglycaemia Hyperinsulinism:

• NOS

• functional

Hyperplasia of pancreatic islet beta cells NOS Posthypoglycaemic coma encephalopathy

E16.2 Hypoglycaemia, unspecified E16.3 Increased secretion of glucagon

Hyperplasia of pancreatic endocrine cells with glucagon excess

E16.4 Abnormal secretion of gastrin Hypergastrinaemia Zollinger–Ellison syndrome

E16.8 Other specified disorders of pancreatic internal secretion

Increased secretion from endocrine pancreas of:

• growth hormone-releasing hormone

• pancreatic polypeptide

• somatostatin

• vasoactive-intestinal polypeptide

E16.9 Disorder of pancreatic internal secretion, unspecified

Islet-cell hyperplasia NOS

Pancreatic endocrine cell hyperplasia NOS

 

Disorders of other endocrine glands (E20–E35)

Excl.: galactorrhoea (N64.3)

gynaecomastia (N62)

  E20 Hypoparathyroidism

Excl.: DiGeorge  syndrome (D82.1) postprocedural hypoparathyroidism (E89.2) tetany NOS (R29.0)

transitory neonatal hypoparathyroidism (P71.4)

E20.0 Idiopathic hypoparathyroidism E20.1 Pseudohypoparathyroidism E20.8 Other hypoparathyroidism

E20.9 Hypoparathyroidism, unspecified

Parathyroid tetany

  E21 Hyperparathyroidism and other disorders of parathyroid gland

Excl.: osteomalacia:

• adult (M83.-)

• infantile and juvenile (E55.0)

E21.0 Primary hyperparathyroidism

Hyperplasia of parathyroid

Osteitis fibrosa cystica generalisata [von Recklinghausen disease of bone]

E21.1 Secondary hyperparathyroidism, not elsewhere classified

Excl.: secondary hyperparathyroidism of renal origin (N25.8)

E21.2 Other hyperparathyroidism

Tertiary hyperparathryoidism

Excl.: familial hypocalciuric hypercalcaemia (E83.5)

E21.3 Hyperparathyroidism, unspecified

E21.4 Other specified disorders of parathyroid gland E21.5 Disorder of parathyroid gland, unspecified

  E22 Hyperfunction of pituitary gland

Excl.: Cushing syndrome (E24.-) Nelson syndrome (E24.1) overproduction of:

• ACTH not associated with Cushing disease (E27.0)

• pituitary ACTH (E24.0)

• thyroid-stimulating hormone (E05.8)

 

E22.0 Acromegaly and pituitary gigantism Arthropathy associated with acromegaly† (M14.5*) Overproduction of growth hormone

Excl.: constitutional:

• gigantism (E34.4)

• tall stature (E34.4)

increased secretion from endocrine pancreas of growth hormone- releasing hormone (E16.8)

E22.1 Hyperprolactinaemia

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

E22.2 Syndrome of inappropriate secretion of antidiuretic hormone E22.8 Other hyperfunction of pituitary gland

Central precocious puberty

E22.9 Hyperfunction of pituitary gland, unspecified

  E23 Hypofunction and other disorders of pituitary gland

Incl.: the listed conditions whether the disorder is in the pituitary or the hypothalamus

Excl.: postprocedural hypopituitarism (E89.3)

E23.0 Hypopituitarism

Fertile eunuch syndrome Hypogonadotropic hypogonadism Idiopathic growth hormone deficiency Isolated deficiency of:

• gonadotropin

• growth hormone

• pituitary hormone Kallmann syndrome Lorain–Levi short stature

Necrosis of pituitary gland (postpartum) Panhypopituitarism

Pituitary:

• cachexia

• insufficiency NOS

• short stature Sheehan syndrome Simmonds disease

E23.1 Drug-induced hypopituitarism

Use additional external cause code (Chapter XX), if desired, to identify drug.

E23.2 Diabetes insipidus

Excl.: nephrogenic diabetes insipidus (N25.1)

 

E23.3 Hypothalamic dysfunction, not elsewhere classified

Excl.: Prader–Willi syndrome (Q87.1) Russell–Silver syndrome (Q87.1)

E23.6 Other disorders of pituitary gland

Abscess of pituitary Adiposogenital dystrophy

E23.7 Disorder of pituitary gland, unspecified

  E24 Cushing syndrome

E24.0 Pituitary-dependent Cushing disease Overproduction of pituitary ACTH Pituitary-dependent hyperadrenocorticism

E24.1 Nelson syndrome

E24.2 Drug-induced Cushing syndrome

Use additional external cause code (Chapter XX), if desired, to identify drug.

E24.3 Ectopic ACTH syndrome

E24.4 Alcohol-induced pseudo-Cushing syndrome E24.8 Other Cushing syndrome

E24.9 Cushing syndrome, unspecified

  E25 Adrenogenital disorders

Incl.: adrenogenital syndromes, virilizing or feminizing, whether acquired or due to adrenal hyperplasia consequent on inborn enzyme defects in hormone synthesis

female:

• adrenal pseudohermaphroditism

• heterosexual precocious pseudopuberty male:

• isosexual precocious pseudopuberty

• macrogenitosomia praecox

• sexual precocity with adrenal hyperplasia virilization (female)

E25.0 Congenital adrenogenital disorders associated with enzyme deficiency

Congenital adrenal hyperplasia 21-Hydroxylase deficiency

Salt-losing congenital adrenal hyperplasia

E25.8 Other adrenogenital disorders

Idiopathic adrenogenital disorder

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

 

E25.9 Adrenogenital disorder, unspecified

Adrenogenital syndrome NOS

  E26 Hyperaldosteronism

E26.0 Primary hyperaldosteronism

Conn syndrome

Primary aldosteronism due to adrenal hyperplasia (bilateral)

E26.1 Secondary hyperaldosteronism E26.8 Other hyperaldosteronism

Bartter syndrome

E26.9 Hyperaldosteronism, unspecified

  E27 Other disorders of adrenal gland

E27.0 Other adrenocortical overactivity

Overproduction of ACTH, not associated with Cushing disease Premature adrenarche

Excl.: Cushing syndrome (E24.-)

E27.1 Primary adrenocortical insufficiency

Addison disease Autoimmune adrenalitis

Excl.: amyloidosis (E85.-)

tuberculous Addison disease (A18.7) Waterhouse–Friderichsen syndrome (A39.1)

E27.2 Addisonian crisis

Adrenal crisis Adrenocortical crisis

E27.3 Drug-induced adrenocortical insufficiency

Use additional external cause code (Chapter XX), if desired, to identify drug.

E27.4 Other and unspecified adrenocortical insufficiency

Adrenal:

• haemorrhage

• infarction

Adrenocortical insufficiency NOS Hypoaldosteronism

Excl.: adrenoleukodystrophy [Addison–Schilder] (E71.3) Waterhouse-Friderichsen syndrome (A39.1)

E27.5 Adrenomedullary hyperfunction Adrenomedullary hyperplasia Catecholamine hypersecretion

E27.8 Other specified disorders of adrenal gland

Abnormality of cortisol-binding globulin

E27.9 Disorder of adrenal gland, unspecified

 

  E28 Ovarian dysfunction

Excl.: isolated gonadotropin deficiency (E23.0) postprocedural ovarian failure (E89.4)

E28.0 Estrogen excess

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

E28.1 Androgen excess

Hypersecretion of ovarian androgens

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

E28.2 Polycystic ovarian syndrome Sclerocystic ovary syndrome Stein–Leventhal syndrome

E28.3 Primary ovarian failure

Decreased estrogen Premature menopause NOS Resistant ovary syndrome

Excl.: menopausal and female climacteric states (N95.1) pure gonadal dysgenesis (Q99.1)

Turner syndrome (Q96.-)

E28.8 Other ovarian dysfunction

Ovarian hyperfunction NOS

E28.9 Ovarian dysfunction, unspecified

  E29 Testicular dysfunction

Excl.: androgen resistance syndrome (E34.5) azoospermia or oligospermia NOS (N46) isolated gonadotropin deficiency (E23.0) Klinefelter syndrome (Q98.0–Q98.2, Q98.4) postprocedural testicular hypofunction (E89.5) testicular feminization (syndrome) (E34.5)

E29.0 Testicular hyperfunction

Hypersecretion of testicular hormones

E29.1 Testicular hypofunction

5-Alpha-reductase deficiency (with male pseudohermaphroditism) Defective biosynthesis of testicular androgen NOS

Testicular hypogonadism NOS

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

E29.8 Other testicular dysfunction

E29.9 Testicular dysfunction, unspecified

 

  E30 Disorders of puberty, not elsewhere classified

E30.0 Delayed puberty

Constitutional delay of puberty Delayed sexual development

E30.1 Precocious puberty

Precocious menstruation

Excl.: Albright(–McCune)(–Sternberg) syndrome (Q78.1) central precocious puberty (E22.8)

congenital adrenal hyperplasia (E25.0)

female heterosexual precocious pseudopuberty (E25.-) male isosexual precocious pseudopuberty (E25.-)

E30.8 Other disorders of puberty

Premature thelarche

E30.9 Disorder of puberty, unspecified

  E31 Polyglandular dysfunction

Excl.: ataxia telangiectasia [Louis–Bar] (G11.3) dystrophia myotonica [Steinert] (G71.1) pseudohypoparathyroidism (E20.1)

E31.0 Autoimmune polyglandular failure

Schmidt’s syndrome

E31.1 Polyglandular hyperfunction

Excl.: multiple endocrine adenomatosis (D44.8)

E31.8 Other polyglandular dysfunction

E31.9 Polyglandular dysfunction, unspecified

  E32 Diseases of thymus

Excl.: aplasia or hypoplasia with immunodeficiency (D82.1) myasthenia gravis (G70.0)

E32.0 Persistent hyperplasia of thymus

Hypertrophy of thymus

E32.1 Abscess of thymus

E32.8 Other diseases of thymus E32.9 Disease of thymus, unspecified

  E34 Other endocrine disorders

Excl.: pseudohypoparathyroidism (E20.1)

E34.0 Carcinoid syndrome

Note: May be used as an additional code, if desired, to identify functional activity associated with a carcinoid tumour.

 

E34.1 Other hypersecretion of intestinal hormones

E34.2 Ectopic hormone secretion, not elsewhere classified E34.3 Short stature, not elsewhere classified

Short stature:

• NOS

• constitutional

• Laron-type

• psychosocial

Excl.: progeria (E34.8)

Russell–Silver syndrome (Q87.1)

short-limbed stature with immunodeficiency (D82.2) short stature:

• achondroplastic (Q77.4)

• hypochondroplastic (Q77.4)

• in specific dysmorphic syndromes – code to syndrome – see Alphabetical index

• nutritional (E45)

• pituitary (E23.0)

• renal (N25.0)

E34.4 Constitutional tall stature

Constitutional gigantism

E34.5 Androgen resistance syndrome

Male pseudohermaphroditism with androgen resistance Peripheral hormonal receptor disorder

Reifenstein syndrome

Testicular feminization (syndrome)

E34.8 Other specified endocrine disorders

Pineal gland dysfunction Progeria

E34.9 Endocrine disorder, unspecified

Disturbance:

• endocrine NOS

• hormone NOS

  E35* Disorders of endocrine glands in diseases classified elsewhere

E35.0* Disorders of thyroid gland in diseases classified elsewhere

Tuberculosis of thyroid gland (A18.8†)

E35.1* Disorders of adrenal glands in diseases classified elsewhere

Tuberculous Addison disease (A18.7†) Waterhouse–Friderichsen syndrome (meningococcal) (A39.1†)

E35.8* Disorders of other endocrine glands in diseases classified elsewhere

 

Malnutrition (E40–E46)

Note:   The degree of malnutrition is usually measured in terms of weight, expressed in standard deviations from the mean of the relevant reference population. When one or more previous measurements are available, lack of weight gain in children, or evidence of weight loss in children or adults, is usually indicative of malnutrition. When only one measurement is available, the diagnosis is based on probabilities and is not definitive without other clinical or laboratory tests. In the exceptional circumstances that no measurement of weight is available, reliance should be placed on clinical evidence.

If an observed weight is below the mean value of the reference population, there is a high probability of severe malnutrition if there is an observed value situated 3 or more standard deviations below the mean value of the reference population; a high probability of moderate malnutrition for an observed value located between 2 and less than 3 standard deviations below this mean; and a high probability of mild malnutrition for an observed value located between 1 and less than 2 standard deviations below this mean.

Excl.: intestinal malabsorption (K90.-) nutritional anaemias (D50–D53)

sequelae of protein-energy malnutrition (E64.0) slim disease (B22.2)

starvation (T73.0)

  E40 Kwashiorkor

Severe malnutrition with nutritional oedema with dyspigmentation of skin and hair.

Excl.: marasmic kwashiorkor (E42)

  E41 Nutritional marasmus

Incl.: severe malnutrition with marasmus

Excl.: marasmic kwashiorkor (E42)

  E42 Marasmic kwashiorkor

Incl.: severe protein-energy malnutrition [as in E43]: intermediate form

with signs of both kwashiorkor and marasmus

  E43 Unspecified severe protein-energy malnutrition

Severe loss of weight [wasting] in children or adults, or lack of weight gain in children leading to an observed weight that is at least 3 standard deviations below the mean value for the reference population (or a similar loss expressed through other statistical approaches). When only one measurement is available, there is a high probability of severe wasting when the observed weight is 3 or more standard deviations below the mean of the reference population.

Incl.: starvation oedema

 

  E44 Protein-energy malnutrition of moderate and mild degree

E44.0 Moderate protein-energy malnutrition

Weight loss in children or adults, or lack of weight gain in children leading to an observed weight that is 2 or more but less than 3 standard deviations below the mean value for the reference population (or a similar loss expressed through other statistical approaches). When only one measurement is available, there is a high probability of moderate protein-energy malnutrition when the observed weight is 2 or more but less than 3 standard deviations below the mean of the reference population.

E44.1 Mild protein-energy malnutrition

Weight loss in children or adults, or lack of weight gain in children leading to an observed weight that is 1 or more but less than 2 standard deviations below the mean value for the reference population (or a similar loss expresssed through other statistical approaches). When only one measurement is available, there is a high probability of mild protein-energy malnutrition when the observed weight is 1 or more but less than 2 standard deviations below the mean of the reference population.

  E45 Retarded development following protein-energy malnutrition

Incl.: nutritional:

• short stature

• stunting

physical retardation due to malnutrition

  E46 Unspecified protein-energy malnutrition

Incl.: malnutrition NOS

protein-energy imbalance NOS

Other nutritional deficiencies (E50–E64)

Excl.: nutritional anaemias (D50–D53)

  E50 Vitamin A deficiency

Excl.: sequelae of vitamin A deficiency (E64.1)

E50.0 Vitamin A deficiency with conjunctival xerosis

E50.1 Vitamin A deficiency with Bitot spot and conjunctival xerosis

Bitot spot in the young child

E50.2 Vitamin A deficiency with corneal xerosis

E50.3 Vitamin A deficiency with corneal ulceration and xerosis E50.4 Vitamin A deficiency with keratomalacia

E50.5 Vitamin A deficiency with night blindness

E50.6 Vitamin A deficiency with xerophthalmic scars of cornea

 

E50.7 Other ocular manifestations of vitamin A deficiency

Xerophthalmia NOS

E50.8 Other manifestations of vitamin A deficiency

Follicular keratosis

Xeroderma due to vitamin A deficiency† (L86*)

E50.9 Vitamin A deficiency, unspecified

Hypovitaminosis A NOS

  E51 Thiamine deficiency

Excl.: sequelae of thiamine deficiency (E64.8)

E51.1 Beriberi

Beriberi:

• dry

• wet† (I98.8*)

E51.2 Wernicke encephalopathy

E51.8 Other manifestations of thiamine deficiency E51.9 Thiamine deficiency, unspecified

  E52 Niacin deficiency [pellagra]

Incl.: deficiency:

• niacin(-tryptophan)

• nicotinamide pellagra (alcoholic)

Excl.: sequelae of niacin deficiency (E64.8)

  E53 Deficiency of other B group vitamins

Excl.: sequelae of vitamin B deficiency (E64.8) vitamin B12 deficiency anaemia (D51.-)

E53.0 Riboflavin deficiency

Ariboflavinosis

E53.1 Pyridoxine deficiency

Vitamin B6 deficiency

Excl.: pyridoxine-responsive sideroblastic anaemia (D64.3)

E53.8 Deficiency of other specified B group vitamins

Deficiency:

• biotin

• cyanocobalamin

• folate

• folic acid

• pantothenic acid

• vitamin B12

E53.9 Vitamin B deficiency, unspecified

 

  E54 Ascorbic acid deficiency

Incl.: deficiency of vitamin C scurvy

Excl.: scorbutic anaemia (D53.2)

sequelae of vitamin C deficiency (E64.2)

  E55 Vitamin D deficiency

Excl.: adult osteomalacia (M83.-) osteoporosis (M80–M81) sequelae of rickets (E64.3)

E55.0 Rickets, active

Osteomalacia:

• infantile

• juvenile

Excl.: rickets:

• coeliac (K90.0)

• Crohn (K50.-)

• inactive (E64.3)

• renal (N25.0)

• vitamin-D-resistant (E83.3)

E55.9 Vitamin D deficiency, unspecified

Avitaminosis D

  E56 Other vitamin deficiencies

Excl.: sequelae of other vitamin deficiencies (E64.8)

E56.0 Deficiency of vitamin E E56.1 Deficiency of vitamin K

Excl.: deficiency of coagulation factor due to vitamin K deficiency (D68.4) vitamin K deficiency of newborn (P53)

E56.8 Deficiency of other vitamins E56.9 Vitamin deficiency, unspecified

  E58 Dietary calcium deficiency

Excl.: disorder of calcium metabolism (E83.5) sequelae of calcium deficiency (E64.8)

  E59 Dietary selenium deficiency

Incl.: Keshan disease

Excl.: sequelae of selenium deficiency (E64.8)

  E60 Dietary zinc deficiency

 

  E61 Deficiency of other nutrient elements

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: disorders of mineral metabolism (E83.-)

iodine-deficiency-related thyroid disorders (E00–E02)

sequelae of malnutrition and other nutritional deficiencies (E64.-)

E61.0 Copper deficiency E61.1 Iron deficiency

Excl.: iron deficiency anaemia (D50.-)

E61.2 Magnesium deficiency E61.3 Manganese deficiency E61.4 Chromium deficiency E61.5 Molybdenum deficiency E61.6 Vanadium deficiency

E61.7 Deficiency of multiple nutrient elements

E61.8 Deficiency of other specified nutrient elements E61.9 Deficiency of nutrient element, unspecified

  E63 Other nutritional deficiencies

Excl.: dehydration (E86) failure to thrive (R62.8)

feeding problems in newborn (P92.-)

sequelae of malnutrition and other nutritional deficiencies (E64.-)

E63.0 Essential fatty acid [EFA] deficiency E63.1 Imbalance of constituents of food intake E63.8 Other specified nutritional deficiencies E63.9 Nutritional deficiency, unspecified

Nutritional cardiomyopathy NOS† (I43.2*)

  E64 Sequelae of malnutrition and other nutritional deficiencies

Note: Not to be used for chronic malnutrition or nutritional deficiency.

Code these to current malnutrition or nutritional deficiency.

E64.0 Sequelae of protein-energy malnutrition

Excl.: retarded development following protein-energy malnutrition (E45)

E64.1 Sequelae of vitamin A deficiency E64.2 Sequelae of vitamin C deficiency

 

E64.3 Sequelae of rickets

Use additional code (M40.1, M41.5), if desired, to identify spinal deformity

E64.8 Sequelae of other nutritional deficiencies E64.9 Sequelae of unspecified nutritional deficiency

Obesity and other hyperalimentation (E65–E68)

  E65 Localized adiposity

Incl.: fat pad

  E66 Obesity

Excl.: adiposogenital dystrophy (E23.6) lipomatosis:

• NOS (E88.2)

• dolorosa [Dercum] (E88.2) Prader–Willi syndrome (Q87.1)

E66.0 Obesity due to excess calories E66.1 Drug-induced obesity

Use additional external cause code (Chapter XX), if desired, to identify drug.

E66.2 Extreme obesity with alveolar hypoventilation Obesity hypoventilation syndrome (OHS) Pickwickian syndrome

E66.8 Other obesity

Morbid obesity

E66.9 Obesity, unspecified

Simple obesity NOS

  E67 Other hyperalimentation

Excl.: hyperalimentation NOS (R63.2) sequelae of hyperalimentation (E68)

E67.0 Hypervitaminosis A E67.1 Hypercarotenaemia

E67.2 Megavitamin-B6 syndrome E67.3 Hypervitaminosis D

E67.8 Other specified hyperalimentation

  E68 Sequelae of hyperalimentation

Note: Not to be used for chronic hyperalimentation. Code these to current hyperalimentation.

 

Metabolic disorders (E70–E90)

Excl.: androgen resistance syndrome (E34.5) congenital adrenal hyperplasia (E25.0) Ehlers–Danlos syndrome (Q79.6)

haemolytic anaemias due to enzyme disorders (D55.-) Marfan syndrome (Q87.4)

5-alpha-reductase deficiency (E29.1)

  E70 Disorders of aromatic amino-acid metabolism

E70.0 Classical phenylketonuria E70.1 Other hyperphenylalaninaemias

E70.2 Disorders of tyrosine metabolism

Alkaptonuria Hypertyrosinaemia Ochronosis Tyrosinaemia Tyrosinosis

E70.3 Albinism

Albinism:

• ocular

• oculocutaneous Syndrome:

• Chediak(–Steinbrinck)–Higashi

• Cross

• Hermansky–Pudlak

E70.8 Other disorders of aromatic amino-acid metabolism

Disorders of:

• histidine metabolism

• tryptophan metabolism

E70.9 Disorder of aromatic amino-acid metabolism, unspecified

  E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

E71.0 Maple-syrup-urine disease

E71.1 Other disorders of branched-chain amino-acid metabolism

Hyperleucine-isoleucinaemia Hypervalinaemia

Isovaleric acidaemia Methylmalonic acidaemia Propionic acidaemia

 

E71.2 Disorder of branched-chain amino-acid metabolism, unspecified

E71.3 Disorders of fatty-acid metabolism Adrenoleukodystrophy [Addison–Schilder] Muscle carnitine palmityltransferase deficiency

Very long chain acyl-CoA dehydrogenase (VLCAD) deficiency

Excl.: Schilder disease (G37.0)

  E72 Other disorders of amino-acid metabolism

Excl.: abnormal findings without manifest disease (R70–R89) disorders of:

• aromatic amino-acid metabolism (E70.-)

• branched-chain amino-acid metabolism (E71.0–E71.2)

• fatty-acid metabolism (E71.3)

• purine and pyrimidine metabolism (E79.-) gout (M10.-)

E72.0 Disorders of amino-acid transport Cystine storage disease† (N29.8*) Cystinosis

Cystinuria

Fanconi(–de Toni)(–Debré) syndrome Hartnup disease

Lowe syndrome

Excl.: disorders of tryptophan metabolism (E70.8)

E72.1 Disorders of sulfur-bearing amino-acid metabolism

Cystathioninuria Homocystinuria Methioninaemia

Sulfite oxidase deficiency

Excl.: transcobalamin II deficiency (D51.2)

E72.2 Disorders of urea cycle metabolism

Argininaemia Argininosuccinic aciduria Citrullinaemia Hyperammonaemia

Excl.: disorders of ornithine metabolism (E72.4)

E72.3 Disorders of lysine and hydroxylysine metabolism

Glutaric aciduria Hydroxylysinaemia Hyperlysinaemia

Excl.: Refsum disease (G60.1) Zellweger syndrome (Q87.8)

 

E72.4 Disorders of ornithine metabolism

Ornithinaemia (types I, II)

E72.5 Disorders of glycine metabolism Hyperhydroxyprolinaemia Hyperprolinaemia (types I, II)

Non-ketotic hyperglycinaemia Sarcosinaemia

E72.8 Other specified disorders of amino-acid metabolism

Disorders of:

• beta-amino-acid metabolism

• gamma-glutamyl cycle

E72.9 Disorder of amino-acid metabolism, unspecified

  E73 Lactose intolerance

E73.0 Congenital lactase deficiency E73.1 Secondary lactase deficiency E73.8 Other lactose intolerance

E73.9 Lactose intolerance, unspecified

  E74 Other disorders of carbohydrate metabolism

Excl.: increased secretion of glucagon (E16.3) diabetes mellitus (E10–E14) hypoglycaemia NOS (E16.2) mucopolysaccharidosis (E76.0–E76.3)

E74.0 Glycogen storage disease

Cardiac glycogenosis Disease:

• Andersen

• Cori

• Forbes

• Hers

• McArdle

• Pompe

• Tarui

• Tauri

• von Gierke

Liver phosphorylase deficiency

E74.1 Disorders of fructose metabolism

Essential fructosuria

Fructose-1,6-diphosphatase deficiency Hereditary fructose intolerance

E74.2 Disorders of galactose metabolism

Galactokinase deficiency Galactosaemia

 

E74.3 Other disorders of intestinal carbohydrate absorption

Glucose-galactose malabsorption Sucrase deficiency

Excl.: lactose intolerance (E73.-)

E74.4 Disorders of pyruvate metabolism and gluconeogenesis

Deficiency of:

• phosphoenolpyruvate carboxykinase

• pyruvate:

– carboxylase

– dehydrogenase

Excl.: with anaemia (D55.-)

E74.8 Other specified disorders of carbohydrate metabolism

Essential pentosuria Oxalosis

Oxaluria

Renal glycosuria

E74.9 Disorder of carbohydrate metabolism, unspecified

  E75 Disorders of sphingolipid metabolism and other lipid storage disorders

Excl.: mucolipidosis, types I–III (E77.0–E77.1) Refsum disease (G60.1)

E75.0 GM2 gangliosidosis

Disease:

• Sandhoff

• Tay–Sachs

GM2 gangliosidosis:

• NOS

• adult

• juvenile

E75.1 Other gangliosidosis

Gangliosidosis:

• NOS

• GM1

• GM3 Mucolipidosis IV

 

E75.2 Other sphingolipidosis

Disease:

• Fabry(–Anderson)

• Gaucher

• Krabbe

• Niemann-–Pick Farber syndrome

Metachromatic leukodystrophy Sulfatase deficiency

Excl.: adrenoleukodystrophy [Addison–Schilder] (E71.3)

E75.3 Sphingolipidosis, unspecified E75.4 Neuronal ceroid lipofuscinosis

Disease:

• Batten

• Bielschowsky–Jansky

• Kufs

• Spielmeyer–Vogt

E75.5 Other lipid storage disorders

Cerebrotendinous cholesterosis [van Bogaert–Scherer–Epstein] Wolman disease

E75.6 Lipid storage disorder, unspecified

  E76 Disorders of glycosaminoglycan metabolism

E76.0 Mucopolysaccharidosis, type I

Syndrome:

• Hurler

• Hurler–Scheie

• Scheie

E76.1 Mucopolysaccharidosis, type II

Hunter syndrome

E76.2 Other mucopolysaccharidoses

Beta-glucuronidase deficiency Mucopolysaccharidosis, types III, IV, VI, VII Syndrome:

• Maroteaux–Lamy (mild)(severe)

• Morquio(-like)(classic)

• Sanfilippo (type B)(type C)(type D)

E76.3 Mucopolysaccharidosis, unspecified

E76.8 Other disorders of glucosaminoglycan metabolism E76.9 Disorder of glucosaminoglycan metabolism, unspecified

 

  E77 Disorders of glycoprotein metabolism

E77.0 Defects in post-translational modification of lysosomal enzymes

Mucolipidosis II [I-cell disease]

Mucolipidosis III [pseudo-Hurler polydystrophy]

E77.1 Defects in glycoprotein degradation

Aspartylglucosaminuria Fucosidosis Mannosidosis

Sialidosis [mucolipidosis I]

E77.8 Other disorders of glycoprotein metabolism E77.9 Disorder of glycoprotein metabolism, unspecified

  E78 Disorders of lipoprotein metabolism and other lipidaemias

Excl.: sphingolipidosis (E75.0–E75.3)

E78.0 Pure hypercholesterolaemia

Familial hypercholesterolaemia

Fredrickson hyperlipoproteinaemia, type IIa Hyperbetalipoproteinaemia Hyperlipidaemia, group A

Low-density-lipoprotein-type [LDL] hyperlipoproteinaemia

E78.1 Pure hyperglyceridaemia

Endogenous hyperglyceridaemia Fredrickson hyperlipoproteinaemia, type IV Hyperlipidaemia, group B Hyperprebetalipoproteinaemia

Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinaemia

E78.2 Mixed hyperlipidaemia

Broad- or floating-betalipoproteinaemia Fredrickson hyperlipoproteinaemia, type IIb or III

Hyperbetalipoproteinaemia with prebetalipoproteinaemia Hypercholesterolaemia with endogenous hyperglyceridaemia Hyperlipidaemia, group C

Tubero-eruptive xanthoma Xanthoma tuberosum

Excl.: cerebrotendinous cholesterosis [van Bogaert–Scherer–Epstein] (E75.5)

E78.3 Hyperchylomicronaemia

Fredrickson hyperlipoproteinaemia, type I or V Hyperlipidaemia, group D

Mixed hyperglyceridaemia

 

E78.4 Other hyperlipidaemia

Familial combined hyperlipidaemia

E78.5 Hyperlipidaemia, unspecified E78.6 Lipoprotein deficiency

Abetalipoproteinaemia

High-density lipoprotein deficiency Hypoalphalipoproteinaemia Hypobetalipoproteinaemia (familial)

Lecithin cholesterol acyltransferase deficiency Tangier disease

E78.8 Other disorders of lipoprotein metabolism E78.9 Disorder of lipoprotein metabolism, unspecified

  E79 Disorders of purine and pyrimidine metabolism

Excl.: calculus of kidney (N20.0)

combined immunodeficiency disorders (D81.-) gout (M10.-)

orotaciduric anaemia (D53.0) xeroderma pigmentosum (Q82.1)

E79.0 Hyperuricaemia without signs of inflammatory arthritis and tophaceous disease

Asymptomatic hyperuricaemia

E79.1 Lesch–Nyhan syndrome

E79.8 Other disorders of purine and pyrimidine metabolism

Hereditary xanthinuria

E79.9 Disorder of purine and pyrimidine metabolism, unspecified

  E80 Disorders of porphyrin and bilirubin metabolism

Incl.: defects of catalase and peroxidase

E80.0 Hereditary erythropoietic porphyria Congenital erythropoietic porphyria Erythropoietic protoporphyria

E80.1 Porphyria cutanea tarda E80.2 Other porphyria

Hereditary coproporphyria

Porphyria:

• NOS

• acute intermittent (hepatic)

Use additional external cause code (Chapter XX), if desired, to identify cause.

E80.3 Defects of catalase and peroxidase

Acatalasia [Takahara]

 

E80.4 Gilbert syndrome

E80.5 Crigler–Najjar syndrome

E80.6 Other disorders of bilirubin metabolism

Dubin–Johnson syndrome Rotor syndrome

E80.7 Disorder of bilirubin metabolism, unspecified

  E83 Disorders of mineral metabolism

Excl.: dietary mineral deficiency (E58–E61) parathyroid disorders (E20–E21) vitamin D deficiency (E55.-)

E83.0 Disorders of copper metabolism Menkes (kinky hair)(steely hair) disease Wilson disease

E83.1 Disorders of iron metabolism

Haemochromatosis

Excl.: anaemia:

• iron deficiency (D50.-)

• sideroblastic (D64.0–D64.3)

E83.2 Disorders of zinc metabolism

Acrodermatitis enteropathica

E83.3 Disorders of phosphorus metabolism and phosphatases

Acid phosphatase deficiency Familial hypophosphataemia Hypophosphatasia

Vitamin-D-resistant:

• osteomalacia

• rickets

Excl.: adult osteomalacia (M83.-) osteoporosis (M80–M81)

E83.4 Disorders of magnesium metabolism

Hypermagnesaemia Hypomagnesaemia

E83.5 Disorders of calcium metabolism Familial hypocalciuric hypercalcaemia Idiopathic hypercalciuria

Excl.: chondrocalcinosis (M11.1–M11.2) hyperparathyroidism (E21.0–E21.3)

E83.8 Other disorders of mineral metabolism E83.9 Disorder of mineral metabolism, unspecified

 

  E84 Cystic fibrosis

Incl.: mucoviscidosis

E84.0 Cystic fibrosis with pulmonary manifestations E84.1 Cystic fibrosis with intestinal manifestations

Distal intestinal obstruction syndromev

Meconium ileus in cystic fibrosis† (P75*)

Excl.: meconium obstruction (ileus) in cases where cystic fibrosis is known not to be present (P76.0)

E84.8 Cystic fibrosis with other manifestations E84.9 Cystic fibrosis, unspecified

  E85 Amyloidosis

Excl.: Alzheimer disease (G30.-)

E85.0 Non-neuropathic heredofamilial amyloidosis

Familial Mediterranean fever Hereditary amyloid nephropathy

E85.1 Neuropathic heredofamilial amyloidosis

Amyloid polyneuropathy (Portuguese)

E85.2 Heredofamilial amyloidosis, unspecified E85.3 Secondary systemic amyloidosis

Haemodialysis-associated amyloidosis

E85.4 Organ-limited amyloidosis

Localized amyloidosis

E85.8 Other amyloidosis

E85.9 Amyloidosis, unspecified

  E86 Volume depletion

Incl.: dehydration

depletion of volume of plasma or extracellular fluid hypovolaemia

Excl.: dehydration of newborn (P74.1) hypovolaemic shock:

• NOS (R57.1)

• postoperative (T81.1)

• traumatic (T79.4)

 

  E87 Other disorders of fluid, electrolyte and acid–base balance

E87.0 Hyperosmolality and hypernatraemia

Sodium [Na] excess Sodium [Na] overload

E87.1 Hypo-osmolality and hyponatraemia

Sodium [Na] deficiency

Excl.: syndrome of inappropriate secretion of antidiuretic hormone (E22.2)

E87.2 Acidosis

Acidosis:

• NOS

• lactic

• metabolic

• respiratory

Excl.: diabetic acidosis (E10–E14 with common fourth character .1)

E87.3 Alkalosis

Alkalosis:

• NOS

• metabolic

• respiratory

E87.4 Mixed disorder of acid–base balance E87.5 Hyperkalaemia

Potassium [K] excess

Potassium [K] overload

E87.6 Hypokalaemia

Potassium [K] deficiency

E87.7 Fluid overload

Excl.: oedema (R60.-)

E87.8 Other disorders of electrolyte and fluid balance, not elsewhere classified

Electrolyte imbalance NOS Hyperchloraemia Hypochloraemia

  E88 Other metabolic disorders

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: histiocytosis X (chronic) (C96.6)

E88.0 Disorders of plasma-protein metabolism, not elsewhere classified

Alpha-1-antitrypsin deficiency Bisalbuminaemia

Excl.: disorder of lipoprotein metabolism (E78.-)

monoclonal gammopathy of undetermined significance (MGUS) (D47.2)

polyclonal hypergammaglobulinaemia (D89.0) Waldenström macroglobulinaemia (C88.0)

E88.1 Lipodystrophy, not elsewhere classified

Lipodystrophy NOS

Excl.: Whipple disease (K90.8)

E88.2 Lipomatosis, not elsewhere classified

Lipomatosis:

• NOS

• dolorosa [Dercum]

E88.3 Tumour lysis syndrome

Tumour lysis (following antineoplastic drug therapy)(spontaneous)

E88.8 Other specified metabolic disorders Launois–Bensaude adenolipomatosis Trimethylaminuria

E88.9 Metabolic disorder, unspecified

  E89 Postprocedural endocrine and metabolic disorders, not elsewhere classified

E89.0 Postprocedural hypothyroidism Postirradiation hypothyroidism Postsurgical hypothyroidism

E89.1 Postprocedural hypoinsulinaemia Postpancreatectomy hyperglycaemia Postsurgical hypoinsulinaemia

E89.2 Postprocedural hypoparathyroidism

Parathyroprival tetany

E89.3 Postprocedural hypopituitarism

Postirradiation hypopituitarism

E89.4 Postprocedural ovarian failure

E89.5 Postprocedural testicular hypofunction

E89.6 Postprocedural adrenocortical(-medullary) hypofunction E89.8 Other postprocedural endocrine and metabolic disorders

E89.9 Postprocedural endocrine and metabolic disorder, unspecified

  E90* Nutritional and metabolic disorders in diseases classified elsewhere

 

CHAPTER V

Mental and behavioural disorders (F00–F99)

Incl.: disorders of psychological development

Excl.: symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

F00–F09 Organic, including symptomatic, mental disorders

F10–F19 Mental and behavioural disorders due to psychoactive substance use F20–F29 Schizophrenia, schizotypal and delusional disorders

F30–F39 Mood [affective] disorders

F40–F48 Neurotic, stress-related and somatoform disorders

F50–F59 Behavioural syndromes associated with physiological disturbances and physical factors

F60–F69 Disorders of adult personality and behaviour F70–F79 Mental retardation

F80–F89 Disorders of psychological development

F90–F98 Behavioural and emotional disorders with onset usually occurring in childhood and adolescence

F99 Unspecified mental disorder

Asterisk categories for this chapter are provided as follows:

F00* Dementia in Alzheimer disease

F02* Dementia in other diseases classified elsewhere

Organic, including symptomatic, mental disorders (F00–F09)

This block comprises a range of mental disorders grouped together on the basis of their having in common a demonstrable etiology in cerebral disease, brain injury, or other insult leading to cerebral dysfunction. The dysfunction may be primary, as in diseases, injuries, and insults that affect the brain directly and selectively; or secondary, as in systemic diseases and disorders that attack the brain only as one of the multiple organs or systems of the body that are involved.

Dementia (F00–F03) is a syndrome due to disease of the brain, usually of a chronic or progressive nature, in which there is disturbance of multiple higher cortical functions, including memory, thinking, orientation, comprehension, calculation, learning capacity, language and judgement. Consciousness is not clouded. The impairments of cognitive function are commonly accompanied, and occasionally preceded, by deterioration in emotional control, social behaviour or motivation. This syndrome occurs in Alzheimer disease, in cerebrovascular disease, and in other conditions primarily or secondarily affecting the brain.

Use additional code, if desired, to identify the underlying disease.

  F00* Dementia in Alzheimer disease (G30.-†)

Alzheimer disease is a primary degenerative cerebral disease of unknown  etiology with characteristic neuropathological and neurochemical features. The disorder is usually insidious in onset and develops slowly but steadily over a period of several years.

F00.0* Dementia in Alzheimer disease with early onset (G30.0†)

Dementia in Alzheimer disease with onset before the age of 65 years, with a relatively rapid deteriorating course and with marked multiple disorders of the higher cortical functions.

Alzheimer disease, type 2 Presenile dementia, Alzheimer type

Primary degenerative dementia of the Alzheimer type, presenile onset

F00.1* Dementia in Alzheimer disease with late onset (G30.1†)

Dementia in Alzheimer disease with onset after the age of 65 years, usually in the late 70s or thereafter, with a slow progression, and with memory impairment as the principal feature.

Alzheimer disease, type 1

Primary degenerative dementia of the Alzheimer type, senile onset Senile dementia, Alzheimer type

F00.2* Dementia in Alzheimer disease, atypical or mixed type (G30.8†)

Atypical dementia, Alzheimer type

F00.9* Dementia in Alzheimer disease, unspecified (G30.9†)

  F01 Vascular dementia

Vascular dementia is the result of infarction of the brain due to vascular disease, including hypertensive cerebrovascular disease. The infarcts are usually small but cumulative in their effect. Onset is usually in later life.

Incl.: arteriosclerotic dementia

F01.0 Vascular dementia of acute onset

Usually develops rapidly after a succession of strokes from cerebrovascular thrombosis, embolism or haemorrhage. In rare cases, a single large infarction may be the cause.

F01.1 Multi-infarct dementia

Gradual in onset, following a number of transient ischaemic episodes that produce an accumulation of infarcts in the cerebral parenchyma.

Predominantly cortical dementia

F01.2 Subcortical vascular dementia

Includes cases with a history of hypertension and foci of ischaemic destruction in the deep white matter of the cerebral hemispheres. The cerebral cortex is usually preserved and this contrasts with the clinical picture, which may closely resemble that of dementia in Alzheimer disease.

F01.3 Mixed cortical and subcortical vascular dementia F01.8 Other vascular dementia

F01.9 Vascular dementia, unspecified

  F02* Dementia in other diseases classified elsewhere

Cases of dementia due, or presumed to be due, to causes other than Alzheimer disease or cerebrovascular disease. Onset may be at any time in life, though rarely in old age.

F02.0* Dementia in Pick disease (G31.0†)

A progressive dementia, commencing in middle age, characterized by early, slowly progressing changes of character and social deterioration, followed by impairment of intellect, memory and language functions, with apathy, euphoria and, occasionally, extrapyramidal phenomena.

F02.1* Dementia in Creutzfeldt–Jakob disease (A81.0†)

A progressive dementia with extensive neurological signs, due to specific neuropathological changes that are presumed to be caused by a transmissible agent. Onset is usually in middle or later life, but may be at any adult age. The course is subacute, leading to death within one to two years.

F02.2* Dementia in Huntington disease (G10†)

A dementia occurring as part of a widespread degeneration of the brain. The disorder is transmitted by a single autosomal dominant gene. Symptoms typically emerge in the third and fourth decade. Progression is slow, leading to death, usually within 10 to 15 years.

Dementia in Huntington chorea

F02.3* Dementia in Parkinson disease (G20†)

A dementia developing in the course of established Parkinson disease. No particular distinguishing clinical features have yet been demonstrated.

Dementia in:

• paralysis agitans

• parkinsonism

F02.4* Dementia in human immunodeficiency virus [HIV] disease (B22.0†)

Dementia developing in the course of HIV disease, in the absence of a concurrent illness or condition other than HIV infection that could explain the clinical features.

F02.8* Dementia in other specified diseases classified elsewhere

Dementia (in):

• cerebral lipidosis (E75.-†)

• epilepsy (G40.-†)

• hepatolenticular degeneration (E83.0†)

• hypercalcaemia (E83.5†)

• hypothyroidism, acquired (E01.-† , E03.-†)

• intoxications (T36-T65†)

• Lewy body (ies) (disease) (G31.8†)

• multiple sclerosis (G35†)

• neurosyphilis (A52.1†)

• niacin deficiency [pellagra] (E52†)

• polyarteritis nodosa (M30.0†)

• systemic lupus erythematosus (M32.-†)

• trypanosomiasis (B56.-† , B57.-†)

• uraemia (N18.5†)

• vitamin B12 deficiency (E53.8†)

  F03 Unspecified dementia

Incl.: presenile:

• dementia NOS

• psychosis NOS

primary degenerative dementia NOS senile:

• dementia:

– NOS

– depressed or paranoid type

• psychosis NOS

Excl.: senile dementia with delirium or acute confusional state (F05.1) senility NOS (R54)

  F04 Organic amnesic syndrome, not induced by alcohol and other psychoactive substances

A syndrome of prominent impairment of recent and remote memory while immediate recall is preserved, with reduced ability to learn new material and disorientation in time. Confabulation may be a marked feature, but perception and other cognitive functions, including the intellect, are usually intact. The prognosis depends on the course of the underlying lesion.

Incl.: Korsakov psychosis or syndrome, nonalcoholic

Excl.: amnesia:

• NOS (R41.3)

• anterograde (R41.1)

• dissociative (F44.0)

• retrograde (R41.2) Korsakov syndrome:

• alcohol-induced or unspecified (F10.6)

• induced by other psychoactive substances (F11–F19 with common fourth character .6)

  F05 Delirium, not induced by alcohol and other psychoactive substances

An etiologically nonspecific organic cerebral syndrome characterized by concurrent disturbances of consciousness and attention, perception, thinking, memory, psychomotor behaviour, emotion and the sleep–wake schedule. The duration is variable and the degree of severity ranges from mild to very severe.

Incl.: acute or subacute:

• brain syndrome

• confusional state (nonalcoholic)

• infective psychosis

• organic reaction

• psycho-organic syndrome

Excl.: delirium tremens, alcohol-induced or unspecified (F10.4) F05.0 Delirium not superimposed on dementia, so described F05.1 Delirium superimposed on dementia

Conditions meeting the above criteria but developing in the course of a dementia (F00–F03).

F05.8 Other delirium Delirium of mixed origin Postoperative delirium

F05.9 Delirium, unspecified

  F06 Other mental disorders due to brain damage and dysfunction and to physical disease

Includes miscellaneous conditions causally related to brain disorder due to primary cerebral disease, to systemic disease affecting the brain secondarily, to exogenous toxic substances or hormones, to endocrine disorders or to other somatic illnesses.

Excl.: associated with:

• delirium (F05.-)

• dementia as classified in F00–F03

resulting from use of alcohol and other psychoactive substances (F10–F19)

F06.0 Organic hallucinosis

A disorder of persistent or recurrent hallucinations, usually visual or auditory, that occur in clear consciousness and may or may not be recognized by the subject as such. Delusional elaboration of the hallucinations may occur, but delusions do not dominate the clinical picture; insight may be preserved.

Organic hallucinatory state (nonalcoholic)

Excl.: alcoholic hallucinosis (F10.5) schizophrenia (F20.-)

F06.1 Organic catatonic disorder

A disorder of diminished (stupor) or increased (excitement) psychomotor activity associated with catatonic symptoms. The extremes of psychomotor disturbance may alternate.

Excl.: catatonic schizophrenia (F20.2) stupor:

• NOS (R40.1)

• dissociative (F44.2)

F06.2 Organic delusional [schizophrenia-like] disorder

A disorder in which persistent or recurrent delusions dominate the clinical picture. The delusions may be accompanied by hallucinations. Some features suggestive of schizophrenia, such as bizarre hallucinations or thought disorder, may be present.

Paranoid and paranoid-hallucinatory organic states Schizophrenia-like psychosis in epilepsy

Excl.: disorder:

• acute and transient psychotic (F23.-)

• persistent delusional (F22.-)

• psychotic drug-induced (F11–F19 with common fourth character .5) schizophrenia (F20.-)

F06.3 Organic mood [affective] disorders

Disorders characterized by a change in mood or affect, usually accompanied by a change in the overall level of activity, depressive, hypomanic, manic or bipolar (see F30–F38), but arising as a consequence of an organic disorder.

Excl.: mood disorders, nonorganic or unspecified (F30–F39)

 

F06.4 Organic anxiety disorder

A disorder characterized by the essential descriptive features of a generalized anxiety disorder (F41.1), a panic disorder (F41.0) or a combination of both, but arising as a consequence of an organic disorder.

Excl.: anxiety disorders, nonorganic or unspecified (F41.-)

F06.5 Organic dissociative disorder

A disorder characterized by a partial or complete loss of the normal integration between memories of the past, awareness of identity and immediate sensations, and control of bodily movements (see F44.-), but arising as a consequence of an organic disorder.

Excl.: dissociative [conversion] disorders, nonorganic or unspecified (F44.-)

F06.6 Organic emotionally labile [asthenic] disorder

A disorder characterized by emotional incontinence or lability, fatigability and a variety of unpleasant physical sensations (e.g. dizziness) and pains, but arising as a consequence of an organic disorder.

Excl.: somatoform disorders, nonorganic or unspecified (F45.-)

F06.7 Mild cognitive disorder

A disorder characterized by impairment of memory, learning difficulties and reduced ability to concentrate on a task for more than brief periods. There is often a marked feeling of mental fatigue when mental tasks are attempted, and new learning is found to be subjectively difficult, even when objectively successful. None of these symptoms is so severe that a diagnosis of either dementia (F00–F03) or delirium (F05.-) can be made. This diagnosis should be made only in association with a specified physical disorder, and should not be made in the presence of any of the mental or behavioural disorders classified to F10–F99. The disorder may precede, accompany or follow a wide variety of infections and physical disorders, both cerebral and systemic, but direct evidence of cerebral involvement is not necessarily present. It can be differentiated from postencephalitic syndrome (F07.1) and postconcussional syndrome (F07.2) by its different etiology, more restricted range of generally milder symptoms and usually shorter duration.

F06.8 Other specified mental disorders due to brain damage and dysfunction and to physical disease

Epileptic psychosis NOS

F06.9 Unspecified mental disorder due to brain damage and dysfunction and to physical disease

Organic:

• brain syndrome NOS

• mental disorder NOS

  F07 Personality and behavioural disorders due to brain disease, damage and dysfunction

Alteration of personality and behaviour can be a residual or concomitant disorder of brain disease, damage or dysfunction.

 

F07.0 Organic personality disorder

A disorder characterized by a significant alteration of the habitual patterns of behaviour displayed by the subject premorbidly, involving the expression of emotions, needs and impulses. Impairment of cognitive and thought functions and altered sexuality may also be part of the clinical picture.

Organic:

• pseudopsychopathic personality

• pseudoretarded personality Syndrome:

• frontal lobe

• limbic epilepsy personality

• lobotomy

• postleucotomy

Excl.: enduring personality change after:

• catastrophic experience (F62.0)

• psychiatric illness (F62.1) postconcussional syndrome (F07.2) postencephalitic syndrome (F07.1) specific personality disorder (F60.-)

F07.1 Postencephalitic syndrome

Residual nonspecific and variable behavioural change following recovery from either viral or bacterial encephalitis. The principal difference between this disorder and the organic personality disorders is that it is reversible.

Excl.: organic personality disorder (F07.0)

F07.2 Postconcussional syndrome

A syndrome that occurs following head trauma (usually sufficiently severe to result in loss of consciousness) and includes a number of disparate symptoms such as headache, dizziness, fatigue, irritability, difficulty in concentration and performing mental tasks, impairment of memory, insomnia and reduced tolerance to stress, emotional excitement or alcohol.

Postcontusional syndrome (encephalopathy) Post-traumatic brain syndrome, nonpsychotic

Excl.: current concussion, brain (S06.0)

F07.8 Other organic personality and behavioural disorders due to brain disease, damage and dysfunction

Right hemispheric organic affective disorder

F07.9 Unspecified organic personality and behavioural disorder due to brain disease, damage and dysfunction

Organic psychosyndrome

  F09 Unspecified organic or symptomatic mental disorder

Incl.: psychosis:

• organic NOS

• symptomatic NOS

Excl.: psychosis NOS (F29)

 

Mental and behavioural disorders due to psychoactive substance use

(F10–F19)

This block contains a wide variety of disorders that differ in severity and clinical form but that are all attributable to the use of one or more psychoactive substances, which may or may not have been medically prescribed. The third character of the code identifies the substance involved and the fourth character specifies the clinical state. The codes should be used, as required, for each substance specified, but it should be noted that not all fourth-character codes are applicable to all substances.

Identification of the psychoactive substance should be based on as many sources of information as possible. These include self-report data, analysis of blood and other body fluids, characteristic physical and psychological symptoms, clinical signs and behaviour, and other evidence such as a drug being in the patient’s possession or reports from informed third parties. Many drug users take more than one type of psychoactive substance. The main diagnosis should be classified, whenever possible, according to the substance or class of substances that has caused or contributed most to the presenting clinical syndrome. Other diagnoses should be coded when other psychoactive substances have been taken in intoxicating amounts (common fourth character .0) or to the extent of causing harm (common fourth character .1), dependence (common fourth character .2) or other disorders (common fourth character .3–.9).

Only in cases in which patterns of psychoactive substance-taking are chaotic and indiscriminate, or in which the contributions of different psychoactive substances are inextricably mixed, should the diagnosis of disorders resulting from multiple drug use (F19.-) be used.

Excl.: abuse of non-dependence-producing substances (F55)

The following fourth-character subdivisions are for use with categories F10–F19:

.0 Acute intoxication

A condition that follows the administration of a psychoactive substance resulting in disturbances in level of consciousness, cognition, perception, affect or behaviour, or other psycho-physiological functions and responses. The disturbances are directly related to the acute pharmacological effects of the substance and resolve with time, with complete recovery, except where tissue damage or other complications have arisen. Complications may include trauma, inhalation of vomitus, delirium, coma, convulsions, and other medical complications. The nature of these complications depends on the pharmacological class of substance and mode of administration.

Acute drunkenness (in alcoholism) ‘Bad trips’ (drugs)

Drunkenness NOS Pathological intoxication

Trance and possession disorders in psychoactive substance intoxication

Excl.: intoxication meaning poisoning (T36–T50)

 

.1 Harmful use

A pattern of psychoactive substance use that is causing damage to health. The damage may be physical (as in cases of hepatitis from the self-administration of injected psychoactive substances) or mental (e.g. episodes of depressive disorder secondary to heavy consumption of alcohol).

Psychoactive substance abuse

.2 Dependence syndrome

A cluster of behavioural, cognitive and physiological phenomena that develop after repeated substance use and that typically include a strong desire to take the drug, difficulties in controlling its use, persisting in its use despite harmful consequences, a higher priority given to drug use than to other activities and obligations, increased tolerance, and sometimes a physical withdrawal state.

The dependence syndrome may be present for a specific psychoactive substance (e.g. tobacco, alcohol or diazepam), for a class of substances (e.g. opioid drugs) or for a wider range of pharmacologically different psychoactive substances.

Chronic alcoholism Dipsomania

Drug addiction

.3 Withdrawal state

A group of symptoms of variable clustering and severity, occurring on absolute or relative withdrawal of a psychoactive substance after persistent use of that substance. The onset and course of the withdrawal state are time-limited and are related to the type of psychoactive substance and dose being used immediately before cessation or reduction of use. The withdrawal state may be complicated by convulsions.

.4 Withdrawal state with delirium

A condition where the withdrawal state as defined in the common fourth character

.3 is complicated by delirium as defined in F05.-. Convulsions may also occur. When organic factors are also considered to play a role in the etiology, the condition should be classified to F05.8.

Delirium tremens (alcohol-induced)

.5 Psychotic disorder

A cluster of psychotic phenomena that occur during or following psychoactive substance use but that are not explained on the basis of acute intoxication alone and do not form part of a withdrawal state. The disorder is characterized by hallucinations (typically auditory, but often in more than one sensory modality), perceptual distortions, delusions (often of a paranoid or persecutory nature), psychomotor disturbances (excitement or stupor) and an abnormal affect, which may range from intense fear to ecstasy. The sensorium is usually clear but some degree of clouding of consciousness, though not severe confusion, may be present.

Alcoholic:

• hallucinosis

• jealousy

• paranoia

• psychosis NOS

Excl.: alcohol- or other psychoactive-substance-induced residual and late- onset psychotic disorder (F10–F19 with common fourth character .7)

 

.6 Amnesic syndrome

A syndrome associated with chronic prominent impairment of  recent  and  remote memory. Immediate recall is usually preserved and recent memory is characteristically more disturbed than remote memory. Disturbances of time  sense and ordering of events are usually evident, as are difficulties in learning new material. Confabulation may be marked but is not invariably present. Other cognitive functions are usually relatively well preserved and amnesic defects are out of proportion to other disturbances.

Amnestic disorder, alcohol- or drug-induced

Korsakov psychosis or syndrome, alcohol- or other psychoactive substance-induced or unspecified

Use additional code, (E51.2†, G32.8*), if desired, when associated with Wernicke disease or syndrome.

Excl.: nonalcoholic Korsakov psychosis or syndrome (F04)

.7 Residual and late-onset psychotic disorder

A disorder in which alcohol- or psychoactive-substance-induced changes of cognition, affect, personality, or behaviour persist beyond the period during which a direct psychoactive-substance-related effect might reasonably be assumed to    be operating. Onset of the disorder should be directly related to the use of the psychoactive substance. Cases in which initial onset of the state occurs later than episode(s) of such substance use should be coded here only where clear and strong evidence is available to attribute the state to the residual effect of the psychoactive substance. Flashbacks may be distinguished from psychotic state partly by their episodic nature, frequently of very short duration, and by their duplication of previous alcohol- or other psychoactive-substance-related experiences.

Alcoholic dementia NOS Chronic alcoholic brain syndrome

Dementia and other milder forms of persisting impairment of cognitive functions

Flashbacks

Late-onset psychoactive substance-induced psychotic disorder Posthallucinogen perception disorder

Residual:

• affective disorder

• disorder of personality and behaviour

Excl.: alcohol- or psychoactive-substance-induced:

• Korsakov syndrome (F10–F19 with common fourth character .6)

• psychotic state (F10–F19 with common fourth character .5)

.8 Other mental and behavioural disorders

.9 Unspecified mental and behavioural disorder

 

Mental and behavioural disorders due to use of alcohol

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of opioids

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of cannabinoids

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of sedatives or hypnotics

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of cocaine

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of other stimulants, including caffeine

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of hallucinogens

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of tobacco

[See before F10 for subdivisions]

Mental and behavioural disorders due to use of volatile solvents

[See before F10 for subdivisions]

Mental and behavioural disorders due to multiple drug use and use of other psychoactive substances

[See before F10 for subdivisions]

This category should be used when two or more psychoactive substances are known to be involved, but it is impossible to assess which substance is contributing most to the disorders. It should also be used when the exact identity of some or even all the psychoactive substances being used is uncertain or unknown, since many multiple drug users themselves often do not know the details of what they are taking.

Incl.: misuse of drugs NOS

 

Schizophrenia, schizotypal and delusional disorders (F20–F29)

This block brings together schizophrenia, as the most important member of the group, schizotypal disorder, persistent delusional disorders, and a larger group of acute and transient psychotic disorders. Schizoaffective disorders have been retained here in spite of their controversial nature.

  F20 Schizophrenia

The  schizophrenic  disorders  are  characterized  in  general  by   fundamental and characteristic distortions of thinking and perception, and affects that are inappropriate or blunted. Clear consciousness and intellectual capacity are usually maintained, although certain cognitive deficits may evolve in the course of time. The most important psychopathological phenomena include thought echo; thought insertion or withdrawal; thought broadcasting; delusional perception and delusions of control; influence or passivity; hallucinatory voices commenting or discussing the patient in the third person; thought disorders; and negative symptoms.

The course of schizophrenic disorders can be either continuous, or episodic with progressive or stable deficit, or there can be one or more episodes with complete or incomplete remission. The diagnosis  of  schizophrenia  should  not  be  made in the presence of extensive depressive or manic symptoms unless it is clear     that schizophrenic symptoms antedate the affective disturbance. Nor should schizophrenia be diagnosed in the presence of overt brain disease or during states of drug intoxication or withdrawal. Similar disorders developing in the presence of epilepsy or other brain disease should be classified under F06.2, and those induced by psychoactive substances under F10–F19 with common fourth character .5.

Excl.: schizophrenia:

• acute (undifferentiated) (F23.2)

• cyclic (F25.2)

schizophrenic reaction (F23.2) schizotypal disorder (F21)

F20.0 Paranoid schizophrenia

Paranoid schizophrenia is dominated by relatively stable, often paranoid delusions, usually accompanied by hallucinations, particularly of the auditory variety, and perceptual disturbances. Disturbances of affect, volition and speech, and catatonic symptoms, are either absent or relatively inconspicuous.

Paraphrenic schizophrenia

Excl.: involutional paranoid state (F22.8) paranoia (F22.0)

F20.1 Hebephrenic schizophrenia

A form of schizophrenia in which affective changes are prominent, delusions and hallucinations fleeting and fragmentary, behaviour irresponsible and unpredictable, and mannerisms common. The mood is shallow and inappropriate, thought is disorganized, and speech is incoherent. There is a tendency to social isolation. Usually the prognosis is poor because of the rapid development of ‘negative’ symptoms, particularly flattening of affect and loss of volition. Hebephrenia should normally be diagnosed only in adolescents or young adults.

Disorganized schizophrenia Hebephrenia

 

F20.2 Catatonic schizophrenia

Catatonic schizophrenia is dominated by prominent psychomotor disturbances that may alternate between extremes such as hyperkinesis and stupor, or automatic obedience and negativism. Constrained attitudes and postures may be maintained for long periods. Episodes of violent excitement may be a striking feature of the condition. The catatonic phenomena may be combined with a dream-like (oneiroid) state with vivid scenic hallucinations.

Catatonic stupor Schizophrenic:

• catalepsy

• catatonia

• flexibilitas cerea

F20.3 Undifferentiated schizophrenia

Psychotic conditions meeting the general diagnostic criteria for schizophrenia but not conforming to any of the subtypes in F20.0–F20.2, or exhibiting the features of more than one of them without a clear predominance of a particular set of diagnostic characteristics.

Atypical schizophrenia

Excl.: acute schizophrenia-like psychotic disorder (F23.2) chronic undifferentiated schizophrenia (F20.5)

post-schizophrenic depression (F20.4)

F20.4 Post-schizophrenic depression

A depressive episode,  which  may  be  prolonged,  arising  in  the  aftermath  of  a schizophrenic illness. Some schizophrenic symptoms, either ‘positive’ or ‘negative’, must still be present but they no longer dominate the clinical picture. These depressive states are associated with an increased risk of suicide. If the patient no longer has any schizophrenic symptoms, a depressive episode should be diagnosed (F32.-). If schizophrenic symptoms are still florid and prominent, the diagnosis should remain that of the appropriate schizophrenic subtype (F20.0– F20.3).

F20.5 Residual schizophrenia

A chronic stage in the development of a schizophrenic illness in which there has been a clear progression from an early stage to a later stage characterized by long- term, though not necessarily irreversible, ‘negative’ symptoms, e.g. psychomotor slowing; underactivity; blunting of affect; passivity and lack of initiative; poverty of quantity or content of speech; poor nonverbal communication by facial expression, eye contact, voice modulation and posture; poor self-care and social performance.

Chronic undifferentiated schizophrenia Restzustand (schizophrenic) Schizophrenic residual state

F20.6 Simple schizophrenia

A disorder in which there is an insidious but progressive development of oddities of conduct, inability to meet the demands of society, and decline in total performance. The characteristic negative features of residual schizophrenia (e.g. blunting of affect and loss of volition) develop without being preceded by any overt psychotic symptoms.

 

F20.8 Other schizophrenia

Cenesthopathic schizophrenia Schizophreniform:

• disorder NOS

• psychosis NOS

Excl.: brief schizophreniform disorders (F23.2)

F20.9 Schizophrenia, unspecified

  F21 Schizotypal disorder

A disorder characterized by eccentric behaviour and anomalies of thinking and affect that resemble those seen in schizophrenia, though no definite and characteristic schizophrenic anomalies occur at any stage. The symptoms may include a cold or inappropriate affect; anhedonia; odd or eccentric behaviour; a tendency to social withdrawal; paranoid or bizarre ideas not amounting to true delusions; obsessive ruminations; thought disorder and perceptual disturbances; occasional transient quasi-psychotic episodes with intense illusions, auditory or other hallucinations and delusion-like ideas, usually occurring without external provocation. There is no definite onset and evolution and course are usually those of a personality disorder.

Incl.: latent schizophrenic reaction schizophrenia:

• borderline

• latent

• prepsychotic

• prodromal

• pseudoneurotic

• pseudopsychopathic schizotypal personality disorder

Excl.: Asperger syndrome (F84.5)

schizoid personality disorder (F60.1)

  F22 Persistent delusional disorders

Includes a variety of disorders in which long-standing delusions constitute the only, or the most conspicuous, clinical characteristic and that cannot be classified as organic, schizophrenic or affective. Delusional disorders that have lasted for less than a few months should be classified, at least temporarily, under F23.-.

 

F22.0 Delusional disorder

A disorder characterized by the development either of a single delusion or of a  set of related delusions that are usually persistent and sometimes lifelong. The content of the delusion or delusions is very variable. Clear and persistent auditory hallucinations (voices), schizophrenic symptoms such as delusions of control and marked blunting of affect, and definite evidence of brain disease are all incompatible with this diagnosis. However, the presence of occasional or transitory auditory hallucinations, particularly in elderly patients, does not rule out this diagnosis, provided that they are not typically schizophrenic and form only a small part of the overall clinical picture.

Paranoia Paranoid:

• psychosis

• state Paraphrenia (late)

Sensitiver beziehungswahn

Excl.: paranoid:

• personality disorder (F60.0)

• psychosis, psychogenic (F23.3)

• reaction (F23.3)

• schizophrenia (F20.0)

F22.8 Other persistent delusional disorders

Disorders in which the delusion or delusions are accompanied by persistent hallucinatory voices or by schizophrenic symptoms that do not justify a diagnosis of schizophrenia (F20.-).

Delusional dysmorphophobia Involutional paranoid state Paranoia querulans

F22.9 Persistent delusional disorder, unspecified

  F23 Acute and transient psychotic disorders

A heterogeneous group of disorders characterized by the acute onset of psychotic symptoms such as delusions, hallucinations and perceptual disturbances, and by the severe disruption of ordinary behaviour. Acute onset is defined as a crescendo development of a clearly abnormal clinical picture in about two weeks or less.  For these disorders, there is no evidence of organic causation. Perplexity and puzzlement are often present but disorientation for time, place and person is not persistent or severe enough to justify a diagnosis of organically caused delirium (F05.-). Complete recovery usually occurs within a few months, often within a few weeks or even days. If the disorder persists, a change in classification will be necessary. The disorder may or may not be associated with acute stress, defined as usually stressful events preceding the onset by one to two weeks.

Acute polymorphic psychotic disorder without symptoms of schizophrenia

An acute psychotic disorder in which hallucinations, delusions or perceptual disturbances are obvious but markedly variable, changing from day to day or even from hour to hour. Emotional turmoil with intense transient feelings of happiness or ecstasy, or anxiety and irritability, is also frequently present. The polymorphism and instability are characteristic for the overall clinical picture and the psychotic features do not justify a diagnosis of schizophrenia (F20.-). These disorders often have an abrupt onset, developing rapidly within a few days, and they frequently show a rapid resolution of symptoms with no recurrence. If the symptoms persist, the diagnosis should be changed to persistent delusional disorder (F22.-).

Bouffée délirante without symptoms of schizophrenia or unspecified Cycloid psychosis without symptoms of schizophrenia or unspecified

F23.1 Acute polymorphic psychotic disorder with symptoms of schizophrenia

An acute psychotic disorder in which the polymorphic and unstable clinical picture is present, as described in F23.0; despite this instability, however, some symptoms typical of schizophrenia are also in evidence for the majority of the time. If the schizophrenic symptoms persist, the diagnosis should be changed to schizophrenia (F20.-).

Bouffée délirante with symptoms of schizophrenia Cycloid psychosis with symptoms of schizophrenia

F23.2 Acute schizophrenia-like psychotic disorder

An acute psychotic disorder in which the psychotic symptoms are comparatively stable and justify a diagnosis of schizophrenia, but have lasted for less than   about one month; the polymorphic unstable features, as described in F23.0, are absent. If the schizophrenic symptoms persist, the diagnosis should be changed to schizophrenia (F20.-).

Acute (undifferentiated) schizophrenia Brief schizophreniform:

• disorder

• psychosis Oneirophrenia Schizophrenic reaction

Excl.: organic delusional [schizophrenia-like] disorder (F06.2) schizophreniform disorders NOS (F20.8)

F23.3 Other acute predominantly delusional psychotic disorders

Acute psychotic disorders in which comparatively stable delusions or hallucinations are the main clinical features, but do not justify a diagnosis of schizophrenia (F20.-). If the delusions persist, the diagnosis should be changed to persistent delusional disorder (F22.-).

Paranoid reaction

Psychogenic paranoid psychosis

 

F23.8 Other acute and transient psychotic disorders

Any other specified acute psychotic disorders for which there is no evidence of organic causation and that do not justify classification to F23.0–F23.3.

F23.9 Acute and transient psychotic disorder, unspecified

Brief reactive psychosis NOS Reactive psychosis

  F24 Induced delusional disorder

A delusional disorder shared by two or more people with close emotional links. Only one of the people suffers from a genuine psychotic disorder; the delusions are induced in the other(s) and usually disappear when the people are separated.

Incl.: folie à deux

induced:

• paranoid disorder

• psychotic disorder

  F25 Schizoaffective disorders

Episodic  disorders  in  which  both  affective   and   schizophrenic   symptoms are prominent but that do not justify a diagnosis of either schizophrenia or depressive or manic episodes. Other conditions in which affective symptoms are superimposed on a pre-existing schizophrenic illness, or coexist or alternate with persistent delusional disorders of other kinds, are classified under F20–F29. Mood- incongruent psychotic symptoms in affective disorders do not justify a diagnosis of schizoaffective disorder.

F25.0 Schizoaffective disorder, manic type

A disorder in which both schizophrenic and manic symptoms are prominent, so that the episode of illness does not justify a diagnosis of either schizophrenia or a manic episode. This category should be used for both a single episode and a recurrent disorder in which the majority of episodes are schizoaffective, manic type.

Schizoaffective psychosis, manic type Schizophreniform psychosis, manic type

F25.1 Schizoaffective disorder, depressive type

A disorder in which both schizophrenic and depressive symptoms are prominent, so that the episode of illness does not justify a diagnosis of either schizophrenia or a depressive episode. This category should be used for both a single episode and a recurrent disorder in which the majority of episodes are schizoaffective, depressive type.

Schizoaffective psychosis, depressive type Schizophreniform psychosis, depressive type

F25.2 Schizoaffective disorder, mixed type

Cyclic schizophrenia

Mixed schizophrenic and affective psychosis

 

F25.8 Other schizoaffective disorders F25.9 Schizoaffective disorder, unspecified

Schizoaffective psychosis NOS

  F28 Other nonorganic psychotic disorders

Delusional or hallucinatory disorders that do not justify a diagnosis of schizophrenia (F20.-), persistent delusional disorders (F22.-), acute and transient psychotic disorders (F23.-), psychotic types of manic episode (F30.2) or severe depressive episode (F32.3).

Incl.: chronic hallucinatory psychosis

  F29 Unspecified nonorganic psychosis

Incl.: psychosis NOS

Excl.: mental disorder NOS (F99)

organic or symptomatic psychosis NOS (F09)

Mood [affective] disorders (F30–F39)

This block contains disorders in which the fundamental disturbance is a change in affect or mood, to depression (with or without associated anxiety) or to elation. The mood change is usually accompanied by a change in the overall level of activity; most of   the other symptoms are either secondary to, or easily understood in the context of, the change in mood and activity. Most of these disorders tend to be recurrent and the onset of individual episodes can often be related to stressful events or situations.

  F30 Manic episode

All the subdivisions of this category should be used only for a single episode. Hypomanic or manic episodes in individuals who have had one or more previous affective episodes (depressive, hypomanic, manic or mixed) should be coded as bipolar affective disorder (F31.-).

Incl.: bipolar disorder, single manic episode

F30.0 Hypomania

A disorder characterized by a persistent mild elevation of mood, increased energy and activity, and usually marked feelings of well-being and both physical and mental efficiency. Increased sociability, talkativeness, over-familiarity, increased sexual energy and a decreased need for sleep are often present but not to the extent that they lead to severe disruption of work or result in social rejection. Irritability, conceit and boorish behaviour may take the place of the more usual euphoric sociability. The disturbances of mood and behaviour are not accompanied by hallucinations or delusions.

 

F30.1 Mania without psychotic symptoms

Mood is elevated out of keeping with the patient’s circumstances and may vary from carefree joviality to almost uncontrollable excitement. Elation is accompanied by increased energy, resulting in overactivity, pressure of speech and a decreased need for sleep. Attention cannot be sustained, and there is often marked distractibility. Self-esteem is often inflated, with grandiose ideas and overconfidence. Loss of normal social inhibitions may result in behaviour that is reckless, foolhardy or inappropriate to the circumstances, and out of character.

F30.2 Mania with psychotic symptoms

In addition to the clinical picture described in F30.1, delusions (usually grandiose) or hallucinations (usually of voices speaking directly to the patient) are present, or the excitement, excessive motor activity and flight of ideas are so extreme that the subject is incomprehensible or inaccessible to ordinary communication.

Mania with:

• mood-congruent psychotic symptoms

• mood-incongruent psychotic symptoms Manic stupor

F30.8 Other manic episodes F30.9 Manic episode, unspecified

Mania NOS

  F31 Bipolar affective disorder

A disorder characterized by two or more episodes in which the patient’s mood and activity levels are significantly disturbed this disturbance consisting on some occasions of an elevation of mood and increased energy and activity (hypomania or mania) and on others of a lowering of mood and decreased energy and activity (depression). Repeated episodes of hypomania or mania only are classified as bipolar.

Incl.: manic depression

manic-depressive:

• illness

• psychosis

• reaction

Excl.: bipolar disorder, single manic episode (F30.-) cyclothymia (F34.0)

F31.0 Bipolar affective disorder, current episode hypomanic

The patient is currently hypomanic and has had at least one other affective episode (hypomanic, manic, depressive or mixed) in the past.

F31.1 Bipolar affective disorder, current episode manic without psychotic symptoms

The patient is currently manic, without psychotic symptoms (as in F30.1) and has had at least one other affective episode (hypomanic, manic, depressive or mixed) in the past.

 

F31.2 Bipolar affective disorder, current episode manic with psychotic symptoms

The patient is currently manic, with psychotic symptoms (as in F30.2), and has had at least one other affective episode (hypomanic, manic, depressive or mixed) in the past.

F31.3 Bipolar affective disorder, current episode mild or moderate depression

The patient is currently depressed, as in a depressive episode of either mild or moderate severity (F32.0 or F32.1), and has had at least one authenticated hypomanic, manic or mixed affective episode in the past.

F31.4 Bipolar affective disorder, current episode severe depression without psychotic symptoms

The patient is currently depressed, as in severe depressive episode without psychotic symptoms (F32.2), and has had at least one authenticated hypomanic, manic or mixed affective episode in the past.

F31.5 Bipolar affective disorder, current episode severe depression with psychotic symptoms

The patient is currently depressed, as in severe depressive episode with psychotic symptoms (F32.3), and has had at least one authenticated hypomanic, manic or mixed affective episode in the past.

F31.6 Bipolar affective disorder, current episode mixed

The patient has had at least one authenticated hypomanic, manic, depressive or mixed affective episode in the past, and currently exhibits either a mixture or a rapid alteration of manic and depressive symptoms.

Excl.: single mixed affective episode (F38.0)

F31.7 Bipolar affective disorder, currently in remission

The patient has had at least one authenticated hypomanic, manic or mixed affective episode in the past, and at least one other affective episode (hypomanic, manic, depressive or mixed) in addition, but is not currently suffering from any significant mood disturbance, and has not done so for several months. Periods of remission during prophylactic treatment should be coded here.

F31.8 Other bipolar affective disorders

Bipolar II disorder

Recurrent manic episodes NOS

F31.9 Bipolar affective disorder, unspecified

Manic depression NOS

 

  F32 Depressive episode

In typical mild, moderate or severe depressive episodes, the patient suffers from lowering of mood, reduction of energy and decrease in activity. Capacity for enjoyment, interest and concentration is reduced, and marked tiredness after even minimum effort is common. Sleep is usually disturbed and appetite diminished. Self- esteem and self-confidence are almost always reduced and, even in the mild form, some ideas of guilt or worthlessness are often present. The lowered mood varies little from day to day, is unresponsive to circumstances and may be accompanied by so-called ‘somatic’ symptoms, such as loss of interest and pleasurable feelings, waking in the morning several hours before the usual time, depression worst in the morning, marked psychomotor retardation, agitation, loss of appetite, weight loss, and loss of libido. Depending upon the number and severity of the symptoms, a depressive episode may be specified as mild, moderate or severe.

Incl.: single episodes of:

• depressive reaction

• psychogenic depression

• reactive depression

Excl.: adjustment disorder (F43.2) recurrent depressive disorder (F33.-)

when associated with conduct disorders in F91.- (F92.0)

F32.0 Mild depressive episode

Two or three of the above symptoms are usually present. The patient is usually distressed by these but will probably be able to continue with most activities.

F32.1 Moderate depressive episode

Four or more of the above symptoms are usually present and the patient is likely to have great difficulty in continuing with ordinary activities.

F32.2 Severe depressive episode without psychotic symptoms

An episode of depression in which several of the above symptoms are marked  and distressing, typically loss of self-esteem and ideas of worthlessness or guilt. Suicidal thoughts and acts are common and a number of ‘somatic’ symptoms are usually present.

Agitated depression Major depression

Vital depression single episode without psychotic symptoms

F32.3 Severe depressive episode with psychotic symptoms

An episode of depression as described in F32.2, but with the presence of hallucinations, delusions, psychomotor retardation or stupor so severe that ordinary social activities are impossible; there may be danger to life from suicide, dehydration or starvation. The hallucinations and delusions may or may not be mood-congruent.

Single episodes of:

• major depression with psychotic symptoms

• psychogenic depressive psychosis

• psychotic depression

• reactive depressive psychosis

 

F32.8 Other depressive episodes

Atypical depression

Single episodes of ‘masked’ depression NOS

F32.9 Depressive episode, unspecified

Depression NOS Depressive disorder NOS

  F33 Recurrent depressive disorder

A disorder characterized by repeated episodes of depression as described for depressive episode (F32.-), without any history of independent episodes of mood elevation and increased energy (mania). There may, however, be brief episodes of mild mood elevation and overactivity (hypomania) immediately after a depressive episode, sometimes precipitated by antidepressant treatment. The more severe forms of recurrent depressive disorder (F33.2 and F33.3) have much in common with earlier concepts such as manic-depressive depression, melancholia, vital depression and endogenous depression. The first episode may occur at any age from childhood to old age, the onset may be either acute or insidious, and the duration varies from a few weeks to many months. The risk that a patient with recurrent depressive disorder will have an episode of mania never disappears completely, however many depressive episodes have been experienced. If such an episode does occur, the diagnosis should be changed to bipolar affective disorder (F31.-).

Incl.: recurrent episodes of:

• depressive reaction

• psychogenic depression

• reactive depression seasonal depressive disorder

Excl.: recurrent brief depressive episodes (F38.1)

F33.0 Recurrent depressive disorder, current episode mild

A disorder characterized by repeated episodes of depression, the current episode being mild, as in F32.0, and without any history of mania.

F33.1 Recurrent depressive disorder, current episode moderate

A disorder characterized by repeated episodes of depression, the current episode being of moderate severity, as in F32.1, and without any history of mania.

F33.2 Recurrent depressive disorder, current episode severe without psychotic symptoms

A disorder characterized by repeated episodes of depression, the current episode being severe without psychotic symptoms, as in F32.2, and without any history of mania.

Endogenous depression without psychotic symptoms Major depression, recurrent without psychotic symptoms

Manic-depressive psychosis, depressed type without psychotic symptoms Vital depression, recurrent without psychotic symptoms

 

F33.3 Recurrent depressive disorder, current episode severe with psychotic symptoms

A disorder characterized by repeated episodes of depression, the current episode being severe with psychotic symptoms, as in F32.3, and with no previous episodes of mania.

Endogenous depression with psychotic symptoms

Manic-depressive psychosis, depressed type with psychotic symptoms Recurrent severe episodes of:

• major depression with psychotic symptoms

• psychogenic depressive psychosis

• psychotic depression

• reactive depressive psychosis

F33.4 Recurrent depressive disorder, currently in remission

The patient has had two or more depressive episodes as described in F33.0–F33.3, in the past, but has been free from depressive symptoms for several months.

F33.8 Other recurrent depressive disorders

F33.9 Recurrent depressive disorder, unspecified

Monopolar depression NOS

  F34 Persistent mood [affective] disorders

Persistent and usually fluctuating disorders of mood in which the majority of     the individual episodes are not sufficiently severe to warrant being described as hypomanic or mild depressive episodes. Because they last for many years, and sometimes for the greater part of the patient’s adult life, they involve considerable distress and disability. In some instances, recurrent or single manic or depressive episodes may become superimposed on a persistent affective disorder.

F34.0 Cyclothymia

A persistent instability of mood involving numerous periods of depression and mild elation, none of which is sufficiently severe or prolonged to justify a diagnosis   of bipolar affective disorder (F31.-) or recurrent depressive disorder (F33.-). This disorder is frequently found in the relatives of patients with bipolar affective disorder. Some patients with cyclothymia eventually develop bipolar affective disorder.

Affective personality disorder Cycloid personality Cyclothymic personality

F34.1 Dysthymia

A chronic depression of mood, lasting at least several years, which is not sufficiently severe, or in which individual episodes are not sufficiently prolonged, to justify a diagnosis of severe, moderate or mild recurrent depressive disorder (F33.-).

Depressive:

• neurosis

• personality disorder Neurotic depression Persistent anxiety depression

Excl.: anxiety depression (mild or not persistent) (F41.2)

 

F34.8 Other persistent mood [affective] disorders F34.9 Persistent mood [affective] disorder, unspecified

  F38 Other mood [affective] disorders

Any other mood disorders that do not justify classification to F30–F34, because they are not of sufficient severity or duration.

F38.0 Other single mood [affective] disorders

Mixed affective episode

F38.1 Other recurrent mood [affective] disorders

Recurrent brief depressive episodes

F38.8 Other specified mood [affective] disorders

  F39 Unspecified mood [affective] disorder

Incl.: affective psychosis NOS

Neurotic, stress-related and somatoform disorders (F40–F48)

Excl.: when associated with conduct disorder in F91.- (F92.8)

  F40 Phobic anxiety disorders

A group of disorders in which anxiety is evoked only, or predominantly,  in certain well-defined situations that are not currently dangerous. As a result, these situations are characteristically avoided or endured with dread. The patient’s concern may be focused on individual symptoms like palpitations or feeling faint and is often associated with secondary fears of dying, losing control, or going mad. Contemplating entry to the phobic situation usually generates anticipatory anxiety. Phobic anxiety and depression often coexist. Whether two diagnoses, phobic anxiety and depressive episode, are needed, or only one, is determined by the time course of the two conditions and by therapeutic considerations at the time of consultation.

F40.0 Agoraphobia

A fairly well-defined cluster of phobias embracing fears of leaving home, entering shops, crowds and public places, or travelling alone in trains, buses or planes. Panic disorder is a frequent feature of both present and past episodes. Depressive and obsessional symptoms and social phobias are also commonly present as subsidiary features. Avoidance of the phobic situation is often prominent, and some agoraphobics experience little anxiety because they are able to avoid their phobic situations.

Agoraphobia without history of panic disorder Panic disorder with agoraphobia

F40.1         Social phobias

Fear of scrutiny by other people, leading to avoidance of social situations. More pervasive social phobias are usually associated with low self-esteem and fear of criticism. They may present as a complaint of blushing, hand tremor, nausea or urgency of micturition, the patient sometimes being convinced that one of these secondary manifestations of their anxiety is the primary problem. Symptoms may progress to panic attacks.

Anthropophobia Social neurosis

F40.2         Specific (isolated) phobias

Phobias restricted to highly specific situations such as proximity to particular animals, heights, thunder, darkness, flying, closed spaces, urinating or defecating in public toilets, eating certain foods, dentistry or the sight of blood or injury. Though the triggering situation is discrete, contact with it can evoke panic as in agoraphobia or social phobia.

Acrophobia Animal phobias Claustrophobia Simple phobia

Excl.: dysmorphophobia (nondelusional) (F45.2) nosophobia (F45.2)

F40.8         Other phobic anxiety disorders F40.9  Phobic anxiety disorder, unspecified

Phobia NOS Phobic state NOS

 

  F41         Other anxiety disorders

Disorders in which manifestation of anxiety is the major symptom and is not restricted to any particular environmental situation. Depressive and obsessional symptoms, and even some elements of phobic anxiety, may also be present, provided that they are clearly secondary or less severe.

F41.0         Panic disorder [episodic paroxysmal anxiety]

The essential feature is recurrent attacks of severe anxiety (panic), which are not restricted to any particular situation or set of circumstances and are therefore unpredictable. As with other anxiety disorders, the dominant symptoms include sudden onset of palpitations, chest pain, choking sensations, dizziness and feelings of unreality (depersonalization or derealization). There is often also a secondary fear of dying, losing control or going mad. Panic disorder should not be given as the main diagnosis if the patient has a depressive disorder at the time the attacks start; in these circumstances, the panic attacks are probably secondary to depression.

Panic:

•   attack

•   state

Excl.: panic disorder with agoraphobia (F40.0)

F41.1         Generalized anxiety disorder

Anxiety that is generalized and persistent but not restricted to, or even strongly predominating in, any particular environmental circumstances (i.e. it is ‘free- floating’). The dominant symptoms are variable but include complaints of persistent nervousness, trembling, muscular tensions, sweating, lightheadedness, palpitations, dizziness and epigastric discomfort. Fears that the patient or a relative will shortly become ill or have an accident are often expressed.

Anxiety:

•  neurosis

•  reaction

•  state

Excl.: neurasthenia (F48.0)

F41.2         Mixed anxiety and depressive disorder

This category should be used when symptoms of anxiety and depression are both present, but neither is clearly predominant, and neither type of symptom is present to the extent that justifies a diagnosis if considered separately. When both anxiety and depressive symptoms are present and severe enough to justify individual diagnoses, both diagnoses should be recorded and this category should not be used.

Anxiety depression (mild or not persistent)

F41.3         Other mixed anxiety disorders

Symptoms of anxiety mixed with features of other disorders in F42–F48. Neither type of symptom is severe enough to justify a diagnosis if considered separately.

F41.8         Other specified anxiety disorders

Anxiety hysteria

F41.9         Anxiety disorder, unspecified

Anxiety NOS

 

  F42         Obsessive-compulsive disorder

The essential feature is recurrent obsessional thoughts or compulsive acts. Obsessional thoughts are ideas, images or impulses that enter the patient’s mind again and again in a stereotyped form. They are almost invariably distressing and the patient often tries, unsuccessfully, to resist them. They are, however, recognized as his or her own thoughts, even though they are involuntary and often repugnant. Compulsive acts or rituals are stereotyped behaviours that are repeated again and again. They are not inherently enjoyable, nor do they result in the completion of inherently useful tasks. Their function is to prevent some objectively unlikely event, often involving harm to, or caused by, the patient, which he or she fears might otherwise occur. Usually, this behaviour is recognized by the patient as pointless or ineffectual and repeated attempts are made to resist. Anxiety is almost invariably present. If compulsive acts are resisted, the anxiety gets worse.

Incl.: anankastic neurosis

obsessive-compulsive neurosis

Excl.: obsessive-compulsive personality (disorder) (F60.5)

F42.0         Predominantly obsessional thoughts or ruminations

These may take the form of ideas, mental images or impulses to act, which are nearly always distressing to the subject. Sometimes the ideas are an indecisive, endless consideration of alternatives, associated with an inability to make trivial but necessary decisions in day-to-day living. The relationship between obsessional ruminations and depression is particularly close and a diagnosis of obsessive- compulsive disorder should be preferred only if ruminations arise or persist in the absence of a depressive episode.

F42.1         Predominantly compulsive acts [obsessional rituals]

The majority of compulsive acts are concerned with cleaning (particularly handwashing), repeated checking to ensure that a potentially dangerous situation has not been allowed to develop, or orderliness and tidiness. Underlying the overt behaviour is a fear, usually of danger either to or caused by the patient, and the ritual is an ineffectual or symbolic attempt to avert that danger.

F42.2         Mixed obsessional thoughts and acts F42.8    Other obsessive-compulsive disorders

F42.9         Obsessive-compulsive disorder, unspecified

 

  F43         Reaction to severe stress, and adjustment disorders

This category differs from others, in that it includes disorders identifiable on the basis of not only symptoms and course but also the existence of one or other of two causative influences: an exceptionally stressful life event producing an acute stress reaction, or a significant life change leading to continued unpleasant circumstances that result in an adjustment disorder. Although less severe psychosocial stress (‘life events’) may precipitate the onset or contribute to the presentation of a very wide range of disorders classified elsewhere in this chapter, its etiological importance is not always clear and in each case will be found to depend on individual, often idiosyncratic, vulnerability, i.e. the life events are neither necessary nor sufficient to explain the occurrence and form of the disorder. In contrast, the disorders brought together here are thought to arise always as a direct consequence of acute severe stress or continued trauma. The stressful events or the continuing unpleasant circumstances are the primary and overriding causal factor and the disorder would not have occurred without their impact. The disorders in this section can thus     be regarded as maladaptive responses to severe or continued stress, in that they interfere with successful coping mechanisms and therefore lead to problems of social functioning.

F43.0         Acute stress reaction

A transient disorder that develops in an individual without any other apparent mental disorder, in response to exceptional physical and mental stress and that usually subsides within hours or days. Individual vulnerability and coping capacity play a role in the occurrence and severity of acute stress reactions. The symptoms show a typically mixed and changing picture and include an initial state of ‘daze’, with some constriction of the field of consciousness and narrowing of attention, inability to comprehend stimuli, and disorientation. This state may be followed either by further withdrawal from the surrounding situation (to the extent of a dissociative stupor – F44.2), or by agitation and overactivity (flight reaction or fugue). Autonomic signs of panic anxiety (tachycardia, sweating, flushing) are commonly present. The symptoms usually appear within minutes of the impact of

 

the stressful stimulus or event, and disappear within two to three days (often within hours). Partial or complete amnesia (F44.0) for the episode may be present. If the symptoms persist, a change in diagnosis should be considered.

Acute:

•  crisis reaction

•  reaction to stress Combat fatigue Crisis state Psychic shock

F43.1         Post-traumatic stress disorder

Arises as a delayed or protracted response to a stressful event or situation (of either brief or long duration) of an exceptionally threatening or catastrophic nature, which is likely to cause pervasive distress in almost anyone. Predisposing factors, such as personality traits (e.g. compulsive, asthenic) or previous history  of neurotic illness, may lower the threshold for the development of the syndrome or aggravate its course, but they are neither necessary nor sufficient to explain its occurrence. Typical features include episodes of repeated reliving of the trauma  in intrusive memories (‘flashbacks’), dreams or nightmares, occurring against   the persisting background of a sense of ‘numbness’ and emotional blunting, detachment from other people, unresponsiveness to surroundings, anhedonia, and avoidance of activities and situations reminiscent of the trauma. There is usually a state of autonomic hyperarousal with hypervigilance, an enhanced startle reaction, and insomnia. Anxiety and depression are commonly associated with the above symptoms and signs, and suicidal ideation is not infrequent. The onset follows  the trauma with a latency period that may range from a few weeks to months. The course is fluctuating but recovery can be expected in the majority of cases. In a small proportion of cases, the condition may follow a chronic course over many years, with eventual transition to an enduring personality change (F62.0).

Traumatic neurosis

F43.2         Adjustment disorders

States of subjective distress and emotional disturbance, usually interfering with social functioning and performance, arising in the period of adaptation to a significant life change or a stressful life event. The stressor may have affected the integrity of an individual’s social network (bereavement, separation experiences) or the wider system of social supports and values (migration, refugee status), or represented a major developmental transition or crisis (going to school, becoming a parent, failure to attain a cherished personal goal, retirement). Individual predisposition or vulnerability plays an important role in the risk of occurrence and the shaping of the manifestations of adjustment disorders, but it is nevertheless assumed that the condition would not have arisen without the stressor. The manifestations vary and include depressed mood, anxiety or worry (or mixture of these) and a feeling of inability to cope, plan ahead or continue in the present situation, as well as some degree of disability in   the performance of daily routine. Conduct disorders may be an associated feature, particularly in adolescents. The predominant feature may be a brief or prolonged depressive reaction, or a disturbance of other emotions and conduct.

Culture shock Grief reaction

Hospitalism in children

Excl.: separation anxiety disorder of childhood (F93.0)

F43.8         Other reactions to severe stress

F43.9         Reaction to severe stress, unspecified

 

  F44         Dissociative [conversion] disorders

The common themes that are shared by dissociative or conversion disorders are a partial or complete loss of the normal integration between memories of the past, awareness of identity and immediate sensations, and control of bodily movements. All types of dissociative disorders tend to remit after a few weeks or months, particularly if their onset is associated with a traumatic life event. More chronic disorders, particularly paralyses and anaesthesias, may develop if the onset is associated with insoluble problems or interpersonal difficulties. These disorders have previously been classified as various types of ‘conversion hysteria’. They are presumed to be psychogenic in origin, being associated closely in time with traumatic events, insoluble and intolerable problems, or disturbed relationships. The symptoms often represent the patient’s concept of how a physical illness would be manifest. Medical examination and investigation do not reveal the presence of any known physical or neurological disorder. In addition, there is evidence that the loss of function is an expression of emotional conflicts or needs. The symptoms may develop in close relationship to psychological stress, and often appear suddenly. Only disorders of physical functions normally under voluntary control, and loss of sensations, are included here. Disorders involving pain and other complex physical sensations, mediated by the autonomic nervous system are classified under somatization disorder (F45.0). The possibility of the later appearance of serious physical or psychiatric disorders should always be kept in mind.

Incl.: conversion:

•  hysteria

•  reaction hysteria

hysterical psychosis

Excl.: malingering [conscious simulation] (Z76.5)

F44.0         Dissociative amnesia

The main feature is loss of memory, usually of important recent events, that is not due to organic mental disorder, and is too great to be explained by ordinary forgetfulness or fatigue. The amnesia is usually centred on traumatic events, such as accidents or unexpected bereavements, and is usually partial and selective. Complete and generalized amnesia is rare, and is usually part of a fugue (F44.1). If this is the case, the disorder should be classified as such. The diagnosis should not be made in the presence of organic brain disorders, intoxication or excessive fatigue.

Excl.: alcohol- or other psychoactive-substance-induced amnesic disorder (F10–F19 with common fourth character .6) amnesia:

•  NOS (R41.3)

•  anterograde (R41.1)

•  retrograde (R41.2)

nonalcoholic organic amnesic syndrome (F04) postictal amnesia in epilepsy (G40.-)

F44.1         Dissociative fugue

Dissociative fugue has all the features of dissociative amnesia, plus purposeful travel beyond the usual everyday range. Although there is amnesia for the period of the fugue, the patient’s behaviour during this time may appear completely normal to independent observers.

Excl.: postictal fugue in epilepsy (G40.-)

F44.2         Dissociative stupor

Dissociative stupor is diagnosed on the basis of a profound diminution or absence of voluntary movement and normal responsiveness to external stimuli such as light, noise and touch, but examination and investigation reveal no evidence of a physical cause. In addition, there is positive evidence of psychogenic causation in the form of recent stressful events or problems.

Excl.: organic catatonic disorder (F06.1) stupor:

•   NOS (R40.1)

•   catatonic (F20.2)

•   depressive (F31–F33)

•   manic (F30.2)

F44.3         Trance and possession disorders

Disorders in which there is a temporary loss of the sense of personal identity and full awareness of the surroundings. Include here only trance states that are involuntary or unwanted, occurring outside religious or culturally accepted situations.

Excl.: states associated with:

•   acute and transient psychotic disorders (F23.-)

•   organic personality disorder (F07.0)

•   postconcussional syndrome (F07.2)

•   psychoactive-substance intoxication (F10–F19 with common fourth character .0)

•   schizophrenia (F20.-)

F44.4         Dissociative motor disorders

In the commonest varieties, there is loss of ability to move the whole or a part of  a limb or limbs. There may be close resemblance to almost any variety of ataxia, apraxia, akinesia, aphonia, dysarthria, dyskinesia, seizures or paralysis.

Psychogenic:

•  aphonia

•  dysphonia

F44.5         Dissociative convulsions

Dissociative convulsions may mimic epileptic seizures very closely in terms of movements, but tongue-biting, bruising due to falling, and incontinence of urine are rare, and consciousness is maintained or replaced by a state of stupor or trance.

F44.6         Dissociative anaesthesia and sensory loss

Anaesthetic areas of skin often have boundaries that make it clear that they are associated with the patient’s ideas about bodily functions, rather than medical knowledge. There may be differential loss between the sensory modalities that cannot be due to a neurological lesion. Sensory loss may be accompanied by complaints of paraesthesia. Loss of vision and hearing are rarely total in dissociative disorders.

Psychogenic deafness

F44.7         Mixed dissociative [conversion] disorders

Combination of disorders specified in F44.0–F44.6

F44.8         Other dissociative [conversion] disorders

Ganser syndrome Multiple personality Psychogenic:

•   confusion

•   twilight state

F44.9         Dissociative [conversion] disorder, unspecified

 

  F45         Somatoform disorders

The main feature is repeated presentation of physical symptoms, together with persistent requests for medical investigations, in spite of repeated negative findings and reassurances by doctors that the symptoms have no physical basis. If any physical disorders are present, they do not explain the nature and extent of the symptoms or the distress and preoccupation of the patient.

Excl.: dissociative disorders (F44.-) hair-plucking (F98.4)

lalling (F80.0) lisping (F80.8) nail-biting (F98.8)

psychological or behavioural factors associated with disorders or diseases classified elsewhere (F54)

sexual dysfunction, not caused by organic disorder or disease (F52.-)

thumb-sucking (F98.8)

tic disorders (in childhood and adolescence) (F95.-) Tourette syndrome (F95.2)

trichotillomania (F63.3)

F45.0         Somatization disorder

The main features are multiple, recurrent and frequently changing physical symptoms of at least two years’ duration. Most patients have a long and complicated history of contact with both primary and specialist medical care services, during which many negative investigations or fruitless exploratory operations may have been carried out. Symptoms may be referred to any part or system of the body. The course of the disorder is chronic and fluctuating, and is often associated with

 

disruption of social, interpersonal and family behaviour. Short-lived (less than two years) and less striking symptom patterns should be classified under undifferentiated somatoform disorder (F45.1).

Briquet disorder

Multiple psychosomatic disorder

Excl.: malingering [conscious simulation] (Z76.5)

F45.1         Undifferentiated somatoform disorder

When somatoform complaints are multiple, varying and persistent, but the complete and typical clinical picture of somatization disorder is not fulfilled, the diagnosis of undifferentiated somatoform disorder should be considered.

Undifferentiated psychosomatic disorder

F45.2         Hypochondriacal disorder

The essential feature is a persistent preoccupation with the possibility of having one or more serious and progressive physical disorders. Patients manifest persistent somatic complaints or a persistent preoccupation with their physical appearance. Normal or commonplace sensations and appearances are often interpreted by patients as abnormal and distressing, and attention is usually focused upon only one or two organs or systems of the body. Marked depression and anxiety are often present, and may justify additional diagnoses.

Body dysmorphic disorder Dysmorphophobia (nondelusional) Hypochondriacal neurosis Hypochondriasis

Nosophobia

Excl.: delusional dysmorphophobia (F22.8)

fixed delusions about bodily functions or shape (F22.-)

F45.3         Somatoform autonomic dysfunction

Symptoms are presented by the patient as if they were due to a physical disorder of a system or organ that is largely or completely under autonomic innervation and control, i.e. the cardiovascular, gastrointestinal, respiratory and urogenital systems. The symptoms are usually of two types, neither of which indicates a physical disorder of the organ or system concerned. First, there are complaints based upon objective signs of autonomic arousal, such as palpitations, sweating, flushing, tremor and expression of fear and distress about the possibility of a physical disorder. Second, there are subjective complaints of a nonspecific or changing nature, such as fleeting aches and pains, sensations of burning, heaviness, tightness and feelings of being bloated or distended, which are referred by the patient to a specific organ or system.

Cardiac neurosis Da Costa syndrome Gastric neurosis

Neurocirculatory asthenia Psychogenic forms of:

•  aerophagy

•  cough

•   diarrhoea

•   dyspepsia

•   dysuria

•   flatulence

•   hiccough

•   hyperventilation

•   increased frequency of micturition

•   irritable bowel syndrome

•   pylorospasm

Excl.: psychological and behavioural factors associated with disorders or diseases classified elsewhere (F54)

F45.4         Persistent somatoform pain disorder

The predominant complaint is of persistent, severe and distressing pain, which cannot be explained fully by a physiological process or a physical disorder, and which occurs in association with emotional conflict or psychosocial problems that are sufficient to allow the conclusion that they are the main causative influences. The result is usually a marked increase in support and attention, either personal or medical. Pain presumed to be of psychogenic origin occurring during the course of depressive disorders or schizophrenia should not be included here.

Psychalgia Psychogenic:

•   backache

•   headache

Somatoform pain disorder

Excl.: backache NOS (M54.9) pain:

•  NOS (R52.9)

•  acute (R52.0)

•  chronic (R52.2)

•  intractable (R52.1) tension headache (G44.2)

F45.8         Other somatoform disorders

Any other disorders of sensation, function and behaviour, not due to physical disorders, that are not mediated through the autonomic nervous system, that are limited to specific systems or parts of the body and that are closely associated in time with stressful events or problems.

Psychogenic:

•   dysmenorrhoea

•   dysphagia, including ‘globus hystericus’

•   pruritus

•   torticollis Teeth-grinding

F45.9         Somatoform disorder, unspecified

Psychosomatic disorder NOS

  F48         Other neurotic disorders

F48.0         Neurasthenia

Considerable cultural variations occur in the presentation of this disorder, and  two main types occur, with substantial overlap. In one type, the main feature is    a complaint of increased fatigue after mental effort, often associated with some decrease in occupational performance or coping efficiency in daily tasks. The mental fatigability is typically described as an unpleasant intrusion of distracting associations or recollections, difficulty in concentrating, and generally inefficient thinking. In the other type, the emphasis is on feelings of bodily or physical weakness and exhaustion after only minimal effort, accompanied by a feeling of muscular aches and pains and inability to relax. In both types, a variety of other unpleasant physical feelings is common, such as dizziness, tension headaches and feelings of general instability. Worry about decreasing mental and bodily well- being, irritability, anhedonia and varying minor degrees of both depression and anxiety are all common. Sleep is often disturbed in its initial and middle phases but hypersomnia may also be prominent.

Fatigue syndrome

Use additional code, if desired, to identify previous physical illness.

Excl.: asthenia NOS (R53) burn-out (Z73.0)

malaise and fatigue (R53)

postviral fatigue syndrome (G93.3) psychasthenia (F48.8)

F48.1         Depersonalization-derealization syndrome

A rare disorder in which the patient complains spontaneously that his or her mental activity, body and surroundings are changed in their quality, so as to be unreal, remote or automatized. Among the varied phenomena of the syndrome, patients complain most frequently of loss of emotions and feelings of estrangement or detachment from their thinking, their body or the real world. In spite of the dramatic nature of the experience, the patient is aware of the unreality of the change. The sensorium is normal and the capacity for emotional expression intact. Depersonalization-derealization symptoms may occur as part of a diagnosable schizophrenic, depressive, phobic or obsessive-compulsive disorder. In such cases, the diagnosis should be that of the main disorder.

F48.8         Other specified neurotic disorders

Dhat syndrome

Occupational neurosis, including writer’s cramp Psychasthenia

Psychasthenic neurosis Psychogenic syncope

F48.9         Neurotic disorder, unspecified

Neurosis NOS

Behavioural syndromes associated with physiological disturbances and physical factors

(F50–F59)

 

  F50         Eating disorders

Excl.: anorexia NOS (R63.0) feeding:

•  difficulties and mismanagement (R63.3)

•  disorder of infancy or childhood (F98.2) polyphagia (R63.2)

F50.0         Anorexia nervosa

A disorder characterized by deliberate weight loss,  induced  and  sustained  by the patient. It occurs most commonly in adolescent girls and young women, but adolescent boys and young men may also be affected, as may children approaching puberty and older women up to the menopause. The disorder is associated with a specific psychopathology whereby a dread of fatness and flabbiness of body contour persists as an intrusive overvalued idea, and the patients impose a low weight threshold on themselves. There is usually undernutrition of varying severity, with secondary endocrine and metabolic changes and disturbances of bodily function. The symptoms include restricted dietary choice, excessive exercise, induced vomiting and purgation, and use of appetite suppressants and diuretics.

Excl.: loss of appetite (R63.0) loss of appetite

•  psychogenic (F50.8)

F50.1         Atypical anorexia nervosa

Disorders that fulfil some of the features of anorexia nervosa but in which the overall clinical picture does not justify that diagnosis. For instance, one of the key symptoms, such as amenorrhoea or marked dread of being fat, may be absent, in the presence of marked weight loss and weight-reducing behaviour. This diagnosis should not be made in the presence of known physical disorders associated with weight loss.

F50.2         Bulimia nervosa

A syndrome characterized by repeated bouts of overeating and an excessive preoccupation with the control of body weight, leading to a pattern of overeating followed by vomiting or use of purgatives. This disorder shares many psychological features with anorexia nervosa, including an overconcern with body shape and weight. Repeated vomiting is likely to give rise to disturbances of body electrolytes and physical complications. There is often, but not always, a history of an earlier episode of anorexia nervosa, the interval ranging from a few months to several years.

Bulimia NOS Hyperorexia nervosa

F50.3         Atypical bulimia nervosa

Disorders that fulfil some of the features of bulimia nervosa, but in which the overall clinical picture does not justify that diagnosis. For instance, there may be recurrent bouts of overeating and overuse of purgatives without significant weight change, or the typical overconcern about body shape and weight may be absent.

F50.4 Overeating associated with other psychological disturbances Overeating due to stressful events, such as bereavement, accident, childbirth, etc. Psychogenic overeating

Excl.: obesity (E66.-)

F50.5         Vomiting associated with other psychological disturbances

Repeated vomiting that occurs in dissociative disorders (F44.-) and hypochondriacal disorder (F45.2), and that is not solely due to conditions classified outside this chapter. This subcategory may also be used in addition to O21.- (excessive vomiting in pregnancy) when emotional factors are predominant in the causation of recurrent nausea and vomiting in pregnancy.

Psychogenic vomiting

Excl.: nausea (R11)

vomiting NOS (R11)

F50.8         Other eating disorders

Pica in adults

Psychogenic loss of appetite

Excl.: pica of infancy and childhood (F98.3)

F50.9         Eating disorder, unspecified

 

  F51         Nonorganic sleep disorders

In many cases, a disturbance of sleep is one of the symptoms of another disorder, either mental or physical. Whether a sleep disorder in a given patient is an independent condition or simply one of the features of another disorder classified elsewhere, either in this chapter or in others, should be determined on the basis of its clinical presentation and course, as well as on the therapeutic considerations and priorities at the time of the consultation. Generally, if the sleep disorder is one of the major complaints and is perceived as a condition in itself, the present code should be used, along with other pertinent diagnoses describing the psychopathology and pathophysiology involved in a given case. This category includes only those sleep disorders in which emotional causes are considered to be a primary factor, and that are not due to identifiable physical disorders classified elsewhere.

Excl.: sleep disorders (organic) (G47.-)

F51.0         Nonorganic insomnia

A condition of unsatisfactory quantity and/or quality of sleep, which persists for a considerable period of time, including difficulty falling asleep, difficulty staying asleep, or early final wakening. Insomnia is a common symptom of many mental and physical disorders, and should be classified here in addition to the basic disorder only if it dominates the clinical picture.

Excl.: insomnia (organic) (G47.0)

F51.1 Nonorganic hypersomnia

Hypersomnia is defined as a condition of either excessive daytime sleepiness and sleep attacks (not accounted for by an inadequate amount of sleep) or prolonged transition to the fully aroused state upon awakening. In the absence of an organic factor for the occurrence of hypersomnia, this condition is usually associated with mental disorders.

Excl.: hypersomnia (organic) (G47.1) narcolepsy (G47.4)

F51.2 Nonorganic disorder of the sleep–wake schedule

A lack of synchrony between the sleep-wake schedule and the desired sleep– wake schedule for the individual’s environment, resulting in a complaint of either insomnia or hypersomnia.

Psychogenic inversion of:

• circadian

• nyctohemeral

• sleep

rhythm

Excl.: disorders of the sleep–wake schedule (organic) (G47.2)

F51.3 Sleepwalking [somnambulism]

A state of altered consciousness in which phenomena of sleep and wakefulness are combined. During a sleepwalking episode, the individual arises from bed, usually during the first third of nocturnal sleep, and walks about, exhibiting low levels of awareness, reactivity and motor skill. Upon awakening, there is usually no recall of the event.

F51.4 Sleep terrors [night terrors]

Nocturnal episodes of extreme terror and panic associated with intense vocalization, motility and high levels of autonomic discharge. The individual sits up or gets up, usually during the first third of nocturnal sleep, with a panicky scream. Quite often, he or she rushes to the door as if trying to escape, although very seldom leaves the room. Recall of the event, if any, is very limited (usually to one or two fragmentary mental images).

F51.5 Nightmares

Dream experiences loaded with anxiety or fear.  There is very detailed recall       of the dream content. The dream experience is very vivid and usually includes themes involving threats to survival, security or self-esteem. Quite often, there is a recurrence of the same or similar frightening nightmare themes. During a typical episode, there is a degree of autonomic discharge but no appreciable vocalization or body motility. Upon awakening, the individual rapidly becomes alert and oriented.

Dream anxiety disorder

F51.8 Other nonorganic sleep disorders F51.9 Nonorganic sleep disorder, unspecified

Emotional sleep disorder NOS

 

  F52 Sexual dysfunction, not caused by organic disorder or disease

Sexual dysfunction covers the various ways in which an individual is unable to participate in a sexual relationship as he or she would wish. Sexual response is a psychosomatic process and both psychological and somatic processes are usually involved in the causation of sexual dysfunction.

Excl.: Dhat syndrome (F48.8)

F52.0 Lack or loss of sexual desire

Loss of sexual desire is the principal problem and is not secondary to other sexual difficulties, such as erectile failure or dyspareunia.

Frigidity

Hypoactive sexual desire disorder

F52.1 Sexual aversion and lack of sexual enjoyment

Either the prospect of sexual interaction produces sufficient fear or anxiety that sexual activity is avoided (sexual aversion) or sexual responses occur normally and orgasm is experienced but there is a lack of appropriate pleasure (lack of sexual enjoyment).

Anhedonia (sexual)

F52.2 Failure of genital response

The principal problem in men is erectile dysfunction (difficulty in developing     or maintaining an erection suitable for satisfactory intercourse). In women, the principal problem is vaginal dryness or failure of lubrication.

Female sexual arousal disorder Male erectile disorder Psychogenic impotence

Excl.: impotence of organic origin (N48.4)

F52.3 Orgasmic dysfunction

Orgasm either does not occur or is markedly delayed.

Inhibited orgasm (male)(female) Psychogenic anorgasmy

F52.4 Premature ejaculation

The inability to control ejaculation sufficiently for both partners to enjoy sexual interaction.

F52.5 Nonorganic vaginismus

Spasm of the pelvic floor muscles that surround the vagina, causing occlusion of the vaginal opening. Penile entry is either impossible or painful.

Psychogenic vaginismus

Excl.: vaginismus (organic) (N94.2)

 

F52.6 Nonorganic dyspareunia

Dyspareunia (or pain during sexual intercourse) occurs in both women and men. It can often be attributed to local pathology and should then properly be categorized under the pathological condition. This category is to be used only if there is no primary nonorganic sexual dysfunction (e.g. vaginismus or vaginal dryness).

Psychogenic dyspareunia

Excl.: dyspareunia (organic) (N94.1)

F52.7 Excessive sexual drive

Nymphomania Satyriasis

F52.8 Other sexual dysfunction, not caused by organic disorder or disease

F52.9 Unspecified sexual dysfunction, not caused by organic disorder or disease

  F53 Mental and behavioural disorders associated with the puerperium, not elsewhere classified

This category includes only mental disorders associated with the puerperium (commencing within six weeks of delivery) that do not meet the criteria for disorders classified elsewhere in this chapter, either because insufficient information is available, or because it is considered that special additional clinical features are present that make their classification elsewhere inappropriate.

F53.0 Mild mental and behavioural disorders associated with the puerperium, not elsewhere classified

Depression:

• postnatal NOS

• postpartum NOS

F53.1 Severe mental and behavioural disorders associated with the puerperium, not elsewhere classified

Puerperal psychosis NOS

F53.8 Other mental and behavioural disorders associated with the puerperium, not elsewhere classified

F53.9 Puerperal mental disorder, unspecified

 

  F54 Psychological and behavioural factors associated with disorders or diseases classified elsewhere

This category should be used to record the presence of psychological or behavioural influences thought to have played a major part in the etiology of physical disorders that can be classified to other chapters. Any resulting mental disturbances are usually mild, and often prolonged (such as worry, emotional conflict, apprehension), and do not of themselves justify the use of any of the categories in this chapter.

Incl.: psychological factors affecting physical conditions examples of the use of this category are:

• asthma F54 and J45.-

• dermatitis F54 and L23–L25

• gastric ulcer F54 and K25.-

• irritable bowel syndrome F54 and K58.-

• ulcerative colitis F54 and K51.-

• urticaria F54 and L50.-

Use additional code, if desired, to identify the associated physical disorder.

Excl.: tension-type headache (G44.2)

  F55 Abuse of non-dependence-producing substances

A wide variety of medicaments and folk remedies may be involved, but the particularly important groups are: (a) psychotropic drugs that do not produce dependence, such as antidepressants, (b) laxatives, and (c) analgesics that may be purchased without medical prescription, such as aspirin and paracetamol.

Persistent use of these substances often involves unnecessary contacts with medical professionals or supporting staff, and is sometimes accompanied by harmful physical effects of the substances. Attempts to dissuade or forbid the use of the substance are often met with resistance; for laxatives and analgesics, this may be in spite of warnings about (or even the development of) physical harm such as renal dysfunction or electrolyte disturbances. Although it is usually clear that the patient has a strong motivation to take the substance, dependence or withdrawal symptoms do not develop as in the case of the psychoactive substances specified in F10–F19.

Incl.: abuse of:

• antacids

• herbal or folk remedies

• steroids or hormones

• vitamins laxative habit

Excl.:  abuse of psychoactive substances (F10-F19)

  F59 Unspecified behavioural syndromes associated with physiological disturbances and physical factors Incl.: psychogenic physiological dysfunction NOS

 

Disorders of adult personality and behaviour (F60–F69)

This block includes a variety of conditions and behaviour patterns of clinical significance that tend to be persistent and appear to be the expression of the individual’s characteristic lifestyle and mode of relating to himself or herself and others. Some of these conditions and patterns of behaviour emerge early in the course of individual development, as a result of both constitutional factors and social experience, while others are acquired later in life. Specific personality disorders (F60.-), mixed and other personality disorders (F61.-) and enduring personality changes (F62.-) are deeply ingrained and enduring behaviour patterns, manifesting as inflexible responses to a broad range of personal and social situations. They represent extreme or significant deviations from the way in which the average individual in a given culture perceives, thinks, feels and, particularly, relates to others. Such behaviour patterns tend to be stable and to encompass multiple domains of behaviour and psychological functioning. They are frequently, but not always, associated with various degrees of subjective distress and problems of social performance.

  F60 Specific personality disorders

These are severe disturbances in the personality and behavioural tendencies of the individual; not directly resulting from disease, damage or other insult to the brain, or from another psychiatric disorder; usually involving several areas of the personality; nearly always associated with considerable personal distress and social disruption; and usually manifest since childhood or adolescence and continuing throughout adulthood.

F60.0 Paranoid personality disorder

Personality disorder characterized by excessive sensitivity to setbacks; unforgiveness of insults; suspiciousness and a tendency to distort experience by misconstruing the neutral or friendly actions of others as hostile or contemptuous; recurrent suspicions, without justification, regarding the sexual fidelity of the spouse or sexual partner; and a combative and tenacious sense of personal rights. There may be excessive self-importance and there is often excessive self-reference.

Personality (disorder):

• expansive paranoid

• fanatic

• querulant

• paranoid

• sensitive paranoid

Excl.: paranoia (F22.0)

paranoia querulans (F22.8) paranoid:

• psychosis (F22.0)

• schizophrenia (F20.0)

• state (F22.0)

 

F60.1 Schizoid personality disorder

Personality disorder characterized by withdrawal from affectional, social and other contacts, with preference for fantasy, solitary activities and introspection. There is a limited capacity to express feelings and to experience pleasure.

Excl.: Asperger syndrome (F84.5) delusional disorder (F22.0)

schizoid disorder of childhood (F84.5) schizophrenia (F20.-)

schizotypal disorder (F21)

F60.2 Dissocial personality disorder

Personality disorder characterized by disregard for social obligations, and callous unconcern for the feelings of others. There is gross disparity between behaviour and the prevailing social norms. Behaviour is not readily modifiable by adverse experience, including punishment. There is a low tolerance to frustration and a low threshold for discharge of aggression, including violence; there is a tendency to blame others, or to offer plausible rationalizations for the behaviour, bringing the patient into conflict with society.

Personality (disorder):

• amoral

• antisocial

• asocial

• psychopathic

• sociopathic

Excl.: conduct disorders (F91.-)

emotionally unstable personality disorder (F60.3)

F60.3 Emotionally unstable personality disorder

Personality disorder characterized by a definite  tendency  to  act  impulsively  and without consideration of the consequences; the mood is unpredictable and capricious. There is a liability to outbursts of emotion and an incapacity to control the behavioural explosions. There is a tendency to quarrelsome behaviour and to conflicts with others, especially when impulsive acts are thwarted or censored. Two types may be distinguished: the impulsive type, characterized predominantly by emotional instability and lack of impulse control, and the borderline type, characterized in addition by disturbances in self-image, aims and internal preferences, by chronic feelings of emptiness, by intense and unstable interpersonal relationships, and by a tendency to self-destructive behaviour, including suicide gestures and attempts.

Personality (disorder):

• aggressive

• borderline

• explosive

Excl.: dissocial personality disorder (F60.2)

 

F60.4 Histrionic personality disorder

Personality disorder characterized by shallow and labile affectivity, self- dramatization, theatricality, exaggerated expression of emotions, suggestibility, egocentricity, self-indulgence, lack of consideration for others, easily hurt feelings, and continuous seeking for appreciation, excitement and attention.

Personality (disorder):

• hysterical

• psychoinfantile

F60.5 Anankastic personality disorder

Personality disorder characterized by feelings of doubt, perfectionism, excessive conscientiousness, checking and preoccupation with details, stubbornness, caution, and rigidity. There may be insistent and unwelcome thoughts or impulses that do not attain the severity of an obsessive-compulsive disorder.

Personality (disorder):

• compulsive

• obsessional

• obsessive-compulsive

Excl.: obsessive-compulsive disorder (F42.-)

F60.6 Anxious [avoidant] personality disorder

Personality disorder characterized by feelings of tension and apprehension, insecurity and inferiority. There is a continuous yearning to be liked and accepted, a hypersensitivity to rejection and criticism, with restricted personal attachments, and a tendency to avoid certain activities by habitual exaggeration of the potential dangers or risks in everyday situations.

F60.7 Dependent personality disorder

Personality disorder characterized by pervasive passive reliance on other people to make one’s major and minor life decisions, great fear of abandonment, feelings of helplessness and incompetence, passive compliance with the wishes of elders and others, and a weak response to the demands of daily life. Lack of vigour may show itself in the intellectual or emotional spheres; there is often a tendency to transfer responsibility to others.

Personality (disorder):

• asthenic

• inadequate

• passive

• self-defeating

F60.8 Other specific personality disorders

Personality (disorder):

• eccentric

• ‘haltlose’ type

• immature

• narcissistic

• passive-aggressive

• psychoneurotic

 

F60.9 Personality disorder, unspecified

Character neurosis NOS Pathological personality NOS

  F61 Mixed and other personality disorders

This category is intended for personality disorders that are often troublesome but do not demonstrate the specific pattern of symptoms that characterize the disorders described in F60.-. As a result, they are often more difficult to diagnose than the disorders in F60.-.

Examples include:

• mixed personality disorders with features of several of the disorders in F60.- but without a predominant set of symptoms that would allow a more specific diagnosis;

• troublesome personality changes, not classifiable to F60.- or F62.-, and regarded as secondary to a main diagnosis of a coexisting affective or anxiety disorder.

Excl.: accentuated personality traits (Z73.1)

  F62 Enduring personality changes, not attributable to brain damage and disease

Disorders of adult personality and behaviour that have developed in persons with no previous personality disorder, following exposure to catastrophic or excessive prolonged stress, or following a severe psychiatric illness. These diagnoses should be made only when there is evidence of a definite and enduring change in a person’s pattern of perceiving, relating to or thinking about the environment and himself  or herself. The personality change should be significant and be associated with inflexible and maladaptive behaviour not present before the pathogenic experience. The change should not be a direct manifestation of another mental disorder or a residual symptom of any antecedent mental disorder.

Excl.: personality and behavioural disorder due to brain disease, damage and dysfunction (F07.-)

F62.0 Enduring personality change after catastrophic experience

Enduring personality change, present for at least two years, following exposure to catastrophic stress. The stress must be so extreme that it is not necessary to consider personal vulnerability in order to explain its profound effect on the personality. The disorder is characterized by a hostile or distrustful attitude toward the world, social withdrawal, feelings of emptiness or hopelessness, a chronic feeling of ‘being on edge’ as if constantly threatened, and estrangement. Post-traumatic stress disorder (F43.1) may precede this type of personality change.

Personality change after:

• concentration camp experiences

• disasters

• prolonged:

– captivity with an imminent possibility of being killed

– exposure to life-threatening situations such as being a victim of terrorism

• torture

Excl.: post-traumatic stress disorder (F43.1)

 

F62.1 Enduring personality change after psychiatric illness

Personality change, persisting for at least two years, attributable to the traumatic experience of suffering from a severe psychiatric illness. The change cannot be explained by a previous personality disorder and should be differentiated from residual schizophrenia and other states of incomplete recovery from an antecedent mental disorder. This disorder is characterized by an excessive dependence on and a demanding attitude towards others; conviction of being changed or stigmatized by the illness, leading to an inability to form and maintain close and confiding personal relationships and to social isolation; passivity, reduced interests, and diminished involvement in leisure activities; persistent complaints of being ill, which may be associated with hypochondriacal claims and illness behaviour; dysphoric or labile mood, not due to the presence of a current mental disorder or antecedent mental disorder with residual affective symptoms; and longstanding problems in social and occupational functioning.

F62.8 Other enduring personality changes

Chronic pain personality syndrome

F62.9 Enduring personality change, unspecified

  F63 Habit and impulse disorders

This category includes certain disorders of behaviour that are not classifiable under other categories. They are characterized by repeated acts that have no clear rational motivation, cannot be controlled, and generally harm the patient’s own interests and those of other people. The patient reports that the behaviour is associated with impulses to action. The cause of these disorders is not understood and they are grouped together because of broad descriptive similarities, not because they are known to share any other important features.

Excl.: habitual excessive use of alcohol or psychoactive substances (F10–F19)

impulse and habit disorders involving sexual behaviour (F65.-)

F63.0 Pathological gambling

The disorder consists of frequent, repeated episodes of gambling that dominate the patient’s life to the detriment of social, occupational, material and family values and commitments.

Compulsive gambling

Excl.: excessive gambling by manic patients (F30.-) gambling and betting NOS (Z72.6)

gambling in dissocial personality disorder (F60.2)

F63.1 Pathological fire-setting [pyromania]

Disorder characterized by multiple acts of, or attempts at, setting fire to property or other objects, without apparent motive, and by a persistent preoccupation with subjects related to fire and burning. This behaviour is often associated with feelings of increasing tension before the act, and intense excitement immediately afterwards.

Excl.: fire-setting (by)(in):

• adult with dissocial personality disorder (F60.2)

• alcohol or psychoactive substance intoxication (F10–F19, with common fourth character .0)

• as the reason for observation for suspected mental disorder (Z03.2)

• conduct disorders (F91.-)

• organic mental disorders (F00–F09)

• schizophrenia (F20.-)

F63.2 Pathological stealing [kleptomania]

Disorder characterized by repeated failure to resist impulses to steal objects that are not acquired for personal use or monetary gain. The objects may instead be discarded, given away or hoarded. This behaviour is usually accompanied by     an increasing sense of tension before, and a sense of gratification during and immediately after, the act.

Excl.: depressive disorder with stealing (F31–F33) organic mental disorders (F00–F09)

shoplifting as the reason for observation for suspected mental disorder (Z03.2)

F63.3 Trichotillomania

A disorder characterized by noticeable hairloss due to a recurrent failure to resist impulses to pull out hairs. The hair-pulling is usually preceded by mounting tension and is followed by a sense of relief or gratification. This diagnosis should not be made if there is a pre-existing inflammation of the skin, or if the hair-pulling is in response to a delusion or a hallucination.

Excl.: stereotyped movement disorder with hair-plucking (F98.4)

F63.8 Other habit and impulse disorders

Other kinds of persistently repeated maladaptive behaviour that are not secondary to a recognized psychiatric syndrome, and in which it appears that the patient is repeatedly failing to resist impulses to carry out the behaviour. There is a prodromal period of tension with a feeling of release at the time of the act.

Intermittent explosive disorder

F63.9 Habit and impulse disorder, unspecified

  F64 Gender identity disorders

F64.0 Transsexualism

Adesire to live and be accepted as a member of the opposite sex, usually accompanied by a sense of discomfort with, or inappropriateness of, one’s anatomic sex, and a wish to have surgery and hormonal treatment to make one’s body as congruent as possible with one’s preferred sex.

F64.1 Dual-role transvestism

The wearing of clothes of the opposite sex for part of the individual’s existence, in order to enjoy the temporary experience of membership of the opposite sex,  but without any desire for a more permanent sex change or associated surgical reassignment, and without sexual excitement accompanying the cross-dressing.

Gender identity disorder of adolescence or adulthood, nontranssexual type

Excl.: fetishistic transvestism (F65.1)

 

F64.2 Gender identity disorder of childhood

A disorder, usually first manifest during early childhood (and always well before puberty), characterized by a persistent and intense distress about assigned sex, together with a desire to be (or insistence that one is) of the other sex. There is     a persistent preoccupation with the dress and activities of the opposite sex and repudiation of the individual’s own sex. The diagnosis requires a profound disturbance of the normal gender identity; mere tomboyishness in girls or girlish behaviour in boys is not sufficient. Gender identity disorders in individuals who have reached or are entering puberty should not be classified here but in F66.-.

Excl.: egodystonic sexual orientation (F66.1) sexual maturation disorder (F66.0)

F64.8 Other gender identity disorders F64.9 Gender identity disorder, unspecified

Gender role disorder NOS

  F65 Disorders of sexual preference

Incl.: paraphilias

F65.0 Fetishism

Reliance on some non-living object as a stimulus for sexual arousal and sexual gratification. Many fetishes are extensions of the human body, such as articles of clothing or footwear. Other common examples are characterized by some particular texture such as rubber, plastic or leather. Fetish objects vary in their importance  to the individual. In some cases they simply serve to enhance sexual excitement achieved in ordinary ways (e.g. having the partner wear a particular garment).

F65.1 Fetishistic transvestism

The wearing of clothes of the opposite sex principally to obtain sexual excitement and to create the appearance of a person of the opposite sex. Fetishistic transvestism is distinguished from transsexual transvestism by its clear association with sexual arousal and the strong desire to remove the clothing once orgasm occurs and sexual arousal declines. It can occur as an earlier phase in the development of transsexualism.

Transvestic fetishism

F65.2 Exhibitionism

A recurrent or persistent tendency to expose the genitalia to strangers (usually of the opposite sex) or to people in public places, without inviting or intending closer contact. There is usually, but not invariably, sexual excitement at the time of the exposure and the act is commonly followed by masturbation.

F65.3 Voyeurism

A recurrent or persistent tendency to look at people engaging in sexual or intimate behaviour such as undressing. This is carried out without the observed people being aware, and usually leads to sexual excitement and masturbation.

F65.4 Paedophilia

A sexual preference for children, boys or girls or both, usually of prepubertal or early pubertal age.

 

F65.5 Sadomasochism

A preference for sexual activity that involves the infliction of pain or humiliation, or bondage. If the subject prefers to be the recipient of such stimulation, this is called masochism; if the provider, sadism. Often an individual obtains sexual excitement from both sadistic and masochistic activities.

Masochism Sadism

F65.6 Multiple disorders of sexual preference

Sometimes more than one abnormal sexual preference occurs in one person and there is none of first rank. The most common combination is fetishism, transvestism and sadomasochism.

F65.8 Other disorders of sexual preference

A variety of other patterns of sexual preference and activity, including making obscene telephone calls, rubbing up against people for sexual stimulation in crowded public places, sexual activity with animals, and use of strangulation or anoxia for intensifying sexual excitement.

Frotteurism Necrophilia

F65.9 Disorder of sexual preference, unspecified

Sexual deviation NOS

  F66 Psychological and behavioural disorders associated with sexual development and orientation

Note: Sexual orientation by itself is not to be regarded as a disorder.

F66.0 Sexual maturation disorder

The patient suffers from uncertainty about his or her gender identity or sexual orientation, which causes anxiety or depression. Most commonly this occurs in adolescents who are not certain whether they are homosexual, heterosexual or bisexual in orientation, or in individuals who, after a period of apparently stable sexual orientation (often within a longstanding relationship), find that their sexual orientation is changing.

F66.1 Egodystonic sexual orientation

The gender identity or sexual preference (heterosexual, homosexual, bisexual or prepubertal) is not in doubt, but the individual wishes it were different because   of associated psychological and behavioural disorders, and may seek treatment in order to change it.

F66.2 Sexual relationship disorder

The gender identity or sexual orientation (heterosexual, homosexual or bisexual) is responsible for difficulties in forming or maintaining a relationship with a sexual partner.

F66.8 Other psychosexual development disorders F66.9 Psychosexual development disorder, unspecified

 

  F68 Other disorders of adult personality and behaviour

F68.0 Elaboration of physical symptoms for psychological reasons

Physical symptoms compatible with and originally due to a confirmed physical disorder, disease or disability become exaggerated or prolonged, due to the psychological state of the patient. The patient is commonly distressed by this pain or disability, and is often preoccupied with worries, which may be justified, of the possibility of prolonged or progressive disability or pain.

Compensation neurosis

F68.1 Intentional production or feigning of symptoms or disabilities, either physical or psychological [factitious disorder]

The patient feigns symptoms repeatedly for no obvious reason and may even inflict self-harm in order to produce symptoms or signs. The motivation is obscure and presumably internal with the aim of adopting the sick role. The disorder is often combined with marked disorders of personality and relationships.

Hospital hopper syndrome Münchausen syndrome Peregrinating patient

Excl.: factitial dermatitis (L98.1)

person feigning illness (with obvious motivation) (Z76.5)

F68.8 Other specified disorders of adult personality and behaviour

Character disorder NOS Relationship disorder NOS

  F69 Unspecified disorder of adult personality and behaviour

Mental retardation (F70–F79)

A condition of arrested or incomplete development of the mind, which is especially characterized by impairment of skills manifested during the developmental period, skills which contribute to the overall level of intelligence, i.e. cognitive, language, motor and social abilities. Retardation can occur with or without any other mental or physical condition.

Degrees of mental retardation are conventionally estimated by standardized intelligence tests. These can be supplemented by scales assessing social adaptation in a given environment. These measures provide an approximate indication of the degree of mental retardation. The diagnosis will also depend on the overall assessment of intellectual functioning by a skilled diagnostician.

Intellectual abilities and social adaptation may change over time, and, however poor, may improve as a result of training and rehabilitation. Diagnosis should be based on the current levels of functioning.

Use additional code, if desired, to identify associated conditions such as autism, other developmental disorders, epilepsy, conduct disorders or severe physical handicap.

 

The following fourth-character subdivisions are for use with categories F70–F79 to identify the extent of impairment of behaviour:

.0 With the statement of no, or minimal, impairment of behaviour

.1 Significant impairment of behaviour requiring attention or treatment

.8 Other impairments of behaviour

.9 Without mention of impairment of behaviour

  F70 Mild mental retardation

[See before F70 for subdivisions]

Approximate IQ range of 50 to 69 (in adults, mental age from 9 to under 12 years). Likely to result in some learning difficulties in school. Many adults will be able to work and maintain good social relationships and contribute to society.

Incl.: feeble-mindedness

mild mental subnormality

  F71 Moderate mental retardation

[See before F70 for subdivisions]

Approximate IQ range of 35 to 49 (in adults, mental age from 6 to under 9 years). Likely to result in marked developmental delays in  childhood  but  most  can learn to develop some degree of independence in self-care and acquire adequate communication and academic skills. Adults will need varying degrees of support to live and work in the community.

Incl.: moderate mental subnormality

  F72 Severe mental retardation

[See before F70 for subdivisions]

Approximate IQ range of 20 to 34 (in adults, mental age from 3 to under 6 years). Likely to result in continuous need of support.

Incl.: severe mental subnormality

  F73 Profound mental retardation

[See before F70 for subdivisions]

IQ under 20 (in adults, mental age below 3 years). Results in severe limitation in self-care, continence, communication and mobility.

Incl.: profound mental subnormality

  F78 Other mental retardation

[See before F70 for subdivisions]

  F79 Unspecified mental retardation

[See before F70 for subdivisions]

Incl.: mental:

• deficiency NOS

• subnormality NOS

 

Disorders of psychological development (F80–F89)

The disorders included in this block have in common: (a) onset invariably during infancy or childhood; (b) impairment or delay in development of functions that are strongly related to biological maturation of the central nervous system; and (c) a steady course without remissions and relapses. In most cases, the functions affected include language, visuo-spatial skills and motor coordination. Usually, the delay or impairment has been present from as early as it could be detected reliably and will diminish progressively as the child grows older, although milder deficits often remain in adult life.

  F80 Specific developmental disorders of speech and language

Disorders in which normal patterns of language acquisition are disturbed from  the early stages of development. The conditions are not directly attributable to neurological or speech-mechanism abnormalities, sensory impairments, mental retardation or environmental factors. Specific developmental disorders of speech and language are often followed by associated problems, such as difficulties in reading and spelling, abnormalities in interpersonal relationships, and emotional and behavioural disorders.

F80.0 Specific speech articulation disorder

A specific developmental disorder in which the child’s use of speech sounds is below the appropriate level for its mental age, but in which there is a normal level of language skills.

Developmental:

• phonological disorder

• speech articulation disorder Dyslalia

Functional speech articulation disorder Lalling

Excl.: speech articulation impairment (due to):

• aphasia NOS (R47.0)

• apraxia (R48.2)

• hearing loss (H90–H91)

• mental retardation (F70–F79)

• with language developmental disorder:

– expressive (F80.1)

– receptive (F80.2)

F80.1 Expressive language disorder

A specific developmental disorder in which the child’s ability to use expressive spoken language is markedly below the appropriate level for its mental age, but in which language comprehension is within normal limits. There may or may not be abnormalities in articulation.

Developmental dysphasia or aphasia, expressive type

 

Excl.: acquired aphasia with epilepsy [Landau–Kleffner] (F80.3) dysphasia and aphasia:

• NOS (R47.0)

• developmental, receptive type (F80.2) elective mutism (F94.0)

mental retardation (F70–F79)

pervasive developmental disorders (F84.-)

F80.2 Receptive language disorder

A specific developmental disorder in which the child’s understanding of language is below the appropriate level for its mental age. In virtually all cases expressive language will also be markedly affected and abnormalities in word-sound production are common.

Congenital auditory imperception Developmental:

• dysphasia or aphasia, receptive type

• Wernicke aphasia Word deafness

Excl.: acquired aphasia with epilepsy [Landau–Kleffner] (F80.3) autism (F84.0–F84.1)

dysphasia and aphasia:

• NOS (R47.0)

• developmental, expressive type (F80.1) elective mutism (F94.0)

language delay due to deafness (H90–H91) mental retardation (F70–F79)

F80.3 Acquired aphasia with epilepsy [Landau–Kleffner]

A disorder in which the child, having previously made normal progress in language development, loses both receptive and expressive language skills but retains general intelligence; the onset of the disorder is accompanied by paroxysmal abnormalities on the EEG, and, in the majority of cases, also by epileptic seizures. Usually the onset is between the ages of three and seven years, with skills being lost over days or weeks. The temporal association between the onset of seizures and loss of language is variable, with one preceding the other (either way round) by a few months to two years. An inflammatory encephalitic process has been suggested as a possible cause of this disorder. About two thirds of patients are left with a more or less severe receptive language deficit.

Excl.: aphasia (due to):

• NOS (R47.0)

• autism (F84.0–F84.1)

• disintegrative disorders of childhood (F84.2–F84.3)

F80.8 Other developmental disorders of speech and language

Lisping

F80.9 Developmental disorder of speech and language, unspecified

Language disorder NOS

 

  F81 Specific developmental disorders of scholastic skills

Disorders in which the normal patterns of skill acquisition are disturbed from    the early stages of development. This is not simply a consequence of a lack of opportunity to learn, it is not solely a result of mental retardation, and it is not due to any form of acquired brain trauma or disease.

F81.0 Specific reading disorder

The main feature is a specific and significant impairment in the development of reading skills that is not solely accounted for by mental age, visual acuity problems or inadequate schooling. Reading comprehension skill, reading word recognition, oral reading skill and performance of tasks requiring reading may all be affected. Spelling difficulties are frequently associated with specific reading disorder and often remain into adolescence, even after some progress in reading has been made. Specific developmental disorders of reading are commonly preceded by a history of disorders in speech or language development. Associated emotional and behavioural disturbances are common during the school age period.

‘Backward reading’ Developmental dyslexia Specific reading retardation

Excl.: alexia NOS (R48.0) dyslexia NOS (R48.0)

reading difficulties secondary to emotional disorders (F93.-)

F81.1 Specific spelling disorder

The main feature is a specific and significant impairment in the development of spelling skills, in the absence of a history of specific reading disorder, which is not solely accounted for by low mental age, visual acuity problems or inadequate schooling. The abilities to spell orally and to write out words correctly are both affected.

Specific spelling retardation (without reading disorder)

Excl.: agraphia NOS (R48.8) spelling difficulties:

• associated with a reading disorder (F81.0)

• due to inadequate teaching (Z55.8)

F81.2 Specific disorder of arithmetical skills

Involves a specific impairment in arithmetical skills that is not solely explicable on the basis of general mental retardation or of inadequate  schooling.  The  deficit concerns mastery of basic computational skills of addition, subtraction, multiplication and division, rather than of the more abstract mathematical skills involved in algebra, trigonometry, geometry or calculus.

Developmental:

• acalculia

• arithmetical disorder

• Gerstmann’s syndrome

Excl.: acalculia NOS (R48.8) arithmetical difficulties:

• associated with a reading or spelling disorder (F81.3)

• due to inadequate teaching (Z55.8)

 

F81.3 Mixed disorder of scholastic skills

An ill-defined residual category of disorders in which both arithmetical and reading or spelling skills are significantly impaired, but in which the disorder is not solely explicable in terms of general mental retardation or of inadequate schooling. It should be used for disorders meeting the criteria for both F81.2 and either F81.0 or F81.1.

Excl.: specific:

• disorder of arithmetical skills (F81.2)

• reading disorder (F81.0)

• spelling disorder (F81.1)

F81.8 Other developmental disorders of scholastic skills

Developmental expressive writing disorder

F81.9 Developmental disorder of scholastic skills, unspecified

Knowledge acquisition disability NOS Learning:

• disability NOS

• disorder NOS

  F82 Specific developmental disorder of motor function

A disorder in which the main feature is a serious impairment in the development of motor coordination that is not solely explicable in terms of general intellectual retardation or of any specific congenital or acquired neurological disorder. Nevertheless, in most cases, a careful clinical examination shows marked neurodevelopmental immaturities such as choreiform movements of unsupported limbs or mirror movements and other associated motor features, as well as signs of impaired fine and gross motor coordination.

Incl.: clumsy child syndrome developmental:

• coordination disorder

• dyspraxia

Excl.: abnormalities of gait and mobility (R26.-) lack of coordination (R27.-)

lack of coordination

• secondary to mental retardation (F70–F79)

  F83 Mixed specific developmental disorders

A residual category for disorders in which there is some admixture of specific developmental disorders of speech and language, of scholastic skills, and of motor function, but in which none predominates sufficiently to constitute the prime diagnosis. This mixed category should be used only when there is a major overlap between each of these specific developmental disorders. The disorders are usually, but not always, associated with some degree of general impairment of cognitive functions. Thus, the category should be used when there are dysfunctions meeting the criteria for two or more of F80.-, F81.- and F82.

  F84 Pervasive developmental disorders

A group of disorders characterized by qualitative abnormalities in reciprocal social interactions and in patterns of communication, and by a restricted, stereotyped, repetitive repertoire of interests and activities. These qualitative abnormalities are a pervasive feature of the individual’s functioning in all situations.

Use additional code, if desired, to identify any associated medical condition and mental retardation.

F84.0 Childhood autism

A type of pervasive developmental disorder that is defined by: (a) the presence of abnormal or impaired development that is manifest before the age of three years, and (b) the characteristic type of abnormal functioning in all the three areas of psychopathology: reciprocal social interaction, communication and restricted, stereotyped, repetitive behaviour. In addition to these specific diagnostic features, a range of other nonspecific problems are common, such as phobias, sleeping and eating disturbances, temper tantrums and (self-directed) aggression.

Autistic disorder Infantile:

• autism

• psychosis Kanner syndrome

Excl.: autistic psychopathy (F84.5)

F84.1 Atypical autism

A type of pervasive developmental disorder that differs from childhood autism, either in age of onset or in failing to fulfil all three sets of diagnostic criteria. This subcategory should be used when there is abnormal and impaired development that is present only after age three years, and a lack of sufficient demonstrable abnormalities in one or two of the three areas of psychopathology required for  the diagnosis of autism (namely, reciprocal social interactions, communication and restricted, stereotyped, repetitive behaviour) in spite of characteristic abnormalities in the other area(s). Atypical autism arises most often in profoundly retarded individuals and in individuals with a severe specific developmental disorder of receptive language.

Atypical childhood psychosis

Mental retardation with autistic features

Use additional code (F70–F79), if desired, to identify mental retardation.

F84.2 Rett syndrome

Acondition, so far found only in girls, in which apparently normal early development is followed by partial or complete loss of speech and of skills in locomotion and use of hands, together with deceleration in head growth, usually with an onset between seven and 24 months of age. Loss of purposive hand movements, hand-wringing stereotypies, and hyperventilation are characteristic. Social and play development are arrested but social interest tends to be maintained. Trunk ataxia and apraxia start to develop by age four years and choreoathetoid movements frequently follow. Severe mental retardation almost invariably results.

 

F84.3 Other childhood disintegrative disorder

A type of pervasive developmental disorder that is defined by a period of entirely normal development before the onset of the disorder, followed by a definite loss of previously acquired skills in several areas of development over the course of    a few months. Typically, this is accompanied by a general loss of interest in the environment, by stereotyped, repetitive motor mannerisms, and by autistic-like abnormalities in social interaction and communication. In some cases the disorder can be shown to be due to some associated encephalopathy but the diagnosis should be made on the behavioural features.

Dementia infantilis Disintegrative psychosis Heller syndrome Symbiotic psychosis

Use additional code, if desired, to identify any associated neurological condition.

Excl.: Rett syndrome (F84.2)

F84.4 Overactive disorder associated with mental retardation and stereotyped movements

An ill-defined disorder of uncertain nosological validity. The category is designed to include a group of children with severe mental retardation (IQ below 35) who show major problems in hyperactivity and in attention, as well as stereotyped behaviours. They tend not to benefit from stimulant drugs (unlike those with an IQ in the normal range) and may exhibit a severe dysphoric reaction (sometimes with psychomotor retardation) when given stimulants. In adolescence, the overactivity tends to be replaced by underactivity (a pattern that is not usual in hyperkinetic children with normal intelligence). This syndrome is also often associated with a variety of developmental delays, either specific or global. The extent to which the behavioural pattern is a function of low IQ or of organic brain damage is not known.

F84.5 Asperger syndrome

A disorder of uncertain nosological validity, characterized by the same type of qualitative abnormalities of reciprocal social interaction that typify autism, together with a restricted, stereotyped, repetitive repertoire of interests and activities. It differs from autism primarily in the fact that there is no general delay or retardation in language or in cognitive development. This disorder is often associated with marked clumsiness. There is a strong tendency for the abnormalities to persist into adolescence and adult life. Psychotic episodes occasionally occur in early adult life.

Autistic psychopathy

Schizoid disorder of childhood

F84.8 Other pervasive developmental disorders F84.9 Pervasive developmental disorder, unspecified

  F88 Other disorders of psychological development

Incl.: developmental agnosia

  F89 Unspecified disorder of psychological development

Incl.: developmental disorder NOS

 

Behavioural and emotional disorders with onset usually occurring in childhood and adolescence

(F90–F98)

  F90 Hyperkinetic disorders

A group of disorders characterized by an early onset (usually in the first five years of life), lack of persistence in activities that require cognitive involvement, and a tendency to move from one activity to another without completing any one, together with disorganized, ill-regulated, and excessive activity. Several other abnormalities may be associated. Hyperkinetic children are often reckless, impulsive and prone to accidents, and find themselves in disciplinary trouble because of unthinking breaches of rules rather than deliberate defiance. Their relationships with adults are often socially disinhibited, with a lack of normal caution and reserve. They are unpopular with other children and may become isolated. Impairment of cognitive functions is common, and specific delays in motor and language development are disproportionately frequent. Secondary complications include dissocial behaviour and low self-esteem.

Excl.: anxiety disorders (F41.-)

mood [affective] disorders (F30–F39) pervasive developmental disorders (F84.-) schizophrenia (F20.-)

F90.0 Disturbance of activity and attention

Attention deficit:

• disorder with hyperactivity

• hyperactivity disorder

• syndrome with hyperactivity

Excl.: hyperkinetic disorder associated with conduct disorder (F90.1)

F90.1 Hyperkinetic conduct disorder

Hyperkinetic disorder associated with conduct disorder

F90.8 Other hyperkinetic disorders F90.9 Hyperkinetic disorder, unspecified

Hyperkinetic reaction of childhood or adolescence NOS

Hyperkinetic syndrome NOS

  F91 Conduct disorders

Disorders characterized by a repetitive and persistent pattern of dissocial, aggressive or defiant conduct. Such behaviour should amount to major violations of age- appropriate social expectations; it should therefore be more severe than ordinary childish mischief or adolescent rebelliousness and should imply an enduring pattern of behaviour (six months or longer). Features of conduct disorder can   also be symptomatic of other psychiatric conditions, in which case the underlying diagnosis should be preferred.

 

Examples of the behaviours on which the diagnosis is based include excessive levels of fighting or bullying, cruelty to other people or animals, severe destructiveness to property, fire-setting, stealing, repeated lying, truancy from school and running away from home, unusually frequent and severe temper tantrums, and disobedience. Any one of these behaviours, if marked, is sufficient for the diagnosis, but isolated dissocial acts are not.

Excl.: mood [affective] (F30–F39)

pervasive developmental disorders (F84.-) schizophrenia (F20.-)

when associated with:

• emotional disorders (F92.-)

• hyperkinetic disorders (F90.1)

F91.0 Conduct disorder confined to the family context

Conduct disorder involving dissocial or aggressive behaviour (and not merely oppositional, defiant, disruptive behaviour), in which the abnormal behaviour is entirely, or almost entirely, confined to the home and to interactions with members of the nuclear family or immediate household. The disorder requires that the overall criteria for F91.- be met; even severely disturbed parent–child relationships are not of themselves sufficient for diagnosis.

F91.1 Unsocialized conduct disorder

Disorder characterized by the combination of persistent dissocial or aggressive behaviour (meeting the overall criteria for F91.- and not merely comprising oppositional, defiant, disruptive behaviour) with significant pervasive abnormalities in the individual’s relationships with other children.

Conduct disorder, solitary aggressive type Unsocialized aggressive disorder

F91.2 Socialized conduct disorder

Disorder involving persistent dissocial or aggressive behaviour (meeting the overall criteria for F91.- and not merely comprising oppositional, defiant, disruptive behaviour) occurring in individuals who are generally well integrated into their peer group.

Conduct disorder, group type Group delinquency

Offences in the context of gang membership Stealing in company with others

Truancy from school

F91.3 Oppositional defiant disorder

Conduct disorder, usually occurring in younger children, primarily characterized by markedly defiant, disobedient, disruptive behaviour that does not include delinquent acts or the more extreme forms of aggressive or dissocial behaviour. The disorder requires that the overall criteria for F91.- be met; even severely mischievous or naughty behaviour is not in itself sufficient for diagnosis. Caution should be employed before using this category, especially with older children, because clinically significant conduct disorder will usually be accompanied by dissocial or aggressive behaviour that goes beyond mere defiance, disobedience or disruptiveness.

 

F91.8 Other conduct disorders F91.9 Conduct disorder, unspecified

Childhood:

• behavioural disorder NOS

• conduct disorder NOS

  F92 Mixed disorders of conduct and emotions

A group of disorders characterized by the combination of persistently aggressive, dissocial or defiant behaviour with overt and marked symptoms of depression, anxiety or other emotional upsets. The criteria for both conduct disorders of childhood (F9l.-) and emotional disorders of childhood (F93.-) or an adult-type neurotic diagnosis (F40–F48) or a mood disorder (F30–F39) must be met.

F92.0 Depressive conduct disorder

This category requires the combination of conduct disorder (F91.-) with persistent and marked depression of mood (F32.-), as demonstrated by symptoms such as excessive misery, loss of interest and pleasure in usual activities, self-blame and hopelessness; disturbances of sleep or appetite may also be present.

Conduct disorder in F91.- associated with depressive disorder in F32.-

F92.8 Other mixed disorders of conduct and emotions

This category requires the combination of conduct disorder (F91.-) with persistent and marked emotional symptoms such as anxiety, obsessions or compulsions, depersonalization or derealization, phobias or hypochondriasis.

Conduct disorder in F91.- associated with:

• emotional disorder in F93.-

• neurotic disorder in F40–F48

F92.9 Mixed disorder of conduct and emotions, unspecified

  F93 Emotional disorders with onset specific to childhood

Mainly exaggerations of normal developmental trends rather than phenomena that are qualitatively abnormal in themselves. Developmental appropriateness is used as the key diagnostic feature in defining the difference between these emotional disorders, with onset specific to childhood, and the neurotic disorders (F40–F48).

Excl.: when associated with conduct disorder (F92.-)

F93.0 Separation anxiety disorder of childhood

Should be diagnosed when fear of separation constitutes the focus of the anxiety and when such anxiety first arose during the early years of childhood. It is differentiated from normal separation anxiety when it is of a degree (severity) that is statistically unusual (including an abnormal persistence beyond the usual age period), and when it is associated with significant problems in social functioning.

Excl.: mood [affective] disorders (F30–F39) neurotic disorders (F40–F48)

phobic anxiety disorder of childhood (F93.1) social anxiety disorder of childhood (F93.2)

 

F93.1 Phobic anxiety disorder of childhood

Fears in childhood that show a marked developmental-phase specificity  and  arise (to some extent) in a majority of children, but that are abnormal in degree. Other fears that arise in childhood but that are not a normal part of psychosocial development (for example agoraphobia) should be coded under the appropriate category in section F40–F48.

Excl.: generalized anxiety disorder (F41.1)

F93.2 Social anxiety disorder of childhood

In this disorder there is a wariness of strangers and social apprehension or anxiety when encountering new, strange or socially threatening situations. This category should be used only where such fears arise during the early years, and are both unusual in degree and accompanied by problems in social functioning.

Avoidant disorder of childhood or adolescence

F93.3 Sibling rivalry disorder

Some degree of emotional disturbance usually following the birth of an immediately younger sibling is shown by a majority of young children. A sibling rivalry disorder should be diagnosed only if the degree or persistence of the disturbance is both statistically unusual and associated with abnormalities of social interaction.

Sibling jealousy

F93.8 Other childhood emotional disorders

Identity disorder Overanxious disorder

Excl.: gender identity disorder of childhood (F64.2)

F93.9 Childhood emotional disorder, unspecified

  F94 Disorders of social functioning with onset specific to childhood and adolescence

A somewhat heterogeneous group of disorders that have in common abnormalities in social functioning that begin during the developmental period, but that (unlike the pervasive developmental disorders) are not primarily characterized by an apparently constitutional social incapacity or deficit that pervades all areas of functioning. In many instances, serious environmental distortions or privations probably play a crucial role in etiology.

F94.0 Elective mutism

Characterized by a marked, emotionally determined selectivity in speaking, such that the child demonstrates a language competence in some situations but fails to speak in other (definable) situations. The disorder is usually associated with marked personality features involving social anxiety, withdrawal, sensitivity or resistance.

Selective mutism

Excl.: pervasive developmental disorders (F84.-) schizophrenia (F20.-)

specific developmental disorders of speech and language (F80.-) transient mutism as part of separation anxiety in young children (F93.0)

 

F94.1 Reactive attachment disorder of childhood

Starts in the first five years of life and is characterized by persistent abnormalities in the child’s pattern of social relationships that are associated with emotional disturbance and are reactive to changes in environmental circumstances (e.g. fearfulness and hypervigilance, poor social interaction with peers, aggression towards self and others, misery, and growth failure in some cases). The syndrome probably occurs as a direct result of severe parental neglect, abuse or serious mishandling.

Use additional code, if desired, to identify any associated failure to thrive or growth retardation.

Excl.: Asperger syndrome (F84.5)

disinhibited attachment disorder of childhood (F94.2) maltreatment syndromes (T74.-)

normal variation in pattern of selective attachment

sexual or physical abuse in childhood, resulting in psychosocial problems (Z61.4–Z61.6)

F94.2 Disinhibited attachment disorder of childhood

A particular pattern of abnormal social functioning that arises during the first five years of life and that tends to persist despite marked changes in environmental circumstances, e.g. diffuse, nonselectively focused attachment behaviour, attention-seeking and indiscriminately friendly behaviour, poorly modulated peer interactions; depending on circumstances, there may also be associated emotional or behavioural disturbance.

Affectionless psychopathy Institutional syndrome

Excl.: Asperger syndrome (F84.5) hospitalism in children (F43.2) hyperkinetic disorders (F90.-)

reactive attachment disorder of childhood (F94.1) F94.8 Other childhood disorders of social functioning F94.9 Childhood disorder of social functioning, unspecified

  F95 Tic disorders

Syndromes in which the predominant manifestation is some form of tic. A tic is an involuntary, rapid, recurrent, nonrhythmic motor movement (usually involving circumscribed muscle groups) or vocal production that is of sudden onset and  that serves no apparent purpose. Tics tend to be experienced as irresistible but usually they can be suppressed for varying periods of time, are exacerbated by stress, and disappear during sleep. Common simple motor tics include only eye- blinking, neck-jerking, shoulder-shrugging and facial grimacing. Common simple vocal tics include throat-clearing, barking, sniffing and hissing. Common complex tics include hitting oneself, jumping and hopping. Common complex vocal tics include the repetition of particular words, and sometimes the use of socially unacceptable (often obscene) words (coprolalia) and the repetition of one’s own sounds or words (palilalia).

 

F95.0 Transient tic disorder

Meets the general criteria for a tic disorder but the tics do not persist longer than 12 months. The tics usually take the form of eye-blinking, facial grimacing or head- jerking.

F95.1 Chronic motor or vocal tic disorder

Meets the general criteria for a tic disorder, in which there are motor or vocal tics (but not both), that may be either single or multiple (but usually multiple) and last for more than a year.

F95.2 Combined vocal and multiple motor tic disorder [Tourette]

A form of tic disorder in which there are, or have been, multiple motor tics and one or more vocal tics, although these need not have occurred concurrently. The disorder usually worsens during adolescence and tends to persist into adult life. The vocal tics are often multiple, with explosive repetitive vocalizations, throat-clearing and grunting, and there may be the use of obscene words or phrases. Sometimes there is associated gestural echopraxia, which may also be of an obscene nature (copropraxia).

F95.8 Other tic  disorders F95.9 Tic disorder, unspecified

Tic NOS

  F98 Other behavioural and emotional disorders with onset usually occurring in childhood and adolescence

A heterogeneous group of disorders that share the characteristic of an onset in childhood but otherwise differ in many respects. Some of the conditions represent well-defined syndromes but others are no more than symptom complexes that need inclusion because of their frequency and association with psychosocial problems, and because they cannot be incorporated into other syndromes.

Excl.: breath-holding spells (R06.8)

gender identity disorder of childhood (F64.2) Kleine–Levin syndrome (G47.8)

obsessive-compulsive disorder (F42.-)

sleep disorders due to emotional causes (F51.-)

F98.0 Nonorganic enuresis

A disorder characterized by involuntary voiding of urine, by day and by night, that is abnormal in relation to the individual’s mental age, and that is not a consequence of a lack of bladder control due to any neurological disorder, to epileptic attacks, or to any structural abnormality of the urinary tract. The enuresis may have been present from birth or it may have arisen following a period of acquired bladder control. The enuresis may or may not be associated with a more widespread emotional or behavioural disorder.

Enuresis (primary)(secondary) of nonorganic origin Functional enuresis

Psychogenic enuresis

Urinary incontinence of nonorganic origin

Excl.: enuresis NOS (R32)

 

F98.1 Nonorganic encopresis

Repeated, voluntary or involuntary passage of faeces, usually of normal or near- normal consistency, in places not appropriate for that purpose in the individual’s own sociocultural setting. The condition may represent an abnormal continuation of normal infantile incontinence, it may involve a loss of continence following the acquisition of bowel control, or it may involve the deliberate deposition of faeces in inappropriate places in spite of normal physiological bowel control. The condition may occur as a monosymptomatic disorder, or it may form part of a wider disorder, especially an emotional disorder (F93.-) or a conduct disorder (F91.-).

Functional encopresis

Incontinence of faeces of nonorganic origin Psychogenic encopresis

Use additional code, if desired, to identify the cause of any coexisting constipation.

Excl.: encopresis NOS (R15)

F98.2 Feeding disorder of infancy and childhood

A feeding disorder of varying manifestations, usually specific to infancy and early childhood. It generally involves food refusal and extreme faddiness in the presence of an adequate food supply,  a reasonably competent caregiver, and the absence  of organic disease. There may or may not be associated rumination (repeated regurgitation without nausea or gastrointestinal illness).

Rumination disorder of infancy

Excl.: anorexia nervosa and other eating disorders (F50.-) feeding:

• difficulties and mismanagement (R63.3)

• problems of newborn (P92.-)

pica of infancy or childhood (F98.3)

F98.3 Pica of infancy and childhood

Persistent eating of non-nutritive substances (such as soil, paint chippings, etc.). It may occur as one of many symptoms that are part of a more widespread psychiatric disorder (such as autism), or as a relatively isolated psychopathological behaviour; only the latter is classified here. The phenomenon is most common in mentally retarded children and, if mental retardation is also present, F70–F79 should be selected as the main diagnosis.

 

F98.4 Stereotyped movement disorders

Voluntary, repetitive, stereotyped, nonfunctional (and often rhythmic) movements that do not form part of any recognized psychiatric or neurological condition. When such movements occur as symptoms of some other disorder, only the overall disorder should be recorded. The movements that are of a non-self-injurious variety include: body-rocking, head-rocking, hair-plucking, hair-twisting, finger-flicking mannerisms, and hand-flapping. Stereotyped self-injurious behaviour includes repetitive head- banging, face-slapping, eye-poking and biting of hands, lips or other body parts. All the stereotyped movement disorders occur most frequently in association with mental retardation (when this is the case, both should be recorded). If eye-poking occurs in a child with visual impairment, both should be coded: eye-poking under this category and the visual condition under the appropriate somatic disorder code.

Stereotype/habit disorder

Excl.: abnormal involuntary movements (R25.-) movement disorders of organic origin (G20–G25) nail-biting (F98.8)

nose-picking (F98.8)

stereotypies that are part of a broader psychiatric condition (F00–F95) thumb-sucking (F98.8)

tic disorders (F95.-) trichotillomania (F63.3)

F98.5 Stuttering [stammering]

Speech that is characterized by frequent repetition or prolongation of sounds or syllables or words, or by frequent hesitations or pauses that disrupt the rhythmic flow of speech. It should be classified as a disorder only if its severity is such as to markedly disturb the fluency of speech.

Excl.: cluttering (F98.6) tic disorders (F95.-)

F98.6 Cluttering

A rapid rate of speech with breakdown in fluency, but no repetitions or hesitations, of a severity to give rise to diminished speech intelligibility. Speech is erratic and dysrhythmic, with rapid jerky spurts that usually involve faulty phrasing patterns.

Excl.:  stuttering (F98.5) tic disorders (F95.-)

F98.8 Other specified behavioural and emotional disorders with onset usually occurring in childhood and adolescence Attention deficit disorder without hyperactivity

Excessive masturbation Nail-biting

Nose-picking Thumb-sucking

F98.9 Unspecified behavioural and emotional disorders with onset usually occurring in childhood and adolescence

 

Unspecified mental disorder (F99)

  F99 Mental disorder, not otherwise specified

Incl.: mental illness NOS

Excl.: organic mental disorder NOS (F06.9)

CHAPTER VI

Diseases of the nervous system (G00–G99)

Excl.: certain conditions originating in the perinatal period (P00–P96) certain infectious and parasitic diseases (A00–B99)

complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90)

injury, poisoning and certain other consequences of external causes (S00–T98) neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

G00–G09 Inflammatory diseases of the central nervous system

G10–G14 Systemic atrophies primarily affecting the central nervous system G20–G26 Extrapyramidal and movement disorders

G30–G32 Other degenerative diseases of the nervous system G35–G37 Demyelinating diseases of the central nervous system G40–G47 Episodic and paroxysmal disorders

G50–G59 Nerve, nerve root and plexus disorders

G60–G64 Polyneuropathies and other disorders of the peripheral nervous system G70–G73 Diseases of myoneural junction and muscle

G80–G83 Cerebral palsy and other paralytic syndromes G90–G99 Other disorders of the nervous system

Asterisk categories for this chapter are provided as follows:

G01* Meningitis in bacterial diseases classified elsewhere

G02* Meningitis in other infectious and parasitic diseases classified elsewhere G05* Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere G07* Intracranial and intraspinal abscess and granuloma in diseases classified

elsewhere

G13* Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere

G22* Parkinsonism in diseases classified elsewhere

G26* Extrapyramidal and movement disorders in diseases classified elsewhere G32* Other degenerative disorders of nervous system in diseases classified elsewhere G46* Vascular syndromes of brain in cerebrovascular diseases

G53* Cranial nerve disorders in diseases classified elsewhere

G55* Nerve root and plexus compressions in diseases classified elsewhere G59* Mononeuropathy in diseases classified elsewhere

G63* Polyneuropathy in diseases classified elsewhere

G73* Disorders of myoneural junction and muscle in diseases classified elsewhere G94* Other disorders of brain in diseases classified elsewhere

G99* Other disorders of nervous system in diseases classified elsewhere

 

Inflammatory diseases of the central nervous system (G00–G09)

  G00 Bacterial meningitis, not elsewhere classified

Incl.: arachnoiditis

leptomeningitis meningitis pachymeningitis

bacterial

Excl.: bacterial:

• meningoencephalitis (G04.2)

• meningomyelitis (G04.2)

G00.0 Haemophilus meningitis

Meningitis due to Haemophilus influenzae

G00.1 Pneumococcal meningitis G00.2 Streptococcal meningitis G00.3 Staphylococcal meningitis G00.8 Other bacterial meningitis

Meningitis due to:

• Escherichia coli

• Friedländer bacillus

• Klebsiella

G00.9 Bacterial meningitis, unspecified

Meningitis:

• purulent NOS

• pyogenic NOS

• suppurative NOS

  G01* Meningitis in bacterial diseases classified elsewhere

Incl.: meningitis (in):

• anthrax (A22.8†)

• gonococcal (A54.8†)

• leptospirosis (A27.-†)

• listerial (A32.1†)

• Lyme disease (A69.2†)

• meningococcal (A39.0†)

• neurosyphilis (A52.1†)

• Salmonella infection (A02.2†)

• syphilis:

– congenital (A50.4†)

– secondary (A51.4†)

• tuberculous (A17.0†)

• typhoid fever (A01.0†)

Excl.: meningoencephalitis and meningomyelitis in bacterial diseases classified elsewhere (G05.0*)

 

  G02* Meningitis in other infectious and parasitic diseases classified elsewhere

Excl.: meningoencephalitis and meningomyelitis in other infectious and parasitic diseases classified elsewhere (G05.1–G05.2*)

G02.0* Meningitis in viral diseases classified elsewhere

Meningitis (due to):

• adenoviral (A87.1†)

• enteroviral (A87.0†)

• herpesviral [herpes simplex] (B00.3†)

• infectious mononucleosis (B27.-†)

• measles (B05.1†)

• mumps (B26.1†)

• rubella (B06.0†)

• varicella [chickenpox] (B01.0†)

• zoster (B02.1†)

G02.1* Meningitis in mycoses

Meningitis (in):

• candidal (B37.5†)

• coccidioidomycosis (B38.4†)

• cryptococcal (B45.1†)

G02.8* Meningitis in other specified infectious and parasitic diseases classified elsewhere

Meningitis due to:

• African trypanosomiasis (B56.-†)

• Chagas disease (chronic) (B57.4†)

  G03 Meningitis due to other and unspecified causes

Incl.: arachnoiditis

leptomeningitis meningitis pachymeningitis

due to other and unspecified causes

Excl.: meningoencephalitis (G04.-) meningomyelitis (G04.-)

G03.0 Nonpyogenic meningitis

Nonbacterial meningitis

G03.1 Chronic meningitis

G03.2 Benign recurrent meningitis [Mollaret] G03.8 Meningitis due to other specified causes G03.9 Meningitis, unspecified

Arachnoiditis (spinal) NOS

 

  G04 Encephalitis, myelitis and encephalomyelitis

Incl.: acute ascending myelitis meningoencephalitis meningomyelitis

Excl.: benign myalgic encephalomyelitis (G93.3) encephalopathy:

• NOS (G93.4)

• alcoholic (G31.2)

• toxic (G92)

multiple sclerosis (G35) myelitis:

• acute transverse (G37.3)

• subacute necrotizing (G37.4)

G04.0 Acute disseminated encephalitis

Encephalitis

Encephalomyelitis postimmunization

Use additional external cause code (Chapter XX), if desired, to identify vaccine.

G04.1 Tropical spastic paraplegia

G04.2 Bacterial meningoencephalitis and meningomyelitis, not elsewhere classified

G04.8 Other encephalitis, myelitis and encephalomyelitis

Postinfectious encephalitis and encephalomyelitis NOS

Use additional code, if desired, to identify any associated epileptic seizures (G40.-).

G04.9 Encephalitis, myelitis and encephalomyelitis, unspecified

Ventriculitis (cerebral) NOS

  G05* Encephalitis, myelitis and encephalomyelitis in diseases classified elsewhere

Incl.: meningoencephalitis and meningomyelitis in diseases classified elsewhere

G05.0* Encephalitis, myelitis and encephalomyelitis in bacterial diseases classified elsewhere

Encephalitis, myelitis or encephalomyelitis (in):

• listerial (A32.1†)

• meningococcal (A39.8†)

• syphilis:

– congenital (A50.4†)

– late (A52.1†)

• tuberculous (A17.8†)

 

G05.1* Encephalitis, myelitis and encephalomyelitis in viral diseases classified elsewhere

Encephalitis, myelitis or encephalomyelitis (in):

• adenoviral (A85.1†)

• cytomegaloviral (B25.8†)

• enteroviral (A85.0†)

• herpesviral [herpes simplex] (B00.4†)

• influenza

– seasonal virus identified (J10.8†)

– virus not identified (J11.8†)

– zoonotic or pandemic influenza virus identified (J09†)

• measles (B05.0†)

• mumps (B26.2†)

• postchickenpox (B01.1†)

• rubella (B06.0†)

• zoster (B02.0†)

G05.2* Encephalitis, myelitis and encephalomyelitis in other infectious and parasitic diseases classified elsewhere Encephalitis, myelitis or encephalomyelitis in:

• African trypanosomiasis (B56.-†)

• Chagas disease (chronic) (B57.4†)

• naegleriasis (B60.2†)

• toxoplasmosis (B58.2†)

Eosinophilic meningoencephalitis (B83.2†)

G05.8* Encephalitis, myelitis and encephalomyelitis in other diseases classified elsewhere

Encephalitis in systemic lupus erythematosus (M32.1†)

  G06 Intracranial and intraspinal abscess and granuloma

Use additional code (B95–B98), if desired, to identify infectious agent.

G06.0 Intracranial abscess and granuloma

abscess (embolic)(of):

• brain [any part]

• cerebellar

• cerebral

• otogenic

Intracranial abscess or granuloma:

• epidural

• extradural

• subdural

G06.1 Intraspinal abscess and granuloma Abscess (embolic) of spinal cord [any part] Intraspinal abscess or granuloma:

• epidural

• extradural

• subdural

G06.2 Extradural and subdural abscess, unspecified

 

  G07* Intracranial and intraspinal abscess and granuloma in diseases classified elsewhere

Incl.: abscess of brain:

• amoebic (A06.6†)

• gonococcal (A54.8†)

• tuberculous (A17.8†)

schistosomiasis granuloma of brain (B65.-†) tuberculoma of:

• brain (A17.8†)

• meninges (A17.1†)

  G08 Intracranial and intraspinal phlebitis and thrombophlebitis

Incl.: septic:

• embolism

• endophlebitis

• phlebitis

• thrombophlebitis

• thrombosis

of intracranial or intraspinal venous sinuses and veins

Excl.: intracranial phlebitis and thrombophlebitis:

• complicating:

– abortion or ectopic or molar pregnancy (O00–O07, O08.7)

– pregnancy, childbirth and the puerperium (O22.5, O87.3)

• of nonpyogenic origin (I67.6)

nonpyogenic intraspinal phlebitis and thrombophlebitis (G95.1)

  G09 Sequelae of inflammatory diseases of central nervous system

Note: Category G09 is to be used to indicate conditions whose primary classification is to G00–G08 (i.e. excluding those marked with    an asterisk (*)) as the cause of sequelae, themselves classifiable elsewhere. The ‘sequelae’ include conditions specified as such or as late effects, or those present one year or more after onset of the causal condition. For use of this category, reference should be made to the relevant morbidity and mortality coding rules and guidelines in Volume 2.

Not to be used for chronic inflammatory diseases of the central nervous system. Code these to current inflammatory diseases of the central nervous system

 

Systemic atrophies primarily affecting the central nervous system

(G10–G14)

  G10 Huntington disease

Incl.:   Huntington chorea

  G11 Hereditary ataxia

Excl.: cerebral palsy (G80.-)

hereditary and idiopathic neuropathy (G60.-) metabolic disorders (E70–E90)

G11.0 Congenital nonprogressive ataxia G11.1 Early-onset cerebellar ataxia

Note: Onset usually before the age of 20.years

Early-onset cerebellar ataxia with:

• essential tremor

• myoclonus [Hunt ataxia]

• retained tendon reflexes

Friedreich ataxia (autosomal recessive) X-linked recessive spinocerebellar ataxia

G11.2 Late-onset cerebellar ataxia

Note: Onset usually after the age of 20 years.

G11.3 Cerebellar ataxia with defective DNA repair

Ataxia telangiectasia [Louis–Bar]

Excl.: Cockayne syndrome (Q87.1) xeroderma pigmentosum (Q82.1)

G11.4 Hereditary spastic paraplegia G11.8 Other hereditary ataxias G11.9 Hereditary ataxia, unspecified

Hereditary cerebellar:

• ataxia NOS

• degeneration

• disease

• syndrome

  G12 Spinal muscular atrophy and related syndromes

G12.0 Infantile spinal muscular atrophy, type I [Werdnig–Hoffman]

 

G12.1 Other inherited spinal muscular atrophy Progressive bulbar palsy of childhood [Fazio–Londe] Spinal muscular atrophy:

• adult form

• childhood form, type II

• distal

• juvenile form, type III [Kugelberg-Welander]

• scapuloperoneal form

G12.2 Motor neuron disease

Familial motor neuron disease Lateral sclerosis:

• amyotrophic

• primary Progressive:

• bulbar palsy

• spinal muscular atrophy

G12.8 Other spinal muscular atrophies and related syndromes G12.9 Spinal muscular atrophy, unspecified

  G13* Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere

G13.0* Paraneoplastic neuromyopathy and neuropathy

Carcinomatous neuromyopathy (C00–C97†)

Sensorial paraneoplastic neuropathy [Denny Brown] (C00–D48†)

G13.1* Other systemic atrophy primarily affecting central nervous system in neoplastic disease

Paraneoplastic limbic encephalopathy (C00–D48†)

G13.2* Systemic atrophy primarily affecting central nervous system in myxoedema (E00.1† , E03.-†)

G13.8* Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere

  G14 Postpolio syndrome

Incl.: postpolio myelitic syndrome

Excl.: sequelae of poliomyelitis (B91)

 

Extrapyramidal and movement disorders (G20–G26)

  G20 Parkinson disease

Incl.: hemiparkinsonism paralysis agitans

parkinsonism or Parkinson disease:

• NOS

• idiopathic

• primary

  G21 Secondary parkinsonism

G21.0 Malignant neuroleptic syndrome

Use additional external cause code (Chapter XX), if desired, to identify drug.

G21.1 Other drug-induced secondary parkinsonism

Use additional external cause code (Chapter XX), if desired, to identify drug.

G21.2 Secondary parkinsonism due to other external agents

Use additional external cause code (Chapter XX), if desired, to identify external agent.

G21.3 Postencephalitic parkinsonism G21.4 Vascular parkinsonism

G21.8 Other secondary parkinsonism

G21.9 Secondary parkinsonism, unspecified

  G22* Parkinsonism in diseases classified elsewhere

Incl.: syphilitic parkinsonism (A52.1†)

  G23 Other degenerative diseases of basal ganglia

G23.0 Hallervorden–Spatz disease

Pigmentary pallidal degeneration

G23.1 Progressive supranuclear ophthalmoplegia [Steele- Richardson–Olszewski]

Progressive supranuclear palsy

G23.2 Multiple system atrophy, parkinsonian type [MSA-P] G23.3 Multiple system atrophy, cerebellar type [MSA-C] G23.8 Other specified degenerative diseases of basal ganglia

Calcification of basal ganglia

Neurogenic orthostatic hypotension [Shy–Drager]

Excl.: orthostatic hypotension NOS (I95.1)

G23.9 Degenerative disease of basal ganglia, unspecified

 

  G24 Dystonia

Incl.: dyskinesia

Excl.: athetoid cerebral palsy (G80.3)

G24.0 Drug-induced dystonia

Use additional external cause code (Chapter XX), if desired, to identify drug.

G24.1 Idiopathic familial dystonia

Idiopathic dystonia NOS

G24.2 Idiopathic nonfamilial dystonia G24.3 Spasmodic torticollis

Excl.: torticollis NOS (M43.6)

G24.4 Idiopathic orofacial dystonia

Orofacial dyskinesia G24.5 Blepharospasm G24.8 Other dystonia

G24.9 Dystonia, unspecified

Dyskinesia NOS

  G25 Other extrapyramidal and movement disorders

G25.0 Essential tremor

Familial tremor

Excl.: tremor NOS (R25.1)

G25.1 Drug-induced tremor

Use additional external cause code (Chapter XX), if desired, to identify drug.

G25.2 Other specified forms of tremor

Intention tremor

G25.3 Myoclonus

Drug-induced myoclonus

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: facial myokymia (G51.4) myoclonic epilepsy (G40.-)

G25.4 Drug-induced chorea

Use additional external cause code (Chapter XX), if desired, to identify drug.

G25.5 Other chorea

Chorea NOS

Excl.: chorea NOS with heart involvement (I02.0) Huntington chorea (G10)

rheumatic chorea (I02.-) Sydenham chorea (I02.-)

G25.6 Drug-induced tics and other tics of organic origin

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: Tourette syndrome (F95.2) tic NOS (F95.9)

G25.8 Other specified extrapyramidal and movement disorders

Akathisia (drug-induced) (treatment-induced) Restless legs syndrome

Stiff-man syndrome

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced

G25.9 Extrapyramidal and movement disorder, unspecified

  G26* Extrapyramidal and movement disorders in diseases classified elsewhere

Other degenerative diseases of the nervous system (G30–G32)

  G30 Alzheimer disease

Incl.: senile and presenile forms

Excl.: senile:

• degeneration of brain NEC (G31.1)

• dementia NOS (F03) senility NOS (R54)

G30.0 Alzheimer disease with early onset

Note: Onset usually before the age of 65 years.

G30.1 Alzheimer disease with late onset

Note: Onset usually after the age of 65 years.

G30.8 Other Alzheimer disease

G30.9 Alzheimer disease, unspecified

  G31 Other degenerative diseases of nervous system, not elsewhere classified

Excl.: Reye syndrome (G93.7)

G31.0 Circumscribed brain atrophy Frontotemporal dementia (FTD) Pick disease

Progressive isolated aphasia

 

G31.1 Senile degeneration of brain, not elsewhere classified

Excl.: Alzheimer disease (G30.-) senility NOS (R54)

G31.2 Degeneration of nervous system due to alcohol

Alcoholic:

• cerebellar:

– ataxia

– degeneration

• cerebral degeneration

• encephalopathy

Dysfunction of autonomic nervous system due to alcohol

G31.8 Other specified degenerative diseases of nervous system

Grey-matter degeneration [Alpers]

Lewy body(ies)(dementia)(disease) (F02.8*) Subacute necrotizing encephalopathy [Leigh]

G31.9 Degenerative disease of nervous system, unspecified

  G32* Other degenerative disorders of nervous system in diseases classified elsewhere

G32.0* Subacute combined degeneration of spinal cord in diseases classified elsewhere

Excl.: subacute combined degeneration of spinal cord in vitamin B12 deficiency (E53.8†)

G32.8* Other specified degenerative disorders of nervous system in diseases classified elsewhere

Demyelinating diseases of the central nervous system (G35–G37)

  G35 Multiple sclerosis

Incl.: multiple sclerosis (of):

• NOS

• brain stem

• cord

• disseminated

• generalized

 

  G36 Other acute disseminated demyelination

Excl.: postinfectious encephalitis and encephalomyelitis NOS (G04.8)

G36.0 Neuromyelitis optica [Devic]

Demyelination in optic neuritis

Excl.: optic neuritis NOS (H46)

G36.1 Acute and subacute haemorrhagic leukoencephalitis [Hurst] G36.8 Other specified acute disseminated demyelination

G36.9 Acute disseminated demyelination, unspecified

  G37 Other demyelinating diseases of central nervous system

G37.0 Diffuse sclerosis

Periaxial encephalitis Schilder disease

Excl.: adrenoleukodystrophy [Addison–Schilder] (E71.3)

G37.1 Central demyelination of corpus callosum G37.2 Central pontine myelinolysis

G37.3 Acute transverse myelitis in demyelinating disease of central nervous system

Acute transverse myelitis NOS

Excl.: multiple sclerosis (G35) neuromyelitis optica [Devic] (G36.0)

G37.4 Subacute necrotizing myelitis G37.5 Concentric sclerosis [Baló]

G37.8 Other specified demyelinating diseases of central nervous system

G37.9 Demyelinating disease of central nervous system, unspecified

Episodic and paroxysmal disorders (G40–G47)

  G40 Epilepsy

Excl.: Landau–Kleffner syndrome (F80.3) seizure (convulsive) NOS (R56.8) status epilepticus (G41.-)

Todd paralysis (G83.8)

G40.0 Localization-related (focal)(partial) idiopathic epilepsy and epileptic syndromes with seizures of localized onset Benign childhood epilepsy with centrotemporal EEG spikes Childhood epilepsy with occipital EEG paroxysms

 

G40.1 Localization-related (focal)(partial) symptomatic epilepsy and epileptic syndromes with simple partial seizures

Attacks without alteration of consciousness

Simple partial seizures developing into secondarily generalized seizures

G40.2 Localization-related (focal)(partial) symptomatic epilepsy and epileptic syndromes with complex partial seizures

Attacks with alteration of consciousness, often with automatisms Complex partial seizures developing into secondarily generalized seizures

G40.3 Generalized idiopathic epilepsy and epileptic syndromes

Benign:

• myoclonic epilepsy in infancy

• neonatal convulsions (familial) Childhood absence epilepsy [pyknolepsy]

Epilepsy with grand mal seizures on awakening Juvenile:

• absence epilepsy

• myoclonic epilepsy [impulsive petit mal] Nonspecific epileptic seizures:

• atonic

• clonic

• myoclonic

• tonic

• tonic–clonic

G40.4 Other generalized epilepsy and epileptic syndromes

Epilepsy with:

• myoclonic absences

• myoclonic-astatic seizures Infantile spasms Lennox–Gastaut syndrome Salaam attacks

Symptomatic early myoclonic encephalopathy West syndrome

G40.5 Special epileptic syndromes Epilepsia partialis continua [Kozhevnikof] Epileptic seizures related to:

• alcohol

• drugs

• hormonal changes

• sleep deprivation

• stress

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

 

G40.6 Grand mal seizures, unspecified (with or without petit mal) G40.7 Petit mal, unspecified, without grand mal seizures

G40.8 Other epilepsy

Epilepsies and epileptic syndromes undetermined as to whether they are focal or generalized

G40.9 Epilepsy, unspecified

Epileptic:

• convulsions NOS

• fits NOS

• seizures NOS

  G41 Status epilepticus

G41.0 Grand mal status epilepticus

Tonic-clonic status epilepticus

Excl.: epilepsia partialis continua [Kozhevnikof] (G40.5)

G41.1 Petit mal status epilepticus

Epileptic absence status

G41.2 Complex partial status epilepticus G41.8 Other status epilepticus

G41.9 Status epilepticus, unspecified

  G43 Migraine

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: headache NOS (R51)

G43.0 Migraine without aura [common migraine] G43.1 Migraine with aura [classical migraine]

Migraine:

• aura without headache

• basilar

• equivalents

• familial hemiplegic

• with:

– acute-onset aura

– prolonged aura

– typical aura

G43.2 Status migrainosus G43.3 Complicated migraine G43.8 Other migraine

Ophthalmoplegic migraine

Retinal migraine

 

G43.9 Migraine, unspecified

  G44 Other headache syndromes

Excl.: atypical facial pain (G50.1) headache NOS (R51) trigeminal neuralgia (G50.0)

G44.0 Cluster headache syndrome Chronic paroxysmal hemicrania Cluster headache:

• chronic

• episodic

G44.1 Vascular headache, not elsewhere classified

Vascular headache NOS

G44.2 Tension-type headache

Chronic tension-type headache Episodic tension headache Tension headache NOS

G44.3 Chronic post-traumatic headache

G44.4 Drug-induced headache, not elsewhere classified

Use additional external cause code (Chapter XX), if desired, to identify drug.

G44.8 Other specified headache syndromes

  G45 Transient cerebral ischaemic attacks and related syndromes

Excl.: neonatal cerebral ischaemia (P91.0) G45.0 Vertebro-basilar artery syndrome G45.1 Carotid artery syndrome (hemispheric)

G45.2 Multiple and bilateral precerebral artery syndromes G45.3 Amaurosis fugax

G45.4 Transient global amnesia

Excl.:  amnesia NOS (R41.3)

G45.8 Other transient cerebral ischaemic attacks and related syndromes

G45.9 Transient cerebral ischaemic attack, unspecified

Spasm of cerebral artery Transient cerebral ischaemia NOS

 

  G46* Vascular syndromes of brain in cerebrovascular diseases (I60–I67†)

G46.0* Middle cerebral artery syndrome (I66.0†) G46.1* Anterior cerebral artery syndrome (I66.1†) G46.2* Posterior cerebral artery syndrome (I66.2†) G46.3* Brain stem stroke syndrome (I60–I67†)

Syndrome:

• Benedikt

• Claude

• Foville

• Millard–Gubler

• Wallenberg

• Weber

G46.4* Cerebellar stroke syndrome (I60–I67†) G46.5* Pure motor lacunar syndrome (I60–I67†) G46.6* Pure sensory lacunar syndrome (I60–I67†) G46.7* Other lacunar syndromes (I60–I67†)

G46.8* Other vascular syndromes of brain in cerebrovascular diseases (I60–I67†)

  G47 Sleep disorders

Excl.: nightmares (F51.5)

nonorganic sleep disorders (F51.-) sleep terrors (F51.4)

sleepwalking (F51.3)

G47.0 Disorders of initiating and maintaining sleep [insomnias] G47.1 Disorders of excessive somnolence [hypersomnias] G47.2 Disorders of the sleep–wake schedule

Delayed sleep phase syndrome

Irregular sleep–wake pattern

G47.3 Sleep apnoea

Sleep apnoea:

• central

• obstructive

Excl.: pickwickian syndrome (E66.2) sleep apnoea of newborn (P28.3)

G47.4 Narcolepsy and cataplexy G47.8 Other sleep disorders

Kleine–Levin syndrome

G47.9 Sleep disorder, unspecified

 

Nerve, nerve root and plexus disorders (G50–G59)

Excl.: current traumatic nerve, nerve root and plexus disorders – see nerve injury by body region

neuralgia

neuritis NOS (M79.2)

peripheral neuritis in pregnancy (O26.8) radiculitis NOS (M54.1)

  G50 Disorders of trigeminal nerve

Incl.: disorders of 5th cranial nerve

G50.0 Trigeminal neuralgia

Syndrome of paroxysmal facial pain Tic douloureux

G50.1 Atypical facial pain

G50.8 Other disorders of trigeminal nerve G50.9 Disorder of trigeminal nerve, unspecified

  G51 Facial nerve disorders

Incl.: disorders of 7th cranial nerve

G51.0 Bell’s palsy

Facial palsy

G51.1 Geniculate ganglionitis

Excl.: postherpetic geniculate ganglionitis (B02.2)

G51.2 Melkersson syndrome

Melkersson–Rosenthal syndrome G51.3 Clonic hemifacial spasm G51.4 Facial myokymia

G51.8 Other disorders of facial nerve G51.9 Disorder of facial nerve, unspecified

  G52 Disorders of other cranial nerves

Excl.: disorders of:

• acoustic [8th] nerve (H93.3)

• optic [2nd] nerve (H46, H47.0)

paralytic strabismus due to nerve palsy (H49.0–H49.2)

G52.0 Disorders of olfactory nerve

Disorder of 1st cranial nerve

 

G52.1 Disorders of glossopharyngeal nerve Disorder of 9th cranial nerve Glossopharyngeal neuralgia

G52.2 Disorders of vagus nerve

Disorder of pneumogastric [10th] nerve

G52.3 Disorders of hypoglossal nerve

Disorder of 12th cranial nerve

G52.7 Disorders of multiple cranial nerves

Polyneuritis cranialis

G52.8 Disorders of other specified cranial nerves G52.9 Cranial nerve disorder, unspecified

  G53* Cranial nerve disorders in diseases classified elsewhere

G53.0* Postzoster neuralgia (B02.2†)

Postherpetic:

• geniculate ganglionitis

• trigeminal neuralgia

G53.1* Multiple cranial nerve palsies in infectious and parasitic diseases classified elsewhere (A00–B99†)

G53.2* Multiple cranial nerve palsies in sarcoidosis (D86.8†)

G53.3* Multiple cranial nerve palsies in neoplastic disease (C00–D48†)

G53.8* Other cranial nerve disorders in other diseases classified elsewhere

  G54 Nerve root and plexus disorders

Excl.: current traumatic nerve root and plexus disorders – see nerve injury by body region

intervertebral disc disorders (M50–M51) neuralgia or neuritis NOS (M79.2) neuritis or radiculitis:

• brachial NOS (M54.1)

• lumbar NOS (M54.1)

• lumbosacral NOS (M54.1)

• thoracic NOS (M54.1) radiculitis NOS (M54.1) radiculopathy NOS (M54.1) spondylosis (M47.-)

G54.0 Brachial plexus disorders

Thoracic outlet syndrome

G54.1 Lumbosacral plexus disorders

G54.2 Cervical root disorders, not elsewhere classified

 

G54.3 Thoracic root disorders, not elsewhere classified G54.4 Lumbosacral root disorders, not elsewhere classified G54.5 Neuralgic amyotrophy

Parsonage–Aldren–Turner syndrome Shoulder–girdle neuritis

G54.6 Phantom limb syndrome with pain G54.7 Phantom limb syndrome without pain

Phantom limb syndrome NOS

G54.8 Other nerve root and plexus disorders G54.9 Nerve root and plexus disorder, unspecified

  G55* Nerve root and plexus compressions in diseases classified elsewhere

G55.0* Nerve root and plexus compressions in neoplastic disease (C00–D48†)

G55.1* Nerve root and plexus compressions in intervertebral disc disorders (M50–M51†)

G55.2* Nerve root and plexus compressions in spondylosis (M47.-†)

G55.3* Nerve root and plexus compressions in other dorsopathies (M45–M46†, M48.-† , M53–M54†)

G55.8* Nerve root and plexus compressions in other diseases classified elsewhere

  G56 Mononeuropathies of upper limb

Excl.: current traumatic nerve disorder – see nerve injury by body region

G56.0 Carpal tunnel syndrome G56.1 Other lesions of median nerve G56.2 Lesion of ulnar nerve

Tardy ulnar nerve palsy

G56.3 Lesion of radial nerve G56.4 Causalgia

G56.8 Other mononeuropathies of upper limb

Interdigital neuroma of upper limb

G56.9 Mononeuropathy of upper limb, unspecified

 

  G57 Mononeuropathies of lower limb

Excl.: current traumatic nerve disorder – see nerve injury by body region

G57.0 Lesion of sciatic nerve

Excl.: sciatica:

• NOS (M54.3)

• attributed to intervertebral disc disorder (M51.1)

G57.1 Meralgia paraesthetica

Lateral cutaneous nerve of thigh syndrome

G57.2 Lesion of femoral nerve

G57.3 Lesion of lateral popliteal nerve

Peroneal nerve palsy

G57.4 Lesion of medial popliteal nerve G57.5 Tarsal tunnel syndrome

G57.6 Lesion of plantar nerve

Morton metatarsalgia

G57.8 Other mononeuropathies of lower limb

Interdigital neuroma of lower limb

G57.9 Mononeuropathy of lower limb, unspecified

  G58 Other mononeuropathies G58.0 Intercostal neuropathy G58.7 Mononeuritis multiplex

G58.8 Other specified mononeuropathies G58.9 Mononeuropathy, unspecified

  G59* Mononeuropathy in diseases classified elsewhere

G59.0* Diabetic mononeuropathy

(E10–E14 with common fourth character .4†)

G59.8* Other mononeuropathies in diseases classified elsewhere

 

Polyneuropathies and other disorders of the peripheral nervous system

(G60–G64)

Excl.: neuralgia NOS (M79.2)

neuritis NOS (M79.2)

peripheral neuritis in pregnancy (O26.8) radiculitis NOS (M54.1)

  G60 Hereditary and idiopathic neuropathy

G60.0 Hereditary motor and sensory neuropathy

Disease:

• Charcot–Marie–Tooth

• Déjerine–Sottas

Hereditary motor and sensory neuropathy, types I-IV Hypertrophic neuropathy of infancy

Peroneal muscular atrophy (axonal type)(hypertrophic type) Roussy–Lévy syndrome

G60.1 Refsum disease

G60.2 Neuropathy in association with hereditary ataxia G60.3 Idiopathic progressive neuropathy

G60.8 Other hereditary and idiopathic neuropathies

Morvan disease Nelaton syndrome Sensory neuropathy:

• dominantly inherited

• recessively inherited

G60.9 Hereditary and idiopathic neuropathy, unspecified

  G61 Inflammatory polyneuropathy

G61.0 Guillain–Barré syndrome

Acute (post –)infective polyneuritis Miller–Fisher syndrome

G61.1 Serum neuropathy

Use additional external cause code (Chapter XX), if desired, to identify cause.

G61.8 Other inflammatory polyneuropathies G61.9 Inflammatory polyneuropathy, unspecified

 

  G62 Other polyneuropathies

G62.0 Drug-induced polyneuropathy

Use additional external cause code (Chapter XX), if desired, to identify drug.

G62.1 Alcoholic polyneuropathy

G62.2 Polyneuropathy due to other toxic agents

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

G62.8 Other specified polyneuropathies

Radiation-induced polyneuropathy

Use additional external cause code (Chapter XX), if desired, to identify cause.

G62.9 Polyneuropathy, unspecified

Neuropathy NOS

  G63* Polyneuropathy in diseases classified elsewhere

G63.0* Polyneuropathy in infectious and parasitic diseases classified elsewhere

Polyneuropathy (in):

• diphtheria (A36.8†)

• infectious mononucleosis (B27.-†)

• leprosy (A30.-†)

• Lyme disease (A69.2†)

• mumps (B26.8†)

• postherpetic (B02.2†)

• syphilis, late (A52.1†)

• congenital syphilis, late (A50.4†)

• tuberculous (A17.8†)

G63.1* Polyneuropathy in neoplastic disease (C00–D48†)

G63.2* Diabetic polyneuropathy (E10–E14 with common fourth character .4†)

G63.3* Polyneuropathy in other endocrine and metabolic diseases (E00–E07†, E15–E16†, E20–E34†, E70–E89†)

G63.4* Polyneuropathy in nutritional deficiency (E40–E64†)

G63.5* Polyneuropathy in systemic connective tissue disorders (M30–M35†)

G63.6* Polyneuropathy in other musculoskeletal disorders (M00–M25†, M40–M96†)

G63.8* Polyneuropathy in other diseases classified elsewhere

Uraemic neuropathy (N18.5†)

  G64 Other disorders of peripheral nervous system

Incl.: disorder of peripheral nervous system NOS

 

Diseases of myoneural junction and muscle (G70–G73)

  G70 Myasthenia gravis and other myoneural disorders

Excl.: botulism (A05.1)

transient neonatal myasthenia gravis (P94.0)

G70.0 Myasthenia gravis

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

G70.1 Toxic myoneural disorders

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

G70.2 Congenital and developmental myasthenia G70.8 Other specified myoneural disorders G70.9 Myoneural disorder, unspecified

  G71 Primary disorders of muscles

Excl.: arthrogryposis multiplex congenita (Q74.3) metabolic disorders (E70–E90)

myositis (M60.-)

G71.0 Muscular dystrophy

Muscular dystrophy:

• autosomal recessive, childhood type, resembling Duchenne or Becker

• benign [Becker]

• benign scapuloperoneal with early contractures [Emery–Dreifuss]

• distal

• facioscapulohumeral

• limb-girdle

• ocular

• oculopharyngeal

• scapuloperoneal

• severe [Duchenne]

Excl.: congenital muscular dystrophy:

• NOS (G71.2)

• with specific morphological abnormalities of the muscle fibre (G71.2)

 

G71.1 Myotonic disorders

Dystrophia myotonica [Steinert] Myotonia:

• chondrodystrophic

• drug-induced

• symptomatic Myotonia congenita:

• NOS

• dominant [Thomsen]

• recessive [Becker] Neuromyotonia [Isaacs] Paramyotonia congenita Pseudomyotonia

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

G71.2 Congenital myopathies

Congenital muscular dystrophy:

• NOS

• with specific morphological abnormalities of the muscle fibre Disease:

• central core

• minicore

• multicore

Fibre-type disproportion Myopathy:

• myotubular (centronuclear)

• nemaline

G71.3 Mitochondrial myopathy, not elsewhere classified G71.8 Other primary disorders of muscles

G71.9 Primary disorder of muscle, unspecified

Hereditary myopathy NOS

  G72 Other myopathies

Excl.: arthrogryposis multiplex congenita (Q74.3) dermatopolymyositis (M33.-)

ischaemic infarction of muscle (M62.2) myositis (M60.-)

polymyositis (M33.2)

G72.0 Drug-induced myopathy

Use additional external cause code (Chapter XX), if desired, to identify drug.

G72.1 Alcoholic myopathy

G72.2 Myopathy due to other toxic agents

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

G72.3 Periodic paralysis

Periodic paralysis (familial):

• hyperkalaemic

• hypokalaemic

• myotonic

• normokalaemic

G72.4 Inflammatory myopathy, not elsewhere classified G72.8 Other specified myopathies

G72.9 Myopathy, unspecified

  G73* Disorders of myoneural junction and muscle in diseases classified elsewhere

G73.0* Myasthenic syndromes in endocrine diseases

Myasthenic syndromes in:

• diabetic amyotrophy (E10–E14 with common fourth character .4†)

• thyrotoxicosis [hyperthyroidism] (E05.-†)

G73.1* Lambert–Eaton syndrome (C00–D48†)

G73.2* Other myasthenic syndromes in neoplastic disease (C00–D48†)

G73.3* Myasthenic syndromes in other diseases classified elsewhere G73.4* Myopathy in infectious and parasitic diseases classified

elsewhere

G73.5* Myopathy in endocrine diseases

Myopathy in:

• hyperparathyroidism (E21.0–E21.3†)

• hypoparathyroidism (E20.-†) Thyrotoxic myopathy (E05.-†)

G73.6* Myopathy in metabolic diseases

Myopathy in:

• glycogen storage disease (E74.0†)

• lipid storage disorders (E75.-†)

G73.7* Myopathy in other diseases classified elsewhere

Myopathy in:

• rheumatoid arthritis (M05–M06†)

• scleroderma (M34.8†)

• sicca syndrome [Sjögren] (M35.0†)

• systemic lupus erythematosus (M32.1†)

 

Cerebral palsy and other paralytic syndromes (G80–G83)

  G80 Cerebral palsy

Excl.: hereditary spastic paraplegia (G11.4)

G80.0 Spastic quadriplegic cerebral palsy

Spastic tetraplegic cerebral palsy

G80.1 Spastic diplegic cerebral palsy Congenital spastic paralysis (cerebral) Spastic cerebral palsy NOS

G80.2 Spastic hemiplegic cerebral palsy G80.3 Dyskinetic cerebral palsy

Athetoid cerebral palsy

Dystonic cerebral palsy

G80.4 Ataxic cerebral palsy G80.8 Other cerebral palsy

Mixed cerebral palsy syndromes

G80.9 Cerebral palsy, unspecified

Cerebral palsy NOS

  G81 Hemiplegia

Note: For primary coding, this category is to be used only when hemiplegia (complete) (incomplete) is reported without further specification, or is stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these types of hemiplegia resulting from any cause.

Excl.: congenital cerebral palsy (G80.-)

G81.0 Flaccid hemiplegia G81.1 Spastic hemiplegia G81.9 Hemiplegia, unspecified

  G82 Paraplegia and tetraplegia

Note: For primary coding, this category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause.

Excl.: congenital cerebral palsy (G80.-)

 

G82.0 Flaccid paraplegia G82.1 Spastic paraplegia G82.2 Paraplegia, unspecified

Paralysis of both lower limbs NOS Paraplegia (lower) NOS

G82.3 Flaccid tetraplegia G82.4 Spastic tetraplegia G82.5 Tetraplegia, unspecified

Quadriplegia NOS

  G83 Other paralytic syndromes

Note: For primary coding, this category is to be used only when the listed conditions are reported without further specification, or are stated to be old or longstanding but of unspecified cause. The category is also for use in multiple coding to identify these conditions resulting from any cause.

Incl.: paralysis (complete)(incomplete), except as in G80–G82

G83.0 Diplegia of upper limbs

Diplegia (upper)

Paralysis of both upper limbs

G83.1 Monoplegia of lower limb

Paralysis of lower limb

G83.2 Monoplegia of upper limb

Paralysis of upper limb

G83.3 Monoplegia, unspecified G83.4 Cauda equina syndrome

Neurogenic bladder due to cauda equina syndrome

Excl.: cord bladder NOS (G95.8)

G83.5 Locked-in syndrome

G83.8 Other specified paralytic syndromes

Todd paralysis (postepileptic)

G83.9 Paralytic syndrome, unspecified

 

Other disorders of the nervous system (G90–G99)

  G90 Disorders of autonomic nervous system

Excl.: dysfunction of autonomic nervous system due to alcohol (G31.2)

G90.0 Idiopathic peripheral autonomic neuropathy

Carotid sinus syncope

G90.1 Familial dysautonomia [Riley–Day] G90.2 Horner syndrome

Bernard(–Horner) syndrome

G90.4 Autonomic dysreflexia

G90.8 Other disorders of autonomic nervous system G90.9 Disorder of autonomic nervous system, unspecified

  G91 Hydrocephalus

Incl.: acquired hydrocephalus

Excl.: hydrocephalus:

• acquired, of newborn (P91.7)

• congenital (Q03.-)

• due to congenital toxoplasmosis (P37.1)

G91.0 Communicating hydrocephalus G91.1 Obstructive hydrocephalus G91.2 Normal-pressure hydrocephalus

G91.3 Post-traumatic hydrocephalus, unspecified G91.8 Other hydrocephalus

G91.9 Hydrocephalus, unspecified

  G92 Toxic encephalopathy

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

  G93 Other disorders of brain

G93.0 Cerebral cysts

Arachnoid cyst Porencephalic cyst, acquired

Excl.: acquired periventricular cysts of newborn (P91.1) congenital cerebral cysts (Q04.6)

 

G93.1 Anoxic brain damage, not elsewhere classified

Excl.: complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.8)

• pregnancy, labour or delivery (O29.2, O74.3, O89.2)

• surgical and medical care (T80–T88) neonatal anoxia (P21.9)

G93.2 Benign intracranial hypertension

Excl.: hypertensive encephalopathy (I67.4)

G93.3 Postviral fatigue syndrome

Benign myalgic encephalomyelitis

G93.4 Encephalopathy, unspecified

Excl.: encephalopathy:

• alcoholic (G31.2)

• toxic (G92)

G93.5 Compression of brain

Compression

Herniation of brain (stem)

Excl.: traumatic compression of brain (diffuse) (S06.2) traumatic compression of brain (diffuse)

• focal (S06.3)

G93.6 Cerebral oedema

Excl.: cerebral oedema:

• due to birth injury (P11.0)

• traumatic (S06.1)

G93.7 Reye syndrome

Use additional external cause code (Chapter XX), if desired, to identify cause.

G93.8 Other specified disorders of brain

Postradiation encephalopathy

Use additional external cause code (Chapter XX), if desired, to identify cause.

G93.9 Disorder of brain, unspecified

  G94* Other disorders of brain in diseases classified elsewhere

G94.0* Hydrocephalus in infectious and parasitic diseases classified elsewhere (A00–B99†)

G94.1* Hydrocephalus in neoplastic disease (C00–D48†) G94.2* Hydrocephalus in other diseases classified elsewhere G94.8* Other specified disorders of brain in diseases classified

elsewhere

 

  G95 Other diseases of spinal cord

Excl.: myelitis (G04.-)

G95.0 Syringomyelia and syringobulbia G95.1 Vascular myelopathies

Acute infarction of spinal cord (embolic)(nonembolic)

Arterial thrombosis of spinal cord Haematomyelia

Nonpyogenic intraspinal phlebitis and thrombophlebitis Oedema of spinal cord

Subacute necrotic myelopathy

Excl.: intraspinal phlebitis and thrombophlebitis, except non-pyogenic (G08)

G95.2 Cord compression, unspecified

G95.8 Other specified diseases of spinal cord

Cord bladder NOS Myelopathy:

• drug-induced

• radiation-induced

Use additional external cause code (Chapter XX), if desired, to identify external agent.

Excl.: neurogenic bladder:

• NOS (N31.9)

• due to cauda equina syndrome (G83.4)

neuromuscular dysfunction of bladder without mention of spinal cord lesion (N31.-)

G95.9 Disease of spinal cord, unspecified

Myelopathy NOS

  G96 Other disorders of central nervous system

G96.0 Cerebrospinal fluid leak

Excl.: from spinal puncture (G97.0)

G96.1 Disorders of meninges, not elsewhere classified

Meningeal adhesions (cerebral)(spinal)

G96.8 Other specified disorders of central nervous system G96.9 Disorder of central nervous system, unspecified

 

  G97 Postprocedural disorders of nervous system, not elsewhere classified

G97.0 Cerebrospinal fluid leak from spinal puncture G97.1 Other reaction to spinal and lumbar puncture

G97.2 Intracranial hypotension following ventricular shunting G97.8 Other postprocedural disorders of nervous system G97.9 Postprocedural disorder of nervous system, unspecified

  G98 Other disorders of nervous system, not elsewhere classified

Incl.: nervous system disorder NOS

  G99* Other disorders of nervous system in diseases classified elsewhere

G99.0* Autonomic neuropathy in endocrine and metabolic diseases

Amyloid autonomic neuropathy (E85.-†)

Diabetic autonomic neuropathy (E10–E14 with common fourth character .4†)

G99.1* Other disorders of autonomic nervous system in other diseases classified elsewhere

G99.2* Myelopathy in diseases classified elsewhere

Anterior spinal and vertebral artery compression syndromes (M47.0†) Myelopathy in:

• intervertebral disc disorders (M50.0† , M51.0†)

• neoplastic disease (C00–D48†)

• spondylosis (M47.-†)

G99.8* Other specified disorders of nervous system in diseases classified elsewhere

Uraemic paralysis (N18.5†)

 

CHAPTER VII

Diseases of the eye and adnexa (H00–H59)

Excl.: certain conditions originating in the perinatal period (P00–P96) certain infectious and parasitic diseases (A00–B99)

complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90)

injury, poisoning and certain other consequences of external causes (S00–T98)

neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

H00–H06 Disorders of eyelid, lacrimal system and orbit H10–H13 Disorders of conjunctiva

H15–H22 Disorders of sclera, cornea, iris and ciliary body H25–H28 Disorders of lens

H30–H36 Disorders of choroid and retina H40–H42 Glaucoma

H43–H45 Disorders of vitreous body and globe H46–H48 Disorders of optic nerve and visual pathways

H49–H52 Disorders of ocular muscles, binocular movement, accommodation and refraction

H53–H54 Visual disturbances and blindness H55–H59 Other disorders of eye and adnexa

Asterisk categories for this chapter are provided as follows:

H03* Disorders of eyelid in diseases classified elsewhere

H06* Disorders of lacrimal system and orbit in diseases classified elsewhere H13* Disorders of conjunctiva in diseases classified elsewhere

H19* Disorders of sclera and cornea in diseases classified elsewhere H22* Disorders of iris and ciliary body in diseases classified elsewhere H28* Cataract and other disorders of lens in diseases classified elsewhere H32* Chorioretinal disorders in diseases classified elsewhere

H36* Retinal disorders in diseases classified elsewhere H42* Glaucoma in diseases classified elsewhere

H45* Disorders of vitreous body and globe in diseases classified elsewhere H48* Disorders of optic [2nd] nerve and visual pathways in diseases classified

elsewhere

H58* Other disorders of eye and adnexa in diseases classified elsewhere

 

Disorders of eyelid, lacrimal system and orbit (H00–H06)

  H00 Hordeolum and chalazion

H00.0 Hordeolum and other deep inflammation of eyelid

Abscess

Furuncle Stye

of eyelid

H00.1 Chalazion

  H01 Other inflammation of eyelid

H01.0 Blepharitis

Excl.: blepharoconjunctivitis (H10.5)

H01.1 Noninfectious dermatoses of eyelid

Dermatitis:

• allergic

• contact

• eczematous

Discoid lupus erythematosus Xeroderma

of eyelid

H01.8 Other specified inflammation of eyelid H01.9 Inflammation of eyelid, unspecified

  H02 Other disorders of eyelid

Excl.: congenital malformations of eyelid (Q10.0–Q10.3)

H02.0 Entropion and trichiasis of eyelid H02.1 Ectropion of eyelid

H02.2 Lagophthalmos H02.3 Blepharochalasis H02.4 Ptosis of eyelid

H02.5 Other disorders affecting eyelid function

Ankyloblepharon Blepharophimosis Lid retraction

Excl.: blepharospasm (G24.5) tic (psychogenic) (F95.-) tic (psychogenic)

• organic (G25.6)

 

H02.6 Xanthelasma of eyelid

H02.7 Other degenerative disorders of eyelid and periocular area

Chloasma

Madarosis Vitiligo

of eyelid

H02.8 Other specified disorders of eyelid

Hypertrichosis of eyelid Retained foreign body in eyelid

H02.9 Disorder of eyelid, unspecified

  H03* Disorders of eyelid in diseases classified elsewhere

H03.0* Parasitic infestation of eyelid in diseases classified elsewhere

Dermatitis of eyelid due to Demodex species (B88.0†) Parasitic infestation of eyelid in:

• leishmaniasis (B55.-†)

• loiasis (B74.3†)

• onchocerciasis (B73†)

• phthiriasis (B85.3†)

H03.1* Involvement of eyelid in other infectious diseases classified elsewhere

Involvement of eyelid in:

• herpesviral [herpes simplex] infection (B00.5†)

• leprosy (A30.-†)

• molluscum contagiosum (B08.1†)

• tuberculosis (A18.4†)

• yaws (A66.-†)

• zoster (B02.3†)

H03.8* Involvement of eyelid in other diseases classified elsewhere

Involvement of eyelid in impetigo (L01.0†)

  H04 Disorders of lacrimal system

Excl.: congenital malformations of lacrimal system (Q10.4–Q10.6)

H04.0 Dacryoadenitis

Chronic enlargement of lacrimal gland

H04.1 Other disorders of lacrimal gland

Dacryops

Dry eye syndrome Lacrimal:

• cyst

• gland atrophy

H04.2 Epiphora

 

H04.3 es

Excl.: neonatal dacryocystitis (P39.1)

H04.4 Chronic inflammation of lacrimal passages

Dacryocystitis

Lacrimal:

• canaliculitis

• mucocele

chronic

H04.5 Stenosis and insufficiency of lacrimal passages

Dacryolith

Eversion of lacrimal punctum Stenosis of lacrimal:

• canaliculi

• duct

• sac

H04.6 Other changes in lacrimal passages

Lacrimal fistula

H04.8 Other disorders of lacrimal system H04.9 Disorder of lacrimal system, unspecified

  H05 Disorders of orbit

Excl.: congenital malformation of orbit (Q10.7)

H05.0 Acute inflammation of orbit

Abscess

Cellulitis Osteomyelitis Periostitis Tenonitis

of orbit

H05.1 Chronic inflammatory disorders of orbit

Granuloma of orbit

H05.2 Exophthalmic conditions

Displacement of globe (lateral) NOS

Haemorrhage

Oedema of orbit

H05.3 Deformity of orbit

Atrophy

Exostosis of orbit

H05.4 Enophthalmos

H05.5 Retained (old) foreign body following penetrating wound of orbit

Retrobulbar foreign body

 

H05.8 Other disorders of orbit

Cyst of orbit

H05.9 Disorder of orbit, unspecified

  H06* Disorders of lacrimal system and orbit in diseases classified elsewhere

H06.0* Disorders of lacrimal system in diseases classified elsewhere H06.1* Parasitic infestation of orbit in diseases classified elsewhere

Echinococcus infection of orbit (B67.-†)

Myiasis of orbit (B87.2†)

H06.2* Dysthyroid exophthalmos (E05.-†)

H06.3* Other disorders of orbit in diseases classified elsewhere

Disorders of conjunctiva (H10–H13)

  H10 Conjunctivitis

Excl.: keratoconjunctivitis (H16.2) H10.0 Mucopurulent conjunctivitis H10.1 Acute atopic conjunctivitis H10.2 Other acute conjunctivitis

H10.3 Acute conjunctivitis, unspecified

Excl.: ophthalmia neonatorum NOS (P39.1)

H10.4 Chronic conjunctivitis H10.5 Blepharoconjunctivitis H10.8 Other conjunctivitis

H10.9 Conjunctivitis, unspecified

  H11 Other disorders of conjunctiva

Excl.: keratoconjunctivitis (H16.2)

H11.0 Pterygium

Excl.: pseudopterygium (H11.8)

H11.1 Conjunctival degenerations and deposits

Conjunctival:

• argyrosis [argyria]

• concretions

• pigmentation

• xerosis NOS

H11.2 Conjunctival scars

Symblepharon

H11.3 Conjunctival haemorrhage

Subconjunctival haemorrhage

H11.4 Other conjunctival vascular disorders and cysts

Conjunctival:

• aneurysm

• hyperaemia

• oedema

H11.8 Other specified disorders of conjunctiva

Pseudopterygium

H11.9 Disorder of conjunctiva, unspecified

  H13* Disorders of conjunctiva in diseases classified elsewhere

H13.0* Filarial infection of conjunctiva (B74.-†)

H13.1* Conjunctivitis in infectious and parasitic diseases classified elsewhere

Conjunctivitis (due to):

• Acanthamoeba (B60.1†)

• adenoviral follicular (acute) (B30.1†)

• chlamydial (A74.0†)

• diphtheritic (A36.8†)

• gonococcal (A54.3†)

• haemorrhagic (acute)(epidemic) (B30.3†)

• herpesviral [herpes simplex] (B00.5†)

• meningococcal (A39.8†)

• Newcastle (B30.8†)

• zoster (B02.3†)

H13.2* Conjunctivitis in other diseases classified elsewhere H13.3* Ocular pemphigoid (L12.-†)

H13.8* Other disorders of conjunctiva in diseases classified elsewhere

Disorders of sclera, cornea, iris and ciliary body (H15–H22)

  H15 Disorders of sclera

H15.0 Scleritis

H15.1 Episcleritis

 

H15.8 Other disorders of sclera

Equatorial staphyloma Scleral ectasia

Excl.:  degenerative myopia (H44.2)

H15.9 Disorder of sclera, unspecified

  H16 Keratitis

H16.0 Corneal ulcer

Ulcer:

• corneal:

– NOS

– central

– marginal

– perforated

– ring

– with hypopyon

• Mooren

H16.1 Other superficial keratitis without conjunctivitis

Keratitis:

• areolar

• filamentary

• nummular

• stellate

• striate

• superficial punctate Photokeratitis

Snow blindness

H16.2 Keratoconjunctivitis

Keratoconjunctivitis:

• NOS

• exposure

• neurotrophic

• phlyctenular Ophthalmia nodosa

Superficial keratitis with conjunctivitis

H16.3 Interstitial and deep keratitis H16.4 Corneal neovascularization

Ghost vessels (corneal)

Pannus (corneal)

H16.8 Other keratitis

H16.9 Keratitis, unspecified

 

  H17 Corneal scars and opacities

H17.0 Adherent leukoma

H17.1 Other central corneal opacity H17.8 Other corneal scars and opacities

H17.9 Corneal scar and opacity, unspecified

  H18 Other disorders of cornea

H18.0 Corneal pigmentations and deposits

Haematocornea Kayser–Fleischer ring Krukenberg spindle Staehli line

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

H18.1 Bullous keratopathy H18.2 Other corneal oedema

H18.3 Changes in corneal membranes

Fold

Rupture in Descemet’s membrane

H18.4 Corneal degeneration

Arcus senilis Band keratopathy

Excl.: Mooren ulcer (H16.0)

H18.5 Hereditary corneal dystrophies

Dystrophy:

• corneal:

– epithelial

– granular

– lattice

– macular

• Fuchs

H18.6 Keratoconus

H18.7 Other corneal deformities

Corneal:

• ectasia

• staphyloma Descemetocele

Excl.: congenital malformations of cornea (Q13.3–Q13.4)

 

H18.8 ea

H18.9 Disorder of cornea, unspecified

  H19* Disorders of sclera and cornea in diseases classified elsewhere

H19.0* Scleritis and episcleritis in diseases classified elsewhere

Syphilitic episcleritis (A52.7†) Tuberculous episcleritis (A18.5†) Zoster scleritis (B02.3†)

H19.1* Herpesviral keratitis and keratoconjunctivitis (B00.5†)

Dendritic and disciform keratitis

H19.2* Keratitis and keratoconjunctivitis in other infectious and parasitic diseases classified elsewhere

Epidemic keratoconjunctivitis (B30.0†)

Keratitis and keratoconjunctivitis (interstitial) in:

• acanthamoebiasis (B60.1†)

• measles (B05.8†)

• syphilis (A50.3†)

• tuberculosis (A18.5†)

• zoster (B02.3†)

H19.3* Keratitis and keratoconjunctivitis in other diseases classified elsewhere

Keratoconjunctivitis sicca (M35.0†)

H19.8* Other disorders of sclera and cornea in diseases classified elsewhere

Keratoconus in Down syndrome (Q90.-†)

  H20 Iridocyclitis

H20.0 Acute and subacute iridocyclitis

Anterior uveitis

Cyclitis Iritis

acute, recurrent or subacute of cornea

H20.1 Chronic iridocyclitis H20.2 Lens-induced iridocyclitis H20.8 Other iridocyclitis

H20.9 Iridocyclitis, unspecified

 

  H21 Other disorders of iris and ciliary body

Excl.: sympathetic uveitis (H44.1)

H21.0 Hyphaema

Excl.: traumatic hyphaema (S05.1)

H21.1 Other vascular disorders of iris and ciliary body

Neovascularization of iris or ciliary body Rubeosis of iris

H21.2 Degeneration of iris and ciliary body

Degeneration of:

• iris (pigmentary)

• pupillary margin Iridoschisis

Iris atrophy (essential)(progressive) Miotic pupillary cyst

Translucency of iris

H21.3 Cyst of iris, ciliary body and anterior chamber

Cyst of iris, ciliary body or anterior chamber:

• NOS

• exudative

• implantation

• parasitic

Excl.: miotic pupillary cyst (H21.2)

H21.4 Pupillary membranes

Iris bombé Pupillary:

• occlusion

• seclusion

H21.5 Other adhesions and disruptions of iris and ciliary body

Goniosynechiae Iridodialysis

Recession, chamber angle Synechiae (iris):

• NOS

• anterior

• posterior

Excl.: corectopia (Q13.2)

H21.8 Other specified disorders of iris and ciliary body H21.9 Disorder of iris and ciliary body, unspecified

 

  H22* Disorders of iris and ciliary body in diseases classified elsewhere

H22.0* Iridocyclitis in infectious and parasitic diseases classified elsewhere

Iridocyclitis in:

• gonococcal infection (A54.3†)

• herpesviral [herpes simplex] infection (B00.5†)

• syphilis (secondary) (A51.4†)

• tuberculosis (A18.5†)

• zoster (B02.3†)

H22.1* Iridocyclitis in other diseases classified elsewhere

Iridocyclitis in:

• ankylosing spondylitis (M45†)

• sarcoidosis (D86.8†)

H22.8* Other disorders of iris and ciliary body in diseases classified elsewhere

Disorders of lens (H25–H28)

  H25 Senile cataract

Excl.: capsular glaucoma with pseudoexfoliation of lens (H40.1)

H25.0 Senile incipient cataract

Senile cataract:

• coronary

• cortical

• punctate

Subcapsular polar senile cataract (anterior)(posterior) Water clefts

H25.1 Senile nuclear cataract

Cataracta brunescens Nuclear sclerosis cataract

H25.2 Senile cataract, morgagnian type

Senile hypermature cataract

H25.8 Other senile cataract

Combined forms of senile cataract

H25.9 Senile cataract, unspecified

 

  H26 Other cataract

Excl.: congenital cataract (Q12.0)

H26.0 Infantile, juvenile and presenile cataract H26.1 Traumatic cataract

Use additional external cause code (Chapter XX), if desired, to identify cause.

H26.2 Complicated cataract

• Cataract in chronic iridocyclitis

• Cataract secondary to ocular disorders

• Glaucomatous flecks (subcapsular)

H26.3 Drug-induced cataract

Use additional external cause code (Chapter XX), if desired, to identify drug.

H26.4 After-cataract

• Secondary cataract

• Soemmerring ring

H26.8 Other specified cataract H26.9 Cataract, unspecified

  H27 Other disorders of lens

Excl.: congenital lens malformations (Q12.-)

mechanical complications of intraocular lens (T85.2) pseudophakia (Z96.1)

H27.0 Aphakia

H27.1 Dislocation of lens

H27.8 Other specified disorders of lens H27.9 Disorder of lens, unspecified

  H28* Cataract and other disorders of lens in diseases classified elsewhere

H28.0* Diabetic cataract (E10–E14 with common fourth character .3†)

H28.1* Cataract in other endocrine, nutritional and metabolic diseases

Cataract in hypoparathyroidism (E20.-†) Malnutrition–dehydration cataract (E40–E46†)

H28.2* Cataract in other diseases classified elsewhere

Myotonic cataract (G71.1†)

H28.8* Other disorders of lens in diseases classified elsewhere

 

Disorders of choroid and retina (H30–H36)

  H30 Chorioretinal inflammation

H30.0 Focal chorioretinal inflammation

Focal:

• chorioretinitis

• choroiditis

• retinitis

• retinochoroiditis

H30.1 Disseminated chorioretinal inflammation

Disseminated:

• chorioretinitis

• choroiditis

• retinitis

• retinochoroiditis

Excl.: exudative retinopathy (H35.0)

H30.2 Posterior cyclitis

Pars planitis

H30.8 Other chorioretinal inflammations

Harada disease

H30.9 Chorioretinal inflammation, unspecified

Chorioretinitis

Choroiditis Retinitis Retinochoroiditis

NOS

  H31 Other disorders of choroid

H31.0 Chorioretinal scars

Macula scars of posterior pole (postinflammatory)(post-traumatic) Solar retinopathy

H31.1 Choroidal degeneration

Atrophy

Sclerosis of choroid

Excl.: angioid streaks (H35.3)

H31.2 Hereditary choroidal dystrophy

Choroideremia

Dystrophy, choroidal (central areolar)(generalized)(peripapillary) Gyrate atrophy, choroid

Excl.: ornithinaemia (E72.4)

 

H31.3 Choroidal haemorrhage and rupture

Choroidal haemorrhage:

• NOS

• expulsive

H31.4 Choroidal detachment

H31.8 Other specified disorders of choroid

Choroidal neovascularization

H31.9 Disorder of choroid, unspecified

  H32* Chorioretinal disorders in diseases classified elsewhere

H32.0* Chorioretinal inflammation in infectious and parasitic diseases classified elsewhere

Chorioretinitis:

• syphilitic, late (A52.7†)

• toxoplasma (B58.0†)

• tuberculous (A18.5†)

H32.8* Other chorioretinal disorders in diseases classified elsewhere

Albuminuric retinitis (N18.5†) Renal retinitis (N18.5†)

  H33 Retinal detachments and breaks

Excl.: detachment of retinal pigment epithelium (H35.7)

H33.0 Retinal detachment with retinal break

Rhegmatogenous retinal detachment

H33.1 Retinoschisis and retinal cysts

Cyst of ora serrata

Parasitic cyst of retina NOS Pseudocyst of retina

Excl.: congenital retinoschisis (Q14.1) microcystoid degeneration of retina (H35.4)

H33.2 Serous retinal detachment

Retinal detachment:

• NOS

• without retinal break

Excl.: central serous chorioretinopathy (H35.7)

H33.3 Retinal breaks without detachment

Horseshoe tear

Round hole of retina, without detachment

Operculum Retinal break NOS

Excl.: chorioretinal scars after surgery for detachment (H59.8) peripheral retinal degeneration without break (H35.4)

 

H33.4 Traction detachment of retina

Proliferative vitreo-retinopathy with retinal detachment

H33.5 Other retinal detachments

  H34 Retinal vascular occlusions

Excl.:  amaurosis fugax (G45.3) H34.0 Transient retinal artery occlusion H34.1 Central retinal artery occlusion

H34.2 Other retinal artery occlusions

Hollenhorst’s plaque Retinal:

• artery occlusion:

– branch

– partial

• microembolism

H34.8 Other retinal vascular occlusions

Retinal vein occlusion:

• central

• incipient

• partial

• tributary

H34.9 Retinal vascular occlusion, unspecified

  H35 Other retinal disorders

H35.0 Background retinopathy and retinal vascular changes

Changes in retinal vascular appearance Retinal:

• micro-aneurysms

• neovascularization

• perivasculitis

• varices

• vascular sheathing

• vasculitis Retinopathy:

• NOS

• background NOS

• Coats

• exudative

• hypertensive

H35.1 Retinopathy of prematurity

Retrolental fibroplasia

H35.2 Other proliferative retinopathy

Proliferative vitreo-retinopathy

Excl.: proliferative vitreo-retinopathy with retinal detachment (H33.4)

 

H35.3 pole

Kuhnt–Junius degeneration

Senile macular degeneration (atrophic)(exudative) Toxic maculopathy

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

H35.4 Peripheral retinal degeneration

Degeneration, retina:

• NOS

• lattice

• microcystoid

• palisade

• paving stone

• reticular

Excl.:  with retinal break (H33.3)

H35.5 Hereditary retinal dystrophy

Dystrophy:

• retinal (albipunctate)(pigmentary)(vitelliform)

• tapetoretinal

• vitreoretinal Retinitis pigmentosa Stargardt’s disease

H35.6 Retinal haemorrhage H35.7 Separation of retinal layers

Central serous chorioretinopathy

Detachment of retinal pigment epithelium H35.8 Other specified retinal disorders H35.9 Retinal disorder, unspecified

  H36* Retinal disorders in diseases classified elsewhere

H36.0* Diabetic retinopathy (E10–E14 with common fourth character .3†) H36.8* Other retinal disorders in diseases classified elsewhere

Atherosclerotic retinopathy (I70.8†)

Proliferative sickle-cell retinopathy (D57.-†) Retinal dystrophy in lipid storage disorders (E75.-†)

 

Glaucoma (H40–H42)

  H40 Glaucoma

Excl.: absolute glaucoma (H44.5) congenital glaucoma (Q15.0)

traumatic glaucoma due to birth injury (P15.3)

H40.0 Glaucoma suspect

Ocular hypertension

H40.1 Primary open-angle glaucoma

Glaucoma (primary)(residual stage):

• capsular with pseudoexfoliation of lens

• chronic simple

• low-tension

• pigmentary

H40.2 Primary angle-closure glaucoma

Angle-closure glaucoma (primary)(residual stage):

• acute

• chronic

• intermittent

H40.3 Glaucoma secondary to eye trauma

Use additional code, if desired, to identify cause.

H40.4 Glaucoma secondary to eye inflammation

Use additional code, if desired, to identify cause.

H40.5 Glaucoma secondary to other eye disorders

Use additional code, if desired, to identify cause.

H40.6 Glaucoma secondary to drugs

Use additional external cause code (Chapter XX), if desired, to identify drug.

H40.8 Other glaucoma

H40.9 Glaucoma, unspecified

  H42* Glaucoma in diseases classified elsewhere

H42.0* Glaucoma in endocrine, nutritional and metabolic diseases

Glaucoma in:

• amyloidosis (E85.-†)

• Lowe syndrome (E72.0†)

H42.8* Glaucoma in other diseases classified elsewhere

Glaucoma in onchocerciasis (B73†)

 

Disorders of vitreous body and globe (H43–H45)

  H43 Disorders of vitreous body

H43.0 Vitreous prolapse

Excl.: vitreous syndrome following cataract surgery (H59.0)

H43.1 Vitreous haemorrhage

H43.2 Crystalline deposits in vitreous body H43.3 Other vitreous opacities

Vitreous membranes and strands

H43.8 Other disorders of vitreous body

Vitreous:

• degeneration

• detachment

Excl.: proliferative vitreo-retinopathy with retinal detachment (H33.4)

H43.9 Disorder of vitreous body, unspecified

  H44 Disorders of globe

Incl.: disorders affecting multiple structures of eye

H44.0 Purulent endophthalmitis

Panophthalmitis Vitreous abscess

H44.1 Other endophthalmitis

Parasitic endophthalmitis NOS Sympathetic uveitis

H44.2 Degenerative myopia

H44.3 Other degenerative disorders of globe

Chalcosis Siderosis of eye

H44.4 Hypotony of eye

H44.5 Degenerated conditions of globe

Absolute glaucoma Atrophy of globe Phthisis bulbi

 

H44.6 Retained (old) intraocular foreign body, magnetic

Retained (old) magnetic foreign body (in):

• anterior chamber

• ciliary body

• iris

• lens

• posterior wall of globe

• vitreous body

H44.7 Retained (old) intraocular foreign body, nonmagnetic

Retained (nonmagnetic)(old) foreign body (in):

• anterior chamber

• ciliary body

• iris

• lens

• posterior wall of globe

• vitreous body

H44.8 Other disorders of globe

Haemophthalmos Luxation of globe

H44.9 Disorder of globe, unspecified

  H45* Disorders of vitreous body and globe in diseases classified elsewhere

H45.0* Vitreous haemorrhage in diseases classified elsewhere H45.1* Endophthalmitis in diseases classified elsewhere

Endophthalmitis in:

• cysticercosis (B69.1†)

• onchocerciasis (B73†)

• toxocariasis (B83.0†)

H45.8* Other disorders of vitreous body and globe in diseases classified elsewhere

 

Disorders of optic nerve and visual pathways (H46–H48)

  H46 Optic neuritis

Incl.: optic

• neuropathy, except ischaemic

• papillitis

retrobulbar neuritis NOS

Excl.: ischaemic optic neuropathy (H47.0) neuromyelitis optica [Devic] (G36.0)

  H47 Other disorders of optic [2nd] nerve and visual pathways

H47.0 Disorders of optic nerve, not elsewhere classified

Compression of optic nerve Haemorrhage in optic nerve sheath Ischaemic optic neuropathy

H47.1 Papilloedema, unspecified H47.2 Optic atrophy

Temporal pallor of optic disc

H47.3 Other disorders of optic disc Drusen of optic disc Pseudopapilloedema

H47.4 Disorders of optic chiasm

H47.5 Disorders of other visual pathways

Disorders of optic tracts, geniculate nuclei and optic radiations

H47.6 Disorders of visual cortex

H47.7 Disorder of visual pathways, unspecified

  H48* Disorders of optic [2nd] nerve and visual pathways in diseases classified elsewhere

H48.0* Optic atrophy in diseases classified elsewhere

Optic atrophy in late syphilis (A52.1†)

H48.1* Retrobulbar neuritis in diseases classified elsewhere

Retrobulbar neuritis in:

• late syphilis (A52.1†)

• meningococcal infection (A39.8†)

• multiple sclerosis (G35†)

H48.8* Other disorders of optic nerve and visual pathways in diseases classified elsewhere

Disorders of ocular muscles, binocular movement, accommodation and refraction

(H49–H52)

Excl.: nystagmus and other irregular eye movements (H55)

  H49 Paralytic strabismus

Excl.: ophthalmoplegia:

• internal (H52.5)

• internuclear (H51.2)

• progressive supranuclear (G23.1) H49.0 Third [oculomotor] nerve palsy H49.1 Fourth [trochlear] nerve palsy H49.2 Sixth [abducent] nerve palsy

H49.3 Total (external) ophthalmoplegia

H49.4 Progressive external ophthalmoplegia H49.8 Other paralytic strabismus

External ophthalmoplegia NOS Kearns–Sayre syndrome

H49.9 Paralytic strabismus, unspecified

  H50 Other strabismus

H50.0 Convergent concomitant strabismus

Esotropia (alternating)(monocular), except intermittent

H50.1 Divergent concomitant strabismus

Exotropia (alternating)(monocular), except intermittent

H50.2 Vertical strabismus Hypertropia Hypotropia

H50.3 Intermittent heterotropia

Intermittent:

• esotropia

• exotropia

(alternating)(monocular)

H50.4 Other and unspecified heterotropia Concomitant strabismus NOS Cyclotropia

Microtropia Monofixation syndrome

 

H50.5 Heterophoria Alternating hyperphoria Esophoria

Exophoria

H50.6 Mechanical strabismus

Brown’s sheath syndrome Strabismus due to adhesions

Traumatic limitation of duction of eye muscle

H50.8 Other specified strabismus

Duane syndrome

H50.9 Strabismus, unspecified

  H51 Other disorders of binocular movement

H51.0 Palsy of conjugate gaze

H51.1 Convergence insufficiency and excess H51.2 Internuclear ophthalmoplegia

H51.8 Other specified disorders of binocular movement H51.9 Disorder of binocular movement, unspecified

  H52 Disorders of refraction and accommodation

H52.0 Hypermetropia

H52.1 Myopia

Excl.: degenerative myopia (H44.2)

H52.2 Astigmatism

H52.3 Anisometropia and aniseikonia H52.4 Presbyopia

H52.5 Disorders of accommodation

Internal ophthalmoplegia (complete)(total)

Paresis

Spasm of accommodation

H52.6 Other disorders of refraction H52.7 Disorder of refraction, unspecified

 

Visual disturbances and blindness (H53–H54)

  H53 Visual disturbances

H53.0 Amblyopia ex anopsia

Amblyopia:

• anisometropic

• deprivation

• strabismic

H53.1 Subjective visual disturbances

Asthenopia Day blindness Hemeralopia

Metamorphopsia Photophobia Scintillating scotoma Sudden visual loss Visual halos

Excl.: visual hallucinations (R44.1)

H53.2 Diplopia

Double vision

H53.3 Other disorders of binocular vision

Abnormal retinal correspondence Fusion with defective stereopsis

Simultaneous visual perception without fusion Suppression of binocular vision

H53.4 Visual field defects

Enlarged blind spot

Generalized contraction of visual field Hemianop(s)ia (heteronymous)(homonymous) Quadrant anop(s)ia

Scotoma:

• arcuate

• Bjerrum

• central

• ring

 

H53.5 Colour vision deficiencies

Achromatopsia

Acquired colour vision deficiency Colour blindness

Deuteranomaly Deuteranopia Protanomaly Protanopia Tritanomaly Tritanopia

Excl.: day blindness (H53.1)

H53.6 Night blindness

Excl.: due to vitamin A deficiency (E50.5)

H53.8 Other visual disturbances H53.9 Visual disturbance, unspecified

  H54 Visual impairment including blindness (binocular or monocular)

Note: For definition of visual impairment categories see table below.

Excl.: amaurosis fugax (G45.3)

H54.0 Blindness, binocular

Visual impairment categories 3,4,5 in both eyes

H54.1 Severe visual impairment, binocular

Visual impairment category 2

H54.2 Moderate visual impairment, binocular

Visual impairment category 1

H54.3 Mild or no visual impairment, binocular

Visual impairment category 0

H54.4 Blindness, monocular

Visual impairment categories 3, 4, 5 in one eye and categories 0, 1, 2 or 9 in the other eye

H54.5 Severe visual impairment, monocular

Visual impairment category 2 in one eye and categories 0, 1 or 9 in other eye

H54.6 Moderate visual impairment, monocular

Visual impairment category 1 in one eye and categories 0 or 9 in other eye

H54.9 Unspecified visual impairment (binocular)

Visual impairment category 9

 

The table below gives a classification of severity of visual impairment recommended by the Resolution of the International Council of Ophthalmology (2002) and the Recommendations of the WHO Consultation on ‘‘Development of Standards for Characterization of Vision Loss and Visual Functioning’’ (September 2003)

For characterizing visual impairment for codes H54.0–H54.3, visual acuity should be measured with both eyes open, with presenting correction if any. For characterizing visual impairment for codes H54.4–H54.6, visual acuity should be measured monocularly with presenting correction if any.

If the extent of the visual field is taken into account, patients with a  visual field of the better eye no greater than 10° in radius around central fixation should be placed under category 3. For monocular blindness (H54.4), this degree of field loss would apply to the affected eye.

Category Presenting distance visual acuity

Worse than: Equal to or better than:

0 Mild or no visual impairment 6/18

3/10 (0.3)

20/70

1 Moderate visual impairment 6/18

3/10 (0.3)

20/70 6/60

1/10 (0.1)

20/200

2 Severe visual impairment 6/60

1/10 (0.1)

20/200 3/60

1/20 (0.05)

20/400

3/60 1/60*

3 Blindness 1/20 (0.05)

20/400 1/50 (0.02)

5/300 (20/1200)

1/60*

4 Blindness 1/50 (0.02)

5/300 (20/1200) light perception

5 Blindness

No light perception

9 Undetermined or unspecified

* or counts fingers (CF) at 1m.

 

Note: The term visual impairment in category H54 comprises category 0 for mild or no visual impairment, category 1 for moderate visual impairment, category 2 for severe visual impairment, categories 3, 4 and 5 for blindness and category 9 for unqualified visual impairment. The term ‘low vision’ included in the previous revision has been replaced by categories 1 and 2, to avoid confusion with those requiring low vision care.

Other disorders of eye and adnexa (H55–H59)

  H55 Nystagmus and other irregular eye movements

Incl.: nystagmus:

• NOS

• congenital

• deprivation

• dissociated

• latent

  H57 Other disorders of eye and adnexa

H57.0 Anomalies of pupillary function H57.1 Ocular pain

H57.8 Other specified disorders of eye and adnexa H57.9 Disorder of eye and adnexa, unspecified

  H58* Other disorders of eye and adnexa in diseases classified elsewhere

H58.0* Anomalies of pupillary function in diseases classified elsewhere

Argyll Robertson phenomenon or pupil, syphilitic (A52.1†)

H58.1* Visual disturbances in diseases classified elsewhere H58.8* Other specified disorders of eye and adnexa in diseases

classified elsewhere

Syphilitic oculopathy NEC:

• congenital:

– early (A50.0†)

– late (A50.3†)

• early (secondary) (A51.4†)

• late (A52.7†)

 

  H59 Postprocedural disorders of eye and adnexa, not elsewhere classified

Excl.: mechanical complication of:

• intraocular lens (T85.2)

• other ocular prosthetic devices, implants and grafts (T85.3) pseudophakia (Z96.1)

H59.0 Keratopathy (bullous aphakic) following cataract surgery

Vitreous (touch) syndrome Vitreal corneal syndrome

H59.8 Other postprocedural disorders of eye and adnexa

Bleb–associated endophthalmitis

Chorioretinal scars after surgery for detachment Inflammation (infection) of postprocedural bleb Postprocedural blebitis

H59.9 Postprocedural disorder of eye and adnexa, unspecified

CHAPTER VIII

Diseases of the ear and mastoid process (H60–H95)

Excl.: certain conditions originating in the perinatal period (P00–P96) certain infectious and parasitic diseases (A00–B99)

complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90)

injury, poisoning and certain other consequences of external causes (S00–T98)

neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

H60–H62 Diseases of external ear

H65–H75 Diseases of middle ear and mastoid H80–H83 Diseases of inner ear

H90–H95 Other disorders of ear

Asterisk categories for this chapter are provided as follows:

H62* Disorders of external ear in diseases classified elsewhere H67* Otitis media in diseases classified elsewhere

H75* Other disorders of middle ear and mastoid in diseases classified elsewhere H82* Vertiginous syndromes in diseases classified elsewhere

H94* Other disorders of ear in diseases classified elsewhere

 

Diseases of external ear (H60–H62)

  H60 Otitis externa

H60.0 Abscess of external ear

Boil

Carbuncle Furuncle

of auricle or external auditory canal

H60.1 Cellulitis of external ear

Cellulitis of:

• auricle

• external auditory canal

H60.2 Malignant otitis externa H60.3 Other infective otitis externa

Otitis externa:

• diffuse

• haemorrhagic Swimmer’s ear

H60.4 Cholesteatoma of external ear

Keratosis obturans of external ear (canal)

H60.5 Acute otitis externa, noninfective

Acute otitis externa:

• NOS

• actinic

• chemical

• contact

• eczematoid

• reactive

H60.8 Other otitis externa

Chronic otitis externa NOS

H60.9 Otitis externa, unspecified

  H61 Other disorders of external ear

H61.0 Perichondritis of external ear Chondrodermatitis nodularis chronica helicis Perichondritis of:

• auricle

• pinna

 

H61.1 Noninfective disorders of pinna

Acquired deformity of:

• auricle

• pinna

Excl.: cauliflower ear (M95.1)

H61.2 Impacted cerumen

Wax in ear

H61.3 Acquired stenosis of external ear canal

Collapse of external ear canal

H61.8 Other specified disorders of external ear

Exostosis of external canal

H61.9 Disorder of external ear, unspecified

  H62* Disorders of external ear in diseases classified elsewhere

H62.0* Otitis externa in bacterial diseases classified elsewhere

Otitis externa in erysipelas (A46†)

H62.1* Otitis externa in viral diseases classified elsewhere

Otitis externa in:

• herpesviral [herpes simplex] infection (B00.1†)

• zoster (B02.8†)

H62.2* Otitis externa in mycoses

Otitis externa in:

• aspergillosis (B44.8†)

• candidiasis (B37.2†) Otomycosis NOS (B36.9†)

H62.3* Otitis externa in other infectious and parasitic diseases classified elsewhere

H62.4* Otitis externa in other diseases classified elsewhere

Otitis externa in impetigo (L01.-†)

H62.8* Other disorders of external ear in diseases classified elsewhere

 

Diseases of middle ear and mastoid (H65–H75)

  H65 Nonsuppurative otitis media

Incl.: with myringitis

Use additional code (H72.-), if desired, to identify presence of perforated tympanic membrane.

H65.0 Acute serous otitis media

Acute and subacute secretory otitis media

H65.1 Other acute nonsuppurative otitis media

Otitis media, acute and subacute:

• allergic (mucoid)(sanguinous)(serous)

• mucoid

• nonsuppurative NOS

• sanguinous

• seromucinous

Excl.: otitic barotrauma (T70.0)

otitis media (acute) NOS (H66.9)

H65.2 Chronic serous otitis media

Chronic tubotympanal catarrh

H65.3 Chronic mucoid otitis media

Glue ear

Otitis media, chronic:

• mucinous

• secretory

• transudative

Excl.: adhesive middle ear disease (H74.1)

H65.4 Other chronic nonsuppurative otitis media

Otitis media, chronic:

• allergic

• exudative

• nonsuppurative NOS

• seromucinous

• with effusion (nonpurulent)

H65.9 Nonsuppurative otitis media, unspecified

Otitis media:

• allergic

• catarrhal

• exudative

• mucoid

• secretory

• seromucinous

• serous

• transudative

 

410

 

• with effusion (nonpurulent)

 

  H66 Suppurative and unspecified otitis media

Incl.: with myringitis

Use additional code (H72.-), if desired, to identify presence of perforated tympanic membrane.

H66.0 Acute suppurative otitis media

H66.1 Chronic tubotympanic suppurative otitis media

Benign chronic suppurative otitis media Chronic tubotympanic disease

H66.2 Chronic atticoantral suppurative otitis media

Chronic atticoantral disease

H66.3 Other chronic suppurative otitis media

Chronic suppurative otitis media NOS

H66.4 Suppurative otitis media, unspecified

Purulent otitis media NOS

H66.9 Otitis media, unspecified

Otitis media:

• NOS

• acute NOS

• chronic NOS

  H67* Otitis media in diseases classified elsewhere

H67.0* Otitis media in bacterial diseases classified elsewhere

Otitis media in:

• scarlet fever (A38†)

• tuberculosis (A18.6†)

H67.1* Otitis media in viral diseases classified elsewhere

Otitis media in:

• influenza:

– seasonal virus identified (J10.8†)

– virus not identified (J11.8†)

– zoonotic or pandemic influenza virus identified (J09†)

• measles (B05.3†)

H67.8* Otitis media in other diseases classified elsewhere

  H68 Eustachian salpingitis and obstruction

H68.0 Eustachian salpingitis

H68.1 Obstruction of Eustachian tube

Compression

Stenosis Stricture

of Eustachian tube

 

  H69 Other disorders of Eustachian tube

H69.0 Patulous Eustachian tube

H69.8 Other specified disorders of Eustachian tube H69.9 Eustachian tube disorder, unspecified

  H70 Mastoiditis and related conditions

H70.0 Acute mastoiditis

Abscess

Empyema of mastoid

H70.1 Chronic mastoiditis

Caries

Fistula of mastoid

H70.2 Petrositis

Inflammation of petrous bone (acute)(chronic) H70.8 Other mastoiditis and related conditions H70.9 Mastoiditis, unspecified

  H71 Cholesteatoma of middle ear

Incl.: cholesteatoma tympani

Excl.: cholesteatoma of external ear (H60.4)

recurrent cholesteatoma of postmastoidectomy cavity (H95.0)

  H72 Perforation of tympanic membrane

Incl.: perforation of ear drum:

• persistent post-traumatic

• postinflammatory

Excl.: traumatic rupture of ear drum (S09.2) H72.0 Central perforation of tympanic membrane H72.1 Attic perforation of tympanic membrane

Perforation of pars flaccida

H72.2 Other marginal perforations of tympanic membrane H72.8 Other perforations of tympanic membrane

H72.9 Perforation of tympanic membrane, unspecified

 

  H73 Other disorders of tympanic membrane

H73.0 Acute myringitis

Acute tympanitis Bullous myringitis

Excl.: with otitis media (H65–H66)

H73.1 Chronic myringitis

Chronic tympanitis

Excl.: with otitis media (H65–H66)

H73.8 Other specified disorders of tympanic membrane H73.9 Disorder of tympanic membrane, unspecified

  H74 Other disorders of middle ear and mastoid

H74.0 Tympanosclerosis

H74.1 Adhesive middle ear disease

Adhesive otitis

Excl.: glue ear (H65.3)

H74.2 Discontinuity and dislocation of ear ossicles H74.3 Other acquired abnormalities of ear ossicles

H74.4 Polyp of middle ear

H74.8 Other specified disorders of middle ear and mastoid H74.9 Disorder of middle ear and mastoid, unspecified

  H75* Other disorders of middle ear and mastoid in diseases classified elsewhere

H75.0* Mastoiditis in infectious and parasitic diseases classified elsewhere

Tuberculous mastoiditis (A18.0†)

H75.8* Other specified disorders of middle ear and mastoid in diseases classified elsewhere

 

Diseases of inner ear (H80–H83)

  H80 Otosclerosis

Incl.: otospongiosis

H80.0 Otosclerosis involving oval window, nonobliterative H80.1 Otosclerosis involving oval window, obliterative H80.2 Cochlear otosclerosis

Otosclerosis involving:

• otic capsule

• round window

H80.8 Other otosclerosis

H80.9 Otosclerosis, unspecified

  H81 Disorders of vestibular function

Excl.: vertigo:

• NOS (R42)

• epidemic (A88.1)

H81.0 Ménière disease

Labyrinthine hydrops Ménière syndrome or vertigo

H81.1 Benign paroxysmal vertigo H81.2 Vestibular neuronitis

H81.3 Other peripheral vertigo

Lermoyez syndrome Vertigo:

• aural

• otogenic

• peripheral NOS

H81.4 Vertigo of central origin

Central positional nystagmus

H81.8 Other disorders of vestibular function H81.9 Disorder of vestibular function, unspecified

Vertiginous syndrome NOS

  H82* Vertiginous syndromes in diseases classified elsewhere

 

  H83 Other diseases of inner ear

H83.0 Labyrinthitis

H83.1 Labyrinthine fistula H83.2 Labyrinthine dysfunction

H83.3 Noise effects on inner ear

Acoustic trauma

Noise-induced hearing loss

H83.8 Other specified diseases of inner ear H83.9 Disease of inner ear, unspecified

Other disorders of ear (H90–H95)

  H90 Conductive and sensorineural hearing loss

Incl.: congenital deafness

Excl.: deaf mutism NEC (H91.3) deafness NOS (H91.9) hearing loss:

• NOS (H91.9)

• noise-induced (H83.3)

• ototoxic (H91.0)

• sudden (idiopathic) (H91.2)

H90.0 Conductive hearing loss, bilateral

H90.1 Conductive hearing loss, unilateral with unrestricted hearing on the contralateral side

H90.2 Conductive hearing loss, unspecified

Conductive deafness NOS

H90.3 Sensorineural hearing loss, bilateral

H90.4 Sensorineural hearing loss, unilateral with unrestricted hearing on the contralateral side

 

H90.5 Sensorineural hearing loss, unspecified

Congenital deafness NOS

Hearing loss:

• central

• neural

• perceptive

• sensory

NOS

Sensorineural deafness NOS

H90.6 Mixed conductive and sensorineural hearing loss, bilateral H90.7 Mixed conductive and sensorineural hearing loss, unilateral

with unrestricted hearing on the contralateral side

H90.8 Mixed conductive and sensorineural hearing loss, unspecified

  H91 Other hearing loss

Excl.: abnormal auditory perception (H93.2) hearing loss as classified in H90.- impacted cerumen (H61.2)

noise-induced hearing loss (H83.3) psychogenic deafness (F44.6) transient ischaemic deafness (H93.0)

H91.0 Ototoxic hearing loss

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

H91.1 Presbycusis

Presbyacusia

H91.2 Sudden idiopathic hearing loss

Sudden hearing loss NOS

H91.3 Deaf mutism, not elsewhere classified H91.8 Other specified hearing loss

H91.9 Hearing loss, unspecified

Deafness:

• NOS

• high frequency

• low frequency

  H92 Otalgia and effusion of ear

H92.0 Otalgia

H92.1 Otorrhoea

Excl.: leakage of cerebrospinal fluid through ear (G96.0)

H92.2 Otorrhagia

Excl.: traumatic otorrhagia – code by type of injury

 

  H93 Other disorders of ear, not elsewhere classified

H93.0 Degenerative and vascular disorders of ear

Transient ischaemic deafness

Excl.: presbycusis (H91.1)

H93.1 Tinnitus

H93.2 Other abnormal auditory perceptions

Auditory recruitment Diplacusis Hyperacusis

Temporary auditory threshold shift

Excl.: auditory hallucinations (R44.0)

H93.3 Disorders of acoustic nerve

Disorder of 8th cranial nerve

H93.8 Other specified disorders of ear H93.9 Disorder of ear, unspecified

  H94* Other disorders of ear in diseases classified elsewhere

H94.0* Acoustic neuritis in infectious and parasitic diseases classified elsewhere

Acoustic neuritis in syphilis (A52.1†)

H94.8* Other specified disorders of ear in diseases classified elsewhere

  H95 Postprocedural disorders of ear and mastoid process, not elsewhere classified

H95.0 Recurrent cholesteatoma of postmastoidectomy cavity H95.1 Other disorders following mastoidectomy

H95.8 Other postprocedural disorders of ear and mastoid process H95.9 Postprocedural disorder of ear and mastoid process,

unspecified

CHAPTER IX

Diseases of the circulatory system (I00–I99)

Excl.: certain conditions originating in the perinatal period (P00–P96) certain infectious and parasitic diseases (A00–B99)

complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90)

injury, poisoning and certain other consequences of external causes (S00–T98)

neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

systemic connective tissue disorders (M30–M36)

transient cerebral ischaemic attacks and related syndromes (G45.-)

This chapter contains the following blocks:

I00–I02 Acute rheumatic fever

I05–I09 Chronic rheumatic heart diseases I10–I15 Hypertensive diseases

I20–I25 Ischaemic heart diseases

I26–I28 Pulmonary heart disease and diseases of pulmonary circulation I30–I52 Other forms of heart disease

I60–I69 Cerebrovascular diseases

I70–I79 Diseases of arteries, arterioles and capillaries

I80–I89 Diseases of veins, lymphatic vessels and lymph nodes, not elsewhere classified

I95–I99 Other and unspecified disorders of the circulatory system

Asterisk categories for this chapter are provided as follows:

I32* Pericarditis in diseases classified elsewhere

I39* Endocarditis and heart valve disorders in diseases classified elsewhere I41* Myocarditis in diseases classified elsewhere

I43* Cardiomyopathy in diseases classified elsewhere I52* Other heart disorders in diseases classified elsewhere

I68* Cerebrovascular disorders in diseases classified elsewhere I79* Disorders of arteries, arterioles and capillaries in diseases

classified elsewhere

I98* Other disorders of circulatory system in diseases classified elsewhere

 

Acute rheumatic fever (I00–I02)

  I00 Rheumatic fever without mention of heart involvement

Incl.: arthritis, rheumatic, acute or subacute

  I01 Rheumatic fever with heart involvement

Excl.: chronic diseases of rheumatic origin (I05–I09) unless rheumatic fever is also present or there is evidence of recrudescence or activity of the rheumatic process. In cases where there is doubt as to rheumatic activity at the time of death, refer to the mortality coding rules and guidelines in Volume 2.

I01.0 Acute rheumatic pericarditis Any condition in I00 with pericarditis Rheumatic pericarditis (acute)

Excl.: when not specified as rheumatic (I30.-)

I01.1 Acute rheumatic endocarditis

Any condition in I00 with endocarditis or valvulitis Acute rheumatic valvulitis

I01.2 Acute rheumatic myocarditis

Any condition in I00 with myocarditis

I01.8 Other acute rheumatic heart disease

Any condition in I00 with other or multiple types of heart involvement Acute rheumatic pancarditis

I01.9 Acute rheumatic heart disease, unspecified

Any condition in I00 with unspecified type of heart involvement Rheumatic:

• carditis, acute

• heart disease, active or acute

  I02 Rheumatic chorea

Incl.: Sydenham chorea

Excl.: chorea:

• NOS (G25.5)

• Huntington (G10)

I02.0 Rheumatic chorea with heart involvement

Chorea NOS with heart involvement

Rheumatic chorea with heart involvement of any type classifiable under I01.-

I02.9 Rheumatic chorea without heart involvement

Rheumatic chorea NOS

 

Chronic rheumatic heart diseases (I05–I09)

  I05 Rheumatic mitral valve diseases

Incl.: conditions classifiable to (I05.0) and (I05.2–105.9), whether specified as rheumatic or not

Excl.: when specified as nonrheumatic (I34.-)

I05.0 Mitral stenosis

Mitral (valve) obstruction (rheumatic)

I05.1 Rheumatic mitral insufficiency

Rheumatic mitral:

• incompetence

• regurgitation

I05.2 Mitral stenosis with insufficiency

Mitral stenosis with incompetence or regurgitation

I05.8 Other mitral valve diseases

Mitral (valve) failure

I05.9 Mitral valve disease, unspecified

Mitral (valve) disorder (chronic) NOS

  I06 Rheumatic aortic valve diseases

Excl.: when not specified as rheumatic (I35.-)

I06.0 Rheumatic aortic stenosis

Rheumatic aortic (valve) obstruction

I06.1 Rheumatic aortic insufficiency

Rheumatic aortic:

• incompetence

• regurgitation

I06.2 Rheumatic aortic stenosis with insufficiency

Rheumatic aortic stenosis with incompetence or regurgitation

I06.8 Other rheumatic aortic valve diseases

I06.9 Rheumatic aortic valve disease, unspecified

Rheumatic aortic (valve) disease NOS

  I07 Rheumatic tricuspid valve diseases

Incl.: whether specified as rheumatic or of unspecified origin

Excl.: when specified as nonrheumatic (I36.-)

I07.0 Tricuspid stenosis

Tricuspid (valve) stenosis (rheumatic)

I07.1 Tricuspid insufficiency

Tricuspid (valve) insufficiency (rheumatic)

 

I07.2 Tricuspid stenosis with insufficiency I07.8 Other tricuspid valve diseases

I07.9 Tricuspid valve disease, unspecified

Tricuspid valve disorder NOS

  I08 Multiple valve diseases

Incl.: whether specified as rheumatic or of unspecified origin

Excl.: endocarditis, valve unspecified (I38)

multiple valve diseases of specified origin other than rheumatic heart disease; use appropriate codes in (I34–I38, Q22–Q23, Q24.8) rheumatic diseases of endocardium, valve unspecified (I09.1)

I08.0 Disorders of both mitral and aortic valves

Involvement of both mitral and aortic valves whether specified as rheumatic or of unspecified origin

I08.1 Disorders of both mitral and tricuspid valves I08.2 Disorders of both aortic and tricuspid valves

I08.3 Combined disorders of mitral, aortic and tricuspid valves I08.8 Other multiple valve diseases

I08.9 Multiple valve disease, unspecified

  I09 Other rheumatic heart diseases

I09.0 Rheumatic myocarditis

Excl.: myocarditis not specified as rheumatic (I51.4)

I09.1 Rheumatic diseases of endocardium, valve unspecified

Rheumatic:

• endocarditis (chronic)

• valvulitis (chronic)

Excl.: endocarditis, valve unspecified (I38)

I09.2 Chronic rheumatic pericarditis Adherent pericardium, rheumatic Chronic rheumatic:

• mediastinopericarditis

• myopericarditis

Excl.: when not specified as rheumatic (I31.-)

I09.8 Other specified rheumatic heart diseases

Rheumatic disease of pulmonary valve

I09.9 Rheumatic heart disease, unspecified

Rheumatic:

• carditis

• heart failure

Excl.: rheumatoid carditis (M05.3)

 

Hypertensive diseases (I10–I15)

Excl.: complicating pregnancy, childbirth and the puerperium (O10–O11, O13–O16)

involving coronary vessels (I20–I25) neonatal hypertension (P29.2) pulmonary hypertension (I27.0)

  I10 Essential (primary) hypertension

Incl.: high blood pressure hypertension

(arterial)(benign)(essential)(malignant)(primary)(systemic)

Excl.: involving vessels of:

• brain (I60–I69)

• eye (H35.0)

  I11 Hypertensive heart disease

Incl.: any condition in I50.-, I51.4–I51.9 due to hypertension

I11.0 Hypertensive heart disease with (congestive) heart failure

Hypertensive heart failure

I11.9 Hypertensive heart disease without (congestive) heart failure

Hypertensive heart disease NOS

  I12 Hypertensive renal disease

Incl.: any condition in N00–N07, N18.-, N19 or N26 due to hypertension arteriosclerosis of kidney

arteriosclerotic nephritis (chronic)(interstitial) hypertensive nephropathy

nephrosclerosis

Excl.: secondary hypertension (I15.-)

I12.0 Hypertensive renal disease with renal failure

Hypertensive renal failure

I12.9 Hypertensive renal disease without renal failure

Hypertensive renal disease NOS

  I13 Hypertensive heart and renal disease

Incl.: any condition in I11.- with any condition in I12.- disease:

• cardiorenal

• cardiovascular renal

I13.0 Hypertensive heart and renal disease with (congestive) heart failure

 

I13.1 Hypertensive heart and renal disease with renal failure

I13.2 Hypertensive heart and renal disease with both (congestive) heart failure and renal failure

I13.9 Hypertensive heart and renal disease, unspecified

  I15 Secondary hypertension

Excl.: involving vessels of:

• brain (I60–I69)

• eye (H35.0)

I15.0 Renovascular hypertension

I15.1 Hypertension secondary to other renal disorders I15.2 Hypertension secondary to endocrine disorders I15.8 Other secondary hypertension

I15.9 Secondary hypertension, unspecified

Ischaemic heart diseases (I20–I25)

Note: For morbidity, duration as used in categories I21, I22, I24 and I25 refers to the interval elapsing between onset of the ischaemic episode and admission to care. For mortality, duration refers to the interval elapsing between onset and death.

Incl.: with mention of hypertension (I10–I15)

Use additional code, if desired, to identify presence of hypertension.

  I20 Angina pectoris

I20.0 Unstable angina

Angina:

• crescendo

• de novo effort

• worsening effort

Intermediate coronary syndrome Pre-infarction syndrome

I20.1 Angina pectoris with documented spasm

Angina:

• angiospastic

• Prinzmetal

• spasm-induced

• variant

 

I20.8 Other forms of angina pectoris

Angina of effort

Coronary slow flow syndrome Stable angina

Stenocardia

I20.9 Angina pectoris, unspecified

Angina:

• NOS

• cardiac

Anginal syndrome Ischaemic chest pain

  I21 Acute myocardial infarction

Incl.: myocardial infarction specified as acute or with a stated duration of 4 weeks (28 days) or less from onset

Excl.: certain current complications following acute myocardial infarction (I23.-)

myocardial infarction:

• old (I25.2)

• specified as chronic or with a stated duration of more than 4 weeks (more than 28 days) from onset (I25.8)

• subsequent (I22.-)

postmyocardial infarction syndrome (I24.1)

I21.0 Acute transmural myocardial infarction of anterior wall

Transmural infarction (acute)(of):

• anterior (wall) NOS

• anteroapical

• anterolateral

• anteroseptal

I21.1 Acute transmural myocardial infarction of inferior wall

Transmural infarction (acute)(of):

• diaphragmatic wall

• inferior (wall) NOS

• inferolateral

• inferoposterior

I21.2 Acute transmural myocardial infarction of other sites

Transmural infarction (acute)(of):

• apical-lateral

• basal-lateral

• high lateral

• lateral (wall) NOS

• posterior (true)

• posterobasal

• posterolateral

• posteroseptal

• septal NOS

 

I21.3 Acute transmural myocardial infarction of unspecified site

Transmural myocardial infarction NOS

I21.4 Acute subendocardial myocardial infarction Myocardial infarction with non-ST elevation Nontransmural myocardial infarction NOS

I21.9 Acute myocardial infarction, unspecified

Myocardial infarction (acute) NOS

  I22 Subsequent myocardial infarction

Note: For morbidity coding, this category should be assigned for infarction of any myocardial site,

Incl.: myocardial infarction:

• extension

• recurrent

• reinfarction

Excl.: specified as chronic or with a stated duration of more than 4 weeks (more than 28 days) from onset (I25.8)

I22.0 Subsequent myocardial infarction of anterior wall

Subsequent infarction (acute)(of):

• anterior (wall) NOS

• anteroapical

• anterolateral

• anteroseptal

I22.1 Subsequent myocardial infarction of inferior wall

Subsequent infarction (acute)(of):

• diaphragmatic wall

• inferior (wall) NOS

• inferolateral

• inferoposterior

I22.8 Subsequent myocardial infarction of other sites

Subsequent myocardial infarction (acute)(of):

• apical-lateral

• basal-lateral

• high lateral

• lateral (wall) NOS

• posterior (true)

• posterobasal

• posterolateral

• posteroseptal

• septal NOS

I22.9 Subsequent myocardial infarction of unspecified site

 

  I23 Certain current complications following acute myocardial infarction

Excl.: the listed conditions, when:

• concurrent with acute myocardial infarction (I21–I22)

• not specified as current complications following acute myocardial infarction (I31.-, I51.-)

I23.0 Haemopericardium as current complication following acute myocardial infarction

I23.1 Atrial septal defect as current complication following acute myocardial infarction

I23.2 Ventricular septal defect as current complication following acute myocardial infarction

I23.3 Rupture of cardiac wall without haemopericardium as current complication following acute myocardial infarction

Excl.: with haemopericardium (I23.0)

I23.4 Rupture of chordae tendineae as current complication following acute myocardial infarction

I23.5 Rupture of papillary muscle as current complication following acute myocardial infarction

I23.6 Thrombosis of atrium, auricular appendage and ventricle as current complications following acute myocardial infarction

I23.8 Other current complications following acute myocardial infarction

  I24 Other acute ischaemic heart diseases

Excl.: angina pectoris (I20.-)

transient myocardial ischaemia of newborn (P29.4)

I24.0 Coronary thrombosis not resulting in myocardial infarction

Coronary (artery)(vein):

• embolism

• occlusion

• thromboembolism not resulting in myocardial infarction

Excl.: specified as chronic or with a stated duration of more than 4 weeks (more than 28 days) from onset (I25.8)

I24.1 Dressler syndrome

Postmyocardial infarction syndrome

I24.8 Other forms of acute ischaemic heart disease

Coronary:

• failure

• insufficiency

I24.9 Acute ischaemic heart disease, unspecified

Excl.: ischaemic heart disease (chronic) NOS (I25.9)

 

  I25 Chronic ischaemic heart disease

Excl.:  cardiovascular disease NOS (I51.6)

I25.0 Atherosclerotic cardiovascular disease, so described I25.1 Atherosclerotic heart disease

Coronary (artery):

• atheroma

• atherosclerosis

• disease

• sclerosis

I25.2 Old myocardial infarction

Healed myocardial infarction

Past myocardial infarction diagnosed by ECG or other special investigation, but currently presenting no symptoms

I25.3 Aneurysm of heart

Aneurysm:

• mural

• ventricular

I25.4 Coronary artery aneurysm and dissection

Coronary arteriovenous fistula, acquired

Excl.: congenital coronary (artery) aneurysm (Q24.5)

I25.5 Ischaemic cardiomyopathy I25.6 Silent myocardial ischaemia

I25.8 Other forms of chronic ischaemic heart disease

Any condition in I21–I22 and I24.- specified as chronic or with a stated duration of more than 4 weeks (more than 28 days) from onset

I25.9 Chronic ischaemic heart disease, unspecified

Ischaemic heart disease (chronic) NOS

Pulmonary heart disease and diseases of pulmonary circulation

(I26–I28)

  I26 Pulmonary embolism

Incl.: pulmonary (artery)(vein):

• infarction

• thromboembolism

• thrombosis

Excl.: complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.2)

• pregnancy, childbirth and the puerperium (O88.-)

I26.0 Pulmonary embolism with mention of acute cor pulmonale

Acute cor pulmonale NOS

I26.9 Pulmonary embolism without mention of acute cor pulmonale

Pulmonary embolism NOS

  I27 Other pulmonary heart diseases I27.0 Primary pulmonary hypertension I27.1 Kyphoscoliotic heart disease

I27.2 Other secondary pulmonary hypertension

Use additional code, if desired, to identify the underlying disease.

I27.8 Other specified pulmonary heart diseases

Excl.: Eisenmenger defect (Q21.8)

I27.9 Pulmonary heart disease, unspecified

Chronic cardiopulmonary disease Cor pulmonale (chronic) NOS

  I28 Other diseases of pulmonary vessels I28.0 Arteriovenous fistula of pulmonary vessels I28.1 Aneurysm of pulmonary artery

I28.8 Other specified diseases of pulmonary vessels

Rupture

Stenosis Stricture

of pulmonary vessel

I28.9 Disease of pulmonary vessels, unspecified

 

Other forms of heart disease (I30–I52)

  I30 Acute pericarditis

Incl.: acute pericardial effusion

Excl.: rheumatic pericarditis (acute) (I01.0) I30.0 Acute nonspecific idiopathic pericarditis I30.1 Infective pericarditis

Pericarditis:

• pneumococcal

• purulent

• staphylococcal

• streptococcal

• viral Pyopericarditis

Use additional code (B95-B98), if desired, to identify infectious agent.

I30.8 Other forms of acute pericarditis I30.9 Acute pericarditis, unspecified

  I31 Other diseases of pericardium

Excl.: current complications following acute myocardial infarction (I23.-) postcardiotomy syndrome (I97.0)

trauma (S26.-)

when specified as rheumatic (I09.2)

I31.0 Chronic adhesive pericarditis

Accretio cordis Adherent pericardium

Adhesive mediastinopericarditis

I31.1 Chronic constrictive pericarditis

Concretio cordis Pericardial calcification

I31.2 Haemopericardium, not elsewhere classified I31.3 Pericardial effusion (noninflammatory)

Chylopericardium

I31.8 Other specified diseases of pericardium

Epicardial plaques

Focal pericardial adhesions

I31.9 Disease of pericardium, unspecified

Cardiac tamponade Pericarditis (chronic) NOS

 

  I32* Pericarditis in diseases classified elsewhere

I32.0* Pericarditis in bacterial diseases classified elsewhere

Pericarditis:

• gonococcal (A54.8†)

• meningococcal (A39.5†)

• syphilitic (A52.0†)

• tuberculous (A18.8†)

I32.1* Pericarditis in other infectious and parasitic diseases classified elsewhere

I32.8* Pericarditis in other diseases classified elsewhere

Pericarditis (in):

• rheumatoid (M05.3†)

• systemic lupus erythematosus (M32.1†)

• uraemic (N18.5†)

  I33 Acute and subacute endocarditis

Excl.: acute rheumatic endocarditis (I01.1) endocarditis NOS (I38)

I33.0 Acute and subacute infective endocarditis

Endocarditis (acute)(subacute):

• bacterial

• infective NOS

• lenta

• malignant

• septic

• ulcerative

Use additional code (B95–B98), if desired, to identify infectious agent.

I33.9 Acute endocarditis, unspecified

Endocarditis

Myoendocarditis Periendocarditis

acute or subacute

  I34 Nonrheumatic mitral valve disorders

Excl.: mitral (valve):

• disease (I05.9)

• failure (I05.8)

• stenosis (I05.0)

when of unspecified cause but with mention of:

• diseases of aortic valve (I08.0)

• mitral stenosis or obstruction (I05.0)

when specified as congenital (Q23.2, Q23.9) when specified as rheumatic (I05.-)

 

I34.0

I34.1 Mitral (valve) prolapse

Floppy mitral valve syndrome

Excl.: Marfan syndrome (Q87.4)

I34.2 Nonrheumatic mitral (valve) stenosis

I34.8 Other nonrheumatic mitral valve disorders

I34.9 Nonrheumatic mitral valve disorder, unspecified

  I35 Nonrheumatic aortic valve disorders

Excl.: hypertrophic subaortic stenosis (I42.1)

when of unspecified cause but with mention of diseases of mitral valve (I08.0)

when specified as congenital (Q23.0, Q23.1, Q23.4-Q23.9) when specified as rheumatic (I06.-)

I35.0 Aortic (valve) stenosis I35.1 Aortic (valve) insufficiency

I35.2 Aortic (valve) stenosis with insufficiency I35.8 Other aortic valve disorders

I35.9 Aortic valve disorder, unspecified

  I36 Nonrheumatic tricuspid valve disorders

Excl.: when of unspecified cause (I07.-)

when specified as congenital (Q22.4, Q22.8, Q22.9) when specified as rheumatic (I07.-)

I36.0 Nonrheumatic tricuspid (valve) stenosis I36.1 Nonrheumatic tricuspid (valve) insufficiency

I36.2 Nonrheumatic tricuspid (valve) stenosis with insufficiency I36.8 Other nonrheumatic tricuspid valve disorders

I36.9 Nonrheumatic tricuspid valve disorder, unspecified

 

  I37 Pulmonary valve disorders

Excl.: when specified as congenital (Q22.1, Q22.2, Q22.3) when specified as rheumatic (I09.8)

I37.0 Pulmonary valve stenosis I37.1 Pulmonary valve insufficiency

 

I37.2 Pulmonary valve stenosis with insufficiency I37.8 Other pulmonary valve disorders

I37.9 Pulmonary valve disorder, unspecified

  I38 Endocarditis, valve unspecified

Incl.: endocarditis (chronic) NOS valvular:

• incompetence

 

NOS or of specified

 

• insufficiency

• regurgitation

• stenosis valvulitis (chronic)

 

of unspecified valve

 

cause, except rheumatic or congenital

 

Excl.: congenital insufficiency of cardiac valve NOS (Q24.8) congenital stenosis of cardiac valve NOS (Q24.8) endocardial fibroelastosis (I42.4)

when specified as rheumatic (I09.1)

  I39* Endocarditis and heart valve disorders in diseases classified elsewhere

Incl.: endocardial involvement in:

• candidal infection (B37.6†)

• gonococcal infection (A54.8†)

• Libman–Sacks disease (M32.1†)

• meningococcal infection (A39.5†)

• rheumatoid arthritis (M05.3†)

• syphilis (A52.0†)

• tuberculosis (A18.8†)

• typhoid fever (A01.0†)

I39.0* Mitral valve disorders in diseases classified elsewhere I39.1* Aortic valve disorders in diseases classified elsewhere I39.2* Tricuspid valve disorders in diseases classified elsewhere I39.3* Pulmonary valve disorders in diseases classified elsewhere I39.4* Multiple valve disorders in diseases classified elsewhere

I39.8* Endocarditis, valve unspecified, in diseases classified elsewhere

 

  I40 Acute myocarditis

I40.0 Infective myocarditis

Septic myocarditis

Use additional code (B95–B98), if desired, to identify infectious agent.

I40.1 Isolated myocarditis I40.8 Other acute myocarditis

I40.9 Acute myocarditis, unspecified

  I41* Myocarditis in diseases classified elsewhere

I41.0* Myocarditis in bacterial diseases classified elsewhere

Myocarditis:

• diphtheritic (A36.8†)

• gonococcal (A54.8†)

• meningococcal (A39.5†)

• syphilitic (A52.0†)

• tuberculous (A18.8†)

I41.1* Myocarditis in viral diseases classified elsewhere

Influenzal myocarditis (acute):

• seasonal virus identified (J10.8†)

• virus not identified (J11.8†)

• zoonotic or pandemic influenza virus identified (J09†) Mumps myocarditis (B26.8†)

I41.2* Myocarditis in other infectious and parasitic diseases classified elsewhere

Myocarditis in:

• Chagas disease (chronic) (B57.2†)

• acute (B57.0†)

• toxoplasmosis (B58.8†)

I41.8* Myocarditis in other diseases classified elsewhere

Rheumatoid myocarditis (M05.3†) Sarcoid myocarditis (D86.8†)

  I42 Cardiomyopathy

Excl.: cardiomyopathy complicating:

• pregnancy (O99.4)

• puerperium (O90.3)

ischaemic cardiomyopathy (I25.5)

I42.0 Dilated cardiomyopathy

Congestive cardiomyopathy

I42.1 Obstructive hypertrophic cardiomyopathy

Hypertrophic subaortic stenosis

 

I42.2 Other hypertrophic cardiomyopathy

Nonobstructive hypertrophic cardiomyopathy

I42.3 Endomyocardial (eosinophilic) disease

Endomyocardial (tropical) fibrosis Löffler endocarditis

I42.4 Endocardial fibroelastosis

Congenital cardiomyopathy

I42.5 Other restrictive cardiomyopathy

Constrictive cardiomyopathy NOS

I42.6 Alcoholic cardiomyopathy

I42.7 Cardiomyopathy due to drugs and other external agents

Use additional external cause code (Chapter XX), if desired, to identify cause.

I42.8 Other cardiomyopathies I42.9 Cardiomyopathy, unspecified

Cardiomyopathy (primary)(secondary) NOS

  I43* Cardiomyopathy in diseases classified elsewhere

I43.0* Cardiomyopathy in infectious and parasitic diseases classified elsewhere

Cardiomyopathy in diphtheria (A36.8†)

I43.1* Cardiomyopathy in metabolic diseases

Cardiac amyloidosis (E85.-†)

I43.2* Cardiomyopathy in nutritional diseases

Nutritional cardiomyopathy NOS (E63.9†)

I43.8* Cardiomyopathy in other diseases classified elsewhere

Gouty tophi of heart (M10.0†) Thyrotoxic heart disease (E05.9†)

  I44 Atrioventricular and left bundle-branch block

I44.0 Atrioventricular block, first degree I44.1 Atrioventricular block, second degree

Atrioventricular block, type I and II

Möbitz block, type I and II Second-degree block, type I and II Wenckebach block

I44.2 Atrioventricular block, complete

Complete heart block NOS Third-degree block

I44.3 Other and unspecified atrioventricular block

Atrioventricular block NOS

 

I44.4 Left anterior fascicular block I44.5 Left posterior fascicular block

I44.6 Other and unspecified fascicular block

Left bundle-branch hemiblock NOS

I44.7 Left bundle-branch block, unspecified

  I45 Other conduction disorders

I45.0 Right fascicular block

I45.1 Other and unspecified right bundle-branch block

Right bundle-branch block NOS

I45.2 Bifascicular block

I45.3 Trifascicular block

I45.4 Nonspecific intraventricular block

Bundle-branch block NOS

I45.5 Other specified heart block

Sinoatrial block Sinoauricular block

Excl.: heart block NOS (I45.9)

I45.6 Pre-excitation syndrome

Anomalous atrioventricular excitation Atrioventricular conduction:

• accelerated

• accessory

• pre-excitation Lown–Ganong–Levine syndrome Wolff–Parkinson–White syndrome

I45.8 Other specified conduction disorders Atrioventricular [AV] dissociation Interference dissociation

Excl.: prolongation of QT interval (R94.3)

I45.9 Conduction disorder, unspecified

Heart block NOS Stokes–Adams syndrome

  I46 Cardiac arrest

Excl.: cardiogenic shock (R57.0) complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.8)

• obstetric surgery and procedures (O75.4)

 

I46.0 Cardiac arrest with successful resuscitation I46.1 Sudden cardiac death, so described

Excl.: sudden death:

• NOS (R96.-)

• with:

– conduction disorder (I44–I45)

– myocardial infarction (I21–I22)

I46.9 Cardiac arrest, unspecified

  I47 Paroxysmal tachycardia

Excl.: complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.8)

• obstetric surgery and procedures (O75.4) tachycardia:

• NOS (R00.0)

• sinoauricular NOS (R00.0)

• sinus [sinusal] NOS (R00.0)

I47.0 Re-entry ventricular arrhythmia I47.1 Supraventricular tachycardia

Tachycardia (paroxysmal):

• atrial

• atrioventricular [AV]:

– NOS

– re-entrant (nodal) [AVNRT][AVRT]

• junctional

• nodal

I47.2 Ventricular tachycardia

I47.9 Paroxysmal tachycardia, unspecified

Bouveret(– Hoffmann) syndrome

  I48 Atrial fibrillation and flutter I48.0 Paroxysmal atrial fibrillation I48.1 Persistent atrial fibrillation I48.2 Chronic atrial fibrillation

I48.3 Typical atrial flutter

Type I atrial flutter

I48.4 Atypical atrial flutter

Type II atrial flutter

I48.9 Atrial fibrillation and atrial flutter, unspecified

 

  I49 Other cardiac arrhythmias

Excl.: bradycardia:

• NOS (R00.1)

• sinoatrial (R00.1)

• sinus (R00.1)

• vagal (R00.1) complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.8)

• obstetric surgery and procedures (O75.4) neonatal cardiac dysrhythmia (P29.1)

I49.0 Ventricular fibrillation and flutter I49.1 Atrial premature depolarization

Atrial premature beats

I49.2 Junctional premature depolarization I49.3 Ventricular premature depolarization

I49.4 Other and unspecified premature depolarization

Ectopic beats Extrasystoles Extrasystolic arrhythmias Premature:

• beats NOS

• contractions

I49.5 Sick sinus syndrome

Tachycardia–bradycardia syndrome

I49.8 Other specified cardiac arrhythmias

Brugada syndrome Long QT syndrome Rhythm disorder:

• coronary sinus

• ectopic

• nodal

I49.9 Cardiac arrhythmia, unspecified

Arrhythmia (cardiac) NOS

  I50 Heart failure

Excl.: complicating:

• abortion or ectopic or molar pregnancy (O00–O07, O08.8)

• obstetric surgery and procedures (O75.4) due to hypertension (I11.0):

• with renal disease (I13.-)

following cardiac surgery or due to presence of cardiac prosthesis (I97.1)

neonatal cardiac failure (P29.0)

 

I50.0 Congestive heart failure

Congestive heart disease

Right ventricular failure (secondary to left heart failure)

I50.1 Left ventricular failure

Cardiac asthma Left heart failure

Oedema of lung

Pulmonary oedema with mention of heart disease NOS or heart failure

I50.9 Heart failure, unspecified

Cardiac, heart or myocardial failure NOS

  I51 Complications and ill-defined descriptions of heart disease

Excl.: any condition in I51.4–I51.9 due to hypertension (I11.-) any condition in I51.4–I51.9 due to hypertension:

• with renal disease (I13.-)

complications following acute myocardial infarction (I23.-) when specified as rheumatic (I00–I09)

I51.0 Cardiac septal defect, acquired

Acquired septal defect (old):

• atrial

• auricular

• ventricular

I51.1 Rupture of chordae tendineae, not elsewhere classified I51.2 Rupture of papillary muscle, not elsewhere classified I51.3 Intracardiac thrombosis, not elsewhere classified

Thrombosis (old):

• apical

• atrial

• auricular

• ventricular

I51.4 Myocarditis, unspecified

Myocardial fibrosis Myocarditis:

• NOS

• chronic (interstitial)

I51.5 Myocardial degeneration

Degeneration of heart or myocardium:

• fatty

• senile Myocardial disease

 

I51.6 Cardiovascular disease, unspecified

Cardiovascular accident NOS

Excl.: atherosclerotic cardiovascular disease, so described (I25.0)

I51.7 Cardiomegaly

Cardiac:

• dilatation

• hypertrophy Ventricular dilatation

I51.8 Other ill-defined heart diseases

Carditis (acute)(chronic) Pancarditis (acute)(chronic)

I51.9 Heart disease, unspecified

  I52* Other heart disorders in diseases classified elsewhere

Excl.: cardiovascular disorders NOS in diseases classified elsewhere (I98.-*)

I52.0* Other heart disorders in bacterial diseases classified elsewhere

Meningococcal carditis NEC (A39.5†)

I52.1* Other heart disorders in other infectious and parasitic diseases classified elsewhere

Pulmonary heart disease in schistosomiasis (B65.-†)

I52.8* Other heart disorders in other diseases classified elsewhere

Rheumatoid carditis (M05.3†)

Cerebrovascular diseases (I60–I69)

Incl.: with mention of hypertension (conditions in I10 and I15.-) Use additional code, if desired, to identify presence of hypertension.

Excl.: transient cerebral ischaemic attacks and related syndromes (G45.-)

traumatic intracranial haemorrhage (S06.-) vascular dementia (F01.-)

  I60 Subarachnoid haemorrhage

Excl.: sequelae of subarachnoid haemorrhage (I69.0)

I60.0 Subarachnoid haemorrhage from carotid siphon and bifurcation I60.1 Subarachnoid haemorrhage from middle cerebral artery

I60.2 Subarachnoid haemorrhage from anterior communicating artery I60.3 Subarachnoid haemorrhage from posterior communicating artery

 

I60.4 Subarachnoid haemorrhage from basilar artery I60.5 Subarachnoid haemorrhage from vertebral artery

I60.6 Subarachnoid haemorrhage from other intracranial arteries

Multiple involvement of intracranial arteries

I60.7 Subarachnoid haemorrhage from intracranial artery, unspecified

Ruptured (congenital) berry aneurysm NOS

Subarachnoid haemorrhage from:

• cerebral

• communicating

artery NOS

I60.8 Other subarachnoid haemorrhage

Meningeal haemorrhage

Rupture of cerebral arteriovenous malformation

I60.9 Subarachnoid haemorrhage, unspecified

  I61 Intracerebral haemorrhage

Excl.: sequelae of intracerebral haemorrhage (I69.1)

I61.0 Intracerebral haemorrhage in hemisphere, subcortical

Deep intracerebral haemorrhage

I61.1 Intracerebral haemorrhage in hemisphere, cortical

Cerebral lobe haemorrhage Superficial intracerebral haemorrhage

I61.2 Intracerebral haemorrhage in hemisphere, unspecified I61.3 Intracerebral haemorrhage in brain stem

I61.4 Intracerebral haemorrhage in cerebellum I61.5 Intracerebral haemorrhage, intraventricular I61.6 Intracerebral haemorrhage, multiple localized I61.8 Other intracerebral haemorrhage

I61.9 Intracerebral haemorrhage, unspecified

  I62 Other nontraumatic intracranial haemorrhage

Excl.: sequelae of intracranial haemorrhage (I69.2)

I62.0 Subdural haemorrhage (acute)(nontraumatic) I62.1 Nontraumatic extradural haemorrhage

Nontraumatic epidural haemorrhage

I62.9 Intracranial haemorrhage (nontraumatic), unspecified

 

  I63 Cerebral infarction

Incl.: occlusion and stenosis of cerebral and precerebral arteries (including truncus

brachiocephalicus), resulting in cerebral infarction

Excl.: sequelae of cerebral infarction (I69.3)

I63.0 Cerebral infarction due to thrombosis of precerebral arteries I63.1 Cerebral infarction due to embolism of precerebral arteries I63.2 Cerebral infarction due to unspecified occlusion or stenosis

of precerebral arteries

I63.3 Cerebral infarction due to thrombosis of cerebral arteries I63.4 Cerebral infarction due to embolism of cerebral arteries I63.5 Cerebral infarction due to unspecified occlusion or stenosis

of cerebral arteries

I63.6 Cerebral infarction due to cerebral venous thrombosis, nonpyogenic

I63.8 Other cerebral infarction

I63.9 Cerebral infarction, unspecified

  I64 Stroke, not specified as haemorrhage or infarction

Incl.: cerebrovascular accident NOS

Excl.: sequelae of stroke (I69.4)

  I65 Occlusion and stenosis of precerebral arteries, not resulting in cerebral infarction

Incl.:  embolism

narrowing

obstruction (complete)(partial) thrombosis of basilar, carotid or vertebral arteries, not resulting in cerebral infarction

Excl.: when causing cerebral infarction (I63.-) I65.0 Occlusion and stenosis of vertebral artery I65.1 Occlusion and stenosis of basilar artery I65.2 Occlusion and stenosis of carotid artery

I65.3 Occlusion and stenosis of multiple and bilateral precerebral arteries

I65.8 Occlusion and stenosis of other precerebral artery

I65.9 Occlusion and stenosis of unspecified precerebral artery

Precerebral artery NOS

 

  I66 Occlusion and stenosis of cerebral arteries, not resulting in cerebral infarction

Incl.:  embolism

narrowing

obstruction (complete)(partial) thrombosis of middle, anterior and posterior cerebral arteries, and cerebellar arteries, not resulting in cerebral infarction

Excl.: when causing cerebral infarction (I63.-)

I66.0 Occlusion and stenosis of middle cerebral artery I66.1 Occlusion and stenosis of anterior cerebral artery I66.2 Occlusion and stenosis of posterior cerebral artery I66.3 Occlusion and stenosis of cerebellar arteries

I66.4 Occlusion and stenosis of multiple and bilateral cerebral arteries

I66.8 Occlusion and stenosis of other cerebral artery

Occlusion and stenosis of perforating arteries

I66.9 Occlusion and stenosis of unspecified cerebral artery

  I67 Other cerebrovascular diseases

Excl.: sequelae of the listed conditions (I69.8)

I67.0 Dissection of cerebral arteries, nonruptured

Excl.: ruptured cerebral arteries (I60.7)

I67.1 Cerebral aneurysm, nonruptured

Cerebral:

• aneurysm NOS

• arteriovenous fistula, acquired

Excl.: congenital cerebral aneurysm, nonruptured (Q28.-) ruptured cerebral aneurysm (I60.-)

I67.2 Cerebral atherosclerosis

Atheroma of cerebral arteries

I67.3 Progressive vascular leukoencephalopathy

Binswanger disease

Excl.: subcortical vascular dementia (F01.2)

I67.4 Hypertensive encephalopathy I67.5 Moyamoya disease

I67.6 Nonpyogenic thrombosis of intracranial venous system

Nonpyogenic thrombosis of:

• cerebral vein

• intracranial venous sinus

Excl.: when causing infarction (I63.6)

I67.7 Cerebral arteritis, not elsewhere classified I67.8 Other specified cerebrovascular diseases

Acute cerebrovascular insufficiency NOS Cerebral ischaemia (chronic)

I67.9 Cerebrovascular disease, unspecified

  I68* Cerebrovascular disorders in diseases classified elsewhere

I68.0* Cerebral amyloid angiopathy (E85.-†)

I68.1* Cerebral arteritis in infectious and parasitic diseases classified elsewhere

Cerebral arteritis:

• listerial (A32.8†)

• syphilitic (A52.0†)

• tuberculous (A18.8†)

I68.2* Cerebral arteritis in other diseases classified elsewhere

Cerebral arteritis in systemic lupus erythematosus (M32.1†)

I68.8* Other cerebrovascular disorders in diseases classified elsewhere

Uraemic apoplexia in chronic kidney disease (N18.5†)

  I69 Sequelae of cerebrovascular disease

Note:  Category I69 is to be used to indicate conditions in I60–I67.1    and I67.4–I67.9 as the cause of sequelae, themselves classified elsewhere. The ‘sequelae’ include conditions specified as such or as late effects, or those present one year or more after onset of the causal condition.

Not to be used for chronic cerebrovascular disease. Code these to I60–I67.

I69.0 Sequelae of subarachnoid haemorrhage I69.1 Sequelae of intracerebral haemorrhage

I69.2 Sequelae of other nontraumatic intracranial haemorrhage I69.3 Sequelae of cerebral infarction

I69.4 Sequelae of stroke, not specified as haemorrhage or infarction I69.8 Sequelae of other and unspecified cerebrovascular diseases

 

Diseases of arteries, arterioles and capillaries (I70–I79)

  I70 Atherosclerosis

Incl.: arteriolosclerosis

arteriosclerosis

arteriosclerotic vascular disease atheroma

degeneration:

• arterial

• arteriovascular

• vascular

endarteritis deformans or obliterans senile:

• arteritis

• endarteritis

Excl.: cerebral (I67.2)

coronary (I25.1) mesenteric (K55.1) pulmonary (I27.0)

The following supplementary classification to indicate the presence or absence of gangrene is provided for optional use with appropriate subcategories in I70.

0 without gangrene

1 with gangrene

I70.0 Atherosclerosis of aorta

I70.1 Atherosclerosis of renal artery

Goldblatt kidney

Excl.: atherosclerosis of renal arterioles (I12.-)

I70.2 Atherosclerosis of arteries of extremities

Atherosclerotic gangrene Mönckeberg (medial) sclerosis

I70.8 Atherosclerosis of other arteries

I70.9 Generalized and unspecified atherosclerosis

  I71 Aortic aneurysm and dissection

I71.0 Dissection of aorta [any part]

Dissecting aneurysm of aorta (ruptured) [any part]

I71.1 Thoracic aortic aneurysm, ruptured

I71.2 Thoracic aortic aneurysm, without mention of rupture I71.3 Abdominal aortic aneurysm, ruptured

 

I71.4 Abdominal aortic aneurysm, without mention of rupture I71.5 Thoracoabdominal aortic aneurysm, ruptured

I71.6 Thoracoabdominal aortic aneurysm, without mention of rupture

I71.8 Aortic aneurysm of unspecified site, ruptured

Rupture of aorta NOS

I71.9 Aortic aneurysm of unspecified site, without mention of rupture

Aneurysm

Dilatation Hyaline necrosis

of aorta

  I72 Other aneurysm and dissection

Incl.: aneurysm (cirsoid)(false)(ruptured)

Excl.: aneurysm (of):

• aorta (I71.-)

• arteriovenous NOS (Q27.3)

• arteriovenous acquired (I77.0)

• cerebral (nonruptured) (I67.1)

• cerebral ruptured (I60.-)

• coronary (I25.4)

• heart (I25.3)

• pulmonary artery (I28.1)

• retinal (H35.0)

• varicose (I77.0) dissection of:

• coronary artery (I25.4)

• precerebral artery, congenital (nonruptured) (Q28.1)

I72.0 Aneurysm and dissection of carotid artery

I72.1 Aneurysm and dissection of artery of upper extremity I72.2 Aneurysm and dissection of renal artery

I72.3 Aneurysm and dissection of iliac artery

I72.4 Aneurysm and dissection of artery of lower extremity I72.5 Aneurysm and dissection of other precerebral arteries

Aneurysm and dissection of basilar artery (trunk)

Excl.: aneurysm and dissection of :

• carotid artery (I72.0)

• vertebral artery (I72.6)

I72.6 Aneurysm and dissection of vertebral artery

I72.8 Aneurysm and dissection of other specified arteries I72.9 Aneurysm and dissection of unspecified site

 

  I73 Other peripheral vascular diseases

Excl.: chilblains (T69.1) frostbite (T33–T35)

immersion hand or foot (T69.0) spasm of cerebral artery (G45.9)

I73.0 Raynaud syndrome

Raynaud:

• disease

• gangrene

• phenomenon (secondary)

I73.1 Thromboangiitis obliterans [Buerger]

I73.8 Other specified peripheral vascular diseases

Acrocyanosis Acroparaesthesia:

• simple [Schultze type]

• vasomotor [Nothnagel type] Erythrocyanosis Erythromelalgia

I73.9 Peripheral vascular disease, unspecified

Intermittent claudication Spasm of artery

  I74 Arterial embolism and thrombosis

Incl.: infarction:

• embolic

• thrombotic occlusion:

• embolic

• thrombotic

Excl.: embolism and thrombosis:

• basilar (I63.0–I63.2, I65.1)

• carotid (I63.0–I63.2, I65.2)

• cerebral (I63.3–I63.5, I66.9)

• complicating:

– abortion or ectopic or molar pregnancy (O00–O07, O08.2)

– pregnancy, childbirth and the puerperium (O88.-)

• coronary (I21–I25)

• mesenteric (K55.0)

• precerebral (I63.0–I63.2, I65.9)

• pulmonary (I26.-)

• renal (N28.0)

• retinal (H34.-)

• vertebral (I63.0–I63.2, I65.0)

 

I74.0 Embolism and thrombosis of abdominal aorta

Aortic bifurcation syndrome Leriche syndrome

I74.1 Embolism and thrombosis of other and unspecified parts of aorta I74.2 Embolism and thrombosis of arteries of upper extremities I74.3 Embolism and thrombosis of arteries of lower extremities I74.4 Embolism and thrombosis of arteries of extremities, unspecified

Peripheral arterial embolism

I74.5 Embolism and thrombosis of iliac artery I74.8 Embolism and thrombosis of other arteries

I74.9 Embolism and thrombosis of unspecified artery

  I77 Other disorders of arteries and arterioles

Excl.: collagen (vascular) diseases (M30–M36) hypersensitivity angiitis (M31.0) pulmonary artery (I28.-)

I77.0 Arteriovenous fistula, acquired

Aneurysmal varix

Arteriovenous aneurysm, acquired

Excl.: arteriovenous aneurysm NOS (Q27.3) cerebral (I67.1)

coronary (I25.4)

traumatic – see injury of blood vessel by body region.

I77.1 Stricture of artery

I77.2 Rupture of artery

Fistula of artery

Excl.: traumatic rupture of artery – see injury of blood vessel by body region.

I77.3 Arterial fibromuscular dysplasia

I77.4 Coeliac artery compression syndrome I77.5 Necrosis of artery

I77.6 Arteritis, unspecified Aortitis NOS Endarteritis NOS

Excl.: arteritis or endarteritis:

• aortic arch [Takayasu] (M31.4)

• cerebral NEC (I67.7)

• coronary (I25.8)

• deformans (I70.-)

• giant cell (M31.5–M31.6)

• obliterans (I70.-)

• senile (I70.-)

 

I77.8 ders of arteries and arterioles

I77.9 Disorder of arteries and arterioles, unspecified

  I78 Diseases of capillaries

I78.0 Hereditary haemorrhagic telangiectasia

Rendu–Osler–Weber disease

I78.1 Naevus, non-neoplastic

Naevus:

• araneus

• spider

• stellar

Excl.: naevus:

• NOS (D22.-)

• blue (D22.-)

• flammeus (Q82.5)

• hairy (D22.-)

• melanocytic (D22.-)

• pigmented (D22.-)

• portwine (Q82.5)

• sanguineous (Q82.5)

• strawberry (Q82.5)

• vascular NOS (Q82.5)

• verrucous (Q82.5)

I78.8 Other diseases of capillaries

I78.9 Disease of capillaries, unspecified

  I79* Disorders of arteries, arterioles and capillaries in diseases classified elsewhere

I79.0* Aneurysm of aorta in diseases classified elsewhere

Syphilitic aneurysm of aorta (A52.0†)

I79.1* Aortitis in diseases classified elsewhere

Syphilitic aortitis (A52.0†)

I79.2* Peripheral angiopathy in diseases classified elsewhere

Diabetic peripheral angiopathy (E10–E14 with common fourth character .5†)

I79.8* Other disorders of arteries, arterioles and capillaries in diseases classified elsewhere

 

Diseases of veins, lymphatic vessels and lymph nodes, not elsewhere classified

(I80–I89)

  I80 Phlebitis and thrombophlebitis

Incl.: endophlebitis

inflammation, vein periphlebitis suppurative phlebitis

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: phlebitis and thrombophlebitis (of):

• complicating:

– abortion or ectopic or molar pregnancy (O00–O07, O08.7)

– pregnancy, childbirth and the puerperium (O22.-, O87.-)

• intracranial and intraspinal, septic or NOS (G08)

• intracranial, nonpyogenic (I67.6)

• intraspinal, nonpyogenic (G95.1)

• portal (vein) (K75.1) postphlebitic syndrome (I87.0) thrombophlebitis migrans (I82.1)

I80.0 Phlebitis and thrombophlebitis of superficial vessels of lower extremities

I80.1 Phlebitis and thrombophlebitis of femoral vein

I80.2 Phlebitis and thrombophlebitis of other deep vessels of lower extremities

Deep vein thrombosis NOS

I80.3 Phlebitis and thrombophlebitis of lower extremities, unspecified

Embolism or thrombosis of lower extremity NOS

I80.8 Phlebitis and thrombophlebitis of other sites  I80.9 Phlebitis and thrombophlebitis of unspecified site

  I81 Portal vein thrombosis

Incl.: portal (vein) obstruction

Excl.: phlebitis of portal vein (K75.1)

 

  I82 Other venous embolism and thrombosis

Excl.: venous embolism and thrombosis (of):

• cerebral (I63.6, I67.6)

• complicating:

– abortion or ectopic or molar pregnancy (O00–O07, O08.7)

– pregnancy, childbirth and the puerperium (O22.-, O87.-)

• coronary (I21–I25)

• intracranial and intraspinal, septic or NOS (G08)

• intracranial, nonpyogenic (I67.6)

• intraspinal, nonpyogenic (G95.1)

• lower extremities (I80.-)

• mesenteric (K55.0)

• portal (I81)

• pulmonary (I26.-) I82.0 Budd–Chiari syndrome I82.1 Thrombophlebitis migrans

I82.2 Embolism and thrombosis of vena cava I82.3 Embolism and thrombosis of renal vein

I82.8 Embolism and thrombosis of other specified veins

I82.9 Embolism and thrombosis of unspecified vein

Embolism of vein NOS Thrombosis (vein) NOS

  I83 Varicose veins of lower extremities

Excl.: complicating:

• pregnancy (O22.0)

• puerperium (O87.8)

I83.0 Varicose veins of lower extremities with ulcer Any condition in I83.9 with ulcer or specified as ulcerated Varicose ulcer (lower extremity, any part)

I83.1 Varicose veins of lower extremities with inflammation

Any condition in I83.9 with inflammation or specified as inflamed Stasis dermatitis NOS

I83.2 Varicose veins of lower extremities with both ulcer and inflammation

Any condition in I83.9 with both ulcer and inflammation

I83.9 Varicose veins of lower extremities without ulcer or inflammation

Phlebectasia

Varicose veins Varix of lower extremity [any part] or of unspecified site

 

  I85 Oesophageal varices

I85.0 Oesophageal varices with bleeding I85.9 Oesophageal varices without bleeding

Oesophageal varices NOS

  I86 Varicose veins of other sites

Excl.: retinal varices (H35.0)

varicose veins of unspecified site (I83.9)

I86.0 Sublingual varices

I86.1 Scrotal varices

Varicocele

I86.2 Pelvic varices

I86.3 Vulval varices

Excl.: complicating:

• childbirth and the puerperium (O87.8)

• pregnancy (O22.1)

I86.4 Gastric varices

I86.8 Varicose veins of other specified sites

Varicose ulcer of nasal septum

  I87 Other disorders of veins

I87.0 Post-thrombotic syndrome

Postphlebitic syndrome

I87.1 Compression of vein

Stricture of vein

Vena cava syndrome (inferior)(superior)

Excl.: pulmonary (I28.8)

I87.2 Venous insufficiency (chronic)(peripheral) I87.8 Other specified disorders of veins

I87.9 Disorder of vein, unspecified

  I88 Nonspecific lymphadenitis

Excl.: acute lymphadenitis, except mesenteric (L04.-) enlarged lymph nodes NOS (R59.-)

human immunodeficiency virus [HIV] disease resulting in generalized lymphadenopathy (B23.1)

 

I88.0 Nonspecific mesenteric lymphadenitis

Mesenteric lymphadenitis (acute)(chronic)

I88.1 Chronic lymphadenitis, except mesenteric

Adenitis

Lymphadenitis chronic, any lymph node except mesenteric

I88.8 Other nonspecific lymphadenitis

I88.9 Nonspecific lymphadenitis, unspecified

Lymphadenitis NOS

  I89 Other noninfective disorders of lymphatic vessels and lymph nodes

Excl.: chylocele:

• filarial (B74.-)

• tunica vaginalis (nonfilarial) NOS (N50.8) enlarged lymph nodes NOS (R59.-) hereditary lymphoedema (Q82.0) postmastectomy lymphoedema (I97.2)

I89.0 Lymphoedema, not elsewhere classified

Lymphangiectasis

I89.1 Lymphangitis

Lymphangitis:

• NOS

• chronic

• subacute

Excl.: acute lymphangitis (L03.-)

I89.8 Other specified noninfective disorders of lymphatic vessels and lymph nodes

Chylocele (nonfilarial) Lipomelanotic reticulosis

I89.9 Noninfective disorder of lymphatic vessels and lymph nodes, unspecified

Disease of lymphatic vessels NOS

 

Other and unspecified disorders of the circulatory system

(I95–I99)

  I95 Hypotension

Excl.:  cardiovascular collapse (R57.9) maternal hypotension syndrome (O26.5)

nonspecific low blood pressure reading NOS (R03.1)

I95.0 Idiopathic hypotension I95.1 Orthostatic hypotension

Hypotension, postural

Excl.: neurogenic orthostatic hypotension [Shy–Drager] (G23.8)

I95.2 Hypotension due to drugs

Use additional external cause code (Chapter XX), if desired, to identify drug.

I95.8 Other hypotension

Chronic hypotension

I95.9 Hypotension, unspecified

  I97 Postprocedural disorders of circulatory system, not elsewhere classified

Excl.: postoperative shock (T81.1)

I97.0 Postcardiotomy syndrome

I97.1 Other functional disturbances following cardiac surgery

Cardiac insufficiency

Heart failure following cardiac surgery or due to presence of cardiac prosthesis

I97.2 Postmastectomy lymphoedema syndrome

Elephantiasis

Obliteration of lymphatic vessels due to mastectomy

I97.8 Other postprocedural disorders of circulatory system, not elsewhere classified

I97.9 Postprocedural disorder of circulatory system, unspecified

 

  I98* Other disorders of circulatory system in diseases classified elsewhere

Excl.: disorders classified to other asterisk categories within this chapter

I98.0* Cardiovascular syphilis

Cardiovascular syphilis:

• NOS (A52.0†)

• congenital, late (A50.5†)

I98.1* Cardiovascular disorders in other infectious and parasitic diseases classified elsewhere

Cardiovascular:

• involvement NEC, in Chagas disease (chronic) (B57.2†)

• lesions of pinta [carate] (A67.2†)

I98.2* Oesophageal varices without bleeding in diseases classified elsewhere

Oesophageal varices without bleeding in:

• liver disorders (K70–K71†, K74.-†)

• schistosomiasis (B65.-†)

I98.3* Oesophageal varices with bleeding in diseases classified elsewhere

Oesophageal varices with bleeding in:

• liver disorders (K70–K71†, K74.-†)

• schistosomiasis (B65.-†)

I98.8* Other specified disorders of circulatory system in diseases classified elsewhere

  I99 Other and unspecified disorders of circulatory system

CHAPTER X

Diseases of the respiratory system (J00–J99)

Note:  When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).

Excl.: certain conditions originating in the perinatal period (P00–P96) certain infectious and parasitic diseases (A00–B99)

complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90)

injury, poisoning and certain other consequences of external causes (S00–T98)

neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

J00–J06 Acute upper respiratory infections J09–J18 Influenza and pneumonia

J20–J22 Other acute lower respiratory infections J30–J39 Other diseases of upper respiratory tract J40–J47 Chronic lower respiratory diseases J60–J70 Lung diseases due to external agents

J80–J84 Other respiratory diseases principally affecting the interstitium J85–J86 Suppurative and necrotic conditions of lower respiratory tract J90–J94 Other diseases of pleura

J95–J99 Other diseases of the respiratory system

Asterisk categories for this chapter are provided as follows:

J17* Pneumonia in diseases classified elsewhere

J91* Pleural effusion in conditions classified elsewhere J99* Respiratory disorders in diseases classified elsewhere

 

Acute upper respiratory infections (J00–J06)

Excl.: chronic obstructive pulmonary disease with acute exacerbation NOS (J44.1)

  J00 Acute nasopharyngitis [common cold]

Incl.: coryza (acute)

nasal catarrh, acute nasopharyngitis:

• NOS

• infective NOS rhinitis:

• acute

• infective

Excl.: nasopharyngitis, chronic (J31.1) pharyngitis:

• NOS (J02.9)

• acute (J02.-)

• chronic (J31.2) rhinitis:

• NOS (J31.0)

• allergic (J30.1–J30.4)

• chronic (J31.0)

• vasomotor (J30.0) sore throat:

• NOS (J02.9)

• acute (J02.-)

• chronic (J31.2)

  J01 Acute sinusitis

Incl.: abscess

empyema infection inflammation suppuration

acute, of sinus (accessory)(nasal)

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: sinusitis, chronic or NOS (J32.-)

J01.0 Acute maxillary sinusitis

Acute antritis

J01.1 Acute frontal sinusitis J01.2 Acute ethmoidal sinusitis J01.3 Acute sphenoidal sinusitis

 

J01.4 Acute pansinusitis J01.8 Other acute sinusitis

Acute sinusitis involving more than one sinus but not pansinusitis

J01.9 Acute sinusitis, unspecified

  J02 Acute pharyngitis

Incl.:   acute sore throat

Excl.: abscess:

• peritonsillar (J36)

• pharyngeal (J39.1)

• retropharyngeal (J39.0)

acute laryngopharyngitis (J06.0) chronic pharyngitis (J31.2)

J02.0 Streptococcal pharyngitis

Streptococcal sore throat

Excl.: scarlet fever (A38)

J02.8 Acute pharyngitis due to other specified organisms

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: pharyngitis (due to):

• enteroviral vesicular (B08.5)

• herpesviral [herpes simplex] (B00.2)

• infectious mononucleosis (B27.-)

• influenza virus:

– identified (J09, J10.1)

– not identified (J11.1)

J02.9 Acute pharyngitis, unspecified

Pharyngitis (acute):

• NOS

• gangrenous

• infective NOS

• suppurative

• ulcerative

Sore throat (acute) NOS

  J03 Acute tonsillitis

Excl.: peritonsillar abscess (J36) sore throat:

• NOS (J02.9)

• acute (J02.-)

• streptococcal (J02.0)

J03.0 Streptococcal tonsillitis

 

J03.8 Acute tonsillitis due to other specified organisms

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: herpesviral [herpes simplex] pharyngotonsillitis (B00.2)

J03.9 Acute tonsillitis, unspecified

Tonsillitis (acute):

• NOS

• follicular

• gangrenous

• infective

• ulcerative

  J04 Acute laryngitis and tracheitis

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: acute obstructive laryngitis [croup] and epiglottitis (J05.-) laryngismus (stridulus) (J38.5)

J04.0 Acute laryngitis

Laryngitis (acute):

• NOS

• oedematous

• subglottic

• suppurative

• ulcerative

Excl.: chronic laryngitis (J37.0)

influenzal laryngitis, influenza virus:

• identified (J09, J10.1)

• not identified (J11.1)

J04.1 Acute tracheitis

Tracheitis (acute):

• NOS

• catarrhal

Excl.:  chronic tracheitis (J42)

J04.2 Acute laryngotracheitis

Laryngotracheitis NOS

Tracheitis (acute) with laryngitis (acute)

Excl.:  chronic laryngotracheitis (J37.1)

  J05 Acute obstructive laryngitis [croup] and epiglottitis

Use additional code (B95–B98), if desired, to identify infectious agent.

J05.0 Acute obstructive laryngitis [croup]

Obstructive laryngitis NOS

J05.1 Acute epiglottitis

Epiglottitis NOS

 

  J06 Acute upper respiratory infections of multiple and unspecified sites

Excl.: acute respiratory infection NOS (J22) influenza virus:

• identified (J09, J10.1)

• not identified (J11.1)

J06.0 Acute laryngopharyngitis

J06.8 Other acute upper respiratory infections of multiple sites J06.9 Acute upper respiratory infection, unspecified

Upper respiratory:

• disease, acute

• infection NOS

Influenza and pneumonia (J09–J18)

  J09 Influenza due to identified zoonotic or pandemic influenza virus

Note: For use of this category, reference must be made to the guidelines of the Global Influenza Programme (GIP, www.who.int/influenza/) of WHO.

Influenza caused by influenza virus strains of special epidemiological importance with an animal–human or inter-human transmission

Use additional code, if desired, to identify pneumonia or other manifestations.

Excl.: Haemophilus influenzae [H. influenzae]:

• infection NOS (A49.2)

• meningitis (G00.0)

• pneumonia (J14)

influenza due to identified seasonal influenza virus (J09)

  J10 influenza due to identified seasonal influenza virus

Incl.: Influenza due to identified influenza B or C virus

Excl.: Haemophilus influenzae [H. influenzae]:

• infection NOS (A49.2)

• meningitis (G00.0)

• pneumonia (J14)

influenza due to identified zoonotic or pandemic influenza virus (J09)

J10.0 Influenza with pneumonia, seasonal influenza virus identified

Influenzal (broncho)pneumonia, seasonal influenza virus identified

 

J10.1 Influenza with other respiratory manifestations, seasonal influenza virus identified

Influenza

Influenzal:

• acute upper respiratory infection

• laryngitis

• pharyngitis

• pleural effusion

seasonal influenza virus identified

J10.8 Influenza with other manifestations, seasonal influenza virus identified

Encephalopathy due to influenza

Influenzal:

• gastroenteritis

• myocarditis (acute)

seasonal influenza virus identified

  J11 Influenza, virus not identified

Incl.: influenza

viral influenza specific virus not stated to have been identified

Excl.: Haemophilus influenzae [H. influenzae]:

• infection NOS (A49.2)

• meningitis (G00.0)

• pneumonia (J14)

J11.0 Influenza with pneumonia, virus not identified Influenzal (broncho)pneumonia, unspecified or specific virus not identified

J11.1 Influenza with other respiratory manifestations, virus not identified

Influenza NOS

Influenzal:

• acute upper respiratory infection

• laryngitis

• pharyngitis

• pleural effusion

unspecified or specific virus not identified

J11.8 Influenza with other manifestations, virus not identified

Encephalopathy due to influenza

Influenzal:

• gastroenteritis

• myocarditis (acute)

unspecified or specific virus not identified

 

  J12 Viral pneumonia, not elsewhere classified

Incl.: bronchopneumonia due to viruses other than influenza viruses

Excl.: congenital rubella pneumonitis (P35.0) pneumonia:

• aspiration (due to):

– NOS (J69.0)

– anaesthesia during:

– labour and delivery (O74.0)

– pregnancy (O29.0)

– puerperium (O89.0)

• neonatal (P24.9)

• solids and liquids (J69.-)

• in influenza (J09, J10.0, J11.0)

• interstitial NOS (J84.9)

• lipid (J69.1)

• viral, congenital (P23.0)

severe acute respiratory syndrome [SARS] (U04.9)

J12.0 Adenoviral pneumonia

J12.1 Respiratory syncytial virus pneumonia J12.2 Parainfluenza virus pneumonia

J12.3 Human metapneumovirus pneumonia J12.8 Other viral pneumonia

J12.9 Viral pneumonia, unspecified

  J13 Pneumonia due to Streptococcus pneumoniae

Incl.: bronchopneumonia due to S. pneumoniae

Excl.: congenital pneumonia due to S. pneumoniae (P23.6) pneumonia due to other Streptococci (J15.3–J15.4)

  J14 Pneumonia due to Haemophilus influenzae

Incl.: bronchopneumonia due to H. influenzae

Excl.: congenital pneumonia due to H. influenzae (P23.6)

  J15 Bacterial pneumonia, not elsewhere classified

Incl.: bronchopneumonia due to bacteria other than S. pneumoniae and

H. influenzae

Excl.: chlamydial pneumonia (J16.0) congenital pneumonia (P23.-) Legionnaire disease (A48.1)

J15.0 Pneumonia due to Klebsiella pneumoniae

J15.1 Pneumonia due to Pseudomonas

 

J15.2 Pneumonia due to Staphylococcus

J15.3 Pneumonia due to Staphylococcus, group B J15.4 Pneumonia due to other Streptococci

Excl.: pneumonia due to:

• Streptococcus, group B (J15.3)

• Streptococcus pneumoniae (J13)

J15.5 Pneumonia due to Escherichia coli

J15.6 Pneumonia due to other aerobic Gram-negative bacteria

Pneumonia (due to):

• Gram-negative (aerobic) bacteria NOS

• Serratia marcescens

J15.7 Pneumonia due to Mycoplasma pneumoniae

J15.8 Other bacterial pneumonia

J15.9 Bacterial pneumonia, unspecified

  J16 Pneumonia due to other infectious organisms, not elsewhere classified

Excl.: ornithosis (A70)

pneumocystosis (B59) pneumonia:

• NOS (J18.9)

• congenital (P23.-)

J16.0 Chlamydial pneumonia

J16.8 Pneumonia due to other specified infectious organisms

  J17* Pneumonia in diseases classified elsewhere

J17.0* Pneumonia in bacterial diseases classified elsewhere

Pneumonia (due to)(in):

• actinomycosis (A42.0†)

• anthrax (A22.1†)

• gonorrhoea (A54.8†)

• nocardiosis (A43.0†)

• Salmonella infection (A02.2†)

• tularaemia (A21.2†)

• typhoid fever (A01.0†)

• whooping cough (A37.-†)

J17.1* Pneumonia in viral diseases classified elsewhere

Pneumonia in:

• cytomegalovirus disease (B25.0†)

• measles (B05.2†)

• rubella (B06.8†)

• varicella (B01.2†)

 

J17.2* Pneumonia in mycoses

Pneumonia in:

• aspergillosis (B44.0–B44.1†)

• candidiasis (B37.1†)

• coccidioidomycosis (B38.0–B38.2†)

• histoplasmosis (B39.-†)

J17.3* Pneumonia in parasitic diseases

Pneumonia in:

• ascariasis (B77.8†)

• schistosomiasis (B65.-†)

• toxoplasmosis (B58.3†)

J17.8* Pneumonia in other diseases classified elsewhere

Pneumonia (in):

• ornithosis (A70†)

• Q fever (A78†)

• rheumatic fever (I00†)

• spirochaetal, not elsewhere classified (A69.8†)

  J18 Pneumonia, organism unspecified

Excl.: abscess of lung with pneumonia (J85.1)

drug-induced interstitial lung disorders (J70.2–J70.4) pneumonia:

• aspiration (due to):

– NOS (J69.0)

– anaesthesia during:

– labour and delivery (O74.0)

– pregnancy (O29.0)

– puerperium (O89.0)

• neonatal (P24.9)

• solids and liquids (J69.-)

• congenital (P23.9)

• interstitial NOS (J84.9)

• lipid (J69.1)

• usual interstitial (J84.1)

pneumonitis, due to external agents (J67–J70)

J18.0 Bronchopneumonia, unspecified

Excl.: bronchiolitis (J21.-)

J18.1 Lobar pneumonia, unspecified J18.2 Hypostatic pneumonia, unspecified

J18.8 Other pneumonia, organism unspecified J18.9 Pneumonia, unspecified

 

Other acute lower respiratory infections (J20–J22)

Excl.: chronic obstructive pulmonary disease with acute:

• exacerbation NOS (J44.1)

• lower respiratory infection (J44.0)

  J20 Acute bronchitis

Incl.: bronchitis:

• NOS, in those under l5 years of age

• acute and subacute (with):

– bronchospasm

– fibrinous

– membranous

– purulent

– septic

– tracheitis tracheobronchitis, acute

Excl.: bronchitis:

• NOS, in those 15 years of age and above (J40)

• allergic NOS (J45.0)

• chronic:

– NOS (J42)

– mucopurulent (J41.1)

– obstructive (J44.-)

– simple (J41.0) tracheobronchitis:

• NOS (J40)

• chronic (J42)

• chronic obstructive (J44.-)

J20.0 Acute bronchitis due to Mycoplasma pneumoniae J20.1 Acute bronchitis due to Haemophilus influenzae J20.2 Acute bronchitis due to Streptococcus

J20.3 Acute bronchitis due to coxsackievirus J20.4 Acute bronchitis due to parainfluenza virus

J20.5 Acute bronchitis due to respiratory syncytial virus J20.6 Acute bronchitis due to rhinovirus

J20.7 Acute bronchitis due to echovirus

 

J20.8 Acute bronchitis due to other specified organisms J20.9 Acute bronchitis, unspecified

  J21 Acute bronchiolitis

Incl.: with bronchospasm

J21.0 Acute bronchiolitis due to respiratory syncytial virus J21.1 Acute bronchiolitis due to human metapneumovirus J21.8 Acute bronchiolitis due to other specified organisms J21.9 Acute bronchiolitis, unspecified

Bronchiolitis (acute)

  J22 Unspecified acute lower respiratory infection

Incl.: acute (lower) respiratory (tract) infection NOS

Excl.: upper respiratory infection (acute) (J06.9)

Other diseases of upper respiratory tract (J30–J39)

  J30 Vasomotor and allergic rhinitis

Incl.: spasmodic rhinorrhoea

Excl.: allergic rhinitis with asthma (J45.0) rhinitis NOS (J31.0)

J30.0 Vasomotor rhinitis

J30.1 Allergic rhinitis due to pollen

Allergy NOS due to pollen Hay fever

Pollinosis

J30.2 Other seasonal allergic rhinitis J30.3 Other allergic rhinitis

Perennial allergic rhinitis

J30.4 Allergic rhinitis, unspecified

  J31 Chronic rhinitis, nasopharyngitis and pharyngitis

J31.0 Chronic rhinitis

Ozena

Rhinitis (chronic):

• NOS

• atrophic

• granulomatous

• hypertrophic

• obstructive

• purulent

• ulcerative

Excl.: rhinitis:

• allergic (J30.1–J30.4)

• vasomotor (J30.0)

J31.1 Chronic nasopharyngitis

Excl.: nasopharyngitis, acute or NOS (J00)

J31.2 Chronic pharyngitis

Chronic sore throat Pharyngitis (chronic):

• atrophic

• granular

• hypertrophic

Excl.: pharyngitis, acute or NOS (J02.9)

  J32 Chronic sinusitis

Incl.: abscess

empyema infection suppuration

(chronic) of sinus (accessory)(nasal)

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: acute sinusitis (J01.-)

J32.0 Chronic maxillary sinusitis

Antritis (chronic) Maxillary sinusitis NOS

J32.1 Chronic frontal sinusitis

Frontal sinusitis NOS

J32.2 Chronic ethmoidal sinusitis

Ethmoidal sinusitis NOS

J32.3 Chronic sphenoidal sinusitis

Sphenoidal sinusitis NOS

J32.4 Chronic pansinusitis

Pansinusitis NOS

 

J32.8 Other chronic sinusitis

Sinusitis (chronic) involving more than one sinus but not pansinusitis

J32.9 Chronic sinusitis, unspecified

Sinusitis (chronic) NOS

  J33 Nasal polyp

Excl.: adenomatous polyps (D14.0)

J33.0 Polyp of nasal cavity

Polyp:

• choanal

• nasopharyngeal

J33.1 Polypoid sinus degeneration

Woakes’ syndrome or ethmoiditis

J33.8 Other polyp of sinus

Polyp of sinus:

• accessory

• ethmoidal

• maxillary

• sphenoidal

J33.9 Nasal polyp, unspecified

  J34 Other disorders of nose and nasal sinuses

Excl.: varicose ulcer of nasal septum (I86.8)

J34.0 Abscess, furuncle and carbuncle of nose

Cellulitis

Necrosis Ulceration

of nose (septum)

J34.1 Cyst and mucocele of nose and nasal sinus J34.2 Deviated nasal septum

Deflection or deviation of septum (nasal)(acquired)

J34.3 Hypertrophy of nasal turbinates

J34.8 Other specified disorders of nose and nasal sinuses

Perforation of nasal septum NOS Rhinolith

  J35 Chronic diseases of tonsils and adenoids

J35.0 Chronic tonsillitis

Excl.: tonsillitis:

• NOS (J03.9)

• acute (J03.-)

J35.1 Hypertrophy of tonsils

Enlargement of tonsils

 

J35.2 Hypertrophy of adenoids

Enlargement of adenoids

J35.3 Hypertrophy of tonsils with hypertrophy of adenoids J35.8 Other chronic diseases of tonsils and adenoids

Adenoid vegetations

Amygdalolith

Cicatrix of tonsil (and adenoid) Tonsillar tag

Ulcer of tonsil

J35.9 Chronic disease of tonsils and adenoids, unspecified

Disease (chronic) of tonsils and adenoids NOS

  J36 Peritonsillar abscess

Incl.: Abscess of tonsil

Peritonsillar cellulitis Quinsy

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: retropharyngeal abscess (J39.0) tonsillitis:

• NOS (J03.9)

• acute (J03.-)

• chronic (J35.0)

  J37 Chronic laryngitis and laryngotracheitis

Use additional code (B95–B98), if desired, to identify infectious agent.

J37.0 Chronic laryngitis

Laryngitis:

• catarrhal

• hypertrophic

• sicca

Excl.: laryngitis:

• NOS (J04.0)

• acute (J04.0)

• obstructive (acute) (J05.0)

J37.1 Chronic laryngotracheitis

Laryngitis, chronic, with tracheitis (chronic) Tracheitis, chronic, with laryngitis

Excl.: laryngotracheitis:

• NOS (J04.2)

• acute (J04.2) tracheitis:

• NOS (J04.1)

• acute (J04.1)

• chronic (J42)

 

  J38 Diseases of vocal cords and larynx, not elsewhere classified

Excl.: laryngitis:

• obstructive (acute) (J05.0)

• ulcerative (J04.0)

postprocedural subglottic stenosis (J95.5) stridor:

• congenital laryngeal NOS (P28.8)

• NOS (R06.1)

J38.0 Paralysis of vocal cords and larynx

Laryngoplegia Paralysis of glottis

J38.1 Polyp of vocal cord and larynx

Excl.:  adenomatous polyps (D14.1)

J38.2 Nodules of vocal cords

Chorditis (fibrinous)(nodosa)(tuberosa) Singer’s nodes

Teacher’s nodes

J38.3 Other diseases of vocal cords

Abscess

Cellulitis Granuloma Leukokeratosis Leukoplakia

of vocal cord(s)

J38.4 Oedema of larynx

Oedema (of):

• glottis

• subglottic

• supraglottic

Excl.: laryngitis:

• acute obstructive [croup] (J05.0)

• oedematous (J04.0)

J38.5 Laryngeal spasm

Laryngismus (stridulus)

J38.6 Stenosis of larynx

J38.7 Other diseases of larynx

Abscess

Cellulitis Disease NOS Necrosis Pachyderma Perichondritis Ulcer

of larynx

 

  J39 Other diseases of upper respiratory tract

Excl.: acute respiratory infection NOS (J22) acute respiratory infection NOS:

• upper (J06.9)

upper respiratory inflammation due to chemicals, gases, fumes or vapours (J68.2)

J39.0 Retropharyngeal and parapharyngeal abscess

Peripharyngeal abscess

Excl.: peritonsillar abscess (J36)

J39.1 Other abscess of pharynx Cellulitis of pharynx Nasopharyngeal abscess

J39.2 Other diseases of pharynx

Cyst

Oedema of pharynx or nasopharynx

Excl.: pharyngitis:

• chronic (J31.2)

• ulcerative (J02.9)

J39.3 Upper respiratory tract hypersensitivity reaction, site unspecified J39.8 Other specified diseases of upper respiratory tract

J39.9 Disease of upper respiratory tract, unspecified

Chronic lower respiratory diseases (J40–J47)

Excl.: cystic fibrosis (E84.-)

  J40 Bronchitis, not specified as acute or chronic

Note: Bronchitis not specified as acute or chronic in those under 15 years of age can be assumed to be of acute nature and should be classified to J20.-.

Incl.: bronchitis:

• NOS

• catarrhal

• with tracheitis NOS tracheobronchitis NOS

Excl.: bronchitis:

• allergic NOS (J45.0)

• asthmatic NOS (J45.9)

• chemical (acute) (J68.0)

 

  J41 Simple and mucopurulent chronic bronchitis

Excl.: chronic bronchitis:

• NOS (J42)

• obstructive (J44.-)

J41.0 Simple chronic bronchitis

J41.1 Mucopurulent chronic bronchitis

J41.8 Mixed simple and mucopurulent chronic bronchitis

  J42 Unspecified chronic bronchitis

Incl.: chronic:

• bronchitis NOS

• tracheitis

• tracheobronchitis

Excl.: chronic:

• asthmatic bronchitis (J44.-)

• bronchitis:

– simple and mucopurulent (J41.-)

– with airways obstruction (J44.-)

• emphysematous bronchitis (J44.-)

• obstructive pulmonary disease NOS (J44.9)

  J43 Emphysema

Excl.: emphysema:

• compensatory (J98.3)

• due to inhalation of chemicals, gases, fumes or vapours (J68.4)

• interstitial (J98.2)

• interstitial:

– neonatal (P25.0)

• mediastinal (J98.2)

• surgical (subcutaneous) (T81.8)

• traumatic subcutaneous (T79.7)

• with chronic (obstructive) bronchitis (J44.-) emphysematous (obstructive) bronchitis (J44.-)

J43.0 MacLeod’s syndrome

Unilateral:

• emphysema

• transparency of lung

J43.1 Panlobular emphysema

Panacinar emphysema

J43.2 Centrilobular emphysema J43.8 Other emphysema

 

J43.9 Emphysema, unspecified

Emphysema (lung)(pulmonary):

• NOS

• bullous

• vesicular Emphysematous bleb

  J44 Other chronic obstructive pulmonary disease

Incl.: chronic:

• bronchitis:

– asthmatic (obstructive)

– emphysematous

– with:

– airways obstruction

– emphysema

• obstructive:

– asthma

– bronchitis

– tracheobronchitis

Excl.: asthma (J45.-)

asthmatic bronchitis NOS (J45.9) bronchiectasis (J47)

chronic:

• bronchitis:

– NOS (J42)

– simple and mucopurulent (J41.-)

• tracheitis (J42)

• tracheobronchitis (J42) emphysema (J43.-)

lung diseases due to external agents (J60–J70)

J44.0 Chronic obstructive pulmonary disease with acute lower respiratory infection

Excl.: with influenza (J09–J11)

J44.1 Chronic obstructive pulmonary disease with acute exacerbation, unspecified

J44.8 Other specified chronic obstructive pulmonary disease

Chronic bronchitis:

• asthmatic (obstructive) NOS

• emphysematous NOS

• obstructive NOS

Excl.: with acute exacerbation (J44.1)

with acute lower respiratory infection (J44.0)

 

J44.9 Chronic obstructive pulmonary disease, unspecified

Chronic obstructive:

• airway disease NOS

• lung disease NOS

  J45 Asthma

Excl.: acute severe asthma (J46)

chronic asthmatic (obstructive) bronchitis (J44.-) chronic obstructive asthma (J44.-)

eosinophilic asthma (J82)

lung diseases due to external agents (J60–J70) status asthmaticus (J46)

J45.0 Predominantly allergic asthma

Allergic:

• bronchitis NOS

• rhinitis with asthma Atopic asthma

Extrinsic allergic asthma Hay fever with asthma

J45.1 Nonallergic asthma

Idiosyncratic asthma Intrinsic nonallergic asthma

J45.8 Mixed asthma

Combination of conditions listed in J45.0 and J45.1

J45.9 Asthma, unspecified

Asthmatic bronchitis NOS Late-onset asthma

  J46 Status asthmaticus

Incl.: acute severe asthma

  J47 Bronchiectasis

Incl.: bronchiolectasis

Excl.: congenital bronchiectasis (Q33.4)

tuberculous bronchiectasis (current disease) (A15–A16)

 

Lung diseases due to external agents (J60–J70)

Excl.: asthma classified to J45.-

  J60 Coalworker’s pneumoconiosis

Incl.: anthracosilicosis anthracosis coalworker’s lung

Excl.: with tuberculosis in A15–A16 (J65)

  J61 Pneumoconiosis due to asbestos and other mineral fibres

Incl.: asbestosis

Excl.: pleural plaque with asbestosis (J92.0) with tuberculosis in A15–A16 (J65)

  J62 Pneumoconiosis due to dust containing silica

Incl.: silicotic fibrosis (massive) of lung

Excl.: pneumoconiosis with tuberculosis in A15–A16 (J65)

J62.0 Pneumoconiosis due to talc dust

J62.8 Pneumoconiosis due to other dust containing silica

Silicosis NOS

  J63 Pneumoconiosis due to other inorganic dusts

Excl.: with tuberculosis in A15–A16 (J65)

J63.0 Aluminosis (of lung) J63.1 Bauxite fibrosis (of lung) J63.2 Berylliosis

J63.3 Graphite fibrosis (of lung) J63.4 Siderosis

J63.5 Stannosis

J63.8 Pneumoconiosis due to other specified inorganic dusts

  J64 Unspecified pneumoconiosis

Excl.: with tuberculosis in A15–A16 (J65)

  J65 Pneumoconiosis associated with tuberculosis

Incl.: any condition in J60–J64 with tuberculosis, any type in A15–A16

 

  J66 Airway disease due to specific organic dust

Excl.: bagassosis (J67.1) farmer’s lung (J67.0)

hypersensitivity pneumonitis due to organic dust (J67.-) reactive airways dysfunction syndrome (J68.3)

J66.0 Byssinosis

Airway disease due to cotton dust

J66.1 Flax-dresser’s disease J66.2 Cannabinosis

J66.8 Airway disease due to other specific organic dusts

  J67 Hypersensitivity pneumonitis due to organic dust

Incl.: allergic alveolitis and pneumonitis due to inhaled organic dust and particles of fungal, actinomycetic or other origin

Excl.: pneumonitis due to inhalation of chemicals, gases, fumes or vapours (J68.0)

J67.0 Farmer’s lung Harvester’s lung Haymaker’s lung Mouldy hay disease

J67.1 Bagassosis

Bagasse:

• disease

• pneumonitis

J67.2 Bird fancier’s lung

Budgerigar fancier’s disease or lung Pigeon fancier’s disease or lung

J67.3 Suberosis

Corkhandler’s disease or lung Corkworker’s disease or lung

J67.4 Maltworker’s lung

Alveolitis due to Aspergillus clavatus

J67.5 Mushroom-worker’s lung J67.6 Maple-bark-stripper’s lung

Alveolitis due to Cryptostroma corticale

Cryptostromosis

J67.7 Air-conditioner and humidifier lung

Allergic alveolitis due to fungi, thermophilic actinomycetes and other organisms growing in ventilation [air-conditioning] systems

 

J67.8 Hypersensitivity pneumonitis due to other organic dusts

Cheese-washer’s lung Coffee-worker’s lung Fishmeal-worker’s lung Furrier’s lung Sequoiosis

J67.9 Hypersensitivity pneumonitis due to unspecified organic dust

Allergic alveolitis (extrinsic) NOS Hypersensitivity pneumonitis NOS

  J68 Respiratory conditions due to inhalation of chemicals, gases, fumes and vapours

Use additional external cause code (Chapter XX), if desired, to identify cause.

J68.0 Bronchitis and pneumonitis due to chemicals, gases, fumes and vapours

Chemical bronchitis (acute)

J68.1 Pulmonary oedema due to chemicals, gases, fumes and vapours

Chemical pulmonary oedema (acute)

J68.2 Upper respiratory inflammation due to chemicals, gases, fumes and vapours, not elsewhere classified

J68.3 Other acute and subacute respiratory conditions due to chemicals, gases, fumes and vapours

Reactive airways dysfunction syndrome

J68.4 Chronic respiratory conditions due to chemicals, gases, fumes and vapours

Emphysema (diffuse)(chronic)

Obliterative bronchiolitis (chronic) (subacute)

Pulmonary fibrosis (chronic)

due to inhalation of chemicals, gases, fumes and vapours

J68.8 Other respiratory conditions due to chemicals, gases, fumes and vapours

J68.9 Unspecified respiratory condition due to chemicals, gases, fumes and vapours

  J69 Pneumonitis due to solids and liquids

Use additional external cause code (Chapter XX), if desired, to identify cause.

Excl.: neonatal aspiration syndromes (P24.-)

 

J69.0 Pneumonitis due to food and vomit

Aspiration pneumonia (due to):

• NOS

• food (regurgitated)

• gastric secretions

• milk

• vomit

Excl.: Mendelson syndrome (J95.4)

J69.1 Pneumonitis due to oils and essences

Lipid pneumonia

J69.8 Pneumonitis due to other solids and liquids

Pneumonitis due to aspiration of blood

  J70 Respiratory conditions due to other external agents

Use additional external cause code (Chapter XX), if desired, to identify cause.

J70.0 Acute pulmonary manifestations due to radiation

Radiation pneumonitis

J70.1 Chronic and other pulmonary manifestations due to radiation

Fibrosis of lung following radiation

J70.2 Acute drug-induced interstitial lung disorders J70.3 Chronic drug-induced interstitial lung disorders

J70.4 Drug-induced interstitial lung disorders, unspecified

J70.8 Respiratory conditions due to other specified external agents J70.9 Respiratory conditions due to unspecified external agent

Other respiratory diseases principally affecting the interstitium

(J80–J84)

  J80 Adult respiratory distress syndrome

Incl.: adult hyaline membrane disease

  J81 Pulmonary oedema

Incl.:  acute oedema of lung pulmonary congestion (passive)

Excl.: hypostatic pneumonia (J18.2) pulmonary oedema:

• chemical (acute) (J68.1)

• due to external agents (J60–J70)

• with mention of heart disease NOS or heart failure (I50.1)

  J82 Pulmonary eosinophilia, not elsewhere classified

Incl.: eosinophilic asthma Löffler pneumonia

tropical (pulmonary) eosinophilia NOS

Excl.: due to:

• aspergillosis (B44.-)

• drugs (J70.2–J70.4)

• specified parasitic infection (B50–B83)

• systemic connective tissue disorders (M30–M36)

  J84 Other interstitial pulmonary diseases

Excl.: drug-induced interstitial lung disorders (J70.2–J70.4) interstitial emphysema (J98.2)

lung diseases due to external agents (J60–J70) lymphoid interstitial pneumonitis resulting from human immunodeficiency virus [HIV] disease (B22.1)

J84.0 Alveolar and parietoalveolar conditions

Alveolar proteinosis

Pulmonary alveolar microlithiasis

 

J84.1 Other interstitial pulmonary diseases with fibrosis

Diffuse pulmonary fibrosis Fibrosing alveolitis (cryptogenic) Hamman–Rich syndrome Idiopathic pulmonary fibrosis Usual interstitial pneumonia

Excl.: pulmonary fibrosis (chronic):

• due to inhalation of chemicals, gases, fumes or vapours (J68.4)

• following radiation (J70.1)

J84.8 Other specified interstitial pulmonary diseases J84.9 Interstitial pulmonary disease, unspecified

Interstitial pneumonia NOS

Suppurative and necrotic conditions of lower respiratory tract

(J85–J86)

  J85 Abscess of lung and mediastinum

J85.0 Gangrene and necrosis of lung J85.1 Abscess of lung with pneumonia

Excl.: with pneumonia due to specified organism (J09–J16)

J85.2 Abscess of lung without pneumonia

Abscess of lung NOS

J85.3 Abscess of mediastinum

  J86 Pyothorax

Incl.: abscess of:

• pleura

• thorax empyema pyopneumothorax

Use additional code (B95–B98), if desired, to identify infectious agent.

Excl.: due to tuberculosis (A15–A16)

J86.0 Pyothorax with fistula J86.9 Pyothorax without fistula

 

Other diseases of pleura (J90–J94)

  J90 Pleural effusion, not elsewhere classified

Incl.: pleurisy with effusion

Excl.: chylous (pleural) effusion (J94.0) pleurisy NOS (R09.1) tuberculous (A15–A16)

  J91* Pleural effusion in conditions classified elsewhere

  J92 Pleural plaque

Incl.: pleural thickening

J92.0 Pleural plaque with presence of asbestos J92.9 Pleural plaque without asbestos

Pleural plaque NOS

  J93 Pneumothorax

Excl.: pneumothorax:

• congenital or perinatal (P25.1)

• traumatic (S27.0)

• tuberculous (current disease) (A15–A16) pyopneumothorax (J86.-)

J93.0 Spontaneous tension pneumothorax J93.1 Other spontaneous pneumothorax J93.8 Other pneumothorax

J93.9 Pneumothorax, unspecified

  J94 Other pleural conditions

Excl.: pleurisy NOS (R09.1) traumatic:

• haemopneumothorax (S27.2)

• haemothorax (S27.1)

tuberculous pleural conditions (current disease) (A15–A16)

J94.0 Chylous effusion

Chyliform effusion

J94.1 Fibrothorax

J94.2 Haemothorax

Haemopneumothorax

 

J94.8 Other specified pleural conditions

Hydrothorax

J94.9 Pleural condition, unspecified

Other diseases of the respiratory system (J95–J99)

  J95 Postprocedural respiratory disorders, not elsewhere classified

Excl.: emphysema (subcutaneous) resulting from a procedure (T81.8) pulmonary manifestations due to radiation (J70.0–J70.1)

J95.0 Tracheostomy malfunction Haemorrhage from tracheostomy stoma Obstruction of tracheostomy airway Sepsis of tracheostomy stoma

Tracheo-oesophageal fistula following tracheostomy

J95.1 Acute pulmonary insufficiency following thoracic surgery J95.2 Acute pulmonary insufficiency following nonthoracic surgery J95.3 Chronic pulmonary insufficiency following surgery

J95.4 Mendelson syndrome

Chemical pneumonitis due to aspiration during anesthesia

Excl.: complicating:

• labour and delivery (O74.0)

• pregnancy (O29.0)

• puerperium (O89.0)

J95.5 Postprocedural subglottic stenosis

J95.8 Other postprocedural respiratory disorders J95.9 Postprocedural respiratory disorder, unspecified

  J96 Respiratory failure, not elsewhere classified

Excl.: cardiorespiratory failure (R09.2) postprocedural respiratory failure (J95.-) respiratory:

• arrest (R09.2)

• distress:

– syndrome of adult (J80)

– in newborn (P22.-)

 

The following supplementary subclassification is provided for optional use with subcategories in J96:

0 Type I [hypoxic]

1 Type II [hypercapnic]

9 Type unspecified

J96.0 Acute respiratory failure J96.1 Chronic respiratory failure

J96.9 Respiratory failure, unspecified

  J98 Other respiratory disorders

Excl.: apnoea:

• NOS (R06.8)

• newborn (P28.4)

• sleep (G47.3)

• sleep:

– newborn (P28.3)

J98.0 Diseases of bronchus, not elsewhere classified

Broncholithiasis

Calcification

Stenosis Ulcer

of bronchus

Tracheobronchial:

• collapse

• dyskinesia

J98.1 Pulmonary collapse

Atelectasis Collapse of lung

Excl.: atelectasis (of):

• newborn (P28.0–P28.1)

• tuberculous (current disease) (A15–A16)

J98.2 Interstitial emphysema

Mediastinal emphysema

Excl.: emphysema:

• NOS (J43.9)

• in fetus and newborn (P25.0)

• surgical (subcutaneous) (T81.8)

• traumatic subcutaneous (T79.7)

J98.3 Compensatory emphysema

 

J98.4 Other disorders of lung

Calcification of lung

Cystic lung disease (acquired) Lung disease NOS Pulmolithiasis

J98.5 Diseases of mediastinum, not elsewhere classified

Fibrosis

Hernia Retraction

of mediastinum

Mediastinitis

Excl.: abscess of mediastinum (J85.3)

J98.6 Disorders of diaphragm

Diaphragmatitis Paralysis of diaphragm Relaxation of diaphragm

Excl.: congenital malformation of diaphragm NEC (Q79.1) diaphragmatic hernia (K44.-)

diaphragmatic hernia:

• congenital (Q79.0)

J98.8 Other specified respiratory disorders J98.9 Respiratory disorder, unspecified

Respiratory disease (chronic) NOS

  J99* Respiratory disorders in diseases classified elsewhere

J99.0* Rheumatoid lung disease (M05.1†)

J99.1* Respiratory disorders in other diffuse connective tissue disorders

Respiratory disorders in:

• dermatomyositis (M33.0–M33.1†)

• polymyositis (M33.2†)

• sicca syndrome [Sjögren] (M35.0†)

• systemic:

– lupus erythematosus (M32.1†)

– sclerosis (M34.8†)

• Wegener granulomatosis (M31.3†)

J99.8* Respiratory disorders in other diseases classified elsewhere

Respiratory disorders in:

• amoebiasis (A06.5†)

• ankylosing spondylitis (M45†)

• cryoglobulinaemia (D89.1†)

• sporotrichosis (B42.0†)

• syphilis (A52.7†)

CHAPTER XI

Diseases of the digestive system (K00–K93)

Excl.: certain conditions originating in the perinatal period (P00–P96) certain infectious and parasitic diseases (A00–B99)

complications of pregnancy, childbirth and the puerperium (O00–O99) congenital malformations, deformations and chromosomal abnormalities (Q00–Q99)

endocrine, nutritional and metabolic diseases (E00–E90)

injury, poisoning and certain other consequences of external causes (S00–T98)

neoplasms (C00–D48)

symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00–R99)

This chapter contains the following blocks:

K00–K14 Diseases of oral cavity, salivary glands and jaws K20–K31 Diseases of oesophagus, stomach and duodenum K35–K38 Diseases of appendix

K40–K46 Hernia

K50–K52 Noninfective enteritis and colitis K55–K63 Other diseases of intestines K65–K67  Diseases of peritoneum K70–K77 Diseases of liver

K80–K87 Disorders of gallbladder, biliary tract and pancreas K90–K93 Other diseases of the digestive system

Asterisk categories for this chapter are provided as follows:

K23* Disorders of oesophagus in diseases classified elsewhere

K67* Disorders of peritoneum in infectious diseases classified elsewhere K77* Liver disorders in diseases classified elsewhere

K87* Disorders of gallbladder, biliary tract and pancreas in diseases classified elsewhere

K93* Disorders of other digestive organs in diseases classified elsewhere

 

Diseases of oral cavity, salivary glands and jaws (K00–K14)

  K00 Disorders of tooth development and eruption

Excl.: embedded and impacted teeth (K01.-)

K00.0 Anodontia Hypodontia Oligodontia

K00.1 Supernumerary teeth

Distomolar Fourth molar Mesiodens Paramolar

Supplementary teeth

K00.2 Abnormalities of size and form of teeth

Concrescence

Fusion Gemination

of teeth

Dens:

• evaginatus

• in dente

• invaginatus Enamel pearls Macrodontia Microdontia

Peg-shaped [conical] teeth Taurodontism Tuberculum paramolare

Excl.: tuberculum Carabelli, which is regarded as a normal variation and should not be coded

K00.3 Mottled teeth Dental fluorosis Mottling of enamel

Nonfluoride enamel opacities

Excl.: deposits [accretions] on teeth (K03.6)

K00.4 Disturbances in tooth formation

Aplasia and hypoplasia of cementum

 

Dilaceration of tooth

Enamel hypoplasia (neonatal)(postnatal)(prenatal) Regional odontodysplasia

Turner tooth

Excl.: Hutchinson teeth and mulberry molars in congenital syphilis (A50.5) mottled teeth (K00.3)

K00.5 Hereditary disturbances in tooth structure, not elsewhere classified

Amelogenesis

Dentinogenesis Odontogenesis

imperfecta

Dentinal dysplasia Shell teeth

K00.6 Disturbances in tooth eruption

Dentia praecox

Natal

Neonatal tooth

Premature:

• eruption of tooth

• shedding of primary [deciduous] tooth Retained [persistent] primary tooth

K00.7 Teething syndrome

K00.8 Other disorders of tooth development Colour changes during tooth formation Intrinsic staining of teeth NOS

K00.9 Disorder of tooth development, unspecified

Disorder of odontogenesis NOS

  K01 Embedded and impacted teeth

Excl.: embedded and impacted teeth with abnormal position of such teeth or adjacent teeth (K07.3)

K01.0 Embedded teeth

An embedded tooth is a tooth that has failed to erupt without obstruction by another tooth.

K01.1 Impacted teeth

An impacted tooth is a tooth that has failed to erupt because of obstruction by another tooth.

 

  K02 Dental caries

K02.0 Caries limited to enamel

White spot lesions [initial caries]

K02.1 Caries of dentine K02.2 Caries of cementum K02.3 Arrested dental caries K02.4 Odontoclasia

Infantile melanodontia

Melanodontoclasia

K02.5 Caries with pulp exposure K02.8 Other dental caries

K02.9 Dental caries, unspecified

  K03 Other diseases of hard tissues of teeth

Excl.: bruxism (F45.8)

dental caries (K02.-)

teeth-grinding NOS (F45.8)

K03.0 Excessive attrition of teeth

Wear:

• approximal

• occlusal

of teeth

K03.1 Abrasion of teeth

Abrasion:

• dentifrice

• habitual

• occupational

• ritual

• traditional

Wedge defect NOS

of teeth

K03.2 Erosion of teeth

Erosion of teeth:

• NOS

• due to:

– diet

– drugs and medicaments

– persistent vomiting

• idiopathic

• occupational

K03.3 Pathological resorption of teeth Internal granuloma of pulp Resorption of teeth (external)

K03.4 Hypercementosis

Cementation hyperplasia

 

K03.5 Ankylosis of teeth

K03.6 Deposits [accretions] on teeth

Dental calculus:

• subgingival

• supragingival

Deposits [accretions] on teeth:

• betel

• black

• green

• materia alba

• orange

• tobacco Staining of teeth:

• NOS

• extrinsic NOS

K03.7 Posteruptive colour changes of dental hard tissues

Excl.: deposits [accretions] on teeth (K03.6)

K03.8 Other specified diseases of hard tissues of teeth

Irradiated enamel Sensitive dentine

Use additional external cause code (Chapter XX), if desired, to identify radiation, if radiation-induced.

K03.9 Disease of hard tissues of teeth, unspecified

  K04 Diseases of pulp and periapical tissues

K04.0 Pulpitis

Pulpitis:

• NOS

• acute

• chronic (hyperplastic)(ulcerative)

• irreversible

• reversible

K04.1 Necrosis of pulp

Pulpal gangrene

K04.2 Pulp degeneration

Denticles Pulpal:

• calcifications

• stones

K04.3 Abnormal hard tissue formation in pulp

Secondary or irregular dentine

K04.4 Acute apical periodontitis of pulpal origin

Acute apical periodontitis NOS

 

K04.5 Chronic apical periodontitis Apical or periapical granuloma Apical periodontitis NOS

K04.6 Periapical abscess with sinus

Dental

Dentoalveolar abscess with sinus

K04.7 Periapical abscess without sinus

Dental

Dentoalveolar Periapical

abscess NOS

K04.8 Radicular cyst

Cyst:

apical (periodontal) periapical

residual radicular

Excl.: lateral periodontal cyst (K09.0)

K04.9 Other and unspecified diseases of pulp and periapical tissues

  K05 Gingivitis and periodontal diseases

K05.0 Acute gingivitis

Excl.: acute necrotizing ulcerative gingivitis (A69.1) herpesviral [herpes simplex] gingivostomatitis (B00.2)

K05.1 Chronic gingivitis

Gingivitis (chronic):

• NOS

• desquamative

• hyperplastic

• simple marginal

• ulcerative

K05.2 Acute periodontitis

Acute pericoronitis Parodontal abscess Periodontal abscess

Excl.: acute apical periodontitis (K04.4) periapical abscess (K04.7)

periapical abscess with sinus (K04.6)

K05.3 Chronic periodontitis

Chronic pericoronitis Periodontitis:

• NOS

• complex

• simplex

 

K05.4 Periodontosis

Juvenile periodontosis

K05.5 Other periodontal diseases K05.6 Periodontal disease, unspecified

  K06 Other disorders of gingiva and edentulous alveolar ridge

Excl.: atrophy of edentulous alveolar ridge (K08.2) gingivitis:

• NOS (K05.1)

• acute (K05.0)

• chronic (K05.1)

K06.0 Gingival recession

Gingival recession (generalized)(localized)(postinfective)(post-operative)

K06.1 Gingival enlargement

Gingival fibromatosis

K06.2 Gingival and edentulous alveolar ridge lesions associated with trauma

Irritative hyperplasia of edentulous ridge [denture hyperplasia]

Use additional external cause code (Chapter XX), if desired, to identify cause.

K06.8 Other specified disorders of gingiva and edentulous alveolar ridge

Fibrous epulis Flabby ridge Giant cell epulis

Peripheral giant cell granuloma Pyogenic granuloma of gingiva

K06.9 Disorder of gingiva and edentulous alveolar ridge, unspecified

  K07 Dentofacial anomalies [including malocclusion]

Excl.: hemifacial atrophy or hypertrophy (Q67.4)

unilateral condylar hyperplasia or hypoplasia (K10.8)

K07.0 Major anomalies of jaw size

Hyperplasia, hypoplasia:

• mandibular

• maxillary

Macrognathism (mandibular)(maxillary) Micrognathism (mandibular)(maxillary)

Excl.: acromegaly (E22.0) Robin syndrome (Q87.0)

 

K07.1 Anomalies of jaw-cranial base relationship

Asymmetry of jaw

Prognathism (mandibular)(maxillary) Retrognathism (mandibular)(maxillary)

K07.2 Anomalies of dental arch relationship

Crossbite (anterior)(posterior) Disto-occlusion

Mesio-occlusion

Midline deviation of dental arch Openbite (anterior)(posterior) Overbite (excessive):

• deep

• horizontal

• vertical Overjet

Posterior lingual occlusion of mandibular teeth

K07.3 Anomalies of tooth position

Crowding

Diastema Displacement Rotation

Spacing, abnormal

Transposition

of tooth or teeth

Impacted or embedded teeth with abnormal position of such teeth or adjacent teeth

Excl.: embedded and impacted teeth without abnormal position (K01.-)

K07.4 Malocclusion, unspecified

K07.5 Dentofacial functional abnormalities

Abnormal jaw closure Malocclusion due to:

• abnormal swallowing

• mouth breathing

• tongue, lip or finger habits

Excl.: bruxism (F45.8)

teeth-grinding NOS (F45.8)

K07.6 Temporomandibular joint disorders Costen complex or syndrome Derangement of temporomandibular joint Snapping jaw

Temporomandibular joint-pain-dysfunction syndrome

Excl.: current temporomandibular joint:

• dislocation (S03.0)

• strain (S03.4)

 

K07.8 Other dentofacial anomalies K07.9 Dentofacial anomaly, unspecified

  K08 Other disorders of teeth and supporting structures

K08.0 Exfoliation of teeth due to systemic causes

K08.1 Loss of teeth due to accident, extraction or local periodontal disease

K08.2 Atrophy of edentulous alveolar ridge K08.3 Retained dental root

K08.8 Other specified disorders of teeth and supporting structures

Alveolar (process) cleft Enlargement of alveolar ridge NOS Irregular alveolar process Toothache NOS

K08.9 Disorder of teeth and supporting structures, unspecified

  K09 Cysts of oral region, not elsewhere classified

Incl.: lesions showing histological features both of aneurysmal cyst and of another fibro-osseous lesion

Excl.: radicular cyst (K04.8)

K09.0 Developmental odontogenic cysts

Cyst (of):

• nasolabial [nasoalveolar]

• nasopalatine duct [incisive canal]

K09.1 Developmental (nonodontogenic) cysts of oral region

Cyst (of):

• nasolabial [nasoalveolar]

• nasopalatine duct [incisive canal]

K09.2 Other cysts of jaw

Cyst of jaw:

• NOS

• aneurysmal

• haemorrhagic

• traumatic

Excl.: latent bone cyst of jaw (K10.0) Stafne cyst (K10.0)

K09.8 Other cysts of oral region, not elsewhere classified

Dermoid cyst

Epidermoid cyst Lymphoepithelial cyst

of mouth

Epstein pearl

K09.9 Cyst of oral region, unspecified

 

  K10 Other diseases of jaws

K10.0 Developmental disorders of jaws

Latent bone cyst of jaw Stafne cyst

Torus:

• mandibularis

• palatinus

K10.1 Giant cell granuloma, central

Giant cell granuloma NOS

Excl.: peripheral giant cell granuloma (K06.8)

K10.2 Inflammatory conditions of jaws

Osteitis

Osteomyelitis (neonatal)

Osteonecrosis (drug-induced)(radiation-induced) Osteo (radio) necrosis

Periostitis

of jaw (acute) (chronic) (suppurative)

Sequestrum of jaw bone

Use additional external cause code (Chapter XX), if desired, to identify radiation, if radiation-induced, or to identify drug, if drug-induced.

K10.3 Alveolitis of jaws

Alveolar osteitis Dry socket

K10.8 Other specified diseases of jaws

Cherubism

Exostosis

Fibrous dysplasia of jaw

Unilateral condylar:

• hyperplasia

• hypoplasia

K10.9 Disease of jaws, unspecified

  K11 Diseases of salivary glands K11.0 Atrophy of salivary gland K11.1 Hypertrophy of salivary gland K11.2 Sialoadenitis

Excl.:  epidemic parotitis (B26.-) uveoparotid fever [Heerfordt] (D86.8)

K11.3 Abscess of salivary gland K11.4 Fistula of salivary gland

Excl.: congenital fistula of salivary gland (Q38.4)

 

K11.5

K11.6 Mucocele of salivary gland

Mucous:

• extravasation cyst

• retention cyst

of salivary gland

Ranula

K11.7 Disturbances of salivary secretion

Hypoptyalism Ptyalism Xerostomia

Excl.: dry mouth NOS (R68.2)

K11.8 Other diseases of salivary glands

Benign lymphoepithelial lesion of salivary gland Mikulicz disease

Necrotizing sialometaplasia Sialectasia

Stenosis

Stricture of salivary gland

Excl.: sicca syndrome [Sjögren] (M35.0)

K11.9 Disease of salivary gland, unspecified

Sialoadenopathy NOS

  K12 Stomatitis and related lesions

Excl.: cancrum oris (A69.0) cheilitis (K13.0)

gangrenous stomatitis (A69.0)

herpesviral [herpes simplex] gingivostomatitis (B00.2) noma (A69.0)

K12.0 Recurrent oral aphthae

Aphthous stomatitis (major)(minor) Bednar aphthae

Periadenitis mucosa necrotica recurrens Recurrent aphthous ulcer

Stomatitis herpetiformis

K12.1 Other forms of stomatitis

Stomatitis:

• NOS

• denture

• ulcerative

• vesicular

 

K12.2 Cellulitis and abscess of mouth Cellulitis of mouth (floor) Submandibular abscess

Excl.: abscess (of):

• periapical (K04.6–K04.7)

• periodontal (K05.2)

• peritonsillar (J36)

• salivary gland (K11.3)

• tongue (K14.0)

K12.3 Oral mucositis (ulcerative)

Mucositis (oral) (oropharyngeal):

• NOS

• drug-induced

• radiation induced

• viral

Use additional external cause code (Chapter XX), if desired, to identify external agent

Excl.: mucositis (ulcerative) of gastrointestinal tract (except oral cavity and oropharynx) (K92.8)

  K13 Other diseases of lip and oral mucosa

Incl.: epithelial disturbances of tongue

Excl.: certain disorders of gingiva and edentulous alveolar ridge (K05–K06)

cysts of oral region (K09.-) diseases of tongue (K14.-)

stomatitis and related lesions (K12.-)

K13.0 Diseases of lips

Cheilitis:

• NOS

• angular

• exfoliative

• glandular Cheilodynia Cheilosis Perlèche NEC

Excl.: ariboflavinosis (E53.0)

cheilitis due to radiation-related disorders (L55–L59) perlèche due to:

• candidiasis (B37.8)

• riboflavin deficiency (E53.0)

K13.1 Cheek and lip biting

K13.2 Leukoplakia and other disturbances of oral epithelium,

 

including tongue

Erythroplakia

Leukoedema

of oral epithelium, including tongue

Leukokeratosis nicotina palati Smoker’s palate

Excl.: hairy leukoplakia (K13.3)

K13.3 Hairy leukoplakia

K13.4 Granuloma and granuloma-like lesions of oral mucosa

Eosinophilic granuloma

Granuloma pyogenicum Verrucous xanthoma

of oral mucosa

K13.5 Oral submucous fibrosis

Submucous fibrosis of tongue

K13.6 Irritative hyperplasia of oral mucosa

Excl.: irritative hyperplasia of edentulous ridge [denture hyperplasia] (K06.2)

K13.7 Other and unspecified lesions of oral mucosa

Focal oral mucinosis

  K14 Diseases of tongue

Incl.: erythroplakia

focal epithelial hyperplasia leukoedema

leukoplakia

of tongue (K13.2)

hairy leukoplakia (K13.3) macroglossia (congenital) (Q38.2) submucous fibrosis of tongue (K13.5)

K14.0 Glossitis

Abscess

Ulceration (traumatic) of tongue

Excl.: atrophic glossitis (K14.4)

K14.1 Geographic tongue

Benign migratory glossitis Glossitis areata exfoliativa

K14.2 Median rhomboid glossitis K14.3 Hypertrophy of tongue papillae

Black hairy tongue

Coated tongue

Hypertrophy of foliate papillae Lingua villosa nigra

K14.4 Atrophy of tongue papillae

 

Atrophic glossitis

K14.5 Plicated tongue

Fissured

Furrowed Scrotal

tongue

Excl.: fissured tongue, congenital (Q38.3)

K14.6 Glossodynia Glossopyrosis Painful tongue

K14.8 Other diseases of tongue

Atrophy

Crenated Enlargement Hypertrophy

(of) tongue

K14.9 Disease of tongue, unspecified

Glossopathy NOS

Diseases of oesophagus, stomach and duodenum (K20–K31)

Excl.: hiatus hernia (K44.-)

The following fourth-character subdivisions are for use with categories K25–K28:

.0 Acute with haemorrhage

.1 Acute with perforation

.2 Acute with both haemorrhage and perforation

.3 Acute without haemorrhage or perforation

.4 Chronic or unspecified with haemorrhage

.5 Chronic or unspecified with perforation

.6 Chronic or unspecified with both haemorrhage and perforation

.7 Chronic without haemorrhage or perforation

.9 Unspecified as acute or chronic, without haemorrhage or perforation

  K20 Oesophagitis

Incl.: abscess of oesophagus oesophagitis:

• NOS

• chemical

• peptic

Use additional external cause code (Chapter XX), if desired, to identify cause.

Excl.: erosion of oesophagus (K22.1) reflux oesophagitis (K21.0)

with gastro-oesophageal reflux disease (K21.0)

  K21 Gastro-oesophageal reflux disease

K21.0 Gastro-oesophageal reflux disease with oesophagitis

Reflux oesophagitis

K21.9 Gastro-oesophageal reflux disease without oesophagitis

Oesophageal reflux NOS

  K22 Other diseases of oesophagus

Excl.: oesophageal varices (I85.-)

K22.0 Achalasia of cardia

Achalasia NOS Cardiospasm

Excl.: congenital cardiospasm (Q39.5)

K22.1 Ulcer of oesophagus

Erosion of oesophagus Ulcer of oesophagus:

• NOS

• due to ingestion of:

– chemicals

– drugs and medicaments

• fungal

• peptic

Ulcerative oesophagitis

Use additional external cause code (Chapter XX), if desired, to identify cause.

K22.2 Oesophageal obstruction

Compression

 

Constriction Stenosis Stricture

 

of oesophagus

 

Excl.: congenital stenosis or stricture of oesophagus (Q39.3)

 

K22.3 Perforation of oesophagus

Rupture of oesophagus

Excl.: traumatic perforation of (thoracic) oesophagus (S27.8)

K22.4 Dyskinesia of oesophagus

Corkscrew oesophagus Diffuse oesophageal spasm Spasm of oesophagus

Excl.: cardiospasm (K22.0)

K22.5 Diverticulum of oesophagus, acquired

Oesophageal pouch, acquired

Excl.: diverticulum of oesophagus (congenital) (Q39.6)

K22.6 Gastro-oesophageal laceration-haemorrhage syndrome

Mallory–Weiss syndrome

K22.7 Barrett oesophagus

Barrett:

• disease

• syndrome

Excl.: Barrett ulcer (K22.1)

K22.8 Other specified diseases of oesophagus

Haemorrhage of oesophagus NOS

K22.9 Disease of oesophagus, unspecified

  K23* Disorders of oesophagus in diseases classified elsewhere

K23.0* Tuberculous oesophagitis (A18.8†)

K23.1* Megaoesophagus in Chagas disease (B57.3†)

K23.8* Disorders of oesophagus in other diseases classified elsewhere

  K25 Gastric ulcer

[See at the beginning of this block for subdivisions]

Incl.: erosion (acute) of stomach ulcer (peptic):

• pylorus

• stomach

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: acute haemorrhagic erosive gastritis (K29.0) peptic ulcer NOS (K27.-)

 

  K26 Duodenal ulcer

[See at the beginning of this block for subdivisions]

Incl.: erosion (acute) of duodenum ulcer (peptic):

• duodenal

• postpyloric

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced.

Excl.: peptic ulcer NOS (K27.-)

  K27 Peptic ulcer, site unspecified

[See at the beginning of this block for subdivisions]

Incl.: gastroduodenal ulcer NOS peptic ulcer NOS

Excl.: peptic ulcer of newborn (P78.8)

  K28 Gastrojejunal ulcer

[See at the beginning of this block for subdivisions]

Incl.: ulcer (peptic) or erosion:

• anastomotic

• gastrocolic

• gastrointestinal

• gastrojejunal

• jejunal

• marginal

• stomal

Excl.: primary ulcer of small intestine (K63.3)

  K29 Gastritis and duodenitis

Excl.: eosinophilic gastritis or gastroenteritis (K52.8) Zollinger–Ellison syndrome (E16.4)

K29.0 Acute haemorrhagic gastritis

Acute (erosive) gastritis with haemorrhage

Excl.: erosion (acute) of stomach (K25.-)

K29.1 Other acute gastritis K29.2 Alcoholic gastritis

K29.3 Chronic superficial gastritis

K29.4 Chronic atrophic gastritis

Gastric atrophy

 

K29.5 Chronic gastritis, unspecified

Chronic gastritis:

• antral

• fundal

K29.6 Other gastritis

Giant hypertrophic gastritis Granulomatous gastritis Ménétrier disease

Excl.: with gastro-oesophageal reflux disease (K21.-)

with Helicobacter pylori associated chronic gastritis (K29.5)

K29.7 Gastritis, unspecified K29.8 Duodenitis

K29.9 Gastroduodenitis, unspecified

  K30 Functional dyspepsia

Incl.: indigestion

Excl.: dyspepsia:

• nervous (F45.3)

• neurotic (F45.3)

• psychogenic (F45.3) heartburn (R12)

  K31 Other diseases of stomach and duodenum

Incl.: functional disorders of stomach

Excl.: diverticulum of duodenum (K57.0–K57.1) gastrointestinal haemorrhage (K92.0–K92.2)

K31.0 Acute dilatation of stomach

Acute distension of stomach

K31.1 Adult hypertrophic pyloric stenosis

Pyloric stenosis NOS

Excl.: congenital or infantile pyloric stenosis (Q40.0)

K31.2 Hourglass stricture and stenosis of stomach

Excl.: congenital hourglass stomach (Q40.2) hourglass contraction of stomach (K31.8)

K31.3 Pylorospasm, not elsewhere classified

Excl.: pylorospasm:

• congenital or infantile (Q40.0)

• neurotic (F45.3)

• psychogenic (F45.3)

 

K31.4 Gastric diverticulum

Excl.: congenital diverticulum of stomach (Q40.2)

K31.5 Obstruction of duodenum

Constriction Stenosis Stricture

of duodenum

Duodenal ileus (chronic)

Excl.: congenital stenosis of duodenum (Q41.0)

K31.6 Fistula of stomach and duodenum

Gastrocolic fistula Gastrojejunocolic fistula

K31.7 Polyp of stomach and duodenum

Excl.: adenomatous polyp of stomach (D13.1)

K31.8 Other specified diseases of stomach and duodenum

Achlorhydria Gastroptosis

Hourglass contraction of stomach

K31.9 Disease of stomach and duodenum, unspecified

Diseases of appendix (K35–K38)

  K35 Acute appendicitis

K35.2 Acute appendicitis with generalized peritonitis Appendicitis (acute) with generalized (diffuse) peritonitis following rupture or perforation

K35.3 Acute appendicitis with localized peritonitis

Acute appendicitis (with or without perforation or rupture) with peritonitis:

• NOS

• localized

Acute appendicitis with peritoneal abscess

K35.8 Acute appendicitis, other and unspecified

Acute appendicitis without mention of localized or generalized peritonitis

  K36 Other appendicitis

Incl.: appendicitis:

• chronic

• recurrent

  K37 Unspecified appendicitis

 

  K38 Other diseases of appendix K38.0 Hyperplasia of appendix K38.1 Appendicular concretions

K38.2 Diverticulum of appendix K38.3 Fistula of appendix

K38.8 Other specified diseases of appendix

Intussusception of appendix

K38.9 Disease of appendix, unspecified

Hernia (K40–K46)

Note: Hernia with both gangrene and obstruction is classified to hernia with gangrene.

Incl.: hernia:

• acquired

• congenital [except diaphragmatic or hiatus]

• recurrent

  K40 Inguinal hernia

Incl.: bubonocele

inguinal hernia:

• NOS

• direct

• double

• indirect

• oblique scrotal hernia

K40.0 Bilateral inguinal hernia, with obstruction, without gangrene K40.1 Bilateral inguinal hernia, with gangrene

 

K40.2 Bilateral inguinal hernia, without obstruction or gangrene

Bilateral inguinal hernia NOS

K40.3 Unilateral or unspecified inguinal hernia, with obstruction, without gangrene

Inguinal hernia (unilateral):

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

K40.4 Unilateral or unspecified inguinal hernia, with gangrene

Inguinal hernia NOS with gangrene

K40.9 Unilateral or unspecified inguinal hernia, without obstruction or gangrene

Inguinal hernia (unilateral) NOS

  K41 Femoral hernia

K41.0 Bilateral femoral hernia, with obstruction, without gangrene K41.1 Bilateral femoral hernia, with gangrene

K41.2 Bilateral femoral hernia, without obstruction or gangrene

Bilateral femoral hernia NOS

K41.3 Unilateral or unspecified femoral hernia, with obstruction, without gangrene

Femoral hernia (unilateral):

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

K41.4 Unilateral or unspecified femoral hernia, with gangrene K41.9 Unilateral or unspecified femoral hernia, without obstruction

or gangrene

Femoral hernia (unilateral) NOS

  K42 Umbilical hernia

Incl.: paraumbilical hernia

Excl.: omphalocele (Q79.2)

K42.0 Umbilical hernia with obstruction, without gangrene

Umbilical hernia:

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

 

K42.1 Umbilical hernia with gangrene

Gangrenous umbilical hernia

K42.9 Umbilical hernia without obstruction or gangrene

Umbilical hernia NOS

  K43 Ventral hernia

K43.0 Incisional hernia with obstruction, without gangrene

Incisional hernia:

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

K43.1 Incisional hernia with gangrene

Gangrenous incisional hernia

K43.2 Incisional hernia without obstruction or gangrene

Incisional hernia NOS

K43.3 Parastomal hernia with obstruction, without gangrene

Parastomal hernia:

• causing obstruction

• incarcerated without gangrene

• irreducible

• strangulated

without gangrene

K43.4 Parastomal hernia with gangrene

Gangrenous parastomal hernia

K43.5 Parastomal hernia without obstruction or gangrene

Parastomal hernia NOS

K43.6 Other and unspecified ventral hernia with obstruction without gangrene

Hernia

• epigastric

• hypogastric

• midline

• spigelian

 

• subxiphoid

Any condition listed under K43.6

• causing obstruction

• incarcerated

• irreducible

• strangulated

 

without gangrene

 

K43.7 Other and unspecified ventral hernia with gangrene

Any condition listed under K43.6 specified as gangrenous

K43.9 Other and unspecified ventral hernia without obstruction or gangrene

Ventral hernia NOS

  K44 Diaphragmatic hernia

Incl.: hiatus hernia (oesophageal)(sliding) paraoesophageal hernia

Excl.: congenital hernia:

• diaphragmatic (Q79.0)

• hiatus (Q40.1)

K44.0 Diaphragmatic hernia with obstruction, without gangrene

Diaphragmatic hernia:

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

K44.1 Diaphragmatic hernia with gangrene

Gangrenous diaphragmatic hernia

K44.9 Diaphragmatic hernia without obstruction or gangrene

Diaphragmatic hernia NOS

  K45 Other abdominal hernia

Incl.: hernia:

• abdominal, specified site NEC

• lumbar

• obturator

• pudendal

• retroperitoneal

• sciatic

K45.0 Other specified abdominal hernia with obstruction, without gangrene

Any condition listed under K45:

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

K45.1 Other specified abdominal hernia with gangrene

Any condition listed under K45 specified as gangrenous

K45.8 Other specified abdominal hernia without obstruction or gangrene

 

  K46 Unspecified abdominal hernia

Incl.: enterocele

epiplocele hernia:

• NOS

• interstitial

• intestinal

• intra-abdominal

Excl.: vaginal enterocele (N81.5)

K46.0 Unspecified abdominal hernia with obstruction, without gangrene

Any condition listed under K46:

• causing obstruction

• incarcerated

• irreducible

• strangulated

without gangrene

K46.1 Unspecified abdominal hernia with gangrene

Any condition listed under K46 specified as gangrenous

K46.9 Unspecified abdominal hernia without obstruction or gangrene

Abdominal hernia NOS

Noninfective enteritis and colitis (K50–K52)

Incl.: noninfective inflammatory bowel disease

Excl.: irritable bowel syndrome (K58.-) megacolon (K59.3)

  K50 Crohn disease [regional enteritis]

Incl.: granulomatous enteritis

Excl.: ulcerative colitis (K51.-)

K50.0 Crohn disease of small intestine

Crohn disease [regional enteritis] of:

• duodenum

• ileum

• jejunum Ileitis:

• regional

• terminal

Excl.: with Crohn disease of large intestine (K50.8)

 

K50.1 Crohn disease of large intestine

Colitis:

• granulomatous

• regional

Crohn disease [regional enteritis] of:

• colon

• large bowel

• rectum

Excl.: with Crohn disease of small intestine (K50.8)

K50.8 Other Crohn disease

Crohn disease of both small and large intestine

K50.9 Crohn disease, unspecified

Regional enteritis NOS

  K51 Ulcerative colitis

K51.0 Ulcerative (chronic) pancolitis

backwash ileitis

K51.2 Ulcerative (chronic) proctitis

K51.3 Ulcerative (chronic) rectosigmoiditis K51.4 Inflammatory polyps

K51.5 Left-sided colitis

left hemicolitis

K51.8 Other ulcerative colitis

K51.9 Ulcerative colitis, unspecified

  K52 Other noninfective gastroenteritis and colitis

K52.0 Gastroenteritis and colitis due to radiation K52.1 Toxic gastroenteritis and colitis

Drug-induced gastroenteritis and colitis

Use additional external cause code (Chapter XX), if desired, to identify drug, if drug-induced, or toxic agent.

K52.2 Allergic and dietetic gastroenteritis and colitis

Food hypersensitivity gastroenteritis or colitis

K52.3 Indeterminate colitis

K52.8 Other specified noninfective gastroenteritis and colitis

Collagenous colitis

Eosinophilic gastritis or gastroenteritis Lymphocytic colitis

Microscopic colitis (collagenous colitis or lymphocytic colitis)

 

K52.9 Noninfective gastroenteritis and colitis, unspecified

Diarrhoea Enteritis Ileitis Jejunitis Sigmoiditis

specified as noninfectious

Excl.: colitis, diarrhoea, enteritis, gastroenteritis:

• infectious (A09.0)

• unspecified origin (A09.9) functional diarrhoea (K59.1)

neonatal diarrhoea (noninfective) (P78.3) psychogenic diarrhoea (F45.3)

Other diseases of intestines (K55–K64)

  K55 Vascular disorders of intestine

Excl.: necrotizing enterocolitis of fetus or newborn (P77)

K55.0 Acute vascular disorders of intestine

Acute:

• fulminant ischaemic colitis

• intestinal infarction

• small intestine ischaemia Mesenteric (artery)(vein):

• embolism

• infarction

• thrombosis

Subacute ischaemic colitis

K55.1 Chronic vascular disorders of intestine

Chronic ischaemic:

• colitis

• enteritis

• enterocolitis

Ischaemic stricture of intestine Mesenteric:

• atherosclerosis

• vascular insufficiency

K55.2 Angiodysplasia of colon

K55.8 Other vascular disorders of intestine

 

K55.9 Vascular disorder of intestine, unspecified

Ischaemic:

• colitis

• enteritis

• enterocolitis

NOS

  K56 Paralytic ileus and intestinal obstruction without hernia

Excl.: congenital stricture or stenosis of intestine (Q41–Q42) ischaemic stricture of intestine (K55.1)

meconium ileus (E84.1) obstruction of duodenum (K31.5)

postoperative intestinal obstruction (K91.3) stenosis of anus or rectum (K62.4)

with hernia (K40–K46)

K56.0 Paralytic ileus

Paralysis of:

• bowel

• colon

• intestine

Excl.: gallstone ileus (K56.3) ileus NOS (K56.7)

obstructive ileus NOS (K56.6)

K56.1 Intussusception

Intussusception or invagination of:

• bowel

• colon

• intestine

• rectum

Excl.: intussusception of appendix (K38.8)

K56.2 Volvulus

Strangulation Torsion Twist

of colon or intestine

K56.3 Gallstone ileus

Obstruction of intestine by gallstone

K56.4 Other impaction of intestine

Enterolith Impaction (of):

• colon

• faecal

K56.5 Intestinal adhesions [bands] with obstruction

Peritoneal adhesions [bands] with intestinal obstruction

 

K56.6 Other and unspecified intestinal obstruction

Enterostenosis Obstructive ileus NOS

Occlusion

Stenosis Stricture

of colon or intestine

Excl.: other and unspecified neonatal intestinal obstruction classifiable to P76.8, P76.9

K56.7 Ileus, unspecified

  K57 Diverticular disease of intestine

Incl.:  diverticulitis

diverticulosis diverticulum

of (small)(large) intestine

Excl.: congenital diverticulum of intestine (Q43.8) diverticulum of appendix (K38.2)

Meckel’s diverticulum (Q43.0)

K57.0 Diverticular disease of small intestine with perforation and abscess

Diverticular disease of small intestine with peritonitis

Excl.: diverticular disease of both small and large intestine with perforation and abscess (K57.4)

K57.1 Diverticular disease of small intestine without perforation or abscess

Diverticular disease of small intestine NOS

Excl.: diverticular disease of both small and large intestine without perforation or abscess (K57.5)

K57.2 Diverticular disease of large intestine with perforation and abscess

Diverticular disease of colon with peritonitis

Excl.: diverticular disease of both small and large intestine with perforation and abscess (K57.4)

K57.3 Diverticular disease of large intestine without perforation or abscess

Diverticular disease of colon NOS

Excl.: diverticular disease of both small and large intestine without perforation or abscess (K57.5)

K57.4 Diverticular disease of both small and large intestine with perforation and abscess

Diverticular disease of both small and large intestine with peritonitis

 

K57.5 Diverticular disease of both small and large intestine without perforation or abscess

Diverticular disease of both small and large intestine NOS

K57.8 Diverticular disease of intestine, part unspecified, with perforation and abscess

Diverticular disease of intestine NOS with peritonitis

K57.9 Diverticular disease of intestine, part unspecified, without perforation or abscess

Diverticular disease of intestine NOS

  K58 Irritable bowel syndrome

Incl.: irritable colon

K58.0 Irritable bowel syndrome with diarrhoea K58.9 Irritable bowel syndrome without diarrhoea

Irritable bowel syndrome NOS

  K59 Other functional intestinal disorders

Excl.: change in bowel habit NOS (R19.4) functional disorders of stomach (K31.-) intestinal malabsorption (K90.-) psychogenic intestinal disorders (F45.3)

K59.0 Constipation

K59.1 Functional diarrhoea

K59.2 Neurogenic bowel, not elsewhere classified K59.3 Megacolon, not elsewhere classified

Dilatation of colon Toxic megacolon

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

Excl.: megacolon (due to) (in):

• Chagas disease (B57.3)

• Clostridium difficile (A04.7)

• congenital (aganglionic) (Q43.1)

• Hirschsprung disease (Q43.1)

K59.4 Anal spasm

Proctalgia fugax

K59.8 Other specified functional intestinal disorders

Atony of colon

K59.9 Functional intestinal disorder, unspecified

  K60        Fissure and fistula of anal and rectal regions

Excl.: with abscess or cellulitis (K61.-)

K60.0         Acute anal fissure K60.1          Chronic anal fissure

K60.2         Anal fissure, unspecified K60.3           Anal fistula

K60.4         Rectal fistula

Fistula of rectum to skin

Excl.: fistula:

•  rectovaginal (N82.3)

•  vesicorectal (N32.1)

K60.5         Anorectal fistula

 

  K61        Abscess of anal and rectal regions

Incl.: abscess cellulitis

of anal and rectal regions with or without fistula

K61.0         Anal abscess

Perianal abscess

Excl.: intrasphincteric abscess (K61.4)

K61.1         Rectal abscess

Perirectal abscess

Excl.: ischiorectal abscess (K61.3)

K61.2         Anorectal abscess K61.3         Ischiorectal abscess

Abscess of ischiorectal fossa

K61.4         Intrasphincteric abscess

 

  K62        Other diseases of anus and rectum

Incl.: anal canal

Excl.: colostomy and enterostomy malfunction (K91.4) faecal incontinence (R15)

haemorrhoids (K64.-) ulcerative proctitis (K51.2)

K62.0         Anal polyp

K62.1         Rectal polyp

Excl.: adenomatous polyp (D12.8)

K62.2         Anal prolapse

Prolapse of anal canal

K62.3         Rectal prolapse

Prolapse of rectal mucosa

K62.4         Stenosis of anus and rectum

Stricture of anus (sphincter)

K62.5         Haemorrhage of anus and rectum

Excl.: neonatal rectal haemorrhage (P54.2)

K62.6         Ulcer of anus and rectum

Ulcer:

•  solitary

•  stercoral

Excl.: fissure and fistula of anus and rectum (K60.-) in ulcerative colitis (K51.-)

K62.7         Radiation proctitis

K62.8         Other specified diseases of anus and rectum

Proctitis NOS

K62.9         Disease of anus and rectum, unspecified

 

  K63        Other diseases of intestine

K63.0         Abscess of intestine

Excl.: abscess of:

•   anal and rectal regions (K61.-)

•   appendix (K35.3)

with diverticular disease (K57.-)

K63.1         Perforation of intestine (nontraumatic)

Excl.: perforation (nontraumatic) of:

•   appendix (K35.2, K35.3)

•   duodenum (K26.-)

with diverticular disease (K57.-)

K63.2         Fistula of intestine

Excl.: fistula (of):

•   anal and rectal regions (K60.-)

•   appendix (K38.3)

•   duodenum (K31.6)

•   intestinal-genital, female (N82.2–N82.4)

•   vesicointestinal (N32.1)

K63.3         Ulcer of intestine

Primary ulcer of small intestine

Excl.: ulcer (of):

•  anus or rectum (K62.6)

•  duodenal (K26.-)

•  gastrointestinal (K28.-)

•  gastrojejunal (K28.-)

•  jejunal (K28.-)

•  peptic, site unspecified (K27.-) ulcerative colitis (K51.-)

K63.4         Enteroptosis

K63.5         Polyp of colon

Excl.: adenomatous polyp of colon (D12.6) polyposis of colon (D12.6)

K63.8         Other specified diseases of intestine K63.9     Disease of intestine, unspecified

K64           Haemorrhoids and perianal venous thrombosis

Incl.: piles

Excl.: complicating:

•  childbirth and the puerperium (O87.2)

•  pregnancy (O22.4)

K64.0         First-degree haemorrhoids

Grade/stage I haemorrhoids

Haemorrhoids (bleeding) without prolapse outside of anal canal

K64.1         Second-degree haemorrhoids

Grade/stage II haemorrhoids

Haemorrhoids (bleeding) that prolapse with straining, but retract spontaneously

K64.2         Third-degree haemorrhoids

Grade/stage III haemorrhoids

Haemorrhoids (bleeding) that prolapse with straining and require manual replacement back inside anal canal

K64.3         Fourth-degree haemorrhoids

Grade/stage IV haemorrhoids

Haemorrhoids (bleeding) with prolapsed tissue that cannot be manually replaced

K64.4         Residual haemorrhoidal skin tags

Skin tags of anus

K64.5         Perianal venous thrombosis

Perianal haematoma

K64.8         Other specified haemorrhoids K64.9     Haemorrhoids, unspecified

Haemorrhoids (bleeding):

•  NOS

•  without mention of degree

 

Diseases of peritoneum (K65–K67)

 

  K65        Peritonitis

Excl.: peritonitis:

•   aseptic (T81.6)

•   benign paroxysmal (E85.0)

•   chemical (T81.6)

•   due to talc or other foreign substance (T81.6)

•   neonatal (P78.0–P78.1)

•   pelvic, female (N73.3–N73.5)

•   periodic familial (E85.0)

•   puerperal (O85)

•   with or following:

–       abortion or ectopic or molar pregnancy (O00–O07, O08.0)

–       appendicitis (K35.-)

–       diverticular disease of intestine (K57.-)

K65.0         Acute peritonitis

Abscess (of):

•  abdominopelvic

•  mesenteric

•  omentum

•  peritoneum

•  retrocaecal

•  retroperitoneal

•  subdiaphragmatic

•  subhepatic

•  subphrenic Peritonitis (acute):

•  generalized

•  pelvic, male

•  subphrenic

•  suppurative

Use additional code (B95–B98), if desired, to identify infectious agent.

K65.8         Other peritonitis

Chronic proliferative peritonitis Mesenteric:

•   fat necrosis

•   saponification Peritonitis due to:

•   bile

•   urine

K65.9         Peritonitis, unspecified

 

  K66        Other disorders of peritoneum

Excl.: ascites (R18)

K66.0         Peritoneal adhesions

Adhesions (of):

•   abdominal (wall)

•   diaphragm

•   intestine

•   male pelvis

•   mesenteric

•   omentum

•   stomach Adhesive bands

Excl.: adhesions [bands] (of):

•  female pelvis (N73.6)

•  with intestinal obstruction (K56.5)

K66.1         Haemoperitoneum

Excl.: traumatic haemoperitoneum (S36.8) K66.8      Other specified disorders of peritoneum K66.9     Disorder of peritoneum, unspecified

  K67*       Disorders of peritoneum in infectious diseases classified elsewhere

K67.0*       Chlamydial peritonitis (A74.8†) K67.1* Gonococcal peritonitis (A54.8†) K67.2*            Syphilitic peritonitis (A52.7†) K67.3*                 Tuberculous peritonitis (A18.3†)

K67.8*       Other disorders of peritoneum in infectious diseases classified elsewhere

Diseases of liver (K70–K77)

Excl.:           haemochromatosis (E83.1)

jaundice NOS (R17) Reye syndrome (G93.7) viral hepatitis (B15–B19) Wilson disease (E83.0)

 

  K70        Alcoholic liver disease K70.0 Alcoholic fatty liver K70.1         Alcoholic hepatitis

K70.2         Alcoholic fibrosis and sclerosis of liver

K70.3         Alcoholic cirrhosis of liver

Alcoholic cirrhosis NOS

K70.4         Alcoholic hepatic failure

Alcoholic hepatic failure:

•  NOS

•  acute

•  chronic

•  subacute

•  with or without hepatic coma

K70.9         Alcoholic liver disease, unspecified

 

  K71        Toxic liver disease

Incl.: drug-induced:

•   idiosyncratic (unpredictable) liver disease

•   toxic (predictable) liver disease

Use additional external cause code (Chapter XX), if desired, to identify toxic agent.

Excl.: alcoholic liver disease (K70.-) Budd–Chiari syndrome (I82.0)

K71.0         Toxic liver disease with cholestasis

Cholestasis with hepatocyte injury ‘Pure’ cholestasis

K71.1         Toxic liver disease with hepatic necrosis

Hepatic failure (acute)(chronic) due to drugs

K71.2         Toxic liver disease with acute hepatitis

K71.3         Toxic liver disease with chronic persistent hepatitis K71.4       Toxic liver disease with chronic lobular hepatitis

K71.5         Toxic liver disease with chronic active hepatitis

Toxic liver disease with lupoid hepatitis

K71.6         Toxic liver disease with hepatitis, not elsewhere classified K71.7       Toxic liver disease with fibrosis and cirrhosis of liver K71.8 Toxic liver disease with other disorders of liver

Toxic liver disease with:

•   focal nodular hyperplasia

•   hepatic granulomas

•   peliosis hepatis

•   veno-occlusive disease of liver

K71.9         Toxic liver disease, unspecified

 

  K72        Hepatic failure, not elsewhere classified

Incl.: hepatic:

•  coma NOS

• 

•   fulminant •   malignant NEC, with hepatic failure

encephalopathy NOS hepatitis:

 

 

liver (cell) necrosis with hepatic failure yellow liver atrophy or dystrophy

Excl.: alcoholic hepatic failure (K70.4) hepatic failure complicating:

•  abortion or ectopic or molar pregnancy (O00–O07, O08.8)

•  pregnancy, childbirth and the puerperium (O26.6) icterus of fetus and newborn (P55–P59)

viral hepatitis (B15–B19)

with toxic liver disease (K71.1)

K72.0         Acute and subacute hepatic failure

Acute non-viral hepatitis NOS K72.1          Chronic hepatic failure K72.9          Hepatic failure, unspecified

  K73        Chronic hepatitis, not elsewhere classified

Excl.: hepatitis (chronic):

•  alcoholic (K70.1)

•  drug-induced (K71.-)

•  granulomatous NEC (K75.3)

•  reactive, nonspecific (K75.2)

•  viral (B15–B19)

K73.0         Chronic persistent hepatitis, not elsewhere classified K73.1    Chronic lobular hepatitis, not elsewhere classified K73.2   Chronic active hepatitis, not elsewhere classified K73.8      Other chronic hepatitis, not elsewhere classified K73.9          Chronic hepatitis, unspecified

  K74        Fibrosis and cirrhosis of liver

Excl.: alcoholic fibrosis of liver (K70.2) cardiac sclerosis of liver (K76.1) cirrhosis (of liver):

•  alcoholic (K70.3)

•  congenital (P78.8)

with toxic liver disease (K71.7)

K74.0         Hepatic fibrosis K74.1   Hepatic sclerosis

K74.2         Hepatic fibrosis with hepatic sclerosis

K74.3         Primary biliary cirrhosis

Chronic nonsuppurative destructive cholangitis

K74.4         Secondary biliary cirrhosis K74.5          Biliary cirrhosis, unspecified

K74.6         Other and unspecified cirrhosis of liver

Cirrhosis (of liver):

•   NOS

•   cryptogenic

•   macronodular

•   micronodular

•   mixed type

•   portal

•   postnecrotic

 

  K75        Other inflammatory liver diseases

Excl.: chronic hepatitis NEC (K73.-) hepatitis:

•  acute or subacute:

– NOS (B17.9)

– non-viral (K72.0)

•  viral (B15–B19)

toxic liver disease (K71.-)

K75.0         Abscess of liver

Hepatic abscess:

•   NOS

•   cholangitic

•   haematogenic

•   lymphogenic

•   pylephlebitic

Excl.: amoebic liver abscess ( A06.4†,, K77.0*) cholangitis without liver abscess (K83.0) pylephlebitis without liver abscess (K75.1)

K75.1         Phlebitis of portal vein

Pylephlebitis

Excl.: pylephlebitic liver abscess (K75.0)

K75.2         Nonspecific reactive hepatitis

K75.3         Granulomatous hepatitis, not elsewhere classified K75.4       Autoimmune hepatitis

Lupoid hepatitis NEC

K75.8         Other specified inflammatory liver diseases

Nonalcoholic steatohepatitis [NASH]

K75.9         Inflammatory liver disease, unspecified

Hepatitis NOS

 

  K76        Other diseases of liver

Excl.: alcoholic liver disease (K70.-) amyloid degeneration of liver (E85.-)

cystic disease of liver (congenital) (Q44.6) hepatic vein thrombosis (I82.0) hepatomegaly NOS (R16.0)

portal vein thrombosis (I81) toxic liver disease (K71.-)

K76.0         Fatty (change of) liver, not elsewhere classified

Nonalcoholic fatty liver disease [NAFLD]

Excl.: nonalcoholic steatohepatitis (K75.8)

K76.1         Chronic passive congestion of liver

Cardiac: •   cirrhosis (so-called) •   sclerosis

of liver

K76.2         Central haemorrhagic necrosis of liver

Excl.: liver necrosis with hepatic failure (K72.-)

K76.3         Infarction of liver K76.4            Peliosis hepatis

Hepatic angiomatosis

K76.5         Hepatic veno-occlusive disease

Excl.: Budd–Chiari syndrome (I82.0)

K76.6         Portal hypertension K76.7         Hepatorenal syndrome

Excl.: following labour and delivery (O90.4)

K76.8         Other specified diseases of liver

Simple cyst of liver

Focal nodular hyperplasia of liver Hepatoptosis

K76.9         Liver disease, unspecified

 

  K77*       Liver disorders in diseases classified elsewhere

K77.0*       Liver disorders in infectious and parasitic diseases classified elsewhere

Amoebic liver abscess (A06.4†) Hepatitis:

•  cytomegaloviral (B25.1†)

•  herpesviral [herpes simplex] (B00.8†)

•  toxoplasma (B58.1†)

Hepatosplenic schistosomiasis (B65.-†)

Portal hypertension in schistosomiasis (B65.-†) Syphilitic liver disease (A52.7†)

K77.8*       Liver disorders in other diseases classified elsewhere

Hepatic granulomas in:

•  berylliosis (J63.2†)

•  sarcoidosis (D86.8†)

 

Disorders of gallbladder, biliary tract and pancreas (K80–K87)

 

  K80        Cholelithiasis

K80.0         Calculus of gallbladder with acute cholecystitis

Any condition listed in K80.2 with acute cholecystitis

K80.1         Calculus of gallbladder with other cholecystitis Any condition listed in K80.2 with cholecystitis (chronic) Cholecystitis with cholelithiasis NOS

K80.2         Calculus of gallbladder without cholecystitis

Cholecystolithiasis Cholelithiasis Colic (recurrent) of gallbladder Gallstone (impacted) of: •   cystic duct •   gallbladder

unspecified or without cholecystitis

K80.3         Calculus of bile duct with cholangitis

Any condition listed in K80.5 with cholangitis

K80.4         Calculus of bile duct with cholecystitis

Any condition listed in K80.5 with cholecystitis (with cholangitis)

K80.5         Calculus of bile duct without cholangitis or cholecystitis

Choledocholithiasis Gallstone (impacted) of: •   bile duct NOS •   common duct •   hepatic duct Hepatic: •   cholelithiasis •   colic (recurrent)

unspecified or without cholangitis or cholecystitis

K80.8         Other cholelithiasis

 

  K81        Cholecystitis

Excl.: with cholelithiasis (K80.-)

K81.0         Acute cholecystitis

Abscess of gallbladder Angiocholecystitis Cholecystitis: •   emphysematous (acute) •   gangrenous •   suppurative Empyema of gallbladder Gangrene of gallbladder

without calculus

K81.1         Chronic cholecystitis K81.8     Other cholecystitis

K81.9         Cholecystitis, unspecified

 

  K82        Other diseases of gallbladder

Excl.: nonvisualization of gallbladder (R93.2) postcholecystectomy syndrome (K91.5)

K82.0         Obstruction of gallbladder

Occlusion Stenosis Stricture

of cystic duct or gallbladder without calculus

Excl.: with cholelithiasis (K80.-)

K82.1         Hydrops of gallbladder

Mucocele of gallbladder

K82.2         Perforation of gallbladder

Rupture of cystic duct or gallbladder

K82.3         Fistula of gallbladder

Cholecystocolic Cholecystoduodenal

fistula

K82.4         Cholesterolosis of gallbladder

Strawberry gallbladder

K82.8         Other specified diseases of gallbladder

Adhesions Atrophy Cyst Dyskinesia Hypertrophy Nonfunctioning Ulcer

of cystic duct or gallbladder

K82.9         Disease of gallbladder, unspecified

 

  K83        Other diseases of biliary tract

Excl.: the listed conditions involving the:

•   cystic duct (K81–K82)

•   gallbladder (K81–K82) postcholecystectomy syndrome (K91.5)

K83.0         Cholangitis

Cholangitis:

•  NOS

•  ascending

•  primary

•  recurrent

•  sclerosing

•  secondary

•  stenosing

•  suppurative

Excl.: cholangitic liver abscess (K75.0)

cholangitis with choledocholithiasis (K80.3–K80.4) chronic nonsuppurative destructive cholangitis (K74.3)

K83.1         Obstruction of bile duct

Occlusion Stenosis Stricture

of bile duct without calculus

Excl.: with cholelithiasis (K80.-)

K83.2         Perforation of bile duct

Rupture of bile duct

K83.3         Fistula of bile duct

Choledochoduodenal fistula K83.4 Spasm of sphincter of Oddi K83.5            Biliary cyst

K83.8         Other specified diseases of biliary tract

Adhesions Atrophy Hypertrophy Ulcer

of bile duct

K83.9         Disease of biliary tract, unspecified

 

  K85        Acute pancreatitis

Incl.: abscess of pancreas necrosis of pancreas:

•  acute

•  infective pancreatitis:

•  NOS

•  acute (recurrent)

•  haemorrhagic

•  subacute

•  suppurative

K85.0         Idiopathic acute pancreatitis K85.1      Biliary acute pancreatitis

Gallstone pancreatitis

K85.2         Alcohol-induced acute pancreatitis K85.3       Drug-induced acute pancreatitis

Use additional external cause code (Chapter XX), if desired, to identify drug

K85.8         Other acute pancreatitis

K85.9         Acute pancreatitis, unspecified

  K86        Other diseases of pancreas

Excl.: fibrocystic disease of pancreas (E84.-) islet cell tumour (of pancreas) (D13.7) pancreatic steatorrhoea (K90.3)

K86.0         Alcohol-induced chronic pancreatitis K86.1      Other chronic pancreatitis

Chronic pancreatitis:

•  NOS

•  infectious

•  recurrent

•  relapsing

K86.2         Cyst of pancreas

K86.3         Pseudocyst of pancreas

K86.8         Other specified diseases of pancreas

Atrophy Calculus Cirrhosis Fibrosis

of pancreas

Pancreatic:

•  infantilism

•  necrosis:

–    NOS

–    aseptic

–    fat

K86.9         Disease of pancreas, unspecified

 

  K87*       Disorders of gallbladder, biliary tract and pancreas in diseases classified elsewhere

K87.0*       Disorders of gallbladder and biliary tract in diseases classified elsewhere

K87.1*       Disorders of pancreas in diseases classified elsewhere

Cytomegaloviral pancreatitis (B25.2†) Mumps pancreatitis (B26.3†)

Other diseases of the digestive system (K90–K93)

 

  K90        Intestinal malabsorption

Excl.: following gastrointestinal surgery (K91.2)

K90.0         Coeliac disease

Gluten-sensitive enteropathy Idiopathic steatorrhoea Nontropical sprue

K90.1         Tropical sprue

Sprue NOS

Tropical steatorrhoea

K90.2         Blind loop syndrome, not elsewhere classified

Blind loop syndrome NOS

Excl.: blind loop syndrome:

•  congenital (Q43.8)

•  postsurgical (K91.2)

K90.3         Pancreatic steatorrhoea

K90.4         Malabsorption due to intolerance, not elsewhere classified

Malabsorption due to intolerance to:

•   carbohydrate

•   fat

•   protein

•   starch

Excl.: gluten-sensitive enteropathy (K90.0) lactose intolerance (E73.-)

K90.8         Other intestinal malabsorption

Whipple disease† (M14.8*)

K90.9         Intestinal malabsorption, unspecified

 

  K91        Postprocedural disorders of digestive system, not elsewhere classified

Excl.: gastrojejunal ulcer (K28.-) radiation:

•  colitis (K52.0)

•  gastroenteritis (K52.0)

•  proctitis (K62.7)

K91.0         Vomiting following gastrointestinal surgery

K91.1         Postgastric surgery syndromes

Syndrome:

•  dumping

•  postgastrectomy

•  postvagotomy

K91.2         Postsurgical malabsorption, not elsewhere classified

Postsurgical blind loop syndrome

Excl.: malabsorption:

•   osteomalacia in adults (M83.2)

•   osteoporosis, postsurgical (M81.3) K91.3      Postoperative intestinal obstruction K91.4            Colostomy and enterostomy malfunction K91.5         Postcholecystectomy syndrome

K91.8         Other postprocedural disorders of digestive system, not elsewhere classified

K91.9         Postprocedural disorder of digestive system, unspecified

 

  K92        Other diseases of digestive system

Excl.: neonatal gastrointestinal haemorrhage (P54.0–P54.3)

K92.0         Haematemesis

K92.1         Melaena

Excl.: occult blood in faeces (R19.5)

K92.2         Gastrointestinal haemorrhage, unspecified

Haemorrhage:

•  gastric NOS

•  intestinal NOS

Excl.: acute haemorrhagic gastritis (K29.0) haemorrhage of anus and rectum (K62.5) with peptic ulcer (K25–K28)

K92.8         Other specified diseases of digestive system K92.9     Disease of digestive system, unspecified

  K93*       Disorders of other digestive organs in diseases classified elsewhere

K93.0*       Tuberculous disorders of intestines, peritoneum and mesenteric glands (A18.3†)

Excl.: tuberculous peritonitis (K67.3*)

K93.1*       Megacolon in Chagas disease (B57.3†)

K93.8*       Disorders of other specified digestive organs in diseases classified elsewhere

Hajriah Fajar Hajriah Fajar (lahir pada bulan Desember 1987) adalah seorang seniman, penulis, dan kreator konten asal Indonesia. Ia lahir dan dibesarkan di sebuah kampung di Kabupaten Bogor. Sebelum terjun ke dunia seni dan tulis-menulis, Fajar pernah bekerja sebagai tukang parkir profesional di beberapa tempat, antara lain Gedung Hijau Arkadia, Plaza Senayan, dan Kafe Lacodefin Kemang. Setelah lulus dari Sekolah Menengah Atas, Fajar melanjutkan pendidikannya di Universitas Nusamandiri, di mana ia memperoleh gelar S1 Komputer Program Dual Degree pada tahun 2019. Setelah lulus, ia bekerja di berbagai perusahaan teknologi dan IT, dan saat ini bekerja di salah satu rumah sakit swasta di Jakarta sebagai IT. Selain bekerja di dunia IT, Fajar juga aktif di media sosial seperti Instagram, Twitter, dan Facebook, di mana ia sering membagikan pemikiran, karya seni, serta konten-konten menarik lainnya. Ia juga menulis di blog pribadinya di hajriahfajar.com dan membuat konten video di kanal YouTube bernama Hajriah Fajar.Fajar diakui sebagai salah satu sosok yang inspiratif dan memotivasi banyak orang untuk berkreasi dan berinovasi dalam bidang seni dan teknologi.

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